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"secondary generalised epilepsy"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
À̰ÍÀ» ¿øÇϼ̽À´Ï±î?
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¿µ¹® epilepsy ÇÑ±Û °£Áú
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  °£ÁúÀº ³úÀÇ ÀÌ»óÀ̳ª, ÀÌ¿¡ µû¸¥ Æ¯Â¡ÀûÀΠ½ÅüÁõ»óµµ °°ÀÌ ³ªÅ¸³­´Ù. ´Ù¾çÇÑ ÇüŰ¡ ÀÖÀ¸¸ç, ³úÆÄ°Ë»ç»ó Àü¹ÝÀûÀΠ³úÀüüÀÇ ÀÌ»óÀÌ ³ªÅ¸³ª¸é Àü½Å¹ßÀÛ(generalized seizure(=epilepsy))À̶ó°í Çϸç, ÀϺÎÀÇ ³ú¿¡¼­ ÀÌ»óÀÌ ³ªÅ¸³ª¸é ºÎºÐ¹ßÀÛ(partial seizure)À̶ó°í ÇÑ´Ù. ¶ÇÇÑ Àü½Å¹ßÀÛ¿¡´Â Å« ÆÈ´Ù¸®ÀÇ ¿îµ¿°ú ÀǽļҽÇ, ÀÚÀ²½Å°æÀÌ»ó µîÀ» È£¼ÒÇϴ °¡Àå ½ÉÇÑ ÇüÅÂÀÇ ´ë¹ßÀÛ(grand mal seizure)¿Í, Àá±ñÀÇ ÀǽļҽǸ¸À» È£¼ÒÇϴ ¼Ò¹ßÀÛ(petit mal seizure)°¡ ÀÖ´Ù. ±×¸®°í ºÎºÐ¹ßÀÛ¿¡´Â ¿îµ¿ºÎÀ§¿¡¸¸ ÀÌ»óÀÌ ³ªÅ¸³ª´Â ¿îµ¿¹ßÀÛ(motor seizure), °¨°¢ºÎÀ§¿¡¸¸ ÀÌ»óÀÌ ³ªÅ¸³ª´Â °¨°¢¹ßÀÛ(sensory seizure), ±×¸®°í °üÀÚ¿±ÀÇ ÀÌ»ó³úÆÄ¼Ò°ßÀ» ³ªÅ¸³»´Â °üÀÚ¿± ¹ßÀÛ(temporal lobe seizure) µîÀÌ ÀÖ´Ù. 3¼¼ ¼Ò¾Æ¿¡ ÀϾ°í, ´Ü¼øÈ÷ ÀǽļҽÇ(5~10Ãʰ£)À» ³ªÅ¸³½´Ù.
¿µ¹® secondary infection ÇÑ±Û ÀÌÂ÷°¨¿°
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  ¾î¶² º´¿øÃ¼ÀÇ °¨¿°¿¡ ÀÇÇÏ¿© º»ÀÎÀÇ ÀúÇ×·ÂÀÌ ¾àÇØÁ³À» ¶§ ¸öÀÇ ´Ù¸¥ ºÎÀ§·Î ÀüÀÌÇÏ¿© ´Ù½Ã °¨¿°À» ÀÏÀ¸Å°´Â °Í. º´¿øÃ¼°¡ ÀÎü¿¡ Ä§ÀÔÇÏ¿© Æ¯Á¤ÇÑ ±â°üÀ̳ª Á¶Á÷¿¡¼­ º´¿øÃ¼°¡ Áõ½ÄÇϰí, ±×°÷¿¡ Æ¯À¯ÀÇ º´Å͸¦ ÀÏÀ¸Å°´Â °ÍÀÌ 1Â÷°¨¿° ¶Ç´Â Ãʰ¨¿°ÀÌ´Ù. ÀÌ 1Â÷°¨¿°ÀÇ º´ÅÍÀÇ º´¿øÃ¼°¡ Ç÷°ü-¸²ÇÁ°ü-±â°ü-¼ÒÈ­°ü-¿ä°ü µîÀÇ ±æÀ» µû¶ó °°Àº ±â°üÀÇ ´Ù¸¥ ºÎÀ§³ª ´Ù¸¥ ±â°üÀ¸·Î ¿î¹ÝµÇ¾î °¨¿°À» ÀÏÀ¸Å²´Ù. µû¶ó¼­ 1Â÷°¨¿°¿¡ ÀÇÇÏ¿© ÃæºÐÇÑ ¸é¿ªÀÌ µÉ °æ¿ì¿¡´Â 2Â÷°¨¿°ÀÌ ÀϾÁö ¾Ê´Â´Ù. ¿¹¸¦ µé¾î, À¯Ç༺ °¨±â¿¡ °É·ÈÀ» ¶§ ¼¼±Õ¿¡ ÀÇÇÑ Æó·ÅÀÌ µÚµû¸£´Â °æ¿ì¸¦ À̸¥´Ù. Æó·Å±Õ, È­³ó¾Ë±Õ, ´ëÀå±Õ µûÀ§°¡ ÀÖ´Ù. 
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • akinetic epilepsy
    ¹«¿îµ¿°£Áú
  • cryptogenic epilepsy
    Àẹ°£Áú
  • epilepsy
    °£Áú
  • focal epilepsy
    ÃÊÁ¡°£Áú
  • frontal lobe epilepsy
    À̸¶¿±°£Áú, ÀüµÎ¿±°£Áú
  • generalized epilepsy
    Àü½Å°£Áú
  • grand mal epilepsy
    ´ë¹ßÀÛ°£Áú
  • hysterical epilepsy
    È÷½ºÅ׸®°£Áú
  • hereditary epilepsy
    À¯Àü°£Áú
  • idiopathic epilepsy
    Ư¹ß°£Áú
  • juvenile myoclonic epilepsy
    û¼Ò³â±Ù(À°)°£´ë°£Áú
  • latent epilepsy
    ÀáÀç°£Áú
  • localized epilepsy
    ±¹¼Ò°£Áú
  • major epilepsy
    ´ë°£Áú
  • minor epilepsy
    ¼Ò°£Áú
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epilepsy
    °£Áú
  • focal epilepsy
    ¿îµ¿ÁßÃß¼Õ»ó°£Áú, ÃÊÁ¡°£Áú
  • generalized epilepsy
    Àü½Å°£Áú
  • localized epilepsy
    ±¹¼Ò°£Áú
  • petit mal epilepsy
    ¼Ò¹ßÀÛ
  • temporal lobe epilepsy
    °üÀÚ¿±°£Áú, ÃøµÎ¿±°£Áú
  • secondary sexual character
    ÀÌÂ÷¼ºÂ¡
  • secondary wound closure
    ÀÌÂ÷»óóºÀÇÕ
  • secondary dentition
    (¢¡permanent tooth) °£´Ï, ¿µ±¸Ä¡¾Æ
  • secondary hemostasis
    ÀÌÂ÷ÁöÇ÷
  • secondary infection
    ÀÌÂ÷°¨¿°
  • secondary nodule
    (¢¡germinal center) Á¾ÀÚÁß½É, ¹èÁß½É
  • secondary
    ÀÌÂ÷-, Á¦ÀÌ-, ¼Ó¹ß-
  • secondary suture
    ÀÌÂ÷ºÀÇÕ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • secondary amenorrhea
    ÀÌÂ÷¹«¿ù°æ, ¼Ó¹ß¹«¿ù°æ
  • secondary aqueous
    Àç»ý¹æ¼ö, ÀÌÂ÷¹æ¼ö
  • secondary cardiomyopathy
    ÀÌÂ÷½ÉÀå±ÙÀ°º´Áõ
  • secondary constriction
    ÀÌÂ÷ÇùÂø
  • secondary contact
    ÀÌÂ÷Á¢ÃË
  • secondary culture
    µÎ¹øÂ°½É±â
  • secondary biliary cirrhosis
    ¼Ó¹ß¾µ°³°ü°£°æÈ­(Áõ)
  • secondary dentition
    (¢¡permanent tooth) °£´Ï, ¿µ±¸Ä¡¾Æ
  • secondary disease
    ¼Ó¹ßº´
  • secondary dysmenorrhea
    ÀÌÂ÷¿ù°æÅë
  • secondary ending
    ÀÌÂ÷Á¾¸»
  • secondary gout
    ÀÌÂ÷Åëdz
  • secondary hemorrhage
    ¼Ó¹ßÃâÇ÷, ÀÌÂ÷ÃâÇ÷
  • secondary hypertension
    ÀÌÂ÷°íÇ÷¾Ð
  • secondary hypogonadism
    ¼Ó¹ß»ý½Ä»ùÀúÇÏÁõ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • grand mal epilepsy See epilepsy
    ´ë¹ßÀÛ°£Áú(ÓÞÛ¡íÂÊÖòð)
  • haploid secondary gametocyte
    Ȭ¹è¼öüÀÌÂ÷»ý½Ä¼¼Æ÷
  • immune response, secondary
    ÀÌÂ÷¸é¿ª¹ÝÀÀ
  • immunodeficiency syndrome, secondary
    ÀÌÂ÷¼º ¸é¿ª°áÇÌ ÁõÈıº, ¼Ó¹ß¼º ¸é¿ª°áÇÌ ÁõÈıº
  • infection, secondary
    ÀÌÂ÷°¨¿°
  • process, secondary (psychic)
    ÀÌÂ÷°úÁ¤.
  • Jacksonian epilepsy
    Àè½¼°£Áú.
  • abortive epilepsy
    ºÎÀü°£Áú.
  • affect epilepsy
    Á¤µ¿¼º °£Áú(ï×ÔÑàõÊÖòð).
  • arithmetical epilepsy
    »ê¼ú¼º °£Áú
  • genuine epilepsy
    Áø¼º°£Áú.
  • grand mal epilepsy
    ´ë¹ßÀÛ°£Áú.
  • gustatory epilepsy
    ¹Ì°¢¼º °£Áú.
  • hereditary epilepsy
    À¯Àü¼º °£Áú(¡­ÊÖòð).
  • hiernosus =epilepsy
    °£Áú(ÊÖòð).
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • grand mal epilepsy See epilepsy
    ´ë¹ßÀÛ°£Áú(ÓÞÛ¡íÂÊÖòð)
  • secondary yolk sac [secondary vitelline sac]
    ÀÌÂ÷³­È²ÁÖ¸Ó´Ï
  • abdominal epilepsy
  • abortive epilepsy
    ºÎÀü°£Áú.
  • affect epilepsy
    Á¤µ¿¼º °£Áú(ï×ÔÑàõÊÖòð).
  • akinetic epilepsy
    ¹«µ¿¼º °£Áú(¡­ÊÖòð).
  • alcoholic epilepsy
    ¾ËÄڿüº °£Áú(¡­ÊÖòð).
  • arithmetical epilepsy
    »ê¼ú¼º °£Áú
  • autonomic epilepsy
    ÀÚÀ²½Å°æ°è °£Áú
  • benign partial epilepsy of childhood
    ¼Ò¾Æ±â ¾ç¼ººÎºÐ°£Áú
  • centrencephalic epilepsy
    Á߽ɳú¼º°£Áú(ñéãýÒààõÊÖòð).
  • childhood absence epilepsy
    ¼Ò¾Æ±â °á½Å¹ßÀÛ
  • complex myoclonic epilepsy
  • cortical epilepsy
    ÇÇÁú(¼º)°£Áú(¡­ÊÖòõ).
  • cryptogenic epilepsy
    Àẹ¼º °£Áú.
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Secondary yolk sac [Secondary vitelline sac]
    ÀÌÂ÷³­È²ÁÖ¸Ó´Ï
    [¿¾ ¿ë¾î] ÀÌÂ÷³­È²³¶
  • Secondary segmental bronchus
    ±¸¿ª±â°üÁö°¡Áö
    [¿¾ ¿ë¾î] ÀÌÂ÷±¸±â°üÁö
  • Secondary tympanic membrane
    µÑ°°í¸·
    [¿¾ ¿ë¾î] Á¦ÀÌ°í¸·
  • Secondary spiral lamina
    µÑ°³ª¼±ÆÇ
    [¿¾ ¿ë¾î] Á¦2³ª¼±ÆÇ
  • Secondary fissure
    µÑ°ƴ»õ
    [¿¾ ¿ë¾î] Á¦2¿­
  • Secondary polar body
    ÀÌÂ÷±ØÃ¼
    [¿¾ ¿ë¾î] ÀÌÂ÷±ØÃ¼
  • Secondary oocyte
    ÀÌÂ÷³­¸ð¼¼Æ÷
    [¿¾ ¿ë¾î] ÀÌÂ÷³­¸ð¼¼Æ÷
  • Secondary oocyte, Metaphase II
    ÀÌÂ÷³­¸ð¼¼Æ÷, ÀÌÂ÷°¨¼öºÐ¿­Áß±â
    [¿¾ ¿ë¾î] Á¦À̳­¸ð¼¼Æ÷,ÀÌÂ÷Áß±â
  • Secondary follicle
    ÀÌÂ÷³­Æ÷
    [¿¾ ¿ë¾î] ÀÌÂ÷³­Æ÷
  • Secondary ovarian follicle
    ÀÌÂ÷³­Æ÷
    [¿¾ ¿ë¾î] ÀÌÂ÷³­Æ÷
  • Secondary visceral nucleus
    ÀÌÂ÷³»Àå½Å°æÇÙ
    [¿¾ ¿ë¾î] Á¦2Àå½Å°æÇÙ
  • Secondary abdominal implantation
    ÀÌÂ÷¹è¾ÈÂø»ó
    [¿¾ ¿ë¾î] ÀÌÂ÷Àûº¹ºÎÂø»ó
  • Secondary bone
    ÀÌÂ÷»À
    [¿¾ ¿ë¾î] ÀÌÂ÷°ñ
  • Secondary osteon
    ÀÌÂ÷»À´ÜÀ§
    [¿¾ ¿ë¾î] ÀÌÂ÷°ñ¿ø
  • Secondary osteogenic bud
    ÀÌÂ÷»À¹ß»ý½Ï
    [¿¾ ¿ë¾î] ÀÌÂ÷°ñÇü¼º¾Æ
´ëÇѱâ»ýÃæÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • secondary amebic meningoencephalitis
    ÀÌÂ÷¾Æ¸Þ¹Ù¼ö¸·³ú¿°
  • secondary echinococcosis
    ÀÌÂ÷Æ÷ÃæÁõ
  • secondary infection
    ÀÌÂ÷°¨¿°
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • secondary acidosis
    ÀÌÂ÷ »êÁõ(ì£ó­ß«ñø)
  • secondary active transport
    ÀÌÂ÷ ´Éµ¿¼ö¼Û(ì£ó­ÒöÔÑâÃáê)
  • secondary alkalosis
    ÀÌÂ÷(ì£ó­) ¾ËÄ®¸®Áõ(ñø)
  • secondary bile acid
    ÀÌÂ÷ ´ãÁó»ê(ì£ó­ÓÅñðß«)
  • secondary bond
    ÀÌÂ÷ °áÇÕ(ì£ó­Ì¿ùê)
  • secondary charge effect
    ÀÌÂ÷ ÇÏÀüÈ¿°ú(ì£ó­ùÃï³üùÍý)
  • secondary culture
    ÀÌÂ÷ ¹è¾ç(ì£ó­ÛÆå×)
  • secondary deficiency
    ÀÌÂ÷ °áÇÌ(ì£ó­ÌÀù¹)
  • secondary derived protein
    ÀÌÂ÷ À¯µµ´Ü¹éÁú(ì£ó­ë¯ÓôÓ±ÛÜòõ)
  • secondary electron
    ÀÌÂ÷ ÀüÀÚ(ì£ó­ï³í­)
  • secondary fluor
    ÀÌÂ÷ Çü±¤Á¦(ì£ó­û«ÎÃð¥)
  • secondary hydration shell
    ÀÌÂ÷(ì£ó­) ¼öÈ­ â©ûù ²®Áú
  • secondary ionization
    ÀÌÂ÷(ì£ó­) ÀÌ¿ÂÈ­(ûù)
  • secondary ion mass spectrometry
    ÀÌÂ÷ ÀÌ¿ÂÁú·®ºÐ±¤¹ý(ì£ó­òõÕáÝÂÎÃÛö)
  • secondary isotope effect
    ÀÌÂ÷ µ¿À§¿ø¼ÒÈ¿°ú(ì£ó­ÔÒêÈêªáÈüùÍý)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epilepsy
    °£Áú
  • focal epilepsy
    ÃÊÁ¡¼º °£Áú, ¿îµ¿ ÁßÃß ¼Õ»ó¼º °£Áú, ÀÛ¼Õ°£Áú
  • hysterical epilepsy
    È÷½ºÅ׸®¼º°£Áú
  • temporal epilepsy
    ÃøµÎ¼º °£Áú
  • secondary
    ÀÌÂ÷(¼º)ÀÇ, ¼Ó¹ß(¼º)ÀÇ
  • secondary anemia
    ¼Ó¹ß¼ººóÇ÷
  • secondary infection
    ÀÌÂ÷°¨¿°, ¼Ó¹ß°¨¿°
  • secondary lesion
    ÀÌÂ÷¼ºº´º¯, ÀÌÂ÷¹ßÁø, ¼Ó¹ßÁø
  • secondary ossification center
    ÀÌÂ÷°ñÈ­Áß½É
  • secondary pneumonia
    ¼Ó¹ß¼ºÆó·Å
  • secondary sex characteristic
    ÀÌÂ÷¼ºÂ¡
  • secondary sterility
    ¼Ó¹ßºÒÀÓ
  • secondary tuberculosis
    ÀÌÂ÷¼º°áÇÙ
  • secondary X-ray
    ÀÌÂ÷X¼±
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
SA salicylic acid; saline [solution]; salt added; sarcoidosis; sarcoma; scalenus anticus; secondary ame...
TLE Temporal Lobe Epilepsy; ÃøµÎ¿± °£Áú
  = Psychomotor Epilepsy; Á¤½Å ¿îµ¿ °£Áú
  = Tem...
SGE secondary generalized epilepsy
JVP [POMD P 49 - 52]
  1) Jugular Vein Pressure
  2) Jugular Venous Pulse
...
CPSC congenital paucity of secondary synaptic clefts [syndrome]; Consumer Products Safety Commission
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
GAM Generalised Additive Models
GAD Generalised Anxiety Disorder
GLM Generalised Linear Model
GABEB Generalised atrophic benign epidermolysis bullosa
GCSE Generalised convulsive status epilepticus
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • abortive epilepsy
    ºÎÀü °£Áú
    ´ë¹ßÀÛÀÇ µ·ÁÂÀû, ¶Ç´Â ÈçÀûÀû ¹ßÀÛÀ̶ó°í »ý°¢µÇ´Â °¡º­¿î ¹ßÀÛ. Àü½Å °æ·ÃÀ» µ¿¹ÝÇÏÁö ¾Ê°í Àá½Ã Áö¼ÓÇÏ´Â ½Åü ¶Ç´Â Á¤½Å Áõ»óÀ̸ç, ¶§·Î´Â ÀüÁ¶
  • affect epilepsy
    Á¤µ¿¼º °£Áú
  • akinetic epilepsy
    ¹«µ¿¼º °£Áú
  • epilepsy
    °£Áú
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  • focal epilepsy
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  • Jackson's epilepsy
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  • juvenile myoclonic epilepsy
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  • myoclonic epilepsy and raggedred fibers
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  • peripheral epilepsy
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  • petit mal epilepsy
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  • post-traumatic epilepsy
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  • temporal epilepsy
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  • traumatic epilepsy
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  • uncinate epilepsy
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  • brain vesicle`s secondary
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CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
secondary generalised epilepsy A group of epilepsy syndromes of diverse aetiologies with diffuse or multifocal cerebral involvement. Patients typically have a variety of generalised seizure types, including tonic, atonic, myoclonic, atypical absence, and generalised tonic-clonic seizures. Partial seizures may also occur. One classic syndrome is the Lennox-Gastaut syndrome.
Synonym: symptomatic epilepsy.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
generalised epilepsy A major category of epilepsy syndromes characterised by one or more types of generalised seizures.
(05 Mar 2000)
generalised tonic-clonic epilepsy tonic-clonic seizure
primary generalised epilepsy Epilepsy without evidence of focal or multifocal central nervous system disease. Seizures are generalised from onset, both by EEG and clinical criteria. Often a pure genetic form of epilepsy.
See: generalised tonic-clonic seizure.
(05 Mar 2000)
epilepsy, generalised Epileptic seizures in which the first clinical changes indicate initial involvement of both hemispheres of the brain, as opposed to epileptic seizures involving a particular focal point of the brain (epilepsy, partial). Generalised seizures can be convulsive or non-convulsive. Consciousness may be impaired and this impairment may be the initial manifestation of the seizure. Motor manifestations, if present, are also bilateral.
(12 Dec 1998)
generalised <zoology> Comprising structural characters which are separated in more specialized forms; synthetic; as, a generalised type.
Source: Websters Dictionary
(01 Mar 1998)
generalised anaphylaxis The immediate response, involving smooth muscles and capillaries throughout the body of a sensitised individual, that follows intravenous (and occasionally intracutaneous) injection of antigen (allergen).
See: anaphylactic shock.
Synonym: systemic anaphylaxis.
(05 Mar 2000)
generalised anxiety disorder Chronic, repeated episodes of anxiety reactions; a psychological disorder in which anxiety or morbid fear and dread accompanied by autonomic changes are prominent features.
See: anxiety.
(05 Mar 2000)
generalised chondromalacia A degenerative disease of cartilage producing a bizarre form of arthritis, with collapse of the ears, the cartilaginous portion of the nose, and the tracheobronchial tree; death may occur from chronic infection or suffocation because of loss of stability in the tracheobronchial tree of autosomal origin.
Synonym: chronic atrophic polychondritis, generalised chondromalacia, Meyenburg's disease, Meyenburg-Altherr-Uehlinger syndrome, relapsing perichondritis, systemic chondromalacia, von Meyenburg's disease.
(05 Mar 2000)
generalised cortical hyperostosis <syndrome> An inherited skeletal dysplasia, with mandibular enlargement and thickening of the diaphyses and calvaria, and increased serum alkaline phosphatase; autosomal recessive inheritance.
Synonym: generalised cortical hyperostosis.
(05 Mar 2000)
generalised elastolysis A group of connective tissue diseases in which skin hangs in loose pendulous folds. It is believed to be associated with decreased elastic tissue formation as well as an abnormality in elastin formation. Cutis laxa is usually a genetic disease, but acquired cases have been reported.
(12 Dec 1998)
generalised emphysema Emphysema affecting all parts of the lobules, in part, or usually the whole, of the lungs, and usually associated with a1-antiprotease deficiency emphysema.
Synonym: diffuse emphysema, generalised emphysema, panacinar emphysema.
(05 Mar 2000)
generalised epidermolytic hyperkeratosis Diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterised by generalised epidermolytic hyperkeratosis and autosomal dominant inheritance.
See: epidermolytic hyperkeratosis.
Synonym: generalised epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix.
(05 Mar 2000)
generalised eruptive histiocytoma A rare recurring generalised eruption in adults of flesh coloured or erythematous papules remaining localised to the skin and consisting of dermal nodules of mononuclear histiocytes that do not stain for lipid.
Synonym: nodular non-X histiocytosis.
(05 Mar 2000)
generalised gangliosidosis Three forms exist: infantile, generalised; juvenile; and adult; gangliosidosis characterised by accumulation of a specific monosialoganglioside, GM1; due to deficiency of GM1-beta-galactosidase.
Synonym: generalised gangliosidosis.
(05 Mar 2000)
generalised glycogenosis Glycogenosis due to lysosomal alpha-1,4-glucosidase deficiency, resulting in accumulation of excessive amounts of glycogen of normal chemical structure in heart, muscle, liver, and nervous system.
Synonym: generalised glycogenosis, Pompe's disease.
(05 Mar 2000)
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