¼±Åà - È­»ìǥŰ/¿£ÅÍŰ ´Ý±â - ESC

 
"primary telangiectasia"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • ataxia telangiectasia
    ¸ð¼¼°üÈ®Àå½ÇÁ¶
  • essential telangiectasia
    º»Å¸ð¼¼Ç÷°üÈ®Àå(Áõ)
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¸ð¼¼Ç÷°üÈ®ÀåÁõ
  • periungual telangiectasia
    ¼Õ¹ßÅéÁÖÀ§¸ð¼¼Ç÷°üÈ®Àå(Áõ)
  • spider telangiectasia
    °Å¹Ì¸ð¼¼Ç÷°üÈ®Àå(Áõ)
  • telangiectasia
    ¸ð¼¼Ç÷°üÈ®Àå(Áõ)
  • unilateral nevoid telangiectasia
    ÀÏÃø¸ð¹Ý¸ð¼¼Ç÷°üÈ®Àå(Áõ)
  • delayed primary suture
    Áö¿¬ÀÏÂ÷ºÀÇÕ
  • primary
    ÀÏÂ÷-, ¿ø¹ß-
  • primary action
    ÀÏÂ÷ÀÛ¿ë
  • primary affect hunger
    ÀÏÂ÷Á¤µ¿°¥¸Á, ÀÏÂ÷¾ÖÁ¤°¥¸Á
  • primary aldosteronism
    ¿ø¹ß¾Ëµµ½ºÅ×·ÐÁõ
  • primary amebic meningoencephalitis
    ¿ø¹ß¾Æ¸Þ¹Ù¼ö¸·³ú¿°
  • primary amenorrhea
    ¿ø¹ß¹«¿ù°æ
  • primary amnion
    ÀÏÂ÷¾ç¸·, ¿ø½Ã¾ç¸·
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • telangiectasia
    ¸ð¼¼Ç÷°üÈ®Àå, ½ÇÇÍÁÙÈ®Àå
  • primary aldosteronism
    ÀÏÂ÷¾Ëµµ½ºÅ×·ÐÁõ
  • primary cancer
    ¿ø¹ß¾Ï
  • primary constriction
    (¢¡centromere) ¸Åµì, µ¿¿øÃ¼, Áß½ÉÀý
  • primary health care
    ÀÏÂ÷º¸°ÇÀÇ·á
  • primary cholestatic liver disease
    ÀÏÂ÷¾µ°³ÁóÁ¤Ã¼°£Áúȯ, ÀÏÂ÷´ãÁóÁ¤Ã¼°£Áúȯ
  • primary irritant dermatitis
    ¿ø¹ßÀÚ±ØÇǺο°
  • primary infection
    ÀÏÂ÷°¨¿°
  • primary
    ¿ø¹ß-, ÀÏÂ÷-
  • primary polydipsia
    ¿ø¹ß¼º´ÙÀ½Áõ, ÀÏÂ÷Àû´ÙÀ½Áõ, ¿ø¹ß¼º´ÙÀ½´Ù°¥Áõ, ÀÏÂ÷Àû´ÙÀ½´Ù°¥Áõ
  • spontaneous primary peritonitis
    ¿ø¹ßº¹¸·¿°, ÀÏÂ÷º¹¸·¿°, ¿ø¹ß¹è¸·¿°, ÀÏÂ÷¹è¸·¿°
  • primary stage
    Ãʱâ
  • primary suture
    ÀÏÂ÷ºÀÇÕ
  • occult primary tumor
    Àẹ¿ø¹ßÁ¾¾ç
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • ataxia telangiectasia
    ¸ð¼¼Ç÷°üÈ®À强Á¶È­¿îµ¿ºÒ´É
  • arborizing telangiectasia
    ºÐÁö¸ð¼¼Ç÷°üÈ®ÀåÁõ, °¡Áö½ÇÇÍÁÙÈ®ÀåÁõ
  • essential telangiectasia
    º»Å¸ð¼¼Ç÷°üÈ®ÀåÁõ,
  • hereditary hemorrhagic telangiectasia
    À¯ÀüÃâÇ÷¸ð¼¼Ç÷°üÈ®ÀåÁõ, À¯ÀüÃâÇ÷½ÇÇÍÁÙÈ®ÀåÁõ
  • periungual telangiectasia
    ¼Õ¹ßÅéÁÖÀ§¸ð¼¼Ç÷°üÈ®ÀåÁõ
  • spider telangiectasia
    (¢¡spider telangiectasis) °Å¹Ì¸ð¼¼Ç÷°üÈ®ÀåÁõ, °Å¹Ì½ÇÇÍÁÙÈ®ÀåÁõ
  • telangiectasia
    ½ÇÇÍÁÙÈ®ÀåÁõ, ¸ð¼¼Ç÷°üÈ®ÀåÁõ
  • telangiectasia
    Âü½ÇÇÍÁÙÈ®ÀåÁõ
  • unilateral nevoid telangiectasia
    ÀÏÃø¸ð¹Ý¸ð¼¼Ç÷°üÈ®ÀåÁõ, ÇÑÂʸð¹Ý½ÇÇÍÁÙÈ®ÀåÁõ
  • primary action
    ÀÏÂ÷ÀÛ¿ë, ÀÏÂ÷±â´É
  • primary amenorrhea
    ¿ø¹ß¹«¿ù°æ, ÀÏÂ÷¹«¿ù°æ
  • primary amnion
    ¿ø½Ã¾ç¸·, ÀÏÂ÷¾ç¸·
  • primary amyloidosis
    ¿ø¹ß¾Æ¹Ð·ÎÀ̵åÁõ
  • primary aqueous
    ¿ø¹æ¼ö, ÀÏÂ÷¹æ¼ö
  • primary olfactory receiving area
    ÀÏÂ÷Èİ¢¿µ¿ª
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • CRST(Calcinosis, Raynauds phenomenon, Sclerodactyly, Telangiectasia) syndrome
    CRST ÁõÈıº.
  • arborizing telangiectasia
    ºÐÁö ¸ð¼¼Ç÷°ü È®Àå
  • generalized essential telangiectasia
    Àü½Å¼º º»Å¼º ¸ð¼¼Ç÷°ü È®Àå(Áõ)
  • hereditary hemorhagic telangiectasia(osler-weber-rendu disease,)
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°ü È®Àå
  • hereditary hemorrhagic telangiectasia
    À¯Àü(¼º) ÃâÇ÷¼º ¸ð¼¼(Ç÷)°üÈ®Àå.
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼º ÃâÇ÷ Ç÷°üÈ®Àå
  • pregnancy,spider telangiectasia
    °Å¹Ì¸ð¾çÇ÷°üÈ®ÀåÁõ(¸ð¼¼Ç÷°üÈ®ÀåÁõ)(¡­Ù¼åÆúìηüªíåñø(Ù¾á¬úìηüªíåñø))
  • primary yolk sac [primary vitellin sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
  • primary yolk sac [primary vitelline sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
  • Ghon s primary complex
    °ï¿ø¹ßÁõÈıº.
  • amyloidosis primary
    ¿ø¹ß¼º(ê«Û¡àõ) ¾Æ¹Ð·ÎÀ̵åÁõ.
  • immune response, primary
    ÀÏÂ÷¸é¿ª¹ÝÀÀ
  • immunodeficiency syndrome, primary
    ÀÏÂ÷¼º ¸é¿ª°áÇÌ ÁõÈıº, ¿ø¹ß¼º ¸é¿ª°áÇÌ ÁõÈıº
  • infection, primary
    ÀÏÂ÷°¨¿°
  • interaction, primary
    ÀÏÂ÷»óÈ£ÀÛ¿ë
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • primary yolk sac [primary vitellin sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
  • primary yolk sac [primary vitelline sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
  • primary yolk sac[primary vitelline sac]
  • primary yolk sac[primary vitelline sac]
  • arborizing telangiectasia
    ºÐÁö ¸ð¼¼Ç÷°ü È®Àå
  • ataxia telangiectasia
    Ç÷°üÈ®À强 ¿îµ¿½ÇÁ¶Áõ.
  • ataxia telangiectasia
    ¸ð¼¼Ç÷°üÈ®À强(Ç÷°üÈ®À强) ¿îµ¿½ÇÁ¶Áõ(Ù½á¬úìηüªíåàõê¡ÔÑã÷ðàñø)
  • ataxia-telangiectasia
    Ç÷°üÈ®À强 ¿îµ¿½ÇÁ¶Áõ
  • ataxia-telangiectasia
    ¸ð¼¼Ç÷°üÈ®À强¿îµ¿½ÇÁ¶
  • essential telangiectasia
    º»Å¼º(Üâ÷¾àõ) ¸ð¼¼Ç÷°ü È®Àå
  • familial telangiectasia
    °¡Á·¼º ¸ð¼¼Ç÷°ü È®Àå
  • generalized essential telangiectasia
    Àü½Å¼º º»Å¼º ¸ð¼¼Ç÷°ü È®Àå(Áõ)
  • hereditary hemorhagic telangiectasia(osler-weber-rendu disease,)
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°ü È®Àå
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼º ÃâÇ÷ Ç÷°üÈ®Àå
  • hereditary hemorrhagic telangiectasia
    À¯Àü(¼º) ÃâÇ÷¼º ¸ð¼¼(Ç÷)°üÈ®Àå.
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Primary yolk sac [Primary vitellin sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
    [¿¾ ¿ë¾î] ÀÏÂ÷³­È²³¶
  • Primary yolk sac [Primary vitelline sac]
    ÀÏÂ÷³­È²ÁÖ¸Ó´Ï
    [¿¾ ¿ë¾î] ÀÏÂ÷³­È²³¶
  • Diploid primary gametocyte
    µÎ¹è¼öüÀÏÂ÷»ý½Ä¼¼Æ÷
    [¿¾ ¿ë¾î] ¹è¼öüÁ¦ÀÏ»ý½Ä¼¼Æ÷
  • Reticulofibrous membranous bone [Primary membranous bone]
    ¼¼¸Á¼¶À¯¸·»À [ÀÏÂ÷¸·»À]
    [¿¾ ¿ë¾î] ÀÏÂ÷¸·¼º°ñ
  • Premaxilla (Primary palate)
    ¾ÕÀ§ÅλÀ [ÀÏÂ÷ÀÔõÀå]
    [¿¾ ¿ë¾î] ¾ÇÀü±¸°³
  • Premaxilla [Primary palate]
    ¾ÕÀ§ÅλÀ [ÀÏÂ÷ÀÔõÀå]
    [¿¾ ¿ë¾î] Àü»ó¾Ç°ñ
  • Primary vitelline sac
    ¿ø½Ã³­È²ÁÖ¸Ó´Ï
    [¿¾ ¿ë¾î] ¿ø½Ã³­È²³¶
  • Primary amnion
    ¿ø½Ã¾ç¸·
    [¿¾ ¿ë¾î] ¿ø½Ã¾ç¸·
  • Primary medullary cavity
    ÀÏÂ÷°ñ¼ö°ø°£
    [¿¾ ¿ë¾î] ÀÏÂ÷°ñ¼ö°­
  • Primary medullary cavity
    ÀÏÂ÷°ñ¼ö°ø°£[ÀÏÂ÷»À¼ÓÁú°ø°£]
    [¿¾ ¿ë¾î] ÀÏÂ÷°ñ¼ö°­
  • Primary polar body
    ÀÏÂ÷±ØÃ¼
    [¿¾ ¿ë¾î] ÀÏÂ÷±ØÃ¼
  • Primary bronchus
    ÀÏÂ÷±â°üÁö
    [¿¾ ¿ë¾î] ¿ø½Ã±â°üÁö
  • Primary oocyte
    ÀÏÂ÷³­¸ð¼¼Æ÷
    [¿¾ ¿ë¾î] ÀÏÂ÷³­¸ð¼¼Æ÷
  • Primary follicle
    ÀÏÂ÷³­Æ÷
    [¿¾ ¿ë¾î] ÀÏÂ÷³­Æ÷
  • Primary ovarian follicle
    ÀÏÂ÷³­Æ÷
    [¿¾ ¿ë¾î] ¿ø½Ã³­Æ÷
´ëÇѱâ»ýÃæÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • primary amebic meningoencephalitis
    ¿ø¹ß¼º¾Æ¸Þ¹Ù¼ö¸·³ú¿°
  • primary infection
    ÀÏÂ÷°¨¿°
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • primary acidosis
    ¿ø¹ß¼º »êÁõ(ê«Û¡àõß«ñø)
  • primary active transport
    ÀÏÂ÷ ´Éµ¿¼ö¼Û(ìéó­ÒöÔÑâÃáê)
  • primary alkali deficit
    ¿ø¹ß¼º(ê«Û¡àõ) ¾ËÄ®¸®°áÇÌ(ÌÀù¹)
  • primary alkali excess
    ¿ø¹ß¼º(ê«Û¡àõ) ¾ËÄ®¸®°úÀ×(Φí¥)
  • primary alkalosis
    ¿ø¹ß¼º(ê«Û¡àõ) ¾ËÄ®¸®Áõ(ñø)
  • primary amino acid
    ÀÏÂ÷(ìéó­) ¾Æ¹Ì³ë»ê(ß«)
  • primary bile acid
    ÀÏÂ÷ ´ãÁó»ê(ìéó­ÓÅñðß«)
  • primary carbon dioxide deficit
    ¿ø¹ß¼º ÀÌ»êȭź¼Ò °áÇÌ(ê«Û¡àõì£ß«ûù÷©áÈÌÀù¹)
  • primary carbon dioxide excess
    ¿ø¹ß¼º ÀÌ»êȭź¼Ò(ê´Û¡àõ ì£ß«ûù÷©áÈ) °úÀ×(Φí¥)
  • primary charge effect
    ÀÏÂ÷ ÀüÇÏÈ¿°ú(ìéó­ï³ùÃüùÍý)
  • primary culture
    ÀÏÂ÷ ¹è¾ç(ìéó­ÛÆå×)
  • primary deficiency
    ¿ø¹ß¼º °áÇÌ(ê«Û¡àõÌÀù¹)
  • primary derived protein
    ÀÏÂ÷ À¯µµ ´Ü¹éÁú(ìéó­ë¯ÓôÓ±ÛÜòõ)
  • primary filament
    ÀÏÂ÷(ìéó­) Çʶó¸àÆ®
  • primary fluor
    ÀÏÂ÷ Çü±¤Ã¼(ìéó­û«ÎÃô÷)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°üÈ®Àå
  • primary
    ÀÏÂ÷(¼º)ÀÇ, Á¦ÀÏÀÇ, ÃʱâÀÇ, ¿ø¹ß(¼º)ÀÇ
  • primary amenorrhea
    ¿ø¹ß(¼º)¹«¿ù°æ
  • primary cancer
    ¿ø¹ß¾Ï
  • primary complex
    Ãʱ⺯ȭ±º
  • primary hypertension
    ¿ø¹ß(¼º)°íÇ÷¾ÐÁõ
  • primary infection
    ÀÏÂ÷°¨¿°
  • primary infiltration
    ÃʱâħÀ±
  • primary lesion
    ÀÏÂ÷¼ºº´º¯, Ãʰ¨¿°¼Ò
  • primary lobule
    ÀÏÂ÷¼Ò¿±
  • primary ossification center
    ÀÏÂ÷°ñÈ­Áß½É
  • primary ray
    ÀÏÂ÷¼±
  • primary tuberculosis
    ÀÏÂ÷°áÇÙ(Áõ), Ãʱâ°áÇÙ(Áõ)
  • primary tumor
    ¿ù¹ßÁ¾¾ç
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
DEF decayed primary teeth requiring filling, decayed primary teeth requiring extraction, and primary tee...
PA panic attack; pantothenic acid; paralysis agitans; paranoia; passive aggressive; pathology; patient'...
PCC Pasteur Culture Collection; percutaneous cecostomy; pheochromocytoma; phosphate carrier compound; pl...
CREST Syndrome   1. Calcinosis cutis
  2. Raynaud's phenomenon
  3. Esophageal ...
CRST Syndrome   1. Calcinosis
  2. Raynaud's Phenomenon
  3. Sclerodactyly
...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
ATM Ataxia Telangiectasia Mutated
HHT Hereditary Haemorrhagic Telangiectasia
HHT1 Hereditary Haemorrhagic Telangiectasia Type 1
primary SS Primary Sjogren's syndrome
COPC Community Oriented Primary Care
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • hereditary telangiectasia
    À¯Àü¼º ¸ð¼¼Ç÷°ü È®ÀåÁõ
    ¼±ÃµÀûÀ¸·Î ¸ð¼¼Ç÷°üÀÌ È®ÀåµÇ´Â ÁúȯÀ¸·Î °üÂû ½Ã ¹ÝÁ¡»ó È«¹ÝÀ¸·Î ³ªÅ¸³ª°í °³º°ÀûÀ¸·Î È®ÀåµÈ Ç÷°ü ¾ç»óÀ» °üÂûÇÒ ¼ö ÀÖ´Ù.
  • telangiectasia
    ¸ð¼¼°ü È®ÀåÁõ, ¸ð¼¼Ç÷°ü È®ÀåÁõ
    µ¿ÀǾî=telagiectasis. 1. ÀÌ¹Ì Á¸ÀçÇÏ´Â Ç÷°ü
  • telangiectasia papulosa disseminata µ¿ÀǾî=cherry hemangioma.

    telangiectasis

    ¸ð¼¼Ç÷°ü È®ÀåÁõ, ¸»ÃÊÇ÷°ü È®Àå
    ¸ð¼¼°ü¸Æ ¶Ç´Â Á¾¸» µ¿¸ÆÀÇ È®Àå¿¡ ÀÇÇØ¼­ Çü¼ºµÇ´Â ¹ÝÁ¡À¸·Î¼­ ¸¹Àº °ÍÀº ÇǺο¡ ¹ßÇöµÈ´Ù.
  • primary vaccination :

    primary's area

    Á¦1¿µ¿ª
    ¿îµ¿°ú °¨°¢ºÎ¸¦ Æ÷ÇÔÇÏ´Â ´ë³ú ÇÇÁú ¿µ¿ª.
  • A alpha primary afferent
    A ¾ËÆÄ ÀÏÂ÷ ±¸½É ½Å°æ
    ±Ù¹æÃß ³»ÀÇ ±Ù ¼¶À¯¿¡ Á¸ÀçÇÏ´Â °¨°¢½Å°æÀÇ Çϳª·Î ¥°a °¨°¢ ½Å°æÀ̶ó°íµµ ÇÑ´Ù. Á÷°æÀº 22§­, Àüµµ ¼Óµµ´Â 120§½ÀÌ´Ù.
  • C primary afferent nociceptor
    C ÀÏÂ÷ ±¸½É¼º Ä§ÇØ ¼ö¿ëü, C ÀÏÂ÷ ±¸½É¼º À¯ÇØ ¼ö¿ë±â
  • early primary closure
    Á¶±â 1Â÷ ºÀÇÕ
  • ensitization 1. administration of antigen to induce a primary immune response; priming; immunization. 2. exposure to allergen that results in the development of hypersensitivity. 3. the coating of erythrocytes with antibody so that they are subject to lys
    ³»¹ø
    ƯÈ÷ ¾È°Ë ¿¬ÀÇ.
  • myelinated primary afferent
    ÀÏÂ÷ À¯¼öÃÊ ±¸½É ½Å°æ
  • nociceptive primary afferent
    Ä§ÇØ ¼ö¿ë¼º ÀÏÂ÷ ±¸½É ½Å°æ, À¯ÇØ ¼ö¿ë¼º ÀÏÂ÷ ±¸½É ½Å°æ
  • non-nociceptive A delta C primary afferent
    ºñÄ§ÇØ ¼ö¿ë¼º A µ¨Å¸ C ÀÏÂ÷ ±¸½É ½Å°æ, ºñÀ¯ÇØ ¼ö¿ë¼º A µ¨Å¸ C ÀÏÂ÷ ±¸½É ½Å°æ
  • non-nociceptive myelinated primary afferent
    ºñÄ§ÇØ ¼ö¿ë¼º ÀÏÂ÷ ±¸½É ¼¶À¯, ºñÀ¯ÇØ ¼ö¿ë¼º ÀÏÂ÷ ±¸½É ¼¶À¯
  • primary
    ÀÏÂ÷¼º, ¿ø¹ß¼º, ¿ø¹ß¼ºÀÇ, ÀÏÂ÷, ÀÏÂ÷ÀÇ, ÀÏÂ÷¼ºÀÇ, Á¦ÀÏÀÇ, ÃʱâÀÇ, ¿ø¹ßÀÇ, ÁÖµÈ
    ¹ß»ýµÇ´Â ½Ã±âÀÇ ¼ø¼­¿¡ À־ óÀ½ÀÎ.
  • primary adaptation
    ÀÏÂ÷ ¼øÀÀ, ÀÏÂ÷¼º ¼øÀÀ
  • primary adrenocortical insuffciency
    ¿ø¹ß¼º ºÎ½Å ÇÇÁú ±â´É ºÎÀü
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
primary telangiectasia angioma serpiginosum
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
ataxia-telangiectasia <neurology, oncology> An intriguing autosomal recessive disorder in which a single defective gene produces myriad and protean effects, presents with cerebellar ataxia, telangiectasias in the eyes and skin, immune deficiency and autoimmune phenomena, propensity for lymphoid and other malignancies, excessive sensitivity to ionising radiation, increased serum alpha-fetoprotein concentrations and a tendency for chromosome breakage and translocation.
A syndrome characterised by choreoathetosis beginning in childhood, progressive cerebellar ataxia, telangiectasis of conjunctiva and skin, slowly progressive mental deterioration and increasing cerebellar degeneration.
There is evidence that heterozygotes show an increased susceptibility to malignancy as well, with breast cancer often cited. The gene was localised by linkage studies to chromosome 11q22-23, and recently cloned, revealing it to be homologous to the PI-3 kinase family so that prenatal diagnosis by RFLP analysis is possible.
Other related genes are suspected to exist. Diagnosis in affected patients is made on clinical grounds, by detection of high concentrations of alpha-fetoprotein, and by a specialised cell culture assay for radiosensitivity and atypical radioresistant DNA synthesis. These cell culture methods are also used for prenatal diagnosis.
A characteristic autopsy feature of ataxia-telangiectasia is the presence of empty basket cells in the cerebellum which results from degeneration of the previously contained Purkinje cells.
Inheritance: autosomal recessive.
(16 Dec 1998)
ataxia telangiectasia syndrome ataxia telangiectasia
cephalo-oculocutaneous telangiectasia An angioma involving the skin of the face, orbit, meninges, and brain.
See: Sturge-Weber syndrome.
(05 Mar 2000)
hereditary haemorrhagic telangiectasia <gastroenterology> An inherited disease characterised by thin blood vessel walls in the nose, skin and gastrointestinal tract. This condition ins associated with a high risk of bleeding complications.
Inheritance: autosomal dominant.
(27 Sep 1997)
secondary telangiectasia Telangiectasia related to a known cause of prolonged dermal vascular dilatation such as sunlight, varicose veins, and connective tissue diseases; often associated with atrophy of the skin.
(05 Mar 2000)
spider telangiectasia spider angioma
telangiectasia <clinical sign> A permanent dilation of preexisting blood vessels (capillaries, arterioles, venules), creating small focal red lesions, usually in the skin or mucous membranes. Also called telangiectasis.
(16 Dec 1997)
telangiectasia, hereditary haemorrhagic An autosomal dominant vascular anomaly characterised by the presence of multiple small telangiectases of the skin, mucous membranes, gastrointestinal tract, and other organs, associated with recurrent episodes of bleeding from affected sites and gross or occult melena.
(12 Dec 1998)
telangiectasia lymphatica Dilatation of the lymphatic vessels.
(12 Dec 1998)
telangiectasia macularis eruptiva perstans A disseminated eruption of telangiectases associated with erythematous and edematous macules.
(05 Mar 2000)
telangiectasia verrucosa A discrete, pink to red telangiectasia having a tendency to undergo secondary epithelial changes, including acanthosis and hyperkeratosis. An underlying vascular abnormality is present in many cases. The term angiokeratoma is applied to a number of quite distinct conditions which share a common clinical presentation with asymptomatic hyperkeratotic vascular skin lesions and a histological combination of superficial dermal vascular ectasia.
(12 Dec 1998)
essential telangiectasia Localised capillary dilation of undetermined origin.
Synonym: angioma serpiginosum.
(05 Mar 2000)
acute primary haemorrhagic meningoencephalitis A disease characterised by acute onset of fever, followed by convulsions, delirium, and coma, and associated with perivascular demyelination and haemorrhagic foci in the central nervous system.
Synonym: acute primary haemorrhagic meningoencephalitis, Strumpell's disease.
(05 Mar 2000)
acyclic monoterpene primary alcohol - NADP oxidoreductase <enzyme> From catmint nepeta racemosa; involved in the biosynthesis of iridoid monoterpenes; oxidises geraniol, nerol, and their 10-hydroxy derivatives in the presence of nadp(+).
Registry number: EC 1.1.1.-
Synonym: monoterpene primary alcohol - nadp oxidoreductase, ampano
(26 Jun 1999)
anterior primary division <anatomy, nerve> The larger, anterolaterally-directed major terminal branch (with the dorsal primary ramus) of all 31 pairs of mixed spinal nerves, formed at the intervertebral foramen. Most ventral primary rami, especially those involved in the innervation of the limbs, participate in the formation of the major nerve plexuses (cervical, brachial, and lumbosacral) and lose their identities. Most in the thoracic region, however, remain separate from adjacent rami to become the intercostal and subcostal nerves. Ventral primary rami provide innervation to the anterolateral body wall and trunk. Nomina Anatomica lists ventral primary rami as "rami ventrales" for each group of spinal nerves: 1) cervical (nervorum cervicalium ), 2) thoracic (nervorum thoracicorum ), 3) lumbar (nervorum lumbalium ), 4) sacral (nervorum sacralium )m, and 5) coccygeal (nervi coccygei ).
Synonym: ramus ventralis nervi spinalis, anterior primary division.
(05 Mar 2000)
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