| 영문 | glycogen | 한글 | 글리코겐, 당원 |
|---|---|---|---|
| 설명 | 동물에서 탄수화물의 저장형태로 주로 간에 대부분이 저장되어 있고 근육에 조금 있다. 포도당으로 분해되어 이용된다. |
||
| 영문 | connective tissue | 한글 | 결합조직 |
|---|---|---|---|
| 설명 | 체내에 널리 분포하며, 장기, 조직사이를 메우고 그것을 기계적으로 지지, 조직이다. 그밖에 혈관, 림프관, 신경을 인도하며 영양, 대사산물의 수송 또는 저류, 나아가서는 손상, 감염에 대한 방어 또는 수복 등에도 작용한다. 결합조직은 세포간질이 풍부하며, 세포간질을 구성하는 기질과 섬유의 성상에 따라 간엽조직, 섬유성 결합조직(성긴섬유성 결합조직, 촘촘한 섬유성 결합조직), 지방조직, 탄성조직, 세망 조직 등으로 분류된다. |
||
| 영문 | osseous tissue | 한글 | 뼈조직, 골조직 |
|---|---|---|---|
| 설명 | 골세포와 골세포주위의 딱딱한 칼슘조직으로 둘러싸인 밀집된 결합조직을 뜻한다. 이 골조직에 의해서 뼈가 이루어져 인체의 골격을 형성한다. |
||
| 영문 | epithelial tissue | 한글 | 상피조직 |
|---|---|---|---|
| 설명 | 상피는 한 층 또는 여러 층의 세포로 이루어진 판 모양의 구조로 신체의 표면과 관상구조의 내강을 둘러싸고 있다. 상피세포와 상피세포사이의 적은 양으로 존재하여 상피사이의 공간을 채우고 있는 세포간질을 합쳐 상피조직이라 한다. 상피조직에는 원칙적으로 혈관이 분포되어 있지 않다. |
||
| 영문 | granulation tissue | 한글 | 육아조직 |
|---|---|---|---|
| 설명 | 모세혈관이 풍부하며 왕성하게 증식을 계속하는 어린 결합조직. 창상 등 조직 결손에 대한 수복, 이물처리의 기질화, 염증이 만성적인 경과에 있거나 종양증식에 동반된 사이물질의 반응성 염증에서 관찰된다. 구성성분은 생긴지 얼마 안되는 어린 육아조직은 섬유모세포의 증식, 새로 생긴 모세혈관과 여러 유주세포 및 다른 중간엽세포(백혈구, 림프구, 형질세포, 조직구, 단핵구, 거대세포)등으로 구성된다. 이것이 시간이 지나 그리되면, 모세혈관과 유주세로, 다른조직성분을 감소시켜 만성화하여 오래된 육아가 되며 결국은 섬유세포와 아교질섬유로 구성된 반흔조직으로 변한다. |
||
| GFFS | glycogen and fat-free solid |
|---|---|
| GSD | genetically significant dose; Gerstmann-Straussler disease; glutathione synthetase deficiency; glyco... |
| GSD-0 | glycogen storage disease-zero |
| GT1-GT10 | glycogen storage disease, types 1 to 10 |
| MLG | mesiolingual groove; mitochondrial lipid glycogen |
| GSK-3 beta | I)/glycogen synthase kinase-3 beta |
|---|---|
| Gly | Glycogen |
| GP | Glycogen Phosphorylase |
| GSD | Glycogen Storage Disease |
| GSDII | Glycogen Storage Disease type II |
acute angle
| brancher glycogen storage disease | Type of glycogen storage disease, due to deficiency of amylo-1,4-1,6-transglucosidase (brancher enzyme). Synonym: brancher deficiency glycogenosis, debrancher deficiency. (05 Mar 2000) |
|---|---|
| glycogen | <biochemistry> Branched polymer of D glucose (mostly _(1-4) linked, but some _(1-6) at branch points). Size range very variable, up to 10exp5 glucose units. Major short term storage polymer of animal cells and is particularly abundant in the liver and to a lesser extent in muscle. In the electron microscope glycogen has a characteristic asterisk or star appearance. (18 Nov 1997) |
| glycogen debranching enzyme system | 1,4-alpha-d-glucan-1,4-alpha-d-glucan 4-alpha-d-glucosyltransferase/dextrin 6 alpha-d-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (ec 2.4.1.25) and amylo-1,6-glucosidase (ec 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-d-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-d-glucan. As a glucosidase it catalyses the endohydrolysis of 1,6-alpha-d-glucoside linkages at points of branching in chains of 1,4-linked alpha-d-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III. (12 Dec 1998) |
| glycogen granule | Glycogen occurring in cells as beta granule's which average about 300 A |
| glycogen phosphorylase | <enzyme> Enzyme that catalyses the sequential removal of glycosyl residues from glycogen to yield one glucose-1-phosphate per reaction. Its activity is controlled by phosphorylation (by phosphorylase kinase). (21 Jun 2000) |
| glycogen storage disease | <hepatology> A group of inherited metabolic disorders involving the enzymes responsible for the synthesis and degradation of glycogen. In some patients, prominent liver involvement is presented. In others, more generalised storage of glycogen occurs, sometimes with prominent cardiac involvement. Synonym: glycogenosis (12 Sep 2002) |
| glycogen storage disease type I | <disease> An autosomal recessive disease in which gene expression of glucose-6-phosphatase is absent, resulting in hypoglycaemia due to lack of glucose production. Accumulation of glycogen in liver and kidney leads to organomegaly, particularly massive hepatomegaly. Increased concentrations of lactic acid and hyperlipidemia appear in the plasma. Clinical gout often appears in early childhood. Inheritance: autosomal recessive. (12 Dec 1998) |
| glycogen storage disease type II | <disease> Glycogenosis due to alpha-1,4-glucosidase (acid maltase) deficiency. It affects muscle, heart, and other organs. (12 Dec 1998) |
| glycogen storage disease type III | <disease> An autosomal recessive metabolic disorder due to deficient expression of amylo-1,6-glucosidase (one part of the glycogen debranching enzyme system). The clinical course of the disease is similar to that of glycogen storage disease type I, but milder. Massive hepatomegaly, which is present in young children, diminishes and occasionally disappears with age. Levels of glycogen with short outer branches are elevated in muscle, liver, and erythrocytes. Six subgroups have been identified, with subgroups type IIIa and type IIIb being the most prevalent. Inheritance: autosomal recessive (12 Dec 1998) |
| glycogen storage disease type IV | <disease> An autosomal recessive metabolic disorder due to a deficiency in expression of branching enzyme (alpha-1,4-glucan-6-alpha-glucosyltransferase), resulting in an accumulation of abnormal glycogen with long outer branches. Clinical features are muscle hypotonia and cirrhosis. Death from liver disease usually occurs before age 2. Inheritance: autosomal recessive (12 Dec 1998) |
| glycogen storage disease type V | <disease> Glycogenosis due to muscle phosphorylase deficiency. Characterised by painful cramps following sustained exercise. Inheritance: autosomal recessive (12 Dec 1998) |
| glycogen storage disease type VI | <disease> A hepatic glycogen storage disease in which there is an apparent deficiency of hepatic phosphorylase activity. However, studies have not been able to distinguish between phosphorylase deficiency and phosphorylase kinase deficiency in patients with hepatic glycogenosis. (12 Dec 1998) |
| glycogen storage disease type VII | <disease> An autosomal recessive muscle glycogen storage disease in which there is deficient expression of muscle phosphofructokinase activity, resulting in increased concentrations of glucose-6-phosphate and fructose-6-phosphate and low concentrations of fructose-1,6-diphosphate in muscle tissue. Glycogen storage in muscle is increased, perhaps due to activation of glycogen synthase by accumulated glucose-6-phosphate. It has been proposed that shunting of glucose-6-phosphate and fructose-6-phosphate into the pentose phosphate pathway may result in increased synthesis of purines and pyrimidines, causing hyperuricaemia and gout. Erythrocytes from patients may show decreased phosphofructokinase activity and 2,3-diphosphoglycerate deficiency. Exercise intolerance is present and severe congenital muscular dystrophy has been reported. Inheritance: autosomal recessive (12 Dec 1998) |
| glycogen storage disease type VIII | <disease> An x-linked recessive hepatic glycogen storage disease resulting from lack of expression of phosphorylase-b-kinase activity. Symptoms are relatively mild; hepatomegaly, increased liver glycogen, and decreased leukocyte phosphorylase are present. Liver shrinkage occurs in response to glucagon. Inheritance: X-linked recessive (12 Dec 1998) |
| glycogen synthase | <enzyme> An enzyme of the transferase class that catalyses the reaction of udpglucose and (1,4-alpha-d-glucosyl)n to yield udp and 1,4-alpha-d-glucosyl)n+1. The reaction is highly regulated by allosteric effectors, by phosphorylation reactions, and by insulin. Chemical name: UDPglucose:glycogen 4-alpha-D-glucosyltransferase Registry number: EC 2.4.1.11 (12 Dec 1998) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|