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  • iduronate sulfatase deficiency
    Iduronate sulfatase deficiency
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  • iduronate sulfatase deficiency
    Iduronate sulfatase deficiency
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IDS iduronate sulfatase; immune deficiency state; inhibitor of DNA synthesis; integrated delivery system...
SIDS sudden infant death syndrome; sulfo-iduronate sulfatase
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IDS Iduronate 2-sulphatase
IDS Iduronate sulfatase
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iduronate The salt or ester of iduronic acid.
(05 Mar 2000)
iduronate sulfatase <enzyme> An enzyme that specifically cleaves the ester sulfate of iduronic acid, and is required for the desulfation of 2-sulfate iduronate residues in heparan sulfate. It is also required in dermatan sulfate degradation.
Its deficiency has been demonstrated in Hunter's syndrome, which is characterised by an excess of dermatan sulfate and heparan sulfate.
Chemical name: L-Iduronate-2-sulfate 2-sulfohydrolase
Registry number: EC 3.1.6.13
(20 Sep 2002)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Iduronate Sulfatase - »õâ An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.
    Synonyms : Iduronate Sulfate Sulfatase, Corrective Factor, Hunter, Factor, Hunter Corrective, Sulfatase, Iduronate, Sulfatase, Iduronate Sulfate, Sulfatase, Sulfoiduronate, Sulfate Sulfatase, Iduronate, Sulfohydrolase, Iduronatesulfate
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iduronate a salt, ester, or anionic form of iduronic acid.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
iduronate-2-sulfatase [EC 3.1.6.13] a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of sulfate groups from the L-iduronate residues of dermatan sulfate and heparan sulfate, a step in the degradation of these glycosaminoglycans. Deficiency of the enzyme, an X-linked recessive trait, results in Hunter's syndrome (mucopolysaccharidosis II).
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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