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"succinic semialdehyde dehydrogenase deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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¿µ¹® iron deficiency anemia ÇÑ±Û Ã¶°áÇ̺óÇ÷
¼³¸í   
  ÀûÇ÷±¸ÀÇ ±â´ÉÀº »ê¼Ò¸¦ ¿î¹ÝÇϴµ¥ ÀÖ´Ù. ÀûÇ÷±¸ ¼Ó¿¡ »ê¼Ò¿Í °áÇÕÀ» ÇÏ¿© »ê¼Ò¸¦ ¿î¹ÝÇϴ Ç÷»ö¼Ò¶ó´Â ¹°ÁúÀÌ ÀÖ´Ù. Ã¶Àº ÀÌ Ç÷»ö¼ÒÀÇ Áß¿äÇÑ ºÎºÐÀ» ÀÌ·ç´Â °ÍÀ¸·Î Ã¶ÀÌ ¾øÀ¸¸é Ç÷»ö¼Ò°¡ ¸¸µé¾îÁú ¼ö°¡ ¾ø´Ù. Ç÷»ö¼Ò°¡ ¾øÀ¸¸é ¿ª½Ã ÀûÇ÷±¸µµ ¸¸µé¾îÁöÁö ¾ÊÀ¸¹Ç·Î Ã¼³»¿¡ Ã¶ÀÌ ºÎÁ·Çϸ頺óÇ÷ÀÌ »ý±ä´Ù. À̠ö°áÇ̼º ºóÇ÷Àº ºóÇ÷ÀÇ ¿øÀΠÁß¿¡¼­ °¡Àå ÈçÇÑ °ÍÀÌ´Ù(¾à 25%¸¦ Â÷ÁöÇÑ´Ù). Ã¶ÀúÀå·®ÀÇ ÀúÇÏ-°áÇÌ, Ç÷ûö³óµµÀÇ ÀúÇÏ, Æ®¶õ½ºÆä¸°·® »ó½Â, Æ®¶õ½ºÆä¸°Æ÷È­µµÀÇ ÀúÇÏ, Ç÷»ö¼Ò³óµµ ¶Ç´Â Ç츶ÅäÅ©¸®Æ®ÀÇ ÀúÇÏ, Àú»ö¼Ò¼º´ëÀûÇ÷±¸¸¦ Æ¯Â¡À¸·Î Çϴ ºóÇ÷·Î¼­, »ýü ³»¿¡¼­ Ã¶ÀÌ Àå±â¿¡ °ÉÃÄ °áÇ̵Ǹ砱נ¶§¹®¿¡ Ç÷»ö¼Ò »ý»ê °¨¼Ò¿¡ ÀÇÇØ ÀϾ´Ù. Ã¢ÀÚ¿¡¼­ÀǠöÈí¼ö·® ºÎÁ·, Ã¶ÀÇ ¼ö¿ä Áõ´ë(À¯¾Æ±â, »çÃá±â, ÀÓ½Å), Ã¶¼Ò½Ç°úÀ×(ÃâÇ÷)¿¡ ÀÇÇØ ÀϾ¸ç, Æ¯È÷ »çÃá±â¿¡¼­ Æó°æ±â±îÁöÀÇ ¿©¼º¿¡°Ô ¸¹´Ù. Áõ»óÀ¸·Î¼­´Â ¾ó±¼Ã¢¹é, ÇǷΰ¨, ÇǺÎâ¹é, ¼ÕÅé º¯È­(½ºÇ¬ ¸ð¾ç) µîÀ» ³ªÅ¸³½´Ù. ±¸°­ ¿µ¿ª¿¡¼­´Â ÇôÀÇ Á¢ÃËÅë, ¹ßÀû, °ÇÁ¶°¨, »ïÅ´°ï¶õÀ» ¼ö¹ÝÇϸé Ç÷¯¸Ó-ºó½¼(Plummer-Vinson)ÁõÈıºÀ̶ó°í ÇÑ´Ù. Ç÷¾× ¼Ò°ßÀº Ç÷ûöÀº ÀúÇÏÇϸç, Ã¶°áÇÕ´É·ÂÀÇ »ó½Â, Àú»ö¼Ò¼º ÀÛÀºÀûÇ÷±¸¼ºÀ» ³ªÅ¸³½´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • succinic dehydrogenase
    ¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
  • succinic acid
    ¼÷½Å»ê
  • alcohol dehydrogenase
    ¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
  • dehydrogenase
    Å»¼ö¼ÒÈ¿¼Ò
  • glucose dehydrogenase
    Æ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
  • glucose-6-phosphate dehydrogenase
    6-ÀλêÆ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
  • glutamate dehydrogenase
    ±Û·çŽ»êÅ»¼ö¼ÒÈ¿¼Ò
  • hydroxybutyrate dehydrogenase
    ¼ö»êÈ­ºÎƼ·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò
  • lactate dehydrogenase
    Á¥»êÅ»¼ö¼ÒÈ¿¼Ò, LDH
  • malate dehydrogenase
    ¸»»êÅ»¼ö¼ÒÈ¿¼Ò
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • biotin deficiency syndrome
    ºñ¿Àƾ°áÇÌÁõÈıº
  • deficiency
    1. °áÇÌ 2. °áÇÌÁõ
  • deficiency disease
    °áÇ̺´
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷ÀÌ¿¡Æ¾°áÇ̺óÇ÷
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • succinic dehydrogenase
    ¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • succinic acid
    ¼÷½Å»ê
  • deficiency
    °áÇÌ(Áõ)
  • dehydrogenase
    Å»¼ö¼ÒÈ¿¼Ò
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • succinic dehydrogenase
    ¼÷½Å»êÅ»¼ö¼ÒÈ¿¼Ò
  • succinic acid
    ¼÷½Å»ê
  • alcohol dehydrogenase
    ¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
  • dehydrogenase
    Å»¼ö¼ÒÈ¿¼Ò
  • glucose dehydrogenase
    Æ÷µµ´çÅ»¼ö¼ÒÈ¿¼Ò
  • glutamate dehydrogenase
    ±Û·çŽ»êÅ»¼ö¼ÒÈ¿¼Ò
  • hydroxybutyrate dehydrogenase
    ¼ö»êÈ­ºÎƼ·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò
  • lactate dehydrogenase
    Á¥»êÅ»¼ö¼ÒÈ¿¼Ò
  • acid lipase deficiency
    »ê¼ºÁöÁúºÐÇØÈ¿¼Ò°áÇÌ
  • acquired immune deficiency
    ÈÄõ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • adhesion deficiency disorder
    À¯Âø°áÇÌÀå¾Ö
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾°áÇ̺óÇ÷
  • folate deficiency anemia
    ¿±»ê°áÇÌ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glucose-6-phosphate dehydrogenase deficiency
    ±Û·çÄÚ½º-6-ÀλêµðÇÏÀÌ µå·ÎÀú³×À̽º °áÇÌ(Áõ)
  • phosphate dehydrogenase deficiency
    Àλ꿰ݼö¼ÒÈ¿¼Ò°áÇÌÁõ
  • 18-dehydrogenase
    18-Å»¼ö¼ÒÈ¿¼Ò, 18-µðÇÏÀ̵å·Î°Ô³ªÁ¦
  • 18-hydroxysteroid dehydrogenase
    18-È÷µå·Ï½Ã½ºÅ×·ÎÀ̵åÅ»¼ö¼ÒÈ¿¼Ò
  • 3-beta-hydroxysteroid dehydrogenase
    3-º£Å¸-È÷µå·Ï½Ã½ºÅ×·ÎÀ̵å Å»¼ö¼ÒÈ¿¼Ò
  • 6-P-gluconate dehydrogenase
    6-ÆÄ¶ó-±Û·çÄÚ³×ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò<--µðÇÏÀ̵å·Î°Ô³ªÁ¦>
  • 6-phosphoglycerate dehydrogenase
    6-Æ÷½ºÆ÷±Û¸®¼¼·¹ÀÌÆ®Å»¼ö¼ÒÈ¿¼Ò<--µðÇÏÀ̵å·Î°Ô³ªÁ¦>
  • GDH= glycerophosphate dehydrogenase
    ±Û¸®¼¼·ÎÀλêÅ»¼ö¼ÒÈ¿¼Ò.
  • Glucose-6-phosphate dehydrogenase
    ±Û·çÄÚ¿À½º-6-Àλê(×òß«)Å»¼ö¼ÒÈ¿¼Ò(÷­â©áÈý£áÈ)
  • LDH = lactic dehydrogenase
    Á¥»ê(¡­ß«) Å»¼ö¼ÒÈ¿¼Ò(÷­â©áÈý£áÈ)
  • LDH= lactic dehydrogenase
    ¶ôÆ®»êÅ»¼ö¼ÒÈ¿¼Ò.
  • Lactic acid dehydrogenase
    ¶ôÆ® »êÅ»¼ö¼ÒÈ¿¼Ò(¡­ß«÷­â©áÈý£áÈ)
  • NADH dehydrogenase
    NADH Å»¼ö¼ÒÈ¿¼Ò
  • acyl-coa dehydrogenase
    acyl-CoA Å»¼ö¼ÒÈ¿¼Ò(¡­÷­â©áÈý£áÈ)
  • glucose 6 phosphate dehydrogenase =G 6 PD
    ±Û·çÄÚ¿À½º 6Àλê Å»¼ö ¼ÒÈ¿¼Ò, ±Û·çÄÚ¿À½º-6-ÀÎ»ê µ¥È÷µå·Î°Ô³ªÁ¦.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • succinic dehydrogenase
    ¼÷½Å»ê Å»¼ö¼ÒÁ¦
  • succinic acid
    ¼÷½Å»ê(¡­ß«).
  • glucose-6-phosphate dehydrogenase deficiency
    ±Û·çÄÚ½º-6-ÀλêµðÇÏÀÌ µå·ÎÀú³×À̽º °áÇÌ(Áõ)
  • phosphate dehydrogenase deficiency
    Àλ꿰ݼö¼ÒÈ¿¼Ò°áÇÌÁõ
  • acyl-coa dehydrogenase
    acyl-CoA Å»¼ö¼ÒÈ¿¼Ò(¡­÷­â©áÈý£áÈ)
  • alcohol dehydrogenase
    ¾ËÄڿõðÇÏÀ̵å·ÎÀú³×À̽º.
  • alcohol dehydrogenase
    ¾ËÄÚ¿ÃÅ»¼ö¼ÒÈ¿¼Ò
  • dehydrogenase
    µðÇÏÀ̵å·ÎÀú³×À̽º, Å»¼ö¼ÒÈ¿¼Ò.
  • dehydrogenase
    Å»¼ö¼ÒÈ¿¼Ò(÷­â©áÈý£áÈ)
  • delta-aminolevulinic acid dehydrogenase
    µ¨Å¸-¾Æ¹Ì³ë·¹ºÒ¸°»êÅ»¼ö¼ÒÈ¿¼Ò<--µðÇÏÀ̵å·Î°Ô³ªÁ¦>
  • glucose 6 phosphate dehydrogenase =G 6 PD
    ±Û·çÄÚ¿À½º 6Àλê Å»¼ö ¼ÒÈ¿¼Ò, ±Û·çÄÚ¿À½º-6-ÀÎ»ê µ¥È÷µå·Î°Ô³ªÁ¦.
  • glucose 6 phosphate dehydrogenase def
    ±Û·çÄÚ¿À½º-6-Àλê Å»¼ö¼Ò È¿¼Ò°á
  • glucose dehydrogenase
    ±Û·çÄÚ¿À½ºÅ»¼ö¼ÒÈ¿¼Ò, ±Û·çÄÚ¿À½ºµ¥È÷µå·Î°Ô³ªÁ¦.
  • glucose-6-phosphate dehydrogenase
    ±Û·çÄÚ½º-6-ÀλêµðÇÏÀ̵å·ÎÀú³×À̽º
  • glucose-6-phosphate dehydrogenase
    ±Û·çÄÚ¿À½º-6-ÀλêÅ»¼ö¼ÒÈ¿¼Ò
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Deficiency (Nanismus)
    °áÇÌ(³­ÀåÀÌÁõ)
    [¿¾ ¿ë¾î] °áÇÌ
  • Organogenetic deficiency
    ±â°ü¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ±â°ü¹ß»ý°áÇÌ
  • Functional deficiency
    ±â´É°áÇÌ
    [¿¾ ¿ë¾î] ±â´ÉÀû°áÇÌ
  • Pituitary hormone deficiency (Pituitary dwarfism)
    ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
    [¿¾ ¿ë¾î] ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
  • Reaction deficiency
    ¹ÝÀÀ°áÇÌ
    [¿¾ ¿ë¾î] ¹ÝÀÀ°áÇÌ
  • Vitamin deficiency (Fetal osteodystrophy)
    ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
    [¿¾ ¿ë¾î] ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
  • Cellular deficiency (Acallosal cerebrum)
    ¼¼Æ÷°áÇÌ (³úµéº¸°á¿©³ú)
    [¿¾ ¿ë¾î] ¼¼Æ÷°áÇÌ
  • Intracellular deficiency (Albinism)
    ¼¼Æ÷¼Ó°áÇÌ (¹é»öÁõ)
    [¿¾ ¿ë¾î] ¼¼Æ÷³»°áÇÌ
  • Chromosomal deficiency
    ¿°»öü°áÇÌ
    [¿¾ ¿ë¾î] ¿°»öü°á½Ç
  • Stimulation deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Sensory deficiency
    °¨°¢°áÇÌ
    [¿¾ ¿ë¾î] °¨°¢°áÇÌ
  • Thyroid hormone deficiency (Cretinism)
    °©»ó»ùÈ£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
    [¿¾ ¿ë¾î] °©»ó¼±È£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
  • Deficiency
    °áÇÌ
    [¿¾ ¿ë¾î] °áÇÌ
  • Deficiency (Monstrous tumor)
    °áÇÌ (±«¹°Á¾)
    [¿¾ ¿ë¾î] °áÇÌ
  • Secretion deficiency
    ºÐºñ°áÇÌ
    [¿¾ ¿ë¾î] ºÐºñ°áÇÌ
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glucose-6-phosphate dehydrogenase deficiency
    ±Û·çÄÚ½º-6-Àλê(×òß«) µðÇÏÀ̵å·ÎÀú³×À̽º °áÇÌ(ÌÀ
  • succinic acid
    ¼÷½Å»ê(ß«)
  • aspartic semialdehyde
    ¾Æ½ºÆÄ¸£Æ®»ê(ß«)¼¼¹Ì¾Ëµ¥ÇÏÀ̵å
  • glutamic semialdehyde
    ±Û·çŽ»ê(ß«) ¼¼¹Ì¾Ëµ¥ÇÏÀ̵å
  • conditioned vitamin deficiency
    Á¶°ÇºÎ(ðÉËìݾ) ºñŸ¹Î°áÇË(ÌÀù¹)
  • deficiency
    °áÇÌ(ÌÀù¹)
  • deficiency disease
    °áÇÌ Áúȯ(ÌÀù¹òðü´)
  • deficiency mutant
    "°áÇÌ º¯ÀÌü(ÌÀù¹Ü¨ì¶ô÷), (ÔÒ) auxotroph"
  • dietary deficiency
    ½ÄÀ̰áÇÌ(ç½å×ÌÀù¹)
  • familial high-density lipoprotein deficiency °¡Á·¼º °í¹Ðµµ ÁöÁú´Ü¹éÁú °áÇÌ (Ê«ðéàõÍÔÚËÓøò·òõ
    Ó±ÛÜòõÌÀù¹)
  • familial lysosomal lipase deficiency
    °¡Á·¼º(Ê«ðéàõ) ¶óÀÌ¼Ò¼Ø ¶óÀÌÆäÀ̽º °áÇÌ(ÌÀù¹)
  • primary deficiency
    ¿ø¹ß¼º °áÇÌ(ê«Û¡àõÌÀù¹)
  • secondary deficiency
    ÀÌÂ÷ °áÇÌ(ì£ó­ÌÀù¹)
  • simian acquired immune deficiency syndrome
    ¿ø¼þÀÌ ÈÄõ¼º¸é¿ª°áÇÌÁúȯ(ý­ô¸àõØóæ¹ÌÀù¹òðü´)
  • sulfite oxidase deficiency
    ¾ÆÈ²»ê(ä¬üÜß«) ¿Á½Ãµ¥À̽º °áÇÌ(ÌÀù¹)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • lactic acid dehydrogenase
    ¶ôÆ®»êÅ»¼ö¼ÒÈ¿¼Ò
  • deficiency
    °áÇÌÁõ
  • deficiency anemia
    °áÇ̼ººóÇ÷
  • iron deficiency anemia
    ö°áÇ̼ººóÇ÷
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)
  • nutritional deficiency disease
    ¿µ¾ç°áÇÌÁõ
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
SSD shaded surface display; single saturating dose; Social Security disability; source-skin distance; so...
MD Doctor of Medicine [Lat. Medicinae Doctor]; magnesium deficiency; main duct; maintenance dose; major...
GDH glucose dehydrogenase; glutamate dehydrogenase; glycerophosphate dehydrogenase; glycol dehydrogenase...
SDA right sacroanterior [fetal position] [Lat. sacrodextra anterior]; sialodacryoadenitis; specific dyna...
LAD lactic acid dehydrogenase; left anterior descending [artery]; left axis deviation; leukocyte adhesio...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
SSADH Succinic semialdehyde dehydrogenase
SDH Succinic dehydrogenase
GSA Glutamate-1-semialdehyde
GSA Guanidino succinic acid
G6PD Glucose-6-Phosphate dehydrogenase deficiency
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • alcohol dehydrogenase
    ¾ËÄÚ¿Ã Å»¼ö¼Ò È¿¼Ò
  • aldehyde dehydrogenase(NAD+)
    ¾Ëµ¥ÇÏÀÌµå µðÇÏÀ̵å·ÎÁö³×À̽º
    acid anion + NADH = aldehyde + NAD + H2O ÀÇ È­ÇйÝÀÀÀ» Ã˸ÅÇÏ´Â »êÈ­ ȯ¿ø È¿¼Ò ÁßÀÇ Çϳª.
  • lactate dehydrogenase
    ¶ôÆ®»ê Å»¼ö¼Ò È¿¼Ò, ¶ôÆ®»ê µ¥È÷µå·Î°Ô³ªÁ¦
  • lactic dehydrogenase
    ¶ôÆ®»ê Å»¼ö¼Ò È¿¼Ò, À¯»ê Å»¼ö¼Ò È¿¼Ò, Á¥»ê Å»¼ö¼Ò È¿¼Ò
  • NADH dehydrogenase
    ubiquinone
    NADH + ubiquinone = NAD
  • 17-hydroxylase deficiency
    17-hydroxylase °áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª °áÇÌ ÁõÈıº
    1. ÇöÀúÇÑ ¸é¿ª °áÇ̰ú ÇÔ²² ±âȸ°¨¿°, ¼Ó¹ß¼º ¾Ï ¹× ½Å°æ°è Áõ¼¼°¡ µ¿¹Ý. ¹ÙÀÌ·¯½º ÀÚü¿¡ ÀÇÇÑ º´º¯°ú ¸é¿ª´É·Â ÀúÇÏ¿¡ µû¸¥ ±âȸ °¨¿° µîÀÇ ÀÌÂ÷Àû º´º¯ÀÇ µÎ °¡Áö·Î ´ëº°. HIV¿¡ ÀÇÇØ ¹ß»ýµÇ´Â ÁúȯÀ¸·Î ½Å°æ°è°¡ Áß¿ä Ç¥ÀûÁß Çϳª. ¹ÙÀÌ·¯½º¿¡ °¨¿°µÈ »ç¶÷ÀÇ 40% Á¤µµ°¡ Áúº´ÀÌ ¹ß»ý. ¹ÙÀÌ·¯½ºÀÇ Á÷Á¢ÀûÀÎ ¿µÇâ¿¡ ÀÌÇÑ º´º¯À¸·Î´Â ¸²ÇÁ±¸¼º ¼ö¸·¿°°ú HIV ³ú¿° µîÀÌ ÀÖÀ½. 2. ÈÄõ¼º ¸é¿ª°áÇÌÁõ. Àΰ£ ¸é¿ª°áÇÌ ¹ÙÀÌ·¯½º
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌ ÁõÈıº
  • adenosine deficiency
    ¾Æµ¥³ë½Å °áÇÌÁõ
  • ascorbic acid deficiency
    ¾Æ½ºÄÚ¸£ºó»ê °áÇÌÁõ
    Ư¡ÀûÀÎ ±«Ç÷º´ÀÌ ³ªÅ¸³ª¸ç ÀÌÀÇ Áõ»óÀ¸·Î´Â ÀÕ¸öÀÌ º×°í ½±°Ô ÃâÇ÷ÀÌ µÇ°í, Ä¡¾Æ Çü¼º Àå¾Ö Ä¡Á¶°ñ Èí¼ö ÇÇÇÏ ÃâÇ÷ µîÀÌ ÀÖÀ¸¸ç â»ó Ä¡À¯°¡ ´Ê¾îÁø´Ù.
  • cell adhesion molecular deficiency
    ¼¼Æ÷ À¯Âø ºÐÀÚ °áÇÌ
  • cellular deficiency
    ¼¼Æ÷ °áÇÌ
    ¼¼Æ÷°¡ À¯ÀüÀû ȤÀº ÀÚ°¡¸é¿ªÀû ¿äÀÎÀ¸·Î ÀÎÇØ¼­ °áÇÌµÈ °Í.
  • chromosomal deficiency
    ¿°»öü °áÇÌ
  • color deficiency
    »ö °áÇÌ
  • deficiency anemia
    °áÇ̼º ºóÇ÷
    Ç÷»ö¼Ò °áÇÌÀ¸·Î ÀÎÇÑ ºóÇ÷.
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
acetoacetyl-succinic thiophorase <enzyme> An enzyme catalyzing the reversible conversion of acetoacetyl-CoA and succinate into succinyl-CoA and acetoacetate; malonyl-CoA can substitute for succinyl-CoA and a few other 3-oxo acids for the acetoacetate; an important step in order for the ketone bodies to serve as a fuel for extrahepatic tissues.
Synonym: 3-ketoacid-CoA transferase, acetoacetyl-succinic thiophorase.
(05 Mar 2000)
alpha-hydroxymethyl-alpha'-(N-acetylaminomethylene)succinic acid hydrolase <enzyme> Involved in degradation of vitamin b6; forms acetic acid plus ammonia plus carbon dioxide plus alpha-hydroxymethyl-succinic monoaldehyde
Registry number: EC 3.5.1.-
Synonym: compound b hydrolase
(26 Jun 1999)
alpha-(N-acetylaminomethylene)succinic acid hydrolase <enzyme> Involved in degradation of vitamin b6; forms acetic acid plus ammonia plus carbon dioxide plus succinic monoaldehyde
Registry number: EC 3.5.1.-
Synonym: compound a hydrolase
(26 Jun 1999)
succinic <chemistry> Pertaining to, or derived from, amber; specif, designating a dibasic acid, CH.(COH), first obtained by the dry distillation of amber. It is found in a number of plants, as in lettuce and wormwood, and is also produced artificially as a white crystalline substance having a slightly acid taste.
Origin: Cf. F. Succinique. See Succinate.
Source: Websters Dictionary
(01 Mar 1998)
succinic acid <chemical> A water-soluble, colourless crystal with an acid taste that is used as a chemical intermediate, in medicine, the manufacture of lacquers, and to make perfume esters. It is also used in foods as a sequestrant, buffer, and a neutralizing agent.
Pharmacological action: anti-ulcer agents, radiation-protective agents.
(12 Dec 1998)
succinic acid cycle A series of oxidation reduction reactions in which succinic acid and other 4-carbon atoms acids (fumaric, malic, oxaloacetic) take part in the oxidation of pyruvic acid as part of the tricarboxylic acid cycle.
See: dicarboxylic acid cycle.
(05 Mar 2000)
succinic acids A class of dicarboxylic acids with the general structure of butanedioic acid (succinic acid). They are used in perfumery and as a chemical intermediate in medicine.
(12 Dec 1998)
succinic anhydrides A subclass of anhydrides with the general structure of dihydrofurandione. They can be substituted on any carbon atom. They modify and inhibit proteins and enzymes and are used in the acylation of amino- and hydroxyl groups.
(12 Dec 1998)
succinic thiokinase A ligase reversibly reacting succinate and CoA with ATP to produce ADP, inorganic phosphate, and succinyl-CoA, a similar synthetase, but one able to use itaconate as well as succinate and GTP (or ITP) in place of ATP; a part of the tricarboxylic acid cycle.
Synonym: succinic thiokinase, succinyl-CoA ligase.
(05 Mar 2000)
glucose-6-dehydrogenase deficiency <biochemistry> An inherited condition that results in a deficiency in glucose-6-phosphate dehydrogenase. Particular drugs (sulphonamides) can exacerbate this problem. The result is haemolytic anaemia.
(27 Sep 1997)
glucose-6-phosphate dehydrogenase deficiency A deficiency of glucose-6-phosphate dehydrogenase, an enzyme important for maintaining cellular concentrations of reduced nucleotides.
Deficiency of this enzyme is the commonest disease-causing enzyme defect in humans affecting an estimated 400 million people.
The gene for this enzyme is on the X chromosome and there are various polymorphic forms.
Males with the enzyme deficiency develop haemolytic anaemia when red blood cells are exposed to oxidant drugs such as the antimalarial primaquine, the sulfonamide antibiotics or sulfones, naphthalene moth balls, or fava beans. It can also cause anaemia of the newborn, and chronic nonspherocytic haemolytic anaemia.
Inheritance: X-linked.
(12 Sep 2002)
glucosephosphate dehydrogenase deficiency A disease-producing enzyme deficiency subject to many variants, some of which cause a deficiency of enzyme activity in erythrocytes, leading to haemolytic anaemia.
(12 Dec 1998)
pyruvate dehydrogenase complex deficiency An autosomal recessive pyruvate metabolism disorder resulting from deficient enzyme activity in one of several proteins of pyruvate dehydrogenase complex, resulting in deficiency of acetyl CoA. Deficiency in acetyl CoA product reduces the synthesis of acetylcholine, thereby causing neurological abnormalities. Clinical presentations include lactic acidosis, mental retardation, and ataxia.
(12 Dec 1998)
deficiency, glucose-6-phosphate dehydrogenase Deficiency of G6PD is the commonest disease-causing enzyme defect in humans affecting an estimated 400 million people. The G6PD gene is on the X chromosome. Males with the enzyme deficiency develop anaemia due to breakup of their red blood cells when they are exposed to oxidant drugs such as the antimalarial primaquine, the sulfonamide antibiotics or sulfones, naphthalene moth balls, or fava beans.
(12 Dec 1998)
abdominal muscle deficiency syndrome <syndrome> Congenital absence (partial or complete) of abdominal muscles, in which the outline of the intestines is visible through the protruding abdominal wall; in males, genitourinary anomalies (urinary tract dilation and cryptorchidism) are also found; genetics unclear.
(05 Mar 2000)
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succinic semialdehyde dehydrogenase deficiency an autosomal recessive aminoacidopathy caused by deficiency of the enzyme succinate semialdehyde dehydrogenase. The resulting increase in γ-aminobutyric acid and γ-hydroxybutyric acid causes mental retardation, hypotonia, and ataxia. Called also γ- or 4-hydroxybutyricaciduria.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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