| IVD | Isovaleryl-CoA dehydrogenase |
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| isovaleryl-CoA | The condensation product of isovaleric acid and coenzyme A; an intermediate in the catabolism of l-leucine. Synonym: isovalerylcoenzyme A. Isovaleryl-CoA dehydrogenase, an enzyme that participates in the catabolism of l-leucine; it converts isovaleryl-CoA to 3-methylcrotonyl-CoA using FAD; a deficiency in this enzyme will result in isovaleric acidemia. (05 Mar 2000) |
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| isovalerylcoenzyme A | The condensation product of isovaleric acid and coenzyme A; an intermediate in the catabolism of l-leucine. Synonym: isovalerylcoenzyme A. Isovaleryl-CoA dehydrogenase, an enzyme that participates in the catabolism of l-leucine; it converts isovaleryl-CoA to 3-methylcrotonyl-CoA using FAD; a deficiency in this enzyme will result in isovaleric acidemia. (05 Mar 2000) |
| 4''-mycarosyl isovaleryl-coenzyme A transferase | <enzyme> Carries out 4"-o-acylation of macrolide antibiotic on the 4"-hydroxy moiety of mycarose; acyb1 isolated from streptomyces thermotolerans; amino acid sequence given in first source Registry number: EC 2.3.1.- Synonym: care protein, acyb1 protein, 4''-mycarosyl isovaleryl-CoA transferase (26 Jun 1999) |
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Synonyms : Isovaleryl CoA Dehydrogenase, Isovaleryl-Coenzyme A Dehydrogenase, A Dehydrogenase, Isovaleryl-Coenzyme, CoA Dehydrogenase, Isovaleryl, Dehydrogenase, Isovaleryl CoA, Dehydrogenase, Isovaleryl-CoA, Dehydrogenase, Isovaleryl-Coenzyme A
| isovaleryl |
the radical of isovaleric acid; the thioester formed with coenzyme A, isovaleryl CoA, is an intermediate in the catabolism of leucine.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| isovaleryl-CoA dehydrogenase |
[EC 1.3.99.10] an enzyme of the oxidoreductase class that catalyzes the dehydrogenation of isovaleryl CoA to 3-methylcrotonyl CoA, using ubiquinone as an electron acceptor. The reaction is a step in the use of leucine as a fuel. Deficiency of the enzyme, an autosomal recessive trait, results in isovalericacidemia.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| isovalerylglycine |
a conjugate of isovaleric acid and the amide group of glycine; high levels are formed and excreted in the urine in isovalericacidemia.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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