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hydranencephaly <radiology> Probably secondary to ICA occlusion in utero; may be developmental, normal or enlarged head, with or without neurologically normal, CT findings: small areas of cortex, usually occipital, basal ganglia and cerebellum normal, ventricles have no roof, may resemble severe hydrocephalus, angio most likely to be sparse, atretic vessels, vs. Stretched vessels in hydrocephalus
(12 Dec 1998)
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  • Hydranencephaly - »õâ A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
    Synonyms : Absence of Cerebral Hemispheres, Congenital, Congenital Absence of Cerebral Hemispheres, Hydranencephaly with Proliferative Vasculopathy, Hemihydranencephalies, Hydranencephalies
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hydranencephaly Complete or almost complete absence of the cerebral hemispheres. The space is filled with cerebrospinal fluid.
Ãâó: www.vet.uga.edu/vpp/gray_book/Handheld/appendix_5....
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