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PBGS, PBG-S porphobilinogen synthase
PBG porphobilinogen
PBGD porphobilinogen deaminase
PGB porphobilinogen; prostaglandin B
ALAS delta-aminolevulinate synthase
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PBGS Porphobilinogen synthase
PBG Porphobilinogen
PBGD Porphobilinogen Deaminase
NO Synthase nitric oxide synthase
iNOS 1.Inducible NO synthase
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porphobilinogen synthase <enzyme> An enzyme that catalyses the formation of porphobilinogen from two molecules of 5-aminolevulinic acid.
Chemical name: 5-Aminolevulinate hydro-lyase (adding 5-aminolevulinate and cyclizing)
Registry number: EC 4.2.1.24
(12 Dec 1998)
porphobilinogen synthase porphyria An inherited disorder in which there is a deficiency of porphobilinogen synthase; d-aminolevulinate levels are elevated, leading to neurological disturbances.
Synonym: porphobilinogen synthase porphyria.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
porphobilinogen <chemical> Chemical name: 1H-Pyrrole-3-propanoic acid, 5-(aminomethyl)-4-(carboxymethyl)-
(12 Dec 1998)
porphobilinogen oxygenase <enzyme> Porphobilinogen is converted to 5-oxo-porphobilinogen
Registry number: EC 1.13.-
(26 Jun 1999)
abequose synthase <enzyme> Converts cdp-4-keto-3,6-dideoxy-d-glucose to cdp-3,6-dideoxy-d-galactose (cdp-abequose); requires NADPH, analogous to udp-glucose-4-epimerase
Registry number: EC 5.1.3.-
Synonym: rfbj gene product
(26 Jun 1999)
acetoacetyl-acyl carrier protein synthase <enzyme> E coli enzyme, that catalyses condensation of malonyl-acyl carrier protein plus acetyl-acyl carrier protein; not inhibited by cerulenin
Registry number: EC 2.3.1.-
Synonym: acetoacetyl-acp synthase
(26 Jun 1999)
acetolactate synthase <enzyme> A flavoprotein that catalyses the formation of acetolactate from 2 moles of pyruvate in the biosynthesis of valine and the formation of acetohydroxybutyrate from pyruvate and alpha-ketobutyrate in the biosynthesis of isoleucine.
Chemical name: Acetolactate pyruvate-lyase (carboxylating)
Registry number: EC 4.1.3.18
(12 Dec 1998)
acridone synthase <enzyme> Catalyses the condensation of n-methylanthraniloyl-CoA and 3 malonyl-CoA to produce 1,3-dihydroxy-n-methylacridone
Registry number: EC 2.3.1.-
(26 Jun 1999)
acyl-malonyl-ACP synthase <enzyme> An enzyme condensing malonyl-ACP and acyl-cys-protein to 3-oxoacyl-ACP + cys-protein + CO2, and similar reactions, as steps in fatty acid synthesis; cys-protein is also a part of the fatty acid synthase complex.
Synonym: acyl-malonyl-ACP synthase, beta-ketoacyl-ACP synthase.
(05 Mar 2000)
adenylosuccinate synthase <enzyme> A carbon-nitrogen ligase. During purine ribonucleotide biosynthesis, this enzyme catalyses the synthesis of adenylosuccinate from GTP, imp, and aspartate with the formation of orthophosphate and GDP.
Chemical name: IMP:L-aspartate ligase (GDP-forming)
Registry number: EC 6.3.4.4
(12 Dec 1998)
adenylylosuccinate synthase <enzyme> A carbon-nitrogen ligase. During purine ribonucleotide biosynthesis, this enzyme catalyses the synthesis of adenylosuccinate from GTP, imp, and aspartate with the formation of orthophosphate and GDP.
Chemical name: IMP:L-aspartate ligase (GDP-forming)
Registry number: EC 6.3.4.4
(12 Dec 1998)
agropine synthase <enzyme> Final enzyme in the three enzyme pathway for agropine synthesis; cyclises deoxymannityl-glutamine to the lactone, agropine
Registry number: EC 4.2.1.-
Synonym: ags gene product
(26 Jun 1999)
alkylglycerone-phosphate synthase <enzyme> Replaces the acyl moiety of acyldhap with a long chain fatty alcohol; intact alcohol including the oxygen atom is incorporated into alkyl-dhap
Registry number: EC 2.5.1.26
Synonym: adhps, alkyl-dihydroxyacetone phosphate synthase, alkyl-dhap synthase, alkyldihydroxyacetone phosphate synthetase, acylglycerone-3-phosphate-long chain-alcohol o-3-phospho-2-oxopropanyl transferase, alkyldihydroxyacetonephosphate synthase
(26 Jun 1999)
aminoadipic d-saemialdehyde synthase <enzyme> A bifunctional enzyme used in lysine degradation; it has a lysine:alpha-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinaemia.
(05 Mar 2000)
aminoadipic saemialdehyde synthase <enzyme> Bifunctional enzyme with both lysine-ketoglutarate reductase (EC 1.5.1.8) and saccharopine dehydrogenase (EC 1.5.1.9) activities
Registry number: EC 1.5.1.-
Synonym: aasa synthase
(26 Jun 1999)
aminodeoxychorismate synthase <enzyme> From E coli; probably catalyses the conversion of chorismate to 4-amino-4-deoxychorismate; see also paba protein
Registry number: EC 2.6.1.-
Synonym: pabb gene product, adc synthase
(26 Jun 1999)
amylopectin synthase <enzyme> From eimeria tenella; catalyses udpglucose alpha 1,4-glucan alpha-4-glucosyltransferase forming amylopectin, similar to glycogen synthase in eukaryotes
Registry number: EC 2.4.1.-
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Porphobilinogen Synthase - »õâ An enzyme that catalyzes the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. EC 4.2.1.24.
    Synonyms : ALA-Dehydrase, delta-Aminolevulinate Dehydratase, delta-Aminolevulinic Acid Dehydratase, ALA Dehydrase, Acid Dehydratase, Aminolevulinic, Acid Dehydratase, delta-Aminolevulinic, Aminolevulinate Hydro Lyase, Dehydratase, Aminolevulinic Acid
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porphobilinogen synthase [EC 4.2.1.24] an enzyme of the lyase class that catalyzes the condensation of two molecules of δ-aminolevulinate to form porphobilinogen in the synthesis of porphyrins. The enzyme is inhibited by minute quantities of lead poisoning. Genetic deficiency of the enzyme causes a porphyria similar to acute intermittent porphyria but with high urinary levels of δ-aminolevulinic acid, coproporphyrinogen III, and protoporphyrin but not porphobilinogen. Called also aminolevulinate dehydratase.
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