| encephalitis periaxialis | Rare demyelinating disease characterised by massive destruction of the myelin in the cerebral hemispheres, cavity formation, and glial scarring. Clinical symptoms include bilateral spasticity, cortical blindness, and progressive dementia. Encephalitis periaxialis diffusa (= schilder's disease) should be reserved for instances of myelinoclastic diffuse sclerosis that correspond to the case described by schilder in 1912. Schilder's disease should not be confused with addison-schilder disease (= adrenoleukodystrophy). (12 Dec 1998) |
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| encephalitis periaxialis concentrica | Encephalitis that is clinically similar to adrenoleukodystrophy, but pathologically characterised by concentric globes or circles of demyelination of cerebral white matter separated by normal tissue. Synonym: Balo's disease. (05 Mar 2000) |
| encephalitis periaxialis diffusa | Term used to describe at least two separate disorders described by Schilder: 1) Diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterised by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetrical area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) The leukodystrophies. Synonym: encephalitis periaxialis diffusa, Flatau-Schilder disease. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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