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HOKPP hypokalemic periodic paralysis
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  • Hypokalemic Periodic Paralysis - »õâ An autosomal dominant familial disorder characterized by recurrent episodes of skeletal muscle weakness associated with falls in serum potassium levels. The condition usually presents in the first or second decade of life with attacks of trunk and leg paresis during sleep or shortly after awakening. Symptoms may persist for hours to days and generally are precipitated by exercise or a meal high in carbohydrates. (Adams et al., Principles of Neurology, 6th ed, p1483)
    Synonyms : Hypokalemic Periodic Paralysis, Familial, Periodic Paralysis, Hypokalemic
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hypokalemic 1. pertaining to or characterized by hypokalemia.  2. an agent that acts to lower the potassium content of the blood.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
hypokalemic a. a type of metabolic alkalosis associated with a low serum potassium level; retention of alkali or loss of acid occurs in the extracellular (but not intracellular) fluid compartment, although the pH of the intracellular fluid may be below normal. It may be caused by hypertrophy and hypoplasia of the juxtaglomerular cells, as in Bartter syndrome.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
hypokalemic n. nephropathy with hypokalemia, interstitial nephritis, swelling and vacuolization of proximal renal tubules, and progressive renal failure, resulting from long-term conditions such as oncotic overloading of the kidney filtration mechanisms by sugars. Cf. potassium-losing n. Called also hypokalemic, osmotic, or vacuolar nephrosis.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
hypokalemic periodic p. see familial periodic p.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
hypokalemic alkalosis Metabolic alkalosis associated with an excessive loss of potassium. It may be caused by diuretic therapy.
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