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  • neuroblastoma,n-myc amplification
    N-myc ÁõÆø(¡­ñòøë)
  • olfactory neuroblastoma
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  • olfactory neuroblastoma
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HNB human neuroblastoma
INSS international neuroblastoma staging system
MNB mannosidase beta; murine neuroblastoma
NB nail bed; neuro-Behc;cet [syndrome]; neuroblastoma; neurometric battery; newborn; nitrous oxide-barb...
NBL neuroblastoma
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INSS International Neuroblastoma Staging System
N1E-115 Neuroblastoma
N2A Neuroblastoma
NB Neuroblastoma
NBL Neuroblastoma
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neuroblastoma <oncology, tumour> Malignant tumour derived from primitive ganglion cells. Mainly a tumour of childhood. Commonest sites are adrenal medulla and retroperitoneal tissue. The cells may partially differentiate into cells having the appearance of immature neurons.
The tumour shows a consistent deletion of the 1p36 region which is considered the site of the neuroblastoma I gene. Loss of the 1p36 region also correlates with amplification for the N-myc oncogene, particularly in later stages of the disease.
Amplification of N-myc with DNA triploidy is associated with poor survival.
Hereditary forms of the condition are rare and in such patients there is no risk for other cancers, which suggests a specificity of the antioncogene for neural tissues.
(16 Dec 1997)
olfactory neuroblastoma <tumour> A rare, often slowly growing malignant tumour of primitive nerve cells, usually arising in the olfactory area of the nasal cavity.
Synonym: olfactory esthesioneuroblastoma.
(05 Mar 2000)
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