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"optic neuritis, hereditary"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
¿µ¹® optic nerve ÇÑ±Û ½Ã°¢½Å°æ
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  ½Ã°¢À» ÀÎÁöÇϴ ½Å°æ. ÀÌ ½Å°æÀº ´ÜÁö °¨°¢½Å°æÀ¸·Î¼­¸¸ ÀÛ¿ëÇÑ´Ù. µû¶ó¼­ ¾î¶² »ç¹°À» µû¶ó ´«À» ¿òÁ÷ÀÏ ¼ö Àִ °ÍÀº ÀÌ ½Ã°¢½Å°æ°ú´Â ¹«°üÇÏ´Ù(À̰ÍÀº ´«µ¹¸²½Å°æ(oculomotor nerve)¿¡ ÀÇÇØ °¡´ÉÇÏ´Ù). ¶ÇÇÑ ½Ã°¢½Å°æÀº °íÀ§ÁßÃ߽Űæ°èÀΠ³ú¿¡¼­ Á÷Á¢ ºÐÁöÇϹǷΠ¼Õ»ó½Ã Àç»ýÀº ºÒ°¡´ÉÇϸç, ÀÌ¿¡ ´ëÇÑ Ä¡·á¹ýÀº ¾ø´Ù.
¿µ¹® optic disk ÇÑ±Û ½Ã½Å°æÀ¯µÎ
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  ¸Á¸·ÀÇ ±¸Á¶¸¦ Á÷»ó°Ë¾È°æ(¸Á¸·À» º¸±â À§ÇØ °í¾ÈµÈ °Ë»ç±â±¸)À¸·Î º¸¸é ´ÙÀ½°ú °°´Ù.
  
  ¸Á¸·¿¡ Ç÷¾×À» °ø±ÞÇϴ ¸Á¸·µ¿¸Æ(retinal artery)°ú, ´Ù½Ã Ç÷¾×À» È¸¼öÇϴ ¸Á¸·Á¤¸Æ(retinal vein)Àº ´Ù°°ÀÌ ½Ã°¢½Å°æ(optic nerve)°ú ÇÔ²² ½Ã°¢½Å°æ±¸¸Û(optic foramen)À» ÅëÇØ ¸Á¸·±îÁö À̸£°Ô µÈ´Ù. Áï, À̵頸Á¸· µ¿, Á¤¸ÆÀº ½Ã°¢½Å°æ¼Ó¿¡ ³¢¿öÁø Ã¤ ¸Á¸·±îÁö À̸£°Ô µÈ´Ù. µû¶ó¼­ À̵頸Á¸· µ¿, Á¤¸Æ ÁÖÀ§¿¡ Á¸ÀçÇϴ ½Ã°¢½Å°æÀ¯µÎ´Â ¹Ù·Î ½Ã°¢½Å°æÀÇ ÀϺκÐÀ» ¸»ÇÑ´Ù. ºûÀÇ ÀÚ±ØÀ» ÀÌÇØÇÒ ¼ö Àִ ½Åȣü°è·Î ¹Ù²Ù´Â ½Ã°¢¼¼Æ÷´Â ¹Þ¾ÆµéÀΠÀÚ±ØÀ» ½Ã°¢½Å°æ¿¡¼­ ºÐÁöÇÑ ¼ö¸¹Àº ½Å°æÀý¼¼Æ÷(ganglion cell: ½Å°æÀü´ÞÀ» ¸ð¾Æ¼­ º¸´Ù Å« Àü´Þ´ÜÀ§·Î ÀüÇØÁִ ¿ªÇÒÀ» Çϸç, ¸Á¸·³»¿¡ À§Ä¡ÇÑ´Ù)·Î Àü´ÞÇϰԠµÇ°í, À̵頽ŰæÀý¼¼Æ÷´Â ´Ù½Ã ÀÌ·± ÀڱصéÀ» ¸ð¾Æ ½Ã°¢½Å°æÀ¯µÎ·Î º¸³»°Ô µÇ¸ç, ½Ã°¢½Å°æÀ¯µÎ¿¡¼­ºÎÅÍ ½Å°æÀü´ÞÀº ³ú±îÁö ÁøÇàÇÑ´Ù.
  
  ½Ã½Å°æÀ¯µÎ
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • optic neuritis
    ½Ã(°¢)½Å°æ¿°
  • retrobulbar optic neuritis
    ´«µÚ½Ã(°¢)½Å°æ¿°, ¾È±¸ÈĽýŰ濰
  • endemic neuritis
    dzÅ亴½Å°æ¿°
  • friction neuritis
    ¸¶Âû½Å°æ¿°
  • lead neuritis
    ³³Áßµ¶½Å°æº´Áõ
  • leprous neuritis
    ³ªº´½Å°æ¿°
  • migrating neuritis
    À̵¿½Å°æ¿°
  • multiple peripheral neuritis
    ´Ù¹ß¸»ÃʽŰ濰
  • neuritis
    ½Å°æ¿°
  • progressive hypertrophic interstitial neuritis
    ÁøÇàºñ´ë»çÀÌÁú½Å°æ¿°, ÁøÇàºñ´ë°£Áú½Å°æ¿°
  • rheumatic neuritis
    ·ù¸¶Æ¼½º½Å°æ¿°
  • sciatic neuritis
    Á°ñ½Å°æ¿°, ±ÃµÕ½Å°æ¿°
  • vestibular neuritis
    ¾È¶ã½Å°æ¿°, ÀüÁ¤½Å°æ¿°
  • congenital hereditary hearing loss
    ¼±ÃµÀ¯Àü³­Ã»
  • hereditary
    À¯Àü-
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • optic neuritis
    ½Ã°¢½Å°æ¿°
  • retrobulbar optic neuritis
    ´«µÚ½Ã°¢½Å°æ¿°, ±¸ÈĽýŰ濰
  • hereditary
    À¯Àü-
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´Áõ
  • hereditary spherocytosis
    À¯ÀüµÕ±ÙÀûÇ÷±¸Áõ, À¯Àü±¸ÇüÀûÇ÷±¸Áõ
  • neuritis
    ½Å°æ¿°
  • vestibular neuritis
    ¾È¶ã½Å°æ¿°, ÀüÁ¤½Å°æ¿°
  • optic atrophy
    ½Ã°¢½Å°æÀ§Ãà
  • optic nerve atrophy
    (¢¡optic atrophy) ½Ã°¢½Å°æÀ§Ãà
  • optic chiasm
    ½Ã°¢±³Â÷
  • optic disc cupping
    ½Ã°¢½Å°æÀ¯µÎÆÐÀÓ, ½Ã°¢½Å°æÀ¯µÎÇÔ¸ô
  • optic disc
    ½Ã°¢½Å°æÀ¯µÎ
  • ischemic optic neuropathy
    ÇãÇ÷½Ã°¢½Å°æº´Áõ
  • optic nerve
    ½Ã°¢½Å°æ
  • optic
    ´«-, ½Ã°¢-
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • optic neuritis
    ½Ã°¢½Å°æ¿°
  • retrobulbar optic neuritis
    ´«µÚ½Ã°¢½Å°æ¿°, ±¸ÈĽýŰ濰
  • endemic neuritis
    Áö¿ª½Å°æ¿°
  • friction neuritis
    ¸¶Âû½Å°æ¿°
  • lead neuritis
    (¢¡lead neuropathy) ³³Áßµ¶½Å°æº´Áõ
  • leprous neuritis
    ³ªº´½Å°æ¿°
  • migrating neuritis
    À̵¿½Å°æ¿°
  • neuritis
    ½Å°æ¿°
  • progressive hypertrophic interstitial neuritis
    ÁøÇàºñ´ë»çÀÌÁú½Å°æ¿°
  • rheumatic neuritis
    ·ù¸¶Æ¼½º½Å°æ¿°
  • sciatic neuritis
    (¢¡sciatica) Á°ñ½Å°æÅë, ±ÃµÕ½Å°æÅë
  • toxic neuritis
    µ¶¼º½Å°æ¿°
  • traumatic neuritis
    ¿Ü»ó½Å°æ¿°
  • vestibular neuritis
    ¾È¶ã½Å°æ¿°, ÀüÁ¤½Å°æ¿°
  • hereditary ataxia
    À¯ÀüÁ¶È­¿îµ¿ºÒ´É
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary optic atrophy
    À¯Àü¼º½Ã½Å°æÀ§Ãà.
  • hereditary optic atrophy
    À¯Àü¼º ½Ã½Å°æÀ§Ãà.
  • adventitial neuritis
    ¿ÜÃʽŰ濰(èâõ¦ãêÌèæú).
  • arsenical neuritis
    ºñ¼Ò(¼º) ½Å°æ¿° (¡­ãêÌèæú).
  • friction neuritis
    ¸¶Âû¼º ½Å°æ¿°.
  • infectious neuritis
    Àü¿°¼º ½Å°æ¿°.
  • porphyrin neuritis
    Æ÷¸£ÇǸ°½Å°æ¿° (¡­ãêÌèæú).
  • porphyrin neuritis
    Æ÷¸£ÇǸ°½Å°æ¿°(¡­ãêÌèæú)
  • progressive hypertrophic interstitial neuritis
    ÁøÇ༺ ºñÈļº °£Áú¼º ½Å°æ¿°(¡­ãêÌèæú).
  • progressive hypertrophic interstitial neuritis
    ÁøÇ༺ ºñÈļº °£Áú¼º ½Å°æ¿°(òäú¼àõ Ýþý§àõ ÊÖòðàõ ãêÌèæú)
  • Devics disease=>optic neuromyelitis
    µ¥ºòº´
  • anterior ischemic optic neuropathy
    Àü¹æÇãÇ÷¼º ½Ã½Å°æº´Áõ(îñÛ°úÈúìàõãÊãêÌèÜ»ñø).
  • anterior ischemic optic neuropathy
    ¾ÕÇãÇ÷½Ã½Å°æº´Áõ
  • geminal body =optic lobe
    ÀÌ´ëü(ì£Óßô÷).
  • glaucomatous optic nerve atrophy
    ³ì³»Àå½Ã½Å°æÀ§Ãà.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • retrobulbar optic neuritis ; axial optic neuritis
    ±¸ÈĽýŰ濰(Ϲý­ãÊãêÌèæú);Ã༺½Ã½Å°æ¿°(õîàõãÊãêÌèæú)
  • axial optic neuritis
    Ã༺½Ã½Å°æ¿°.
  • retrobulbar optic neuritis
    ±¸ÈĽýŰ濰
  • hereditary optic atrophy
    À¯Àü¼º ½Ã½Å°æÀ§Ãà.
  • hereditary optic atrophy
    À¯Àü¼º½Ã½Å°æÀ§Ãà.
  • lebers hereditary optic neuropathy
    ·¹¹ö¾¾¼±Ãµ¼º½Ã½Å°æº´Áõ(¡­à»ô¸àõãÊãêÌèÜ»ñø)
  • optic nerve disk [optic papilla]
    ½Ã°¢½Å°æ¿ø¹Ý
  • adventitial neuritis
    ¿ÜÃʽŰ濰(èâõ¦ãêÌèæú).
  • alcoholic neuritis
    ¾ËÄÚ¿Ã(¼º) ½Å°æ¿°(¡­ãêÌèæú).
  • arsenical neuritis
    ºñ¼Ò(¼º) ½Å°æ¿° (¡­ãêÌèæú).
  • ascending neuritis
    »óÇ༺ ½Å°æ¿°.
  • axial neuritis
    Ã༺½Å°æ¿°.
  • axial retrobulbar neuritis
    Ã༺±¸ÈĽýŰ濰
  • brachial neuritis
    »ó¿Ï½Å°æ¿°.
  • brachial neuritis
    »ó¿Ï ½Å°æ¿°.
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Optic nerve disk [Optic papilla]
    ½Ã°¢½Å°æ¿ø¹Ý
    [¿¾ ¿ë¾î] ½Ã½Å°æ¿øÆÇ
  • Optic cavity
    ´«¼ÒÆ÷°ø°£
    [¿¾ ¿ë¾î] ¾È°­
  • Optic stalk
    ´«¼ÒÆ÷ÁÙ±â
    [¿¾ ¿ë¾î] ¾È°æ
  • Cavity of optic cup
    ´«¼úÀܰø°£
    [¿¾ ¿ë¾î] ¾È¹è°­
  • External plate of optic cup
    ´«¼úÀܹٱùÆÇ
    [¿¾ ¿ë¾î] ¾È¹è¿ÜÆÇ
  • Internal plate of optic cup
    ´«¼úÀܼӯÇ
    [¿¾ ¿ë¾î] ¾È¹è³»ÆÇ
  • Optic fovea
    ´«¿À¸ñ
    [¿¾ ¿ë¾î] ¾È¿Í
  • Optic mesenchyme
    ´«Áß°£¿±
    [¿¾ ¿ë¾î] ¾È°£¿±
  • Optic part of retina
    ¸Á¸·½Ã°¢ºÎºÐ
    [¿¾ ¿ë¾î] ¸Á¸·½ÃºÎ
  • Optic chiasm
    ½Ã°¢±³Â÷
    [¿¾ ¿ë¾î] ½Ã½Å°æ±³Â÷
  • Optic tract
    ½Ã°¢·Î
    [¿¾ ¿ë¾î] ½Ã»è
  • Optic tract branches
    ½Ã°¢·Î°¡Áö
    [¿¾ ¿ë¾î] ½Ã»èÁö
  • Optic radiation
    ½Ã°¢·ÎºÎê»ì
    [¿¾ ¿ë¾î] ½Ã¹æ»ç
  • Optic canal
    ½Ã°¢½Å°æ°ü
    [¿¾ ¿ë¾î] ½Ã½Å°æ°ü
  • Vascular ring of optic nerve
    ½Ã°¢½Å°æÇ÷°ü°í¸®
    [¿¾ ¿ë¾î] ½Ã½Å°æÇ÷°ü·û
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary code
    À¯Àü ºÎÈ£(ë¶îîݬûÜ)
  • hereditary material
    À¯Àü ¹°Áú(ë¶îîÚªòõ)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • optic neuritis
    ½Ã½Å°æ¿°
  • neuritis
    ½Å°æ¿°
  • retrobulbar neuritis
    ±¸ÈĽýŰ濰
  • hereditary
    À¯Àü¼ºÀÇ
  • hereditary craniofacial dysostosis
    À¯Àü¼ºµÎ°³¾È¸éÀ̰ñÁõ
  • hereditary disease
    À¯Àüº´
  • hereditary ectodermal polydysplasia
    À¯Àü¼º¿Ü¹è¿±¼º´Ù¹ßÀÌÇü¼ºÁõ
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°üÈ®Àå
  • optic
    ´«ÀÇ, ½Ã°¢ÀÇ, °úÇÐÀÇ
  • optic atrophy
    ½Ã½Å°æÀ§Ãà
  • optic chiasma
    ½Ã½Å°æ±³Â÷
  • optic commissure
    ½Ã½Å°æ±³·Ã
  • optic disc
    ½Ã½Å°æÀ¯µÎ
  • optic foramen
    ½Ã½Å°æ°ø
  • optic nerve
    ½Ã½Å°æ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
LHON Leber hereditary optic neuropathy
BN bladder neck; branchial neuritis; bronchial node; brown Norway [rat]; bulimia nervosa
EAN experimental allergic neuritis
PBN paralytic brachial neuritis; peripheral benign neoplasm; polymyxin B sulfate, bacitracin, and neomyc...
RBN retrobulbar neuritis
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
ON Optic Neuritis
LHON Leber hereditary optic neuropathy
LHON Leber hereditary optic neuroretinopathy
EAN Experimental Allergic Neuritis
EAN Experimental autoimmune neuritis
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • optic neuritis
    ½Ã½Å°æ¿°
  • lebers hereditary optic neuropathy
    ·¹¹ö¾¾ ¼±Ãµ¼º ½Ã½Å°æº´Áõ
  • ascending neuritis
    »óÇ༺ ½Å°æ¿°
  • diabetic neuritis
    ´ç´¢º´ ½Å°æ¿°, ´ç´¢º´¼º ½Å°æ¿°
    ´ç´¢º´¿¡ ÀÇÇØ º´º¯À» º¸ÀÌ´Â Á¶Á÷Áß ½Å°æµµ Æ÷ÇԵȴÙ. ÀÓ»óÀûÀ¸·Î ¿øÀ§ ½Å°æÀ» ´ëμºÀ¸·Î ħ¹üÇϸç ÁÖ·Î °¨°¢¼º ´Ù¹ß ½Å°æº´ÁõÀÇ ÇüŸ¦ ÃëÇÑ´Ù. º´¸®ÇÐÀûÀ¸·Î´Â ÁÖ·Î Ãà»èÀÇ º´º¯À̳ª ºÎÀ§¿¡ µû¶ó Å»¼öÃÊÀÇ Çö»óÀ» º¸À̱⵵ ÇÑ´Ù.
  • experimental allergic neuritis
    ½ÇÇèÀû ¾Ë·¹¸£±â¼º ½Å°æ¿°
    ÀÌ ÁúȯÀº Freund ¿ÏÀü adjuvant¸¦ À¯Á¦·Î ÇÑ µ¿Á¾ ¶Ç´Â ÀÌÁ¾ µ¿¹° À¯·¡ÀÇ ¸»ÃÊ ½Å°æ ÃßÃâ¹° ȤÀº ¸»ÃÊ ½Å°æ ´Ü¹éÁúÀ» ½ÇÇè µ¿¹°¿¡ Åõ¿©Çϸé 10-24ÀÏ ÈÄ¿¡ ¹«·Â, ¸¶ºñÀÇ Áõ»óÀ» ÀÏÀ¸Å°´Â ÀÏÁ¾ÀÇ ÀÚ°¡ ¸é¿ª¼º ½Å°æ¿°ÀÌ´Ù. ÁÖµÈ ¿øÀÎÀº ¼¼Æ÷¼º ¸é¿ª ±âÀü¿¡ ÀÇÇÑ °ÍÀ¸·Î µÇ¾î ÀÖ´Ù.
  • lead neuritis
    ¿¬ ½Å°æ¿°
  • neuritis
    ½Å°æ¿°
    1. ½Å°æ ¼¶À¯ ¶Ç´Â ±× Á¶Á÷ÀÇ ¿°Áõ ¹× ³ÐÀº ¶æÀÇ ÅðÇ༺ º¯¼º
  • hereditary
    À¯Àü¼º
    ºÎ¸ð·ÎºÎÅÍ ´ÙÀ½ ¼¼´ë·Î À¯ÀüÀÚ¿¡ ÀÇÇØ Àü´ÞµÇ´Â.
  • hereditary amyloidosis
    À¯Àü¼º À¯ÀüºÐÁõ
    1. À¯Àü¿¡ ÀÇÇØ ¿ø¼¶À¯¼º ´ç ´Ü¹éÀÌ ÇǺÎ, Á¡¸·, ³»ºÎ Àå±â¿¡ ħÀüµÇ´Â º´. 2. À¯ÀüÀûÀ¸·Î ½ÅüÀÇ °¢Á¾ ºÎÀ§¿¡ ¾Æ¹Ð·ÎÀ̵å
  • hereditary angioedema
    À¯Àü¼º ¸Æ°ü ºÎÁ¾, À¯Àü¼º Ç÷°ü ºÎÁ¾
    ½ÉºÎÀÇ ÁøÇÇ, ÇÇÇÏ Á¶Á÷, Á¡¸·ÇÏÁ¶Á÷À» ħ½ÀÇÏ´Â Ç÷°ü ¹ÝÀÀÀ¸·Î¼­, ¸ð¼¼Ç÷°üÀÇ È®Àå°ú Åõ°ú¼º Ç×Áø¿¡ ÀÇÇØ ÀϾ´Â ±¹ÇѼº ºÎÁ¾À» ³ªÅ¸³»¸ç °Å´ëÇÑ ÆØÁøÀÇ ¹ß»ýÀ» Ư¡À¸·Î ÇÑ´Ù. »ó¿°»öü¼º ¿ì¼º ÇüÁú·Î À¯ÀüÇÑ´Ù. »ê¹ß¼ºº¸´Ù ³»Àå º´º¯À» ´õ Àß ÀÏÀ¸Å°´Â °æÇâÀÌ ÀÖ´Ù.
  • hereditary aphasia
    À¯Àü ½Ç¾î, À¯Àü¼º ½Ç¾î, À¯Àü ½Ç¾îÁõ, À¯Àü¼º ½Ç¾îÁõ
  • hereditary brown tooth
    À¯Àü¼º °¥»ö Ä¡¾Æ
  • hereditary cerebrospinal paralysis
    ¿ìÀü¼º ³úô¼ö ¸¶ºñ
    º¸Åë Áß³â Ãʱ⿡ ÁøÇàÇÏ´Â À¯Àü¼º ÁúȯÀ¸·Î »óÁö ¶Ç´Â ÇÏÁöÀÇ ¾çÁö ¶Ç´Â ÀÏÃøÀ̳ª »çÁö¿¡ ³ªÅ¸³ª¸ç, ¼­¼­È÷ ÁøÇàµÇ´Â ¸¶ºñ°¡ Ư¡ÀÌ´Ù.
  • hereditary craniofacial dysostosis
    À¯Àü¼º µÎ°³ ¾È¸é À̰ñÁõ
    ž»ó µÎ°³, ¾È±¸ µ¹Ãâ, ¾ç¾È °Ý¸®, »ç½Ã, ¾Þ¹«»õ ºÎ¸® ¸ð¾ç1114-377786/377786Àüµ¹À» ¼ö¹ÝÇÏ´Â »ó¾Ç Çü¼º ºÎÀüÀ» Ư¡À¸·Î ÇÏ´Â À¯ÀüÀû Áúȯ.
  • hereditary disease
    À¯Àüº´
    À¯ÀüÀÚ¿¡ ÀÇÇÏ¿© ÀϾ´Â ½ÅüÀû, Á¤½ÅÀûÀÎ ÀÌ»óÀÇ ÃÑĪ. À¯Àü¼º ÁúȯÀ̶ó°íµµ ÇÑ´Ù. º´, ÀÌ»ó ÇüÁúÀÌ À¯ÀüÀû ¿äÀΰú °ü·ÃÀÌ ÀÖÀ½¿¡ µû¶ó¼­ ¹Ýµå½Ã À¯ÀüÀÚ¿¡ ÀÇÇÏÁö ¾Ê´Â À¯ÀüÀûÀÎ º´µµ À¯Àüº´À̶ó°í ÇÏ°Ô µÇ¾ú´Ù. 1°³ÀÇ ¿ì¼º À¯ÀüÀÚ¿¡ ÀÇÇÏ¿© ÀϾ´Â ÇåÆÃÅÏ ¹«µµº´, ¹ß·»ºÎ¸£Å© ÁõÈıº, ¿­¼º À¯ÀüÀÚÀÇ µ¿Çü Á¢ÇÕ¿¡ ÀÇÇÏ¿© ³ªÅ¸³ª´Â ¹éÀÚ, Æä´ÒÄÉÅæ´¢Áõ, X ¿°»öü À§ÀÇ ¹Ý¼º À¯ÀüÀÚ¿¡ ÀÇÇÑ Àû·Ï »ö¸Í, Ç÷¿ìº´, ÁøÇ༺ ±Ù µð½ºÆ®·ÎÇÇÁõ µîÀº ¸í¹éÈ÷ ÀÌÀ¯ ÀüÀÚ¿¡ ÀÇÇÑ °ÍÀ¸·Î¼­, À¯Àüº´ÀÇ ´ëÇ¥ÀûÀÎ °ÍÀ̶ó°í ÇÒ ¼ö ÀÖ´Ù. ¹Ý¼º À¯ÀüÀÚ´Â X ¿°»öü À§¿¡ À§Ä¡ÇÏ´Â °Í¸¸ ¾Ë·ÁÁ® ÀÖ°í, ³²¼ºÀ» °áÁ¤ÇÏ´Â Y ¿°»öü À§¿¡´Â ÇöÀç±îÁö ƯÈ÷ È®½ÇÇÑ ÇüÁúÀ» °áÁ¤ÇÏ´Â À¯ÀüÀÚ´Â Á¸ÀçÇÏÁö ¾Ê´Â´Ù°í º¸°í ÀÖ´Ù. À¯ÀüÀÚ¿¡ ÀÇÇÑ ÀÌ»óÀ̳ª º´Àº Ãâ»ýÇÏ´Â ¾Æ±âÀÇ 1 %°¡ ÀÌ¹Ì °¡Áö°í Àְųª ¹ßº´ÇÒ °¡´É¼ºÀ» Áö´Ï°í ÀÖ´Ù. ¿°»öüÀÇ ±¸Á¶ ¶Ç´Â ±¸¼ºÀÇ ÀÌ»ó¿¡ ÀÇÇÏ¿© ÀϾ´Â ¿©·¯ °¡Áö ÀÌ»ó ´Ù¿î ÁõÈıº, ÅÍ³Ê ÁõÈıº, Ŭ¶óÀÎÆçÅÍ ÁõÈıº µîµµ ¿°»öü À§¿¡ À¯ÀüÀÚ°¡ ÀÖ´Ù°í ÇÏ´Â Àǹ̿¡¼­´Â À¯ÀüÇÐÀûÀÎ °ÍÀ̶ó°í ÇÒ ¼ö ÀÖ´Ù. ±×·¯³ª ´ë°³´Â ÀÌ»ó °³Ã¼¸¦ ¸¸µç ¹è¿ìÀÚ
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optic neuritis <pathology> Inflammation of the optic nerve. This may occur secondary to a wide variety of causes: multiple sclerosis, posterior uveitis, vascular lesions of the optic nerve (interruption of blood supply to the optic nerve), temporal arteritis, central retinal artery occlusion, methyl alcohol poisoning, drug side effects and acute demyelinative disease of the optic nerves (destruction of optic nerve sheath).
(27 Sep 1997)
optic atrophy, hereditary An inherited disorder in which optic atrophy is associated with muscle weakness, peroneal muscular atrophy and, in some patients, lancinating pains. In these patients the peripheral sensory neurons are probably affected.
(12 Dec 1998)
Leber's hereditary optic atrophy Hereditary degeneration of the optic nerve and papillomacular bundle with resulting rapid loss of central vision, progressive for several weeks, then usually stationary with permanent central scotoma; age of onset is variable, most often in the third decade; more males than females are affected and transmission is cytoplasmic and strictly on the female side. Mutation on the mitochondrial chromosome involved, which presumably interacts with an X-linked mutant. This mechanism may explain the bizarre sex ratio, which differs significantly from one country to another.
(05 Mar 2000)
adventitial neuritis Inflammation of the sheath of a nerve.
See: perineuritis.
(05 Mar 2000)
ascending neuritis Inflammation progressing upward along a nerve trunk in a direction away from the periphery.
(05 Mar 2000)
axial neuritis Inflammation of the nervous substance proper, the axons, and myelin.
Synonym: axial neuritis, central neuritis.
(05 Mar 2000)
brachial neuritis neuralgic amyotrophy
parenchymatous neuritis Inflammation of the nervous substance proper, the axons, and myelin.
Synonym: axial neuritis, central neuritis.
(05 Mar 2000)
central neuritis Inflammation of the nervous substance proper, the axons, and myelin.
Synonym: axial neuritis, central neuritis.
(05 Mar 2000)
retrobulbar neuritis Optic neuritis without swelling of the optic disk.
(05 Mar 2000)
multiple neuritis <neurology> A disease process involving a number of peripheral nerves.
Origin: Gr. Pathos = disease
(14 Oct 1997)
sciatic neuritis A syndrome characterised by pain radiating from the back into the buttock and into the lower extremity along its posterior or lateral aspect and most commonly caused by prolapse of the intervertebral disk, the term is also used to refer to pain anywhere along the course of the sciatic nerve.
(18 Nov 1997)
segmental neuritis Inflammation occurring at several points along the course of a nerve, segmental demyelinating neuropathy
(05 Mar 2000)
neuritis <clinical sign> Inflammation of a nerve, a condition attended by pain and tenderness over the nerves, anaesthesia and paraesthesias, paralysis, wasting and disappearance of the reflexes. In practice, the term is also used to denote noninflammatory lesions of the peripheral nervous system.
If the involvement is in one nerve it is called mononeuritis, in several nerves, mononeuritis multiplex, if diffuse and bilateral, polyneuritis.
See: neuropathy.
(16 Dec 1997)
neuritis, experimental allergic An autoimmune demyelinating disorder of peripheral nerves produced by injection of peripheral nerve tissue protein.
(12 Dec 1998)
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