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SBH sea-blue histiocyte
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sea-blue histiocyte A histiocyte containing cytoplasmic granules that stain bright blue with haematologic stains such as Wright-Giemsa; found in bone marrow and in the spleen, associated with hepatosplenomegaly and thrombocytopenic purpura and in other blood diseases.
(05 Mar 2000)
sea-blue histiocyte disease Splenomegaly and mild thrombocytopenia, with histiocytes in the bone marrow which contain cytoplasmic granules that stain bright blue; sometimes familial; perhaps a lipidosis; autosomal recessive inheritance.
(05 Mar 2000)
sea-blue histiocyte syndrome <syndrome> Rare disorder consisting of splenomegaly, mild purpura secondary to thrombocytopenia, and occasionally, hepatic cirrhosis associated with the appearance of numerous histiocytes in the spleen and bone marrow which stain a sea-blue colour. It is sometimes considered a variant of niemann-pick disease.
(12 Dec 1998)
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cardiac histiocyte A large mononuclear cell found in connective tissue of the heart wall in inflammatory conditions, especially in the Aschoff body. The ovoid nucleus contains a central chromatin mass appearing as a wavy bar in longitudinal section.
Synonym: Anitschkow cell, Anitschkow myocyte, caterpillar cell.
(05 Mar 2000)
histiocyte <pathology> Long lived resident macrophage found within tissues.
(11 Jan 1998)
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  • Sea-Blue Histiocyte Syndrome - »õâ A congenital disease caused by an inborn error involving APOLIPOPROTEIN E leading to abnormal LIPID METABOLISM and the accumulation of GLYCOSPHINGOLIPIDS, particularly SPHINGOMYELINS in the HISTIOCYTES. This disorder is characterized by SPLENOMEGALY and the sea-blue histiocytes in the spleen and bone marrow after May Grunwald staining.
    Synonyms : Histiocyte Syndrome, Sea Blue, Histiocyte Syndromes, Sea Blue, Sea Blue Histiocytosis, Histiocyte Syndrome, Sea-Blue, Histiocyte Syndromes, Sea-Blue, Histiocytoses, Sea Blue, Histiocytoses, Sea-Blue, Histiocytosis, Sea Blue, Sea Blue Histiocyte Syndrome
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sea-blue histiocyte s. a rare disorder characterized by the presence of abnormal histiocytes that stain blue with Wright and Giemsa stains (sea-blue histiocytes), accompanied by splenomegaly. Clinically it may range from a benign course with mild purpura secondary to thrombocytopenia, to progressive cirrhosis, hepatic failure, and death. The etiology is unknown, but sometimes it is inherited as an autosomal recessive condition. Called also sea-blue histiocytosis.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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