| urocanase | <enzyme> An enzyme that catalyses the conversion of 4,5-dihydro-4-oxo-5-imidazolepropanoate to urocanate and water. Chemical name: 4,5-Dihydro-4-oxo-5-imidazolepropanoate hydro-lyase Registry number: EC 4.2.1.49 (12 Dec 1998) |
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| urocanase |
urocanate hydratase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| urocanase deficiency |
an inherited disorder of histidine catabolism caused by deficiency of urocanate hydratase; it is characterized by excess urinary excretion of urocanic acid and growth retardation and may also be associated with mental retardation.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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