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steryl-sulfatase <enzyme> Arylsulfatases a and b hydrolyze nitrocatechol sulfate, but p-nitrophenyl sulfate is hydrolyzed only slightly by both enzymes; arylsulfatase c hydrolyzes both p-nitrophenyl sulfate and nitrocatechol sulfate, low substrate specificity located chiefly in microsomes; a and b are found in lysosomes; arylsulfatase a is cerebroside sulfatase and arylsulfatase b is chondro-4-sulfatase
Registry number: EC 3.1.6.2
Synonym: arylsulfatase c, dehydroepiandrosterone sulfate sulfatase, steroid sulfatase, estrone sulfate sulfohydrolase, steroid sulphatase, cholesterol sulfatase, dhea sulfatase, 3 beta-hydroxysteroid sulfate sulfatase, estrone sulfate sulfatase, sterylsulfatase, steroid sulfohydrolase, cholesterol sulfate sulfatase, arylsulphatase c
(26 Jun 1999)
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  • Steryl-Sulfatase - »õâ An arylsulfatase with high specificity towards sulfated steroids. Defects in this enzyme are the cause of ICHTHYOSIS, X-LINKED.
    Synonyms : 3 Beta-Hydroxysteroid Sulfate Sulfatase, Arylsulfatase C, Arylsulphatase C, Cholesterol Sulfatase, Cholesterol Sulfate Sulfatase, DHEA Sulfatase, Dehydroepiandrosterone Sulfate Sulfatase, Estrone Sulfate Sulfatase, Estrone Sulfate Sulfohydrolase
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steryl-sulfatase [EC 3.1.6.2] a microsomal enzyme of the hydrolase class that catalyzes the cleavage of the sulfate group from sulfated sterols. Deficiency of the enzyme, an X-linked trait, causes X-linked ichthyosis. Called also steroid sulfatase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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