| LacCer | Lactosylceramide |
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| lactosylceramides | Glycosphingolipids which contain as their polar head group a lactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in lactosylceramide beta-galactosidase, is the cause of lactosylceramidosis. (12 Dec 1998) |
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| UDP-galactose-lactosylceramide alpha 1-4-galactosyltransferase | <enzyme> Catalyses transfer of galactose from udp-galactose to lactosylceramide; exclusively an alpha1-4-galactosyltransferase Registry number: EC 2.4.1.- Synonym: udpgal-galactosyl-beta-1-4-glucosylceramide alpha1-4-galactosyltransferase, globotriaosylceramide synthase, udp-glcg-transferase, udp galactose lactosylceramide alpha-galactosyltransferase, udp-gal lcgtase, udp-gal-galactose alpha(1,4)-galactosyltransferase, alpha1,4galt (26 Jun 1999) |
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| UDP-galactose-lactosylceramide beta 1-3-galactosyltransferase | <enzyme> Catalyses transfer of galactose from udp-galactose to lactose or lactosylceramide Registry number: EC 2.4.1.- Synonym: udp-galactose-lactose beta 1-3 galactosyltransferase, udp-galactose-lactose (lactosylceramide) beta-3-galactosyltransferase, udpgal-lac-3-transferase (26 Jun 1999) |
Synonyms : Ceramides, Lactosyl
| lactosylceramide |
any of the glycosphingolipids in which the head group on the ceramide is lactose; they occur at low concentrations in all tissues.
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