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MTHFR 10-Methylenetetrahydrofolate reductase
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methylenetetrahydrofolate dehydrogenase <enzyme> Catalyses the oxidation of methylenetetrahydrofolate to 5,10-methenyltetrahydrofolate. Includes EC 1.5.1.15 which uses NAD+.
Chemical name: 5,10-Methylenetetrahydrofolate:NADP+ oxidoreductase
Registry number: EC 1.5.1.5
(12 Dec 1998)
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formyl-methenyl-methylenetetrahydrofolate synthetase <chemical> Trifunctional enzyme which contains EC 6.3.4.3, formyltetrahydrofolate synthetase, plus EC 3.5.4.9, methenyltetrahydrofolate cyclohydrolase, and EC 1.5.1.5, methylenetetrahydrofolate dehydrogenase as a complex in sheep liver
Chemical name: synthetase, formyl-methenyl-methylenetetrahydrofolate
Synonym: c1-thf synthase, c1-tetrahydrofolate synthase, formyl-methenyl-methylenetetrahydrofolate synthetase (combined), c-1-tetrahydrofolate synthetase, nadp-dependent methylenetetrahydrofolate dehydrogenase-cyclohydrolase-synthetase
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 3 ÆäÀÌÁö: 1
  • Methylenetetrahydrofolate Dehydrogenase (NAD+) - »õâ A NAD-dependent oxidoreductase that catalyzes the conversion of 5,10-methylenetetrahydrofolate to 5,10-methenyl-tetrahdyrofolate. It has been found in a variety of microorganisms.
    Synonyms : 5, 10-Methylenetetrahydrofolate:NAD Oxidoreductase, Methylenetetrahydrofolate Dehydrogenase (NAD), NADH-Dependent 5, 10-Methylenetetrahydrofolate Reductase, 5, 10 Methylenetetrahydrofolate:NAD Oxidoreductase, Oxidoreductase, 5, 10-Methylenetetrahydrofolate:NAD
  • Methylenetetrahydrofolate Dehydrogenase (NADP) - »õâ An NADP-dependent oxidoreductase that catalyses the conversion of 5,10-methyleneterahydrofolate to 5,10-methenyl-tetrahydrofolate. In higher eukaryotes a trifunctional enzyme exists with additional METHENYLTETRAHYDROFOLATE CYCLOHYDROLASE and FORMATE-TETRAHYDROFOLATE LIGASE activity. The enzyme plays an important role in the synthesis of 5-methyltetrahydrofolate, the methyl donor for the VITAMIN B12-dependent remethylation of HOMOCYSTEINE to METHIONINE via METHIONINE SYNTHETASE.
    Synonyms : Methylenetetrahydrofolate Dehydrogenase, Dehydrogenase, Methylenetetrahydrofolate
  • Methylenetetrahydrofolate Reductase (NADPH2) - »õâ A flavoprotein amine oxidoreductase that catalyzes the reversible conversion of 5-METHYLTETRAHYDROFOLATE to 5,10-METHYLENETETRAHYDROFOLATE. This enzyme was formerly classified as EC 1.1.1.171.
    Synonyms : 5, 10-Methylenetetrahydrofolate Reductase (NADPH), Methylene Tetrahydrofolate Reductase, Methylenetetrahydrofolate Reductase, Methylenetetrahydrofolate Reductase (NADPH), Tetrahydrofolate Reductase, Methylene
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methylenetetrahydrofolate (THF) reductase deficiency the most common genetic aminoacidopathy of folate metabolism; the chief biochemical finding is homocystinuria with normal levels of plasma methionine; the chief clinical sign is CNS damage.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
methylenetetrahydrofolate dehydrogenase (NADP+) [EC 1.5.1.5] an enzyme activity of the oxidoreductase class that catalyzes the oxidation of 5,10-methylenetetrahydrofolate to 5,10-methenyltetrahydrofolate, using NADP+ as an electron acceptor. The reaction occurs in the system of folate-mediated one-carbon transfer reactions. The enzyme activity is part of a trifunctional enzyme that also includes methenyltetrahydrofolate cyclohydrolase and formate–tetrahydrofolate ligase activities.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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