| GDH | glucose dehydrogenase; glutamate dehydrogenase; glycerophosphate dehydrogenase; glycol dehydrogenase... |
|---|---|
| HADH | hydroxyacyl CoA dehydrogenase |
| MADD | Mothers Against Drunk Driving; multiple acyl-CoA dehydrogenase deficiency |
| MCAD | medium chain acyl-CoA dehydrogenase |
| GPD | glucose-6-phosphate dehydrogenase; glycerol-phosphate dehydrogenase |
| HMG CoA | 3-hydroxy-3-methylglutaroyl CoA |
|---|---|
| HMG-CoA reductase | 3-Hydroxy-3-methylglutaryl CoA reductase |
| HMG-CoA | 3-hydroxymethylglutaryl-CoA |
| LC-CoA | long chain acyl-CoA |
| HAD | 3-Hydroxyacyl-CoA dehydrogenase |
| long-chain 3-hydroxyacyl CoA dehydrogenase | <enzyme> Deficiency may cause some cases of hypoglycaemic 3-hydroxydicarboxylic aciduria Registry number: EC 1.1.1.211 Synonym: l-chad (26 Jun 1999) |
|---|
| enoyl-CoA hydratase - 3-hydroxyacyl-CoA dehydrogenase - dodecanoyl-coenzyme A delta-isomerase | <chemical> Catalyses the second and third reactions of the fatty acid beta-oxidation cycle, converting enoyl-CoA to 3-ketoacyl-CoA; EC 4.2.1.17 and EC 1.1.1.35 and EC 5.3.3.8; consider also multifunctional protein-a Synonym: peroxisomal bifunctional enzyme, enoyl-coenzyme a hydratase -- 3-hydroxyacyl-coenzyme a dehydrogenase, peroxisomal trifunctional enzyme, delta(3), delta(2)-enoyl-CoA isomerase--2-enoyl-CoA hydratase--3-hydroxyacyl-CoA dehydrogenase (26 Jun 1999) |
|---|---|
| butyryl-CoA acetoacetate CoA transferase | <enzyme> Butyryl-CoA + acetoacetate yields butyrate + acetoacetyl-CoA Registry number: EC 2.8.3.- Synonym: butyryl-coenzyme a acetoacetate coenzyme a transferase (26 Jun 1999) |
| malonyl-CoA-acetyl CoA-acyl carrier protein S-acyltransferase | <enzyme> Specific for either malonyl-CoA or acetyl-CoA; a component of fatty acid synthase Registry number: EC 2.8.3.- Synonym: mcoa-acoa acp acyltransferase (26 Jun 1999) |
| succinyl-CoA-3-hydroxy-3-methylglutarate CoA transferase | <enzyme> Rat liver mitochondrial enzyme which catalyses transfer of a conezyme a molecule from succinyl-CoA to 3-hydroxy-3-methylglutarate Registry number: EC 2.8.3.- Synonym: succinylcoa-hmg CoA transferase, sca-hmg cat (26 Jun 1999) |
| succinyl CoA propionate CoA-transferase | <enzyme> Succinyl CoA and propionate gives propionyl CoA and succinate Registry number: EC 2.8.3.- Synonym: succinyl coenzyme a propionate coenzyme a-transferase (26 Jun 1999) |
| acyl-CoA dehydrogenase | <enzyme> See also records for specific fatty acyl groups which have full EC nomenclature number; electron-transferring flavoprotein system reducing ubiquinone and other acceptors; formerly EC 1.3.2.2 Registry number: EC 1.3.99.3 Synonym: fatty-acyl CoA dehydrogenase, palmitoyl-CoA dehydrogenase, short-chain acyl-CoA dehydrogenase, acyl-coenzyme a dehydrogenase, lauroyl-CoA oxidase (26 Jun 1999) |
| acyl-CoA dehydrogenase (NADPH+) | Enzyme catalyzing the reversible reduction of enoyl-CoA derivatives of chain length 4 to 16, with NADPH as the hydrogen donor, forming acyl-CoA and NADP+. Synonym: enoyl-CoA reductase. (05 Mar 2000) |
| butyryl-CoA dehydrogenase | <enzyme> Electron-transferring flavoprotein system reducing ubiquinone and other acceptors; formerly EC 1.3.2.1; a short-chain acyl-CoA dehydrogenase Registry number: EC 1.3.99.2 Synonym: butyryl dehydrogenase, butyryl-coenzyme a dehydrogenase (26 Jun 1999) |
| palmitoyl-CoA dependent dehydrogenase | <chemical> Sum of reactions catalyzed by fatty acyl-CoA oxidase, enoyl-CoA hydratase (EC 4.2.1.17) and beta-hydroxyacyl-CoA dehydrogenase (EC 1.1.1.35) Synonym: palmitoyl-coenzyme a dependent dehydrogenase (26 Jun 1999) |
| glutaryl-CoA dehydrogenase | <enzyme> Glutaric aciduria may be due to deficiency of this enzyme Registry number: EC 1.3.99.7 Synonym: glutaryl CoA dehydrogenase, glutaryl-coenzyme a dehydrogenase (26 Jun 1999) |
| medium-chain acyl-CoA dehydrogenase | <enzyme> Deficiency in mitochondrial beta oxidation of fatty acids gives a disorder frequently masquerading as reye syndrome or sudden infant death; leads to buildup of octanoyl carnitine in urine Registry number: EC 1.3.- Synonym: mcaca-dehydrogenase, medium-chain acyl-coenzyme a dehydrogenase, octanoyl-CoA dehydrogenase, mcad enzyme (26 Jun 1999) |
| short-chain acyl-CoA dehydrogenase | See: acyl-CoA dehydrogenase (NADPH+). (05 Mar 2000) |
| 2-furoyl-CoA dehydrogenase | <enzyme> Chemical name: 2-furoyl-CoA hydroxylase Registry number: EC 1.3.99.8 Synonym: 2-furoyl-coenzyme a dehydrogenase (26 Jun 1999) |
| 2-methylacyl-CoA dehydrogenase | <enzyme> Involved in isoleucine and valine metabolism; from rat liver mitochondria Registry number: EC 1.3.99.12 Synonym: s-2-methylbutyryl-CoA dehydrogenase, isobutyryl-CoA dehydrogenase, 2-methyl-branched chain acyl coenzyme a dehydrogenase, 2-methyl-branched chain acyl-CoA dehydrogenase, 2-methylacyl-coenzyme a dehydrogenase, branched-chain acyl-CoA dehydrogenase (26 Jun 1999) |
| 3-hydroxy-2-methylpropionyl-CoA dehydrogenase | <enzyme> Forms methylmalonyl-CoA saemialdehyde Registry number: EC 1.1.1.- Synonym: 3-hydroxyisobutyryl-CoA dehydrogenase (26 Jun 1999) |
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