| porphobilin | General term denoting intermediates between the monopyrrole, porphobilinogen, and the cyclic tetrapyrrole of haem (a porphin derivative). See: bilin. (05 Mar 2000) |
|---|---|
| porphobilinogen | <chemical> Chemical name: 1H-Pyrrole-3-propanoic acid, 5-(aminomethyl)-4-(carboxymethyl)- (12 Dec 1998) |
| porphobilinogen oxygenase | <enzyme> Porphobilinogen is converted to 5-oxo-porphobilinogen Registry number: EC 1.13.- (26 Jun 1999) |
| porphobilinogen synthase | <enzyme> An enzyme that catalyses the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. Chemical name: 5-Aminolevulinate hydro-lyase (adding 5-aminolevulinate and cyclizing) Registry number: EC 4.2.1.24 (12 Dec 1998) |
| porphobilinogen synthase porphyria | An inherited disorder in which there is a deficiency of porphobilinogen synthase; d-aminolevulinate levels are elevated, leading to neurological disturbances. Synonym: porphobilinogen synthase porphyria. (05 Mar 2000) |
| porphobilinogenase | <enzyme> A combination of uroporphyrinogen I synthase and uroporphyrinogen isomerase which catalyses the formation of uroporphyrinogen III from porphobilinogen; minor descriptor (75-84); on-line and index medicus search ammonia-lyases (75-84) Registry number: EC 5.- (26 Jun 1999) |
Synonyms :
Synonyms : ALA-Dehydrase, delta-Aminolevulinate Dehydratase, delta-Aminolevulinic Acid Dehydratase, ALA Dehydrase, Acid Dehydratase, Aminolevulinic, Acid Dehydratase, delta-Aminolevulinic, Aminolevulinate Hydro Lyase, Dehydratase, Aminolevulinic Acid
| porphobilinogen |
the immediate precursor of the porphyrins, a pyrrole ring with acetyl, propionyl, and aminomethyl side chains; four molecules of porphobilinogen are condensed to form one molecule of uroporphyrinogen III, which is then converted successively to coproporphyrinogen III, protoporphyrin IX, and heme. Porphobilinogen is produced in excess and excreted in the urine in acute intermittent porphyria and several other porphyrias. Abbreviated PBG.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|---|
| porphobilinogen deaminase |
hydroxymethylbilane synthase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| porphobilinogen synthase |
[EC 4.2.1.24] an enzyme of the lyase class that catalyzes the condensation of two molecules of δ-aminolevulinate to form porphobilinogen in the synthesis of porphyrins. The enzyme is inhibited by minute quantities of lead poisoning. Genetic deficiency of the enzyme causes a porphyria similar to acute intermittent porphyria but with high urinary levels of δ-aminolevulinic acid, coproporphyrinogen III, and protoporphyrin but not porphobilinogen. Called also aminolevulinate dehydratase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| porphobilinogen t. |
a test for the presence of porphobilinogen; see Watson-Schwartz t.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| porphobilinogenuria |
the excretion of urine containing porphobilinogen, as in acute intermittent porphyria and certain other porphyrias.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|