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  • lipoamide
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  • lysyl-lipoamide
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LAD lactic acid dehydrogenase; left anterior descending [artery]; left axis deviation; leukocyte adhesio...
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LipDH Lipoamide dehydrogenase
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lipoamide <biochemistry> The functional form of lipoic acid in which the carboxyl group is attached to protein by an amide linkage to a lysine amino group.
(18 Nov 1997)
lipoamide dehydrogenase <enzyme> An enzyme that regenerates lipoamide from the reduced form dihydrolipoamide.
(18 Nov 1997)
lipoamide disulfide Oxidised lipoic acid in amide combination with the &vepsilon;-amino group of an l-lysyl residue of pyruvic acid dehydrogenase.
(05 Mar 2000)
lipoamide reductase <enzyme> An enzyme oxidizing dihydrolipoamide at the expense of NAD+; completes the oxidative decarboxylation of pyruvate; a part of several enzyme complexes (e.g., alpha-ketoglutarate dehydrogenase complex). Decreased activity leads to neuronal loss in brain resulting in psychomotor retardation.
Synonym: coenzyme factor, lipoamide dehydrogenase, lipoamide reductase (NADH), lipoyl dehydrogenase.
(05 Mar 2000)
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pyruvate dehydrogenase (lipoamide) An oxidoreductase catalyzing conversion of pyruvate and (oxidised) lipoamide to CO2 and S6-acetyldihydrolipoamide in two successive reactions: the first between pyruvate and thiamin pyrophosphate to yield CO2 and alpha-hydroxyethylthiamin pyrophosphate (active pyruvate); the second between the last named and lipoamide to regain the thiamin pyrophosphate and yield S6-acetylhydrolipoamide.
Compare: alpha-ketodecarboxylase.
(05 Mar 2000)
pyruvate dehydrogenase (lipoamide)-phosphatase <enzyme> (pyruvate dehydrogenase (lipoamide))-phosphate phosphohydrolase. A mitochondrial enzyme that catalyses the hydrolytic removal of a phosphate on a specific seryl hydroxyl group of pyruvate dehydrogenase, reactivating the enzyme complex.
Registry number: EC 3.1.3.43
(12 Dec 1998)
(pyruvate dehydrogenase (lipoamide))kinase Registry number: EC 2.7.1.99
Synonym: pyruvate dehydrogenase kinase
(26 Jun 1999)
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lipoamide dehydrogenase (lipo
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
lipoamide dehydrogenase deficiency (lipo
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
lipoamide lipoic acid in amide linkage with lysine side chains of enzymes of the α-ketoglutarate dehydrogenase, branched-chain α-keto acid dehydrogenase, and pyruvate dehydrogenase complexes (q.v.). Its reactive disulfide group and long, flexible chain enable it to transfer intermediates among the enzymes of each complex.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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