| 영문 | cystic fibrosis | 한글 | 낭성섬유증 |
|---|---|---|---|
| 설명 | 유전병의 하나로 땀샘, 기관지에서 점액을 분비하는 샘, 이자등의 외분비샘(몸 밖으로 액체를 분비하는 샘. 내분비샘을 제외한 모든 샘을 이른다)의 이상을 특징으로 하는 병이다. 중요한 병적인 변화는 주로 기관지에서 점액을 분비하는 분비샘에서 지나치게 점도가 높은 점액이 분비되어 기관지를 막아 호흡장애를 일으키는 폐의 병터이며, 땀에서 과도한 전해질 특히 염화나트륨(NaCl)이 분비되어 몸에 전해질이 부족하게 된다. 또 이자의 소화액을 분비하는 분비샘의 이상으로 이자관이 막히거나 이자의 기능이 떨어져서 소화의 장애를 일으키기도 한다. 유태계에 많으며 우리나라에는 아주 드물다. |
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| 영문 | fibrosis | 한글 | 섬유증, 섬유화 |
|---|---|---|---|
| 설명 | 아교질섬유를 형성하는 섬유조직의 증식으로 몸의 실질세포의 괴사나 손상에 이어서 나타나는 경우가 보통이다. 두 단계, 즉 손상부위에서 섬유모세포의 이주와 증식, 그리고 섬유모세포에 의한 세포의 바탕질 축적으로 진행된다. 피부의 경우 진피내 섬유모세포의 증식과 아교질 섬유의 증식이 있는 경우를 섬유화, 거의 아교질 섬유로만 구성되는 경우를 경화라고 한다. |
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| NSF | National Science Foundation; nodular subepidermal fibrosis |
|---|---|
| MF | 1) Myelo-Fibrosis = Agnogenic Myeloid Metaplasia with Myelo-F... |
| CFF | critical flicker fusion [test]; critical fusion frequency; cystic fibrosis factor; Cystic Fibrosis F... |
| CFP | chronic false positive; Clinical Fellowship Program; cyclophosphamide, fluorouracil, prednisone; cys... |
| IPF | idiopathic pulmonary fibrosis; infection-potentiating factor; interstitial pulmonary fibrosis |
| CHF | Congenital hepatic fibrosis |
|---|---|
| CF | cvstic fibrosis |
| CFTR | Cystic Fibrosis Transmembrane Conductance Regulator |
| CFTR | Cystic Fibrosis Transmembrane Conductance Regulator Gene |
| CFTR | Cystic Fibrosis Transmembrane Regulator |
| nodular subepidermal fibrosis | A slowly growing benign skin nodule consisting of poorly demarcated cellular fibrous tissue enclosing collapsed capillaries with scattered haemosiderin-pigmented and lipid macrophages. They are common, usually about 1 cm in diameter and occur in the dermis. Simple excision is always curative. (12 Dec 1998) |
|---|---|
| subepidermal | Situated beneath the epidermis, subepidermal. (18 Nov 1997) |
| subepidermal abscess | A microscopic abscess located in the dermis just beneath the epidermis. (05 Mar 2000) |
| African endomyocardial fibrosis | Fibrosis of the inner layers of the myocardium, often including the endocardium, causing diastolic restriction of the heart; indigenous to East Africa. (05 Mar 2000) |
| radiation fibrosis | The formation of scar tissue as a result of radiation therapy to the lung. (12 Dec 1998) |
| mediastinal fibrosis | <radiology> Histoplasmosis most common cause, can cause superior vena cava obstruction (12 Dec 1998) |
| replacement fibrosis | The formation of fibrous tissue that occupies sites where various other cells and tissues have become atrophied, or degenerated and necrotic. (05 Mar 2000) |
| retroperitoneal fibrosis | <radiology> Ureters tapered or obstructed, most severe at L4-5, ureters deviated medially, Treatment: symptomatic; steroids have ? long-term benefit Differential diagnosis: malignancy, lymphoma (especially Hodgkin's), metastasis from colon and breast, retroperitoneal sarcoma, drugs, methysergide (Sansert), haemorrhage, aortic aneurysm, trauma or surgery, inflammation, Crohn's disease, diverticulitis, pancreatitis, extravasated urine, radiation (12 Dec 1998) |
| pericentral fibrosis | Fibrosis occurring around the central veins in the hepatic lobules. (05 Mar 2000) |
| perimuscular fibrosis | Fibrosis in the outer media of arteries, usually the renal arteries of young women, where it causes segmental stenosis and hypertension; a variety of fibromuscular dysplasia. Synonym: subadventitial fibrosis. (05 Mar 2000) |
| pipestem fibrosis | A characteristic pipe-shaped fibrosis formed around hepatic portal veins in some cases of long-continued heavy infection with Schistosoma mansoni; thought to be induced by the presence of large numbers of schistosome eggs in the hepatic tissues. Synonym: Symmers' clay pipestem fibrosis, Symmers' fibrosis. (05 Mar 2000) |
| congenital fibrosis of the extraocular muscles | An autosomal dominant disorder associated with blepharoptosis and absence of eye movements. (05 Mar 2000) |
| cystic fibrosis | <chest medicine> A generalised disorder of infants, children and young adults, in which there is widespread dysfunction of the exocrine glands, characterised by signs of chronic pulmonary disease (due to excess mucus production in the respiratory tract), pancreatic deficiency, abnormally high levels of electrolytes in the sweat and occasionally by biliary cirrhosis. There is an ineffective immunologic defense against bacteria in the lungs. Pathologically, the pancreas shows obstruction of the pancreatic ducts by amorphous eosinophilic concretions, with consequent deficiency of pancreatic enzymes, resulting in steatorrhoea and azotorrhoea and intestinal malabsorption. The degree of involvement of organs and glandular systems may vary greatly, with consequent variations in the clinical picture. Inheritance: autosomal recessive. (13 Nov 1997) |
| cystic fibrosis antigen | Now known to be MRP 8. See: calgranulins. (18 Nov 1997) |
| cystic fibrosis transmembrane conductance regulator | Gene believed to be defective in cystic fibrosis. Gene encodes a chloride channel, homologous to a family of proteins that actively transport small solutes in an ATP dependent manner (ABC transporters). The regulator protein is a protein which is embedded in the cell membrane and acts as a channel for certain ions to be transported into or out of the cell. The disease cystic fibrosis is caused by a defect in the gene for this protein. (09 Oct 1997) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|