| maleylacetoacetate | An intermediate in l-phenylalanine and l-tyrosine catabolism; accumulates in certain inherited disorders of tyrosine metabolism. Maleylacetoacetate cis,trans-isomerase, an enzyme that catalyses the reversible conversion of maleylacetoacetate to 4-fumarylacetoacetate; an enzyme that participates in l-tyrosine catabolism; a deficiency of this enzyme is associated with tyrosinaemia type IB. Structure: -OOC-CH==CH-COCH2COCH2COO- (05 Mar 2000) |
|---|
| maleylacetoacetate isomerase |
[EC 5.2.1.2] an enzyme of the isomerase class that catalyzes the interconversion of the isomers 4-maleylacetoacetate and 4-fumarylacetoacetate. The reaction is a step in the use of phenylalanine and tyrosine as fuel.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|
Á¦Ç°¸í |
ÆÇ¸Å»ç |
º¸ÇèÄÚµå | ¼ººÐ/ÇÔ·® | ±¸ºÐ/º¸Çè±Þ¿© |
|---|
Á¦Ç°¸í |
ÆÇ¸Å»ç |
º¸ÇèÄÚµå | ¼ººÐ/ÇÔ·® | ±¸ºÐ/º¸Çè±Þ¿© |
|---|