| Schilder's disease | Term used to describe at least two separate disorders described by Schilder: 1) Diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterised by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetrical area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) The leukodystrophies. Synonym: encephalitis periaxialis diffusa, Flatau-Schilder disease. (05 Mar 2000) |
|---|
| schilder syndrome | <radiology> Sudanophilic leukodystrophy, males (2:1), onset prepuberty, rapidly progressive demyelinating disease, weakness may lead to paralysis, apathy may lead to stupor, death usually in months, occipital and temporal most severely affected (12 Dec 1998) |
|---|---|
| Flatau-Schilder disease | Term used to describe at least two separate disorders described by Schilder: 1) Diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterised by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetrical area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) The leukodystrophies. Synonym: encephalitis periaxialis diffusa, Flatau-Schilder disease. (05 Mar 2000) |
| Schilder's d. |
a subacute or chronic form of leukoencephalopathy of children and adolescents. Clinical symptoms include blindness, deafness, bilateral spasticity, and progressive mental deterioration. There is massive destruction of the white substance of the cerebral hemispheres, cavity formation, and glial scarring. The disease as a separate diagnostic entity has been disputed. It usually occurs sporadically, but a familial form has been reported. Called also encephalitis periaxialis diffusa, Flatau-Schilder d., and Schilder's encephalitis.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|---|
| Schilder's disease (encephalitis) |
see under disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| Schilder's e. |
see under disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
Á¦Ç°¸í |
ÆÇ¸Å»ç |
º¸ÇèÄÚµå | ¼ººÐ/ÇÔ·® | ±¸ºÐ/º¸Çè±Þ¿© |
|---|
Á¦Ç°¸í |
ÆÇ¸Å»ç |
º¸ÇèÄÚµå | ¼ººÐ/ÇÔ·® | ±¸ºÐ/º¸Çè±Þ¿© |
|---|