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  • Fatty acid-CoA
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  • acyl-coa dehydrogenase
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  • methylmalonyl acidemia
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  • acetyl CoA
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  • acetyl-S-CoA
    ¾Æ¼¼Æ¿-S-CoA
  • acyl-S-CoA
    ¾Æ½Ç-S-CoA
  • CoA
    (å²) coenzyme A
  • fatty acid CoA ligase
    Áö¹æ»ê(ò·Û¸ß«) CoA ¶óÀ̰ÔÀ̽º
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mm methylmalonyl; millimeter; mucous membrane; muscles
CoA Coarctation of Aorta
  - Complications
    1. Severe Hypertensi...
acetyl-CoA acetyl coenzyme A
COA Canadian Ophthalmological Association; Canadian Orthopaedic Association; certificate of authority; c...
CoA coenzyme A
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MCM Methylmalonyl CoA mutase
HMG CoA 3-hydroxy-3-methylglutaroyl CoA
HMG-CoA reductase 3-Hydroxy-3-methylglutaryl CoA reductase
HMG-CoA 3-hydroxymethylglutaryl-CoA
LC-CoA long chain acyl-CoA
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methylmalonyl-CoA An intermediate in the degradation of several metabolites (e.g., valine, methionine, odd-chain fatty acids, theronine); elevated in cases of pernicious anaemia.
(05 Mar 2000)
methylmalonyl-CoA epimerase <enzyme> An enzyme that catalyses the interconversion of d-methylmalonyl-CoA and l-methylmalonyl-CoA.
(05 Mar 2000)
methylmalonyl-CoA mutase <enzyme> An enzyme that catalyses the conversion of methylmalonyl-CoA to succinyl-CoA by transfer of the carbonyl group. It requires a cobamide coenzyme. A block in this enzymatic conversion leads to the metabolic disease, methylmalonic aciduria.
Chemical name: (R)-2-Methyl-3-oxopropanoyl-CoA CoA-carbonylmutase
Registry number: EC 5.4.99.2
(12 Dec 1998)
D-methylmalonyl coenzyme A hydrolase <enzyme> does not act on l-methylmalonyl-CoA
Registry number: EC 3.1.2.-
Synonym: d-methylmalonyl CoA hydrolase
(26 Jun 1999)
butyryl-CoA acetoacetate CoA transferase <enzyme> Butyryl-CoA + acetoacetate yields butyrate + acetoacetyl-CoA
Registry number: EC 2.8.3.-
Synonym: butyryl-coenzyme a acetoacetate coenzyme a transferase
(26 Jun 1999)
malonyl-CoA-acetyl CoA-acyl carrier protein S-acyltransferase <enzyme> Specific for either malonyl-CoA or acetyl-CoA; a component of fatty acid synthase
Registry number: EC 2.8.3.-
Synonym: mcoa-acoa acp acyltransferase
(26 Jun 1999)
succinyl-CoA-3-hydroxy-3-methylglutarate CoA transferase <enzyme> Rat liver mitochondrial enzyme which catalyses transfer of a conezyme a molecule from succinyl-CoA to 3-hydroxy-3-methylglutarate
Registry number: EC 2.8.3.-
Synonym: succinylcoa-hmg CoA transferase, sca-hmg cat
(26 Jun 1999)
succinyl CoA propionate CoA-transferase <enzyme> Succinyl CoA and propionate gives propionyl CoA and succinate
Registry number: EC 2.8.3.-
Synonym: succinyl coenzyme a propionate coenzyme a-transferase
(26 Jun 1999)
enoyl-CoA hydratase - 3-hydroxyacyl-CoA dehydrogenase - dodecanoyl-coenzyme A delta-isomerase <chemical> Catalyses the second and third reactions of the fatty acid beta-oxidation cycle, converting enoyl-CoA to 3-ketoacyl-CoA; EC 4.2.1.17 and EC 1.1.1.35 and EC 5.3.3.8; consider also multifunctional protein-a
Synonym: peroxisomal bifunctional enzyme, enoyl-coenzyme a hydratase -- 3-hydroxyacyl-coenzyme a dehydrogenase, peroxisomal trifunctional enzyme, delta(3), delta(2)-enoyl-CoA isomerase--2-enoyl-CoA hydratase--3-hydroxyacyl-CoA dehydrogenase
(26 Jun 1999)
acetate-CoA ligase <enzyme> An enzyme that catalyses the formation of CoA derivatives from ATP, acetate, and CoA to form AMP, pyrophosphate, and acetyl CoA. It acts also on propionates and acrylates.
Chemical name: Acetate:CoA ligase (AMP-forming)
Registry number: EC 6.2.1.1
(12 Dec 1998)
acetate-succinate CoA-transferase <enzyme> Tritichomonas and trichomonas enzyme converts acetyl-CoA and succinate to acetate and succinyl-CoA
Registry number: EC 2.8.3.-
Synonym: acetate-succinate coenzyme a-transferase
(26 Jun 1999)
acetoacetyl-CoA Intermediate in the oxidation of fatty acids and in the formation of ketone bodies; also formed from two molecules of acetyl-CoA; major role is condensation with acetyl-CoA to form the important beta-hydroxy-beta-methylglutaryl-CoA.
Synonym: acetoacetyl-coenzyme A.
(05 Mar 2000)
acetoacetyl-CoA reductase An oxidoreductase catalyzing interconversion of a 3-oxoacyl-CoA and NADPH, and the corresponding d-3-hydroxyacyl-CoA, and NADP+. A step in fatty acid synthesis.
(05 Mar 2000)
acetoacetyl-CoA synthetase <enzyme> Catalyses the conversion of acetoacetate and CoA in the presence of ATP to yield AMP, pyrophosphate and acetoacetyl-CoA; the latter is the first intermediate in cholesterogenesis; also acts more slowly on l-3-hydroxybutanoate
Registry number: EC 6.2.1.16
Synonym: acetoacetyl-CoA ligase, acetoacetate-CoA ligase, acetoacetyl-coenzyme a synthetase
(26 Jun 1999)
acetoacetyl-CoA thiolase An acetyltransferase forming acetoacetyl-CoA from two molecules of acetyl-CoA, releasing one CoA. A key step in ketogenesis and sterol synthesis.
Synonym: acetoacetyl-CoA thiolase, acetyl-CoA thiolase, thiolase.
(05 Mar 2000)
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