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MSU maple sugar urine; maple syrup urine; medical studies unit; mid-stream urine; monosodium urate; myoc...
MSUD maple syrup urine disease
ACR Amylase-Creatinine Clearance Ratio
          &...
FENa, FeNa Fractional Excretion of Sodium
  ; VolumeÀÇ °³³äÀ» Á¦°ÅÇÏ¿© Á» ´õ Á¤È®ÇÑ ½ÅÀåÀÇ ³óÃà ´É·ÂÀ» Æò°¡,
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HCG, hCG Human Chorionic Gonadotropin; »ç¶÷À¶¸ð¼º¼º¼±ÀÚ±ØÈ£¸£¸ó
  1. Placental Glycoprotein Hormone
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KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
MSUD Maple Syrup Urine Disease
HFCS High-Fructose Corn Syrup
FCU First catch urine
FVU First void urine
MSU Midstream urine
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CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
maple syrup urine See: maple syrup urine disease.
(05 Mar 2000)
maple syrup urine disease Hereditary disease due to deficiency of an enzyme involved in amino acid metabolism, characterised by urine that smells like maple syrup.
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
disease, maple syrup urine Hereditary disease due to deficiency of an enzyme involved in amino acid metabolism, characterised by urine that smells like maple syrup.
(12 Dec 1998)
maple <botany> A tree of the genus Acer, including about fifty species. A. Saccharinum is the rock maple, or sugar maple, from the sap of which sugar is made, in the United States, in great quantities, by evaporation; the red or swamp maple is A. Rubrum; the silver maple, A. Dasycarpum, having fruit wooly when young; the striped maple, A. Pennsylvanium, called also moosewood. The common maple of Europe is A. Campestre, the sycamore maple is A. Pseudo-platanus, and the Norway maple is A. Platanoides.
Maple is much used adjectively, or as the first part of a compound; as, maple tree, maple leaf, etc. Bird's-eye maple, Curled maple, varieties of the wood of the rock maple, in which a beautiful lustrous grain is produced by the sinuous course of the fibres. Maple honey, Maple molasses, or Maple sirup, maple sap boiled to the consistency of molasses. Maple sugar, sugar obtained from the sap of the sugar maple by evaporation.
Origin: AS. Mapolder, mapulder, mapol; akin to Icel. Mopurr; cf. OHG. Mazzaltra, mazzoltra, G. Massholder.
Source: Websters Dictionary
(01 Mar 1998)
maple bark disease <radiology> Type of extrinsic allergic alveolitis, source: moldy maple bark in saw mills, organism: Cryptostroma corticale
(12 Dec 1998)
maple sugar Sucrose extracted from the sap of the sugar maple, Acer saccharinum.
Synonym: saccharum canadense.
(05 Mar 2000)
syrup 1. A thick and viscid liquid made from the juice of fruits, herbs, etc, boiled with sugar.
2. A thick and viscid saccharine solution of superior quality (as sugarhouse sirup or molasses, maple sirup); specifically, in pharmacy and often in cookery, a saturated solution of sugar and water (simple sirup), or such a solution flavored or medicated. "Lucent sirups tinct with cinnamon." (Keats) Mixing sirup. See the Note under Dextrose.
Origin: F. Sirop (cf. It. Siroppo, Sp. Jarabe, jarope, LL. Siruppus, syrupus), fr. Ar. Sharab a drink, wine, coffee, sirup. Cf. Sherbet.
Source: Websters Dictionary
(01 Mar 1998)
ipecac syrup A sweetened liquid medicinal preparation containing powdered ipecac extract, which contains the alkaloids emetine and cephaline; used as an emetic in certain cases of poisoning and (at lower doses) as an expectorant.
(05 Mar 2000)
ipecac (syrup) <chemical> A syrup made from the dried rhizomes of two different species, c. Ipecacuanha and c. Acuminata of cephaelis (or uragoga) of the rubiaciae; they contain emetine, cephaeline, psychotrine and other isoquinolines. Ipecac syrup is used widely as an emetic acting both locally on the gastric mucosa and centrally on the chemoreceptor trigger zone. It may also be used as an expectorant.
Pharmacological action: emetics, expectorants.
Chemical name: Ipecac
(12 Dec 1998)
ammoniacal urine <nephrology> Excretion of urine that contains an excessive amount of ammonia.
Synonym: ammoniacal urine.
Origin: ammonia + G. Ouron, urine
(05 Mar 2000)
black urine The dark urine of melanuria or haemoglobinuria.
(05 Mar 2000)
Gerhardt's test for urobilin in the urine The urobilin is extracted with chloroform and then treated with iodine and potassium hydrate, a fluorescent green colour being produced.
(05 Mar 2000)
residual urine Urine remaining in the bladder at the end of micturition in cases of prostatic obstruction, bladder atony, etc.
(05 Mar 2000)
gouty urine Urine of a high colour containing uric acid in excess.
(05 Mar 2000)
chylous urine Urine of a milky appearance, containing chyle.
Synonym: milky urine.
(05 Mar 2000)
citric acid urine test <investigation> A test which measures the amount of citric acid in the urine. This test is used to diagnose renal tubular acidosis and evaluate those with kidney stones.
A below normal level of citric acid in the urine can indicate renal tubular acidosis. Urine citric acid levels can be increased in those with have a high carbohydrate diet, are on oestrogen therapy or vitamin D therapy.
(27 Sep 1997)
milky urine Urine of a milky appearance, containing chyle.
Synonym: milky urine.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Maple Syrup Urine Disease - »õâ An autosomal recessive inherited disorder with multiple forms of phenotypic expression, caused by a defect in the oxidative decarboxylation of branched-chain amino acids (AMINO ACIDS, BRANCHED-CHAIN). These metabolites accumulate in body fluids and render a "maple syrup" odor. The disease is divided into classic, intermediate, intermittent, and thiamine responsive subtypes. The classic form presents in the first week of life with ketoacidosis, hypoglycemia, emesis, neonatal seizures, and hypertonia. The intermediate and intermittent forms present in childhood or later with acute episodes of ataxia and vomiting. (From Adams et al., Principles of Neurology, 6th ed, p936)
    Synonyms : Classic Maple Syrup Urine Disease, Classical Maple Syrup Urine Disease, Intermediate Maple Syrup Urine Disease, Intermittent Maple Syrup Urine Disease, MSUD (Maple Syrup Urine Disease), Maple Syrup Urine Disease, Classic, Maple Syrup Urine Disease, Classical
¿ÜºÎ ¸µÅ© - Merriam-Webster's ÀÇÇлçÀü ¸ÂÃã °Ë»ö (https://www.merriam-webster.com) °á°ú: 1 ÆäÀÌÁö: 1
¿ÜºÎ ¸µÅ© - A.D.A.M. Medical Encyclopedia ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú: 1 ÆäÀÌÁö: 1
¿ÜºÎ ¸µÅ© - MedlinePlus Health Topics ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú: 1 ÆäÀÌÁö: 1
KMLE À¥ ¿ë¾î ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
maple syrup urine d. an autosomal recessive aminoacidopathy due to a defect in the second step in branched-chain amino acid catabolism; the decarboxylation of the corresponding α-keto acids by the branched-chain α-keto acid dehydrogenase complex. Branched-chain amino acids and their keto acid analogues accumulate in blood and urine, causing severe ketoacidosis, seizures, coma, physical and mental retardation, and a characteristic smell of maple syrup in the urine and on the body. The disease can be divided into four clinical phenotypes: classic, the most severe, with neonatal onset and usually rapid death; intermediate, of lessened severity and usually later onset; intermittent, with normal periods punctuated by periods of ataxia and ketoacidosis; and thiamine-responsive, caused by decreased affinity of the dehydrogenase complex for the cofactor thiamine pyrophosphate. In at least some cases, MSUD is due to deficiency of one of the enzymes of the branched-chain α-keto acid dehydrogenase complex (see under complex). See also lipoamide dehydrogenase deficiency. Called also branched-chain ketoaciduria.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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    °ñµç ½Ã·´(²Ü ½Ã·´)
  • maple
    (½Ä) ´Üdz (³ª¹«)
  • maple leaf
    ´ÜdzÀÙ (ij³ª´ÙÀÇ Ç¥Àå)
  • maple sugar
    ´Üdz´ç
  • rock maple
    =SUGAR MAPLE
  • syrup
    ½Ã·´
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maple syrup urine an inherited disorder of metabolism in which the urine has a odor characteristic of maple syrup
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