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  • properdin system
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P Properdin
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properdin <protein> Component of the alternative pathway for complement activation: complexes with C3b and stabilises the alternative pathway C3 convertase (C3bBbP) that cleaves C3.
(18 Nov 1997)
properdin factor A A component of the properdin system; a hydrazine-sensitive b1-globulin (mw about 180,000), now known to be C3 (third component of complement).
(05 Mar 2000)
properdin factor b <enzyme> A glycine-rich, heat-labile beta-glycoprotein found in blood. It is a proactivator of complement 3 in the alternate pathway of complement activation. Factor b is converted by factor d to c3 convertase.
Registry number: EC 3.4.21.47
(12 Dec 1998)
properdin factor d <enzyme> A serum protein which during the alternate pathway of complement activation converts the inactive properdin factor b to c3 convertase.
Registry number: EC 3.4.21.46
(12 Dec 1998)
properdin factor E A serum protein (mw 160,000) required for activation of C3 (third component of complement) by cobra venom factor.
See: properdin system.
(05 Mar 2000)
properdin system An immunological system that is the alternative pathway for complement, composed of several distinct proteins that react in a serial manner and activate C3 (third component of complement), seemingly without utilizing components C1, C4, and C2; in addition to properdin, the system includes properdin factors A (native C3), B (C3 proactivator), D (C3 proactivator convertase), and perhaps at least one other, E; the system can be activated, in the absence of specific antibody, by bacterial endotoxins, by a variety of polysaccharides and lipopolysaccharides, and by a component of cobra venom.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Properdin - »õâ A 53-kDa protein that is a positive regulator of the alternate pathway of complement activation (COMPLEMENT ACTIVATION PATHWAY, ALTERNATIVE). It stabilizes the ALTERNATIVE PATHWAY C3 CONVERTASE (C3bBb) and protects it from rapid inactivation, thus facilitating the cascade of COMPLEMENT ACTIVATION and the formation of MEMBRANE ATTACK COMPLEX. Individuals with mutation in the PFC gene exhibit properdin deficiency and have a high susceptibility to infections.
    Synonyms : Factor P, Complement
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properdin a nonimmunoglobulin gamma globulin component of the alternative pathway of complement activation; it complexes with C3b and stabilizes alternative pathway C3 and C5 convertases (C3bBb and C3bnBb). Called also factor P.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
properdin p. former name for alternative complement p.; see complement.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
properdin s. former name for the alternative complement pathway.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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