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  • sphingolipid activator protein I deficiency
  • ceramide
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  • d-Glucose ceramide
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  • sphingolipid
    ½ºÇΰíÁöÁú(ò·òõ)
  • ceramide
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  • ceramide glycoside
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  • ceramide lactoside
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  • glycosyl ceramide
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SAP sensory action potential; serum acid phosphatase; serum alkaline phosphatase; serum amyloid P; situs...
SAPD sphingolipid activator protein deficiency
CDH ceramide dihexoside; congenital diaphragmatic hernia; congenital dislocation of hip; congenital dysp...
CER capital expenditure review; ceramide; conditioned emotional response; control electrical rhythm; cor...
CTH ceramide trihexoside; chronic tension headache; cystathionase
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SAP Sphingolipid activator protein
CER Ceramide
CMH Ceramide monohexoside
GalCer Galactosyl ceramide
CGalt UDP-galactose-ceramide galactosyl transferase
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  • ceramide
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    õ¿¬¿¡ Á¸ÀçÇÏ´Â ½ºÇÎ°í¸®Çǵå·Î¼­ ½ºÇΰí½ÅÀÇ NH2°¡ Áö¹æ»ê ¾Æ½Ç ÄÚ¿¡ÀÌ À¯µµÃ¼·Î ¾Æ½ÇÈ­µÊÀ¸·Î½á N-acetyls
  • ceramide trihexosidase
    ¼¼¶ó¸¶ÀÌµå Æ®¶óÀÌÇí¼Ò»çÀ̵å, »ï´ç ¼¼¶ó¸¶À̵å
    Fabry º´¿¡¼­ ÃàÀûµÇ´Â ÁÖµÈ s
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
sphingolipid ceramide N-deacylase <enzyme> Hydrolyzes the n-acyl linkage between fatty acids and sphingosine bases in ceramides in various sphingolipids, as well as sphingomyelin to produce their lyso forms; mw 52 kD
Registry number: EC 3.5.1.-
Synonym: scdase
(26 Jun 1999)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
sphingolipid <biochemistry> Structural lipid of which the parent structure is sphingosine rather than glycerol. Synthesised in the Golgi complex.
(18 Nov 1997)
ceramide <chemical> An N acyl sphingosine, the lipid moiety of glycosphingolipids.
(18 Nov 1997)
ceramide 1-phosphorylcholine <biochemistry> A sphingolipid in which the head group is phosphoryl choline. A close analogue of phosphatidylcholine. In many cells the concentration of sphingomyelin and phosphatidylcholine in the plasma membrane seems to bear a reciprocal relationship.
(18 Nov 1997)
ceramide-activated protein kinase <enzyme> Mw 97 kD; stimulation of kinase takes place during sphingomyelin pathway; has membrane-bound activity capable of phosphorylating a peptide derived from the sequence surrounding thr(699) of the epidermal growth factor receptor; has role in signal transduction for tumour necrosis factor
Registry number: EC 2.7.10.-
Synonym: cap kinase
(26 Jun 1999)
ceramide-activated protein phosphatase <enzyme> Belongs to the heterotrimeric subfamily of the pp2a group of serine-threonine protein phosphatases; involved in ceramide-mediated signal transduction; inhibited by okadaic acid
Registry number: EC 3.1.3.-
Synonym: ceramide-stimulated phosphatase, capp (enzyme)
(26 Jun 1999)
ceramide cholinephosphotransferase <enzyme> Do not confuse with phosphatidylcholine-ceramide phosphotransferase which is also called sphingomyelin synthase
Registry number: EC 2.7.8.3
Synonym: sphingomyelin synthetase, phosphorylcholine-ceramide transferase, cdpcholine-n-acylsphingosine cholinephosphotransferase
(26 Jun 1999)
ceramide dihexoside The accumulated glycolipid noted in glycolipid lipidosis.
(05 Mar 2000)
ceramide glycanase <enzyme> Glycosphingolipid splitting enzyme from leech; cleaves linkage between oligosaccharide and ceramide
Registry number: EC 3.2.1.-
Synonym: cer glycanase
(26 Jun 1999)
ceramide kinase <enzyme> Catalyses the conversion of ceramide to ceramide 1-phosphate; calcium dependent
Registry number: EC 2.7.1.138
(26 Jun 1999)
ceramide lactosidase A hydrolytic enzyme (a beta-galactosidase) that acts on ceramide lactoside, producing glucosylceramide and galactose. A deficiency of this enzyme can result in ceramide lactoside liposis.
Compare: cytolipin.
(05 Mar 2000)
ceramide lactoside A lactosylceramide that accumulates in individuals with ceremide lactoside liposis.
Compare: cytolipin.
(05 Mar 2000)
ceramide lactoside lipidosis An inherited disorder associated with an accumulation of ceramide lactoside due to a deficiency of ceramide lactosidase; results in progressive brain damage with liver and spleen enlargement.
(05 Mar 2000)
ceramide saccharide <biochemistry> Ceramide derivatives containing more than one sugar residue. If sialic acid is present these are called gangliosides.
(18 Nov 1997)
ceramide trihexosidase <enzyme> An enzyme that catalyses the hydrolysis of a ceramidetrihexoside to a ceramidedihexoside plus galactose.
Chemical name: D-Galactosyl-D-galactosyl-D-glucosyl-N-acylsphingosine galactohydrolase
Registry number: EC 3.2.1.47
(12 Dec 1998)
phosphatidylcholine-ceramide phosphocholine transferase <enzyme> Cdpcholine is not a donor; imvolved in sphingomyelin synthesis
Registry number: EC 2.7.8.-
Synonym: pc-cer-pch transferase, sphingomyelin synthase
(26 Jun 1999)
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