| methylmalonyl-CoA | An intermediate in the degradation of several metabolites (e.g., valine, methionine, odd-chain fatty acids, theronine); elevated in cases of pernicious anaemia. (05 Mar 2000) |
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| methylmalonyl-CoA epimerase | <enzyme> An enzyme that catalyses the interconversion of d-methylmalonyl-CoA and l-methylmalonyl-CoA. (05 Mar 2000) |
| methylmalonyl-CoA mutase | <enzyme> An enzyme that catalyses the conversion of methylmalonyl-CoA to succinyl-CoA by transfer of the carbonyl group. It requires a cobamide coenzyme. A block in this enzymatic conversion leads to the metabolic disease, methylmalonic aciduria. Chemical name: (R)-2-Methyl-3-oxopropanoyl-CoA CoA-carbonylmutase Registry number: EC 5.4.99.2 (12 Dec 1998) |
Synonyms : Propionyl-Coenzyme A Carboxylase, Carboxylase, Propionyl-Coenzyme A, Decarboxylase, Methylmalonyl-CoA, Methylmalonyl CoA Decarboxylase, Propionyl CoA Carboxylase, Propionyl Coenzyme A Carboxylase
Synonyms : Isomerase, Methylmalonyl-CoA, Methylmalonyl CoA Isomerase, Methylmalonyl CoA Mutase, Mutase, Methylmalonyl-CoA
| methylmalonyl-CoA epimerase |
[EC 5.1.99.1] an enzyme of the isomerase class that catalyzes the equilibration of the D- and L- isomers of methylmalonyl CoA. The reaction is part of the route by which three-carbon compounds from some amino acids and from odd number chain length fatty acids are used as fuels. Called also methylmalonyl-CoA racemase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| methylmalonyl-CoA mutase |
[EC 5.4.99.2] an enzyme of the isomerase class that catalyzes the isomerization of L- methylmalonyl coenzyme A to succinyl coenzyme A, requiring adenosylcobalamin as a coenzyme. The reaction is a step in the use of isoleucine, threonine, valine, propionate, and other odd number chain length fatty acids as fuels. Deficiency of enzyme activity, which may be caused by defects in the apoenzyme, in the coenzyme, or in cobalamin metabolism, results in methylmalonicacidemia.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| methylmalonyl-CoA racemase |
methylmalonyl-CoA epimerase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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