| 영문 | amyloidosis | 한글 | 아밀로이드증 |
|---|---|---|---|
| 설명 | 본래 생체에는 없는 당단백질의 일종으로 비정상적으로 아밀로이드단백이 조직이나 장기에 침착되는 병. 발현부위가 전신성인 경우의 아밀로이드증(전신성 아밀로이드증)에는 명백한 원인없이 일어나는 원발성 아밀로드증과 만성화농성 염증이나 결핵 등 소모성 질환에서 찾아볼 수 있는 속발성 아밀로이드증이 있다. 발현부위가 국소성인 경우의 국소성 아밀로이드증으로서는 뇌의 노인반이 그 예이며, 특히 입안에서는 혀나 잇몸에 대한 침착이 현저하고 여러 가지 기능장애를 나타낸다. 조직학적으로는 헤마톡실린 에오진염색에서는 에오진성 무구조인 유리화를 나타내며 콩고레드, 편광상(녹색) 등으로 확인한다. 구조적으로는 아밀로이드 섬유의 집합으로 이루어지는 여러 가지 아밀로이드 침착이 있으며 그것들에 대한 병형이 분류되어 있다. 가족형, 다발성 골수종과 수반하는 형 그리고 가족성 지중해열을 수반하는 형 등이 있다. |
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| 영문 | systemic lupus erythematosus | 한글 | 전신홍반루푸스 |
|---|---|---|---|
| 설명 | 전신 자가면역병의 대표적 병이다. 여성에게 압도적으로 많고, 10~39세까지가 70%를 차지한다. 원인은 잘 모르나 자가면역 조절기능에 장애가 있는 것으로 생각된다. 유전요인, 호르몬의 영향, 환경요소가 종합적으로 보조 T세포와 B세포를 활성화시켜서 여러 가지 자가항체들, 즉 천연 DNA, 이중가닥 DNA, 외가닥 DNA, RNA, 핵단백질 등과 같은 핵 항원에 대한 항체, 비핵항원에 대한 여러 가지 항체가 쏟아져 나온다. 이 중 이중가닥 DNA를 포함한 순환면역복합체가 콩팥에 침착하여 손상을 일으키는데 관여한다. DNA와 여러 가지 세포성분에 대한 자가면역질환으로 전콩팥기를 침범하여 염증을 일으킨다. 여러 자가항원에 대한 면역반응에 의한 항체의존성 면역반응과 면역복합체 반응으로 토리콩팥염, 혈관염, 관절염 및 빈혈을 동반한다. |
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| 영문 | systemic circulation | 한글 | 체순환 |
|---|---|---|---|
| 설명 | 왼심실에서 신체를 돌아 오른심방까지의 순환을 의미하며, 왼심실 → 대동맥 → 동맥 → 모세혈관 → 정맥 → 대정맥 → 오른심방의 회로를 순환한다. |
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| AL | absolute latency; acinar lumen; acute leukemia; adaptation level; albumin; alcoholism [and other dru... |
|---|---|
| DAA | decompensated autonomous adenoma; dementia associated with alcoholism; dialysis-associated amyloidos... |
| HCHWA | hereditary cerebral hemorrhage with amyloidosis |
| PSS | painful shoulder syndrome; physiologic saline solution; porcine stress syndrome; primary Sjogren syn... |
| SMCD | senile macular choroidal degeneration; systemic mast cell disease; systemic meningococcal disease |
| AL | Amyloidosis |
|---|---|
| DRA | Dialysis related amyloidosis |
| FAF | Familial amyloidosis, Finnish type |
| HCHWA-D | Hereditary cerebral haemorrhage with amyloidosis, Dutch type |
| MAP | Mean systemic arterial pressure |
| amyloidosis | Deposition of amyloid. A common complication of several diseases (leprosy, tuberculosis), often associated with perturbation of the immune system, although there may be immunosuppression or enhancement. (18 Nov 1997) |
|---|---|
| amyloidosis: bone manifestations | <radiology> Joint pain without radiographic findings, osteoporosis, especially in axial skeleton, lytic lesions that destroy cortex and invade soft tissue, wrist, scaphoid and lunate lesions that may extend into the carpal tunnel, inducing the classic complaints of carpal tunnel syndrome amyloid arthropathy Differential diagnosis: pigmented villonodular synovitis, synovial chondromatosis, rheumatoid arthritis, TB (12 Dec 1998) |
| amyloidosis cutis | Localised cutaneous amyloidosis with pruritic brownish-red papules, most commonly on the lower legs, due to amyloid infiltration of the papillary dermis. Synonym: amyloidosis cutis, lichen amyloidosis. Origin: G. Leichen, lichen, a lichen-like eruption + eidos, resemblance (05 Mar 2000) |
| amyloidosis: gastrointestinal manifestations | <radiology> Oesophagus, loss of peristalsis, megaesophagus, stomach, small and rigid (simulate linitis plastica), effaced rugal pattern, diminished/absent peristalsis, may be localised to antrum, amyloidoma: well defined submucosal mass, small bowel, diffuse form (more common), diffuse, uniform thickening of valvulae conniventes, broadened flat undulated mucosal folds (mucosal atrophy), jejunalization of ileum, impaired motility, small bowel dilatation, localised form: multiple small deposits; associated with pseudoobstruction, colon, psudopolyps (12 Dec 1998) |
| amyloidosis of multiple myeloma | Foci of amyloidosis in mesenchymal tissues of some persons with multiple myeloma; no direct relation between amyloid and Bence Jones protein is conclusively known. (05 Mar 2000) |
| macular amyloidosis | A localised form of amyloidosis cutis characterised by pruritic symmetrical brown reticulated macules, especially on the upper back; microscopically, amyloid is deposited as small subepidermal globules. (05 Mar 2000) |
| renal amyloidosis | Renal deposits of amyloid, especially in glomerular capillary walls, which may cause albuminuria and the nephrotic syndrome. Synonym: amyloid nephrosis. (05 Mar 2000) |
| cerebral amyloidosis | A condition where there is a deposition of amyloid (insoluble protein) in the walls of the arteries which supply the brain. This results in an increased risk of dementia and-or intracerebral haemorrhage. Cerebral amyloidosis or cerebral amyloid angiopathy, is a complication of primary amyloidosis. (27 Sep 1997) |
| primary amyloidosis | <immunology, nephrology> A disease which is characterised by the deposition of the fibrous protein amyloid in one or more locations within the body. Amyloid deposition may occur in the kidney, brain, liver, heart, skin and lungs. A recognised complication is a restrictive cardiomyopathy. (05 Mar 1998) |
| hereditary amyloidosis | <neurology> A disorder in which various peripheral nerves are infiltrated with amyloid and their functions disturbed, an abnormal prealbumin is also formed and is present in the blood; characteristically, it begins during mid-life and is found largely in persons of Portuguese descent. Other rare clinical types occur. Inheritance: autosomal dominant. Synonym: familial amyloidosis, hereditary amyloidosis. (05 Mar 2000) |
| secondary amyloidosis | Amyloidosis occurring in association with another chronic inflammatory disease; organs chiefly involved are the liver, spleen, and kidneys, and the adrenal glands less frequently. (05 Mar 2000) |
| senile amyloidosis | A common form of amyloidosis in very old people, usually mild and limited to the heart. See: amyloidosis of aging. (05 Mar 2000) |
| nodular amyloidosis | A localised form of amyloidosis in which amyloid occurs as masses or nodules beneath the skin or mucous membranes, e.g., in the larynx. Synonym: amyloid tumour, focal amyloidosis. (05 Mar 2000) |
| familial amyloidosis | <neurology> A disorder in which various peripheral nerves are infiltrated with amyloid and their functions disturbed, an abnormal prealbumin is also formed and is present in the blood; characteristically, it begins during mid-life and is found largely in persons of Portuguese descent. Other rare clinical types occur. Inheritance: autosomal dominant. Synonym: familial amyloidosis, hereditary amyloidosis. (05 Mar 2000) |
| focal amyloidosis | A localised form of amyloidosis in which amyloid occurs as masses or nodules beneath the skin or mucous membranes, e.g., in the larynx. Synonym: amyloid tumour, focal amyloidosis. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|