| 영문 | myasthenia gravis | 한글 | 중증근육무력증 |
|---|---|---|---|
| 설명 | 활동시에 근대약과 피로를 호소하다가 안정 후에는 회복되는 특징적인 증상을 호소하는 병으로, 근육과 신경접합부 사이 연결부분 이상으로 발생한다. 주로 젊은 여성에서 빈발하고, 눈주위 근육을 잘 침범한다. 대개 아침이나 휴식 후에는 호전되었다가 운동시 악화되는 피로현상을 보인다. 메커니즘은 아마 면역계의 이상으로 인해 발생하는 것으로 보이며, 치료 또한 면역을 억제하는 약을 다량 투여함으로써 호전되었다는 보고가 많다. 침범부위의 근육에 따라 여러 가지 종류가 있으며, 호흡근까지 침범하게 되면, 호흡기능상실로 사망한다. 신경-근육 접합부 중 접합뒤막의 아세틸콜린 수용체의 장애가 발생하는 자가면역병이다. 따라서 신경-근육 접합부에서 신경자극 전달이 차단되어 근육쇠약과 조기 피로가 온다. 환자의 85~90%에서 혈중에 아세틸콜린 수용체에 대한 항체가 있다. 전자현미경으로 관찰시 신경 근육 접합부 접합주름 감소 및 단순화를 보인다. 환자의 15~50%는 가슴샘종과 동반되고 나머지는 가슴샘과다형성과 잘 동반된다. 광학현미경상에서는 2형 근육섬유의 위축과 탈신경에 의한 작고 각진 근육섬유가 나타나는 것 이외에는 특별한 소견을 보이지 않는다. |
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| FIMG | familial infantile myasthenia gravis |
|---|---|
| MG | 1) Myasthenia Gravis 2) MonoGlyceride 3) Monoclonal Gammop... |
| CMG | canine or congenital myasthenia gravis; chopped meat glucose [medium]; cystometrography, cystometrog... |
| EAMG | experimental autoimmune myasthenia gravis |
| JAMG | juvenile autoimmune myasthenia gravis |
| EAMG | Experimental Autoimmune Myasthenia Gravis |
|---|---|
| MG | MYASTHENIA GRAVIS |
| EIEE | Early infantile epileptic encephalopathy |
| IHPS | Infantile Hypertrophic Pyloric Stenosis |
| IM | Infantile Myofibromatosis |
| myasthenia gravis | <disease, neurology> The characteristic feature of the disease is easy fatigue of certain voluntary muscle groups on repeated use. Muscles of the face or upper trunk are especially likely to be affected. In most and perhaps all cases due to the development of autoantibodies against the acetylcholine receptor in neuromuscular junctions. Immunisation of mice or rats with this receptor protein leads to a disease with the features of myasthenia. (18 Nov 1997) |
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| myasthenia gravis and thymoma | <radiology> Of patients with MG 15% have thymoma, of patients with thymoma 50% have MG (12 Dec 1998) |
| diffuse infantile familial sclerosis | <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia Synonym: Krabbe leukodystrophy (12 Dec 1998) |
| myasthenia | <anatomy, neurology> Muscular debility, any constitutional anomaly of muscle. Origin: Gr. Astheneia = weakness (18 Nov 1997) |
| myasthenia angiosclerotica | <symptom> A symptom complex characterised by leg pain and weakness brought on by walking, with the disappearance of the symptoms following a brief rest. (12 Dec 1998) |
| anaemia gravis | <haematology> This form of anaemia occurs when the bone marrow ceases sufficient red and white blood cell production. It may be induced by exposures to high levels of toxic chemicals, radiation and certain drugs. It is generally unresponsive to specific therapy, often accompanied by granulocytopenia and thrombocytopenia, in which the bone marrow may not necessarily be hypocellular or hypoplastic but fails to produce adequate numbers of peripheral blood elements. The term actually is all inclusive and most probably encompasses several clinical syndromes. Origin: Gr. Haima = blood (29 Sep 1997) |
| colitis gravis | An obsolete term for ulcerative colitis. (05 Mar 2000) |
| neurasthenia gravis | A condition of extreme and lasting neurasthenia. (05 Mar 2000) |
| icterus gravis | Jaundice associated with high fever and delirium; seen in severe hepatitis and other diseases of the liver with severe functional failure. Synonym: malignant jaundice. (05 Mar 2000) |
| oneirodynia gravis | 1. A fiend or incubus formerly supposed to cause trouble in sleep. 2. A condition in sleep usually caused by improper eating or by digestive or nervous troubles, and characterised by a sense of extreme uneasiness or discomfort (as of weight on the chest or stomach, impossibility of motion or speech, etc), or by frightful or oppressive dreams, from which one wakes after extreme anxiety, in a troubled state of mind; incubus. 3. Hence, any overwhelming, oppressive, or stupefying influence. Origin: Night + mare incubus. See Mare incubus. Source: Websters Dictionary (01 Mar 1998) |
| aggressive infantile fibromatosis | A childhood counterpart of abdominal or extra-abdominal desmoid tumours, characterised by firm subcutaneous nodules that grow rapidly in any part of the body that invade locally and recur but do not metastasize. (05 Mar 2000) |
| autism, infantile | A syndrome beginning in infancy and characterised by a lack of responsiveness to other people, gross impairment in verbal and nonverbal communication skills, and bizarre responses to the environment. (12 Dec 1998) |
| progressive infantile spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| spasms, infantile | Primary generalised epileptic seizures occurring in infants between birth and twelve months of age consisting of brief synchronous contractions of the neck, torso, and both arms. These seizures often occur in infants with underlying neurologic diseases. The prognosis for these infants is grave, with approximately ninety percent developing mental retardation in addition to their seizures. The eeg has a typical hypsarrhythmia pattern. The spasms and hypsarrhythmia have a tendency to disappear over the first three to five years of life, only to be replaced by other forms of generalised seizures. Infantile spasms sometimes respond to valproic acid or acth. (12 Dec 1998) |
| supravalvar aortic stenosis-infantile hypercalcaemia syndrome | <syndrome> Supravalvar aortic stenosis associated with elfin facies, mental retardation, and hypercalcaemia; usually sporadic; perhaps an irregular dominant trait. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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