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  • olivopontocerebellar
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  • olivopontocerebellar atrophy
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  • olivopontocerebellar atrophy
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  • olivopontocerebellar atrophy =OPCA
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  • olivopontocerebellar atrophy =opca
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  • olivopontocerebellar atrophy(OPCA)
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OCA oculocutaneous albinism; olivopontocerebellar atrophy; oral contraceptive agent
OPCA olivopontocerebellar atrophy
OPCD olivopontocerebellar degeneration
SOPCA sporadic olivopontocerebellar ataxia
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olivopontocerebellar Relating to the olivary nucleus, basis pontis, and cerebellum.
(05 Mar 2000)
olivopontocerebellar atrophy A collection of diseases with atrophy of the cerebellum, pons, and inferior olives described in 1900 by dejerine and thomas. Signs and symptoms include ataxia of trunk and limbs, dysarthria, intention tremor, followed by generalised rigidity and dementia.
(12 Dec 1998)
olivopontocerebellar degeneration <neurology> An inherited disease especially. Of mid to late life that is characterised by ataxia, hypotonia, dysarthria, and degeneration of the cerebellar cortex, middle cerebellar peduncles, and inferior olives.
(09 Oct 1997)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Olivopontocerebellar Atrophies - »õâ A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)
    Synonyms : Familial Olivopontocerebellar Atrophy, Inherited Olivopontocerebellar Atrophy, Nonfamilial Olivopontocerebellar Atrophy, Olivo-Ponto-Cerebellar Atrophy, Olivo-Ponto-Cerebellar Degeneration, Olivopontocerebellar Atrophy, Olivopontocerebellar Degeneration
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  • Olivopontocerebellar atrophy - »õâ
  • Olivopontocerebellar degeneration - »õâ
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olivopontocerebellar atrophy These are a group of diseases characterized by neuronal degeneration in the cerebellum, pontine nuclei, and inferior olive. They are also referred to as spinocerebellar atrophies or ataxias (SCA). Some also involve brain stem motor nuclei and/or cerebral cortex. All produce gait ataxia, and some also result in tremors, proprioceptive abnormalities, dysarthria, brain stem motor impairment, or dementia. Most are autosomal dominant in inderitance pattern. ...
Ãâó: en.wikipedia.org/wiki/Olivopontocerebellar_atrophy
olivopontocerebellar pertaining to the olivae, the middle peduncles, and the cortex of the cerebellum.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
olivopontocerebellar a. any of a group of progressive hereditary disorders involving degeneration of the cerebellar cortex, middle peduncles, ventral pontine surface, and olivary nuclei. They occur in the young to middle-aged and are characterized by ataxia, dysarthria, and tremors similar to those of parkinsonism. Both autosomal dominant and autosomal recessive types have been distinguished. Called also olivopontocerebellar degeneration and Dejerine-Thomas syndrome.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
olivopontocerebellar d. see under atrophy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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