| 영문 | dwarfism | 한글 | 난쟁이, 왜소증 |
|---|---|---|---|
| 설명 | 신장발육이 부진하여 표준보다 훨씬 키가 작은 경우, 또는 그런 사람을 말한다. 병명도 주유증, 소치증, 유치증, 발육부전, 왜소증 등 여러 가지이다. 같은 인종, 같은 연령의 평균 키에 대한 표준편차의 3~4배가 작을 경우, 성인의 경우 1m미만인 경우로 정의하고 있으나 그 판단기준이 애매하다. 난쟁이 중에서 지능 및 생식기의 발육장애가 없고 연령과 뼈의 X-선 촬영으로 측정되는 골연령이 일치되어 있는 경우를 원발난쟁이(primordial dwarfism)라 한다. 이 경우에는 유전적 소인 외에는 원인이 될 만한 결함을 찾을 수 없다고 한다. 대뇌의 밑부분에 존재하면서 여러 가지 호르몬을 분비하는 뇌하수체의 이상으로 인해서 뼈의 성장에 관여하는 성장호르몬의 분비 저하에 의한 소인증을 하수체난쟁이(pituitary dwarfism)라고 한다. 즉 종양, 외상 등으로 인해서 뇌하수체 부위에 기질적인 변화가 생기거나 원인이 없이 성장 호르몬의 분비 저하가 되는 경우이다. 지능의 발육 정도는 비교적 양호하지만 대개 제2차 성징을 볼 수 없다. 성인이 될 때까지 갑상선 기능이 쇠퇴해서 호르몬 분비량이 적어서 일어나는 갑상샘성 난쟁이가 있다. 어릴 때 갑상샘제거수술을 해도 같은 결과가 된다. 손발의 성장이 정지될 뿐 아니라, 지능-정신의 발육부전을 동반한다. 얼굴은 어린애같지만 피부에 주름이 잡혀 노인같이 보인다. |
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| MOPD | microcephalic osteodysplastic primordial dwarfism |
|---|---|
| PGC | progastricin; primordial germ cell |
| CMD | campomelic dysplasia; camptomelic dwarfism; cartilage matrix deficiency; chief medical director; chi... |
| LTD | Laron-type dwarfism; leukotriene D; long-term disability |
| TD | tabes dorsalis; tardive dyskinesia; T-cell dependent; temporary disability; terminal device; tetanus... |
| LTD | Laron type dwarfism |
|---|---|
| PGC | Primordial germ cell |
| primordial dwarfism | Dwarfism characterised by normal development that is at a strikingly lesser rate than that for members of the same family, race, or other races. Synonym: primordial dwarfism, true dwarfism. (05 Mar 2000) |
|---|
| primordial | 1. First in order; primary; original; of earliest origin; as, primordial condition. "The primordial facts of our intelligent nature." 2. <geology> Of or pertaining to the lowest beds of the Silurian age, corresponding to the Acadian and Potsdam periods in American geology. It is called also Cambrian, and by many geologists is separated from the Silurian. 3. <biology> Originally or earliest formed in the growth of an individual or organ; as, a primordial leaf; a primordial cell. <botany> Primordial utricle, the interior lining of a young vegetable cell. Origin: L. Primordialis, from primordium the first beginning; primus first + ordiri to begin a web, to begin: cf. F. Primordial. Source: Websters Dictionary (01 Mar 1998) |
|---|---|
| primordial cartilage | Cartilage in an early stage in its development. (05 Mar 2000) |
| primordial cell | A cell from a group that constitutes the primordium of an organ or part of the embryo. (05 Mar 2000) |
| primordial cyst | A cyst which develops in place of a tooth through cystic degeneration of the enamel organ prior to formation of calcified odontogenic tissue. (05 Mar 2000) |
| primordial germ cell | The most primitive undifferentiated sex cell, found initially outside the gonad. Synonym: gonocyte. (05 Mar 2000) |
| primordial gigantism | Unusually large size from birth due to familial or genetic factors or intrauterine environment (e.g., maternal prediabetic state) and not to hyperpituitarism. (05 Mar 2000) |
| primordial kidney | 1. The definitive excretory organ of primitive fishes. Synonym: head kidney. 2. In the embryos of higher vertebrates, a vestigial structure consisting of a series of tortuous tubules emptying into the cloaca by way of the primary nephric duct; in the human embryo, the pronephros is a very rudimentary and temporary structure, followed by the mesonephros and still later by the metanephros. Synonym: forekidney, primordial kidney. Origin: pro-+ G. Nephros, kidney (05 Mar 2000) |
| primordial ovarian follicle | A follicle in which the primordial oocyte is surrounded by a single layer of flattened follicular cells. (05 Mar 2000) |
| achondroplastic dwarfism | See: achondroplasia. (05 Mar 2000) |
| acromelic dwarfism | A form of dwarfism in which shortening is striking in the most distal segment of the limbs; autosomal recessive inheritance. Synonym: acromelic dwarfism. Origin: acro-+ G. Melos, limb, + ia, condition (05 Mar 2000) |
| aortic dwarfism | Underdevelopment of physical stature associated with severe aortic stenosis. (05 Mar 2000) |
| asexual dwarfism | Dwarfism in which adult sexual development is deficient. (05 Mar 2000) |
| ateliotic dwarfism | A state in which the secretion of all anterior pituitary hormones is inadequate or absent; caused by a variety of disorders that result in destruction or loss of function of all or most of the anterior pituitary gland. Rare forms of PHP are inherited as autosomal recessive or as an X-linked recessive. Synonym: ateliotic dwarfism, hypophyseal cachexia, hypophysial cachexia. (05 Mar 2000) |
| camptomelic dwarfism | Dwarfism with shortening of the lower limbs due to anterior bending of the femur and tibia. (05 Mar 2000) |
| panhypopituitary dwarfism | Type I is an autosomal recessive disorder with deficient human growth hormone, ACTH, FSH, etc., having delayed sexual development, hypothyroidism, and adrenal insufficiency; type II is similar but is an X-linked disorder. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|