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  • mannosidase, alpha-mannosidase, deficiency
    #NAME?
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MANA mannosidase alpha
MANB mannosidase beta
MNB mannosidase beta; murine neuroblastoma
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
mannosidase <enzyme> Catalysing hydrolysis of the glycosidic bond between mannose residues and a variety of hydroxyl containing groups. _ mannosidases in rough endoplasmic reticulum and cis Golgi are responsible for removing four mannose residues during the synthesis of the complex type N linked glycan chains of glycoproteins.
(18 Nov 1997)
mannosidases <enzyme> Alpha or beta-mannoside mannohydrolases. Catalyses the hydrolysis of terminal, non-reducing alpha or beta-d-mannose residues in mannosides. Deficiency of the alpha form can cause mannosidosis.
Registry number: EC 3.2.1.
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 9 ÆäÀÌÁö: 1
alpha1-2,alpha1-3,alpha1-6-mannosidase <enzyme> From rat liver; releases alpha1-2, alpha1-3, alpha1-6 linked residues from oligosaccharide substrates; end product of reaction is manalpha1-3(manalpha1-6)manbeta1-4glcnac; mw 110 kD; inhibited by edta, zn++ and cu++, swainsonine and 1-deoxymannojirimycin
Registry number: EC 3.2.1.-
Synonym: 2,3,6-alpha-mannosidase
(26 Jun 1999)
alpha(1-6)mannosidase <enzyme> Human lysosomal enzyme highly specific for alpha 1-6 mannose residues; inhibited by swainsonine; not the same enzyme which is deficient in alpha-mannosidosis
Registry number: EC 3.2.1.-
(26 Jun 1999)
alpha-mannosidase <enzyme> Catalyses hydrolysis of terminal, non-reducing alpha-d-mannose residues in alpha-d-mannosides
Registry number: EC 3.2.1.24
Synonym: alpha-d-mannoside mannohydrolase, alpha-d-mannosidase, neutral alpha-mannosidase, alpha mannosidase a, alpha mannosidase b, lysosomal alpha-mannosidase, laman
(26 Jun 1999)
aryl-alpha-mannosidase <enzyme> Act on p-nitrophenyl-alpha-d-mannopyranoside
Registry number: EC 3.2.1.-
Synonym: aryl-alpha-mannosidase a, aryl-alpha-mannosidase b
(26 Jun 1999)
beta-D-mannosidase <enzyme> Catalyses hydrolysis of terminal, non-reducing beta-d-mannose residues in beta-d-mannosides
Registry number: EC 3.2.1.25
Synonym: mannanase, beta-mannosidase, mana gene product
(26 Jun 1999)
mannosyl-oligosaccharide 1,2-alpha-mannosidase <enzyme> Cleaves off terminal alpha-1,2-linked mannose residues resulting in the oligosaccharide man(9)glcnac(2)
Registry number: EC 3.2.1.113
Synonym: alpha-d-mannosidase I, mannosidase I, man9-mannosidase, man9-alpha-mannosidase, alpha 1,2-mannosidase, 1,2-alpha-d-mannosidase, msds protein
(26 Jun 1999)
mannosyl-oligosaccharide 1,3 - 1,6-alpha-mannosidase <enzyme> Removes alpha-1,3- and alpha-1,6-mannosyl residues during post-translational modification of glycoproteins; amino acid sequence of gmii (drosophila) given in second source; genbank x77652
Registry number: EC 3.2.1.114
Synonym: mannosidase II, alpha-d-mannosidase II, 1,3-(1,6-)mannosyl-oligosaccharide alpha-d-mannohydrolase, golgi alpha-mannosidase II, gmii gene product
(26 Jun 1999)
glycoprotein endo-alpha-1,3-mannosidase <enzyme> An endomannosidase; cleaves glucosyl alpha1-3-mannose from monoglucosylated oligosaccharide (glcman(7-9)glcnac) of the glycoprotein produced in the golgi membrane
Registry number: EC 3.2.1.130
Synonym: glucosyl mannosidase
(26 Jun 1999)
endo-alpha-D-mannosidase <enzyme> Catalyses the cleavage of glc(1)man(9)glcnac to yield man(8)glcnac and glcalpha1-3man
Registry number: EC 3.2.1.-
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 2 ÆäÀÌÁö: 1
  • Mannosidase Deficiency Diseases - »õâ Diseases caused by the loss of one or more enzymes involved in the hydrolysis of mannoside linkages (MANNOSIDASES). The defects in enzyme activity are primarily associated with genetic mutation of the genes that codes for a particular mannosidase isoenzyme.
    Synonyms : Mannosidase Deficiency Syndromes, Deficiency Disease, Mannosidase, Deficiency Diseases, Mannosidase, Deficiency Syndrome, Mannosidase, Deficiency Syndromes, Mannosidase, Diseases, Mannosidase Deficiency, Mannosidase Deficiency Disease, Mannosidoses
  • Mannosidases - »õâ Glycoside hydrolases that catalyze the hydrolysis of alpha or beta linked MANNOSE.
    Synonyms :
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