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"hexose-1-phosphate uridylyltransferase"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
hexose-1-phosphate uridylyltransferase <enzyme> An enzyme that catalyses the transfer of ump from udpglucose to galactose 1-phosphate, forming udpgalactose and glucose 1-phosphate. Deficiency in this enzyme is the major cause of galactosaemia.
Chemical name: UDPglucose:alpha-D-galactose-1-phosphate uridylyltransferase
Registry number: EC 2.7.7.12
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
galactose-1-phosphate uridylyltransferase <enzyme> An enzyme catalyzing the reaction of UTP and alpha-d-galactose 1-phosphate to form UDPgalactose and pyrophosphate, the second and most important step in the metabolism of d-galactose; a deficiency of this enzyme results in an accumulation of galactose, galactose-1-phosphate, and galactitol.
(05 Mar 2000)
glucose-1-phosphate uridylyltransferase <enzyme> An enzyme that activates d-glucose by reacting d-glucose 1-phosphate with UTP, producing pyrophosphate and UDP glucose; a crucial step in glycogen biosynthesis.
(05 Mar 2000)
udpglucose-hexose-1-phosphate uridylyltransferase <enzyme> An enzyme that catalyses the transfer of ump from udpglucose to galactose 1-phosphate, forming udpgalactose and glucose 1-phosphate. Deficiency in this enzyme is the major cause of galactosaemia.
Chemical name: UDPglucose:alpha-D-galactose-1-phosphate uridylyltransferase
Registry number: EC 2.7.7.12
(12 Dec 1998)
uridylyl removing-uridylyltransferase <enzyme> Modifies a regulatory protein, pii, which modulates an adenyltransferase which regulates E coli glutamine synthetase
Registry number: EC 2.7.7.-
Synonym: ur-ut
(26 Jun 1999)
utp-glucose-1-phosphate uridylyltransferase <enzyme> An enzyme that catalyses the formation of udpglucose from utp plus glucose 1-phosphate.
Chemical name: UTP:alpha-D-glucose-1-phosphate uridylyltransferase
Registry number: EC 2.7.7.9
(12 Dec 1998)
utp-hexose-1-phosphate uridylyltransferase <enzyme> An enzyme that catalyses the synthesis of udpgalactose from utp and galactose-1-phosphate. It is present in low levels in foetal and infant liver, but increases with age, thereby enabling galactosaemic infants who survive to develop the capacity to metabolise galactose.
Chemical name: UTP:alpha-D-hexose-1-phosphate uridylyltransferase
Registry number: EC 2.7.7.10
(12 Dec 1998)
UTP-RNA uridylyltransferase <enzyme> Catalyses addition of single ump residue from utp to 3'-end of RNA primer
Registry number: EC 2.7.7.-
Synonym: terminal uridylyltransferase, ump transferase
(26 Jun 1999)
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