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  • succinyl CoA
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  • Fatty acid-CoA
    Áö¹æ»ê(ò·Û¸ß«) ÄÚ¿£ÀÚÀÓA
  • Hydroxymethylglutary-CoA
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  • acyl-coa dehydrogenase
    acyl-CoA Å»¼ö¼ÒÈ¿¼Ò(¡­÷­â©áÈý£áÈ)
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  • acyl-coa dehydrogenase
    acyl-CoA Å»¼ö¼ÒÈ¿¼Ò(¡­÷­â©áÈý£áÈ)
  • methylmalonyl CoA
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  • acetoacetyl CoA
    ¾Æ¼¼Å侯¼¼Æ¿ CoA
  • acetyl CoA
    ¾Æ¼¼Æ¿ CoA
  • acetyl-S-CoA
    ¾Æ¼¼Æ¿-S-CoA
  • acyl-S-CoA
    ¾Æ½Ç-S-CoA
  • CoA
    (å²) coenzyme A
  • fatty acid CoA ligase
    Áö¹æ»ê(ò·Û¸ß«) CoA ¶óÀ̰ÔÀ̽º
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HADH hydroxyacyl CoA dehydrogenase
HAGH hydroxyacyl-glutathione hydrolase
CoA Coarctation of Aorta
  - Complications
    1. Severe Hypertensi...
acetyl-CoA acetyl coenzyme A
COA Canadian Ophthalmological Association; Canadian Orthopaedic Association; certificate of authority; c...
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HAD 3-Hydroxyacyl-CoA dehydrogenase
LCHAD Long chain 3-hydroxyacyl-CoA-dehydrogenase
HMG CoA 3-hydroxy-3-methylglutaroyl CoA
HMG-CoA reductase 3-Hydroxy-3-methylglutaryl CoA reductase
HMG-CoA 3-hydroxymethylglutaryl-CoA
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enoyl-CoA hydratase - 3-hydroxyacyl-CoA dehydrogenase - dodecanoyl-coenzyme A delta-isomerase <chemical> Catalyses the second and third reactions of the fatty acid beta-oxidation cycle, converting enoyl-CoA to 3-ketoacyl-CoA; EC 4.2.1.17 and EC 1.1.1.35 and EC 5.3.3.8; consider also multifunctional protein-a
Synonym: peroxisomal bifunctional enzyme, enoyl-coenzyme a hydratase -- 3-hydroxyacyl-coenzyme a dehydrogenase, peroxisomal trifunctional enzyme, delta(3), delta(2)-enoyl-CoA isomerase--2-enoyl-CoA hydratase--3-hydroxyacyl-CoA dehydrogenase
(26 Jun 1999)
short-chain beta-hydroxyacyl-CoA dehydrase <enzyme> Forms trans-2-enoyl-CoA; maximal activity with trans-2-hexenoyl-CoA, followed by crotonyl-CoA; not the same as EC 4.2.1.17
Registry number: EC 4.2.1.-
Synonym: beta-hydroxybutyryl-CoA dehydrase, short-chain beta-hydroxyacyl-coenzyme a dehydrase
(26 Jun 1999)
D-3-hydroxyacyl CoA dehydratase <enzyme> From rat liver peroxisomes; catalyses the epimerization of d-3-hydroxyacyl CoA by the dehydration of 3-hydroxyacyl-CoA to 2-trans-enoyl-CoA followed by the hydration of the latter enzyme to l-3-hydroxyacyl-CoA by enoyl-CoA hydratase (EC 4.2.1.17); is not active on 2-cis-enoyl CoA; consider also EC 4.2.1.74
Registry number: EC 4.2.1.-
Synonym: d-3-hydroxyacyl coenzyme a dehydratase, beta-hydroxyacyl-CoA dehydratase
(26 Jun 1999)
3-hydroxyacyl-CoA dehydrogenase Beta-Hydroxyacyl dehydrogenase;enzyme catalyzing the oxidation of an l-3-hydroxyacyl-CoA to a 3-ketoacyl-CoA with reduction of NAD+; one of the enzymes of the b oxidation of fatty acids.
Synonym: beta-ketohydrogenase, beta-ketoreductase.
(05 Mar 2000)
3-hydroxyacyl CoA dehydrogenases <enzyme> Enzymes that reversibly catalyze the oxidation of a 3-hydroxyacyl CoA to 3-ketoacyl CoA in the presence of NAD. They are key enzymes in the oxidation of fatty acids and in mitochondrial fatty acid synthesis.
Chemical name: (S)-3-Hydroxyacyl-CoA:NAD+ oxidoreductase
Registry number: EC 1.1.1.35
(12 Dec 1998)
long-chain 3-hydroxyacyl CoA dehydrogenase <enzyme> Deficiency may cause some cases of hypoglycaemic 3-hydroxydicarboxylic aciduria
Registry number: EC 1.1.1.211
Synonym: l-chad
(26 Jun 1999)
beta-hydroxyacyl-(acyl-carrier-protein)dehydrase <enzyme> In fatty acid synthesis; specific for acyl carrier protein; cannot use acyl CoA; see also faba gene product
Registry number: EC 4.2.1.-
Synonym: beta-ohacyl-acp dehydrase, beta-hydroxyacyl-acyl carrier protein dehydratase, fabz gene product
(26 Jun 1999)
butyryl-CoA acetoacetate CoA transferase <enzyme> Butyryl-CoA + acetoacetate yields butyrate + acetoacetyl-CoA
Registry number: EC 2.8.3.-
Synonym: butyryl-coenzyme a acetoacetate coenzyme a transferase
(26 Jun 1999)
malonyl-CoA-acetyl CoA-acyl carrier protein S-acyltransferase <enzyme> Specific for either malonyl-CoA or acetyl-CoA; a component of fatty acid synthase
Registry number: EC 2.8.3.-
Synonym: mcoa-acoa acp acyltransferase
(26 Jun 1999)
succinyl-CoA-3-hydroxy-3-methylglutarate CoA transferase <enzyme> Rat liver mitochondrial enzyme which catalyses transfer of a conezyme a molecule from succinyl-CoA to 3-hydroxy-3-methylglutarate
Registry number: EC 2.8.3.-
Synonym: succinylcoa-hmg CoA transferase, sca-hmg cat
(26 Jun 1999)
succinyl CoA propionate CoA-transferase <enzyme> Succinyl CoA and propionate gives propionyl CoA and succinate
Registry number: EC 2.8.3.-
Synonym: succinyl coenzyme a propionate coenzyme a-transferase
(26 Jun 1999)
acetate-CoA ligase <enzyme> An enzyme that catalyses the formation of CoA derivatives from ATP, acetate, and CoA to form AMP, pyrophosphate, and acetyl CoA. It acts also on propionates and acrylates.
Chemical name: Acetate:CoA ligase (AMP-forming)
Registry number: EC 6.2.1.1
(12 Dec 1998)
acetate-succinate CoA-transferase <enzyme> Tritichomonas and trichomonas enzyme converts acetyl-CoA and succinate to acetate and succinyl-CoA
Registry number: EC 2.8.3.-
Synonym: acetate-succinate coenzyme a-transferase
(26 Jun 1999)
acetoacetyl-CoA Intermediate in the oxidation of fatty acids and in the formation of ketone bodies; also formed from two molecules of acetyl-CoA; major role is condensation with acetyl-CoA to form the important beta-hydroxy-beta-methylglutaryl-CoA.
Synonym: acetoacetyl-coenzyme A.
(05 Mar 2000)
acetoacetyl-CoA reductase An oxidoreductase catalyzing interconversion of a 3-oxoacyl-CoA and NADPH, and the corresponding d-3-hydroxyacyl-CoA, and NADP+. A step in fatty acid synthesis.
(05 Mar 2000)
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hydroxyacyl CoA hydroxyacyl coenzyme A.
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