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  • ichthyosiform
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  • ichthyosiform dermatitis
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  • ichthyosiform erythroderma
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  • ichthyosiform nevus
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  • ichthyosiform
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  • ichthyosiform dermatitis
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  • ichthyosiform erythroderma
    ºñ´ÃÇǺÎÁõ¸ð¾çÈ«»öÇǺÎÁõ
  • ichthyosiform nevus
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  • ichthyosiform
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  • ichthyosiform dermatitis
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  • ichthyosiform erythroderma
    ¾î¸°¼±¾çÈ«ÇÇÁõ
  • ichthyosiform nevus
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  • ichthyosiform
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  • ichthyosiform dermatitis
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  • ichthyosiform erythroderma
    ¾î¸°¼±¾çÈ«ÇÇÁõ
  • ichthyosiform nevus
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  • congenital bullous ichthyosiform erythroderma
    ¼±Ãµ¼º ¼öÆ÷¼º¾î¸°¼±¾ç È«ÇÇÁõ
  • congenital ichthyosiform erythroderma
    ¼±Ãµ¾î¸°¼±Çü È«ÇÇÁõ
  • congenital nonbullous ichthyosiform erythroderma
    ¼±Ãµ¼º ºñ¼öÆ÷¼º ¾î¸°¼±¾ç È«ÇÇÁõ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
BIE bullous ichthyosiform erythroderma
CHILD congenital hemidysplasia with ichthyosiform erythroderma and limb defects [syndrome]
NBCIE nonbullous congential ichthyosiform erythroderma
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  • congenital bullous ichthyosiform erythroderma
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CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
ichthyosiform erythroderma A genodermatosis characterised by diffuse chronic erythema and scale formation which may be separated into bullous and nonbullous forms.
Synonym: ichthyosiform erythroderma, ichthyosis spinosa, keratoma malignum.
(05 Mar 2000)
ichthyosiform erythroderma, congenital Designation for several severe forms of ichthyosis, present at birth, that are characterised by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalised scaling. The forms include bullous (hyperkeratosis, epidermolytic), non-bullous (ichthyosis, lamellar), wet type, and dry type.
(12 Dec 1998)
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bullous congenital ichthyosiform erythroderma Diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterised by generalised epidermolytic hyperkeratosis and autosomal dominant inheritance.
See: epidermolytic hyperkeratosis.
Synonym: generalised epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix.
(05 Mar 2000)
congenital ichthyosiform erythroderma A genodermatosis characterised by diffuse chronic erythema and scale formation which may be separated into bullous and nonbullous forms.
Synonym: ichthyosiform erythroderma, ichthyosis spinosa, keratoma malignum.
(05 Mar 2000)
nonbullous congenital ichthyosiform erythroderma Erythroderma or a collodion membrane at birth, usually without improvement during childhood, characterised by proliferation of epidermal keratinocytes with lipid accumulation; autosomal recessive inheritance.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Ichthyosiform Erythroderma, Congenital - »õâ Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
    Synonyms : Congenital Ichthyosiform Erythroderma, Dry Type, Congenital Ichthyosiform Erythroderma, Wet Type, Erythroderma, Congenital Ichthyosiform, Congenital Ichthyosiform Erythrodermas, Erythrodermas, Congenital Ichthyosiform
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ichthyosiform resembling ichthyosis.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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