| UI | uroporphyrin isomerase |
|---|---|
| UP | parallax unsharpness; ulcerative proctitis; ultrahigh purity; unipolar; upright posture; ureteropelv... |
| URO | urology; uroporphyrin; uroporphyrinogen; utilization review organization |
| UUP | urinary uroporphyrin |
| URO | Uroporphyrin |
|---|---|
| UP | uroporphyrin |
| uroporphyrin | <protein> Porphyrins are pigments found in both animal and plant life. This test is useful in evaluating any number of porphyrin disorders (involving the various porphyrins) of red blood cells. Increased levels of coproporphyrins can indicate congenital erythropoietic porphyria or sideroblastic anaemia. Increased protoporphyrins may be seen in infection, thalassaemia, sideroblastic anaemia, iron deficient anaemia, increased erythropoiesis and lead poisoning. Increased uroporphyrins may indicate congenital erythropoietic porphyria or erythropoietic protoporphyria. (27 Sep 1997) |
|---|---|
| uroporphyrin-III C-methyltransferase | <enzyme> From pseudomonas denitrificans; enzyme of the cobalamin biosynthetic pathway which catalyses the c methylation of uroporphyrinogen III; also catalyses both nad+ dependent oxidation of precorrin-2 to sirohydrochlorin and insertion of iron into it to produce siroheme; cysg gene is from E coli; product of coba gene of pseudomonas; do not confuse with coba gene product of salmonella typhimurium which yields ATP-corrinoid adenosyltransferase Registry number: EC 2.1.1.107 Synonym: uroiii methyltransferase, uroporphyrinogen III methylase, sumt methyltransferase, s-adenosylmethionine-uroporphyrinogen III methyltransferase, cysg gene product, siroheme synthase, coba gene product, propionibacterium (26 Jun 1999) |
| uroporphyrinogen | See: porphyrinogens. Uroporphyrinogen decarboxylase, an enzyme that participates in haem biosynthesis; it catalyses the decarboxylation of uroporphyrinogen III to produce coproporphyrinogen III; it also acts on uroporphyrinogen I; a deficiency of this enzyme will result in either porphyria cutanea tarda or hepatoerythropoietic porphyria. Uroporphyrinogen III cosynthase, an enzyme in haem biosynthesis that participates in the formation of uroporphyrinogen III; a deficiency of this protein results in congenital erythropoietic porphyria. (05 Mar 2000) |
| uroporphyrinogen decarboxylase | <enzyme> One of the enzymes active in haem biosynthesis. It catalyses the decarboxylation of uroporphyrinogen III to coproporphyrinogen III by the conversion of four acetic acid groups to four methyl groups. Chemical name: Uroporphyrinogen-III carboxy-lyase Registry number: EC 4.1.1.37 (12 Dec 1998) |
| uroporphyrinogen I synthetase | <enzyme> An enzyme of haem biosynthesis that is defective in the inherited (autosomal dominant) disease, acute intermittent porphyria. UP I is isomerised to UP III by UP III synthetase, defective in the autosomal recessive disease, congenital erythropoietic porphyria. (18 Nov 1997) |
| uroporphyrinogen-III synthase | <enzyme> An enzyme that catalyses the cyclization of hydroxymethylbilane to yield uroporphyrinogen III and water. Chemical name: Hydroxymethylbilane hydro-lyase (cyclizing) Registry number: EC 4.2.1.75 (12 Dec 1998) |
| uroporphyrinogens | Porphyrinogens which are intermediates in haem biosynthesis. They have four acetic acid and four propionic acid side chains attached to the pyrrole rings. Uroporphyrinogen I and III are formed from polypyrryl methane in the presence of uroporphyrinogen III cosynthetase and uroporphyrin I synthetase, respectively. They can yield uroporphyrins by autooxidation or coproporphyrinogens by decarboxylation. (12 Dec 1998) |
| uroporphyrins | Porphyrins with four acetic acid and four propionic acid side chains attached to the pyrrole rings. (12 Dec 1998) |
Synonyms : Uroporphyrinogen III Decarboxylase, Carboxy-Lyase, Uroporphyrinogen, Decarboxylase, Uroporphyrinogen, Decarboxylase, Uroporphyrinogen III, Uroporphyrinogen Carboxy Lyase
Synonyms : Cosynthetase, Uroporphyrinogen III, Isomerase, Uroporphyrinogen, Synthase, Uroporphyrinogen-III, Synthetase, Uroporphyrinogen III, Uroporphyrinogen III Synthase
Synonyms : Uroporphyrinogen III
Synonyms :
| uroporphyrin |
the porphyrin (q.v.) produced by oxidation of the methylene bridges in uroporphyrinogen. Excessive amounts of uroporphyrin I are excreted in congenital erythropoietic porphyria, and both types I and III are excreted in porphyria cutanea tarda. See uroporphyrinogen.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|---|
| uroporphyrinogen |
a porphyrinogen (q.v.) in which each pyrrole ring has one acetate side chain and one propionate side chain; it is formed by condensation of four molecules of porphobilinogen. Four isomers are possible but only two exist naturally, types I and III; the latter is a functional intermediate in heme biosynthesis while the former is produced in an abortive side reaction.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| uroporphyrinogen decarboxylase |
[EC 4.1.1.37] an enzyme of the lyase class that catalyzes the decarboxylation of uroporphyrinogen III to coproporphyrinogen III in the biosynthesis of heme. Decreased enzyme activity is associated with porphyria cutanea tarda and the variant hepatoerythropoietic porphyria.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| uroporphyrinogen I synthase |
hydroxymethylbilane synthase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| uroporphyrinogen III cosynthase |
uroporphyrinogen-III synthase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|