¼±Åà - È­»ìǥŰ/¿£ÅÍŰ ´Ý±â - ESC

 
"hereditary spinal sclerosis"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
¿µ¹® spinal tap, spinal puncture ÇÑ±Û Ç㸮õÀÚ, ¿äÃßõÀÚ, ¿äÃß¶Õ±â
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  Áúº´ÀÇ Áø´ÜÀ̳ª Ä¡·á ¶Ç´Â ¸¶Ã븦 Çϱâ À§ÇØ ÇǺο¡¼­ °Å¹Ì¸·¹Ø°ø°£À¸·Î ¹Ù´ÃÀ» Â ¶§°¡ ÀÖ´Ù. À̰ÍÀº ¼Â° Ç㸮»À ¾Æ·¡ÂÊ¿¡¼­ ½ÃÇàÇÑ´Ù. Ã´¼ö°¡ Ã¹Â° Ç㸮»À ¾Æ·§¸ð¼­¸®¿¡¼­ ³¡³ª°í, °Å¹Ì¸·¹Ø°ø°£Àº µÑ° ¾ûÄ¡»À ºÐÀý±îÁö »¸¾î Àֱ⠶§¹®¿¡ ÀÌ ºÎÀ§´Â ¹Ù´Ã·Î Ã´¼ö¸¦ Â À§ÇèÀÌ ¾ø´Ù. ¶Ç Ã´Ãß»À°í¸®ÆÇÀ̠ª¾Æ ¼­·Î °ãÃÄÀÖÁö ¾Ê±â ¶§¹®¿¡ Ç㸮»À »çÀ̷Π¹Ù´ÃÀ» Â ¼ö ÀÖ´Ù. ÀÌ ºÎÀ§ÀÇ °Å¹Ì¸·¹Ø°ø°£¿¡´Â Ã´¼ö½Å°æ »Ñ¸®°¡ ÀÖÀ¸³ª, À̵éÀº ³úô¼ö¾×¼Ó¿¡ Àֱ⠶§¹®¿¡ ¹Ù´ÃÀ» ³ÖÀ» ¶§ ÇÑÂÊÀ¸·Î ¹Ð·Á ¼Õ»ó¹Þ´Â °æ¿ì´Â °ÅÀÇ ¾ø´Ù. ¹è¸¦ ³ÐÀû´Ù¸®¿¡ ºÙÀÏÁ¤µµ·Î Ç㸮¸¦ ±¸ºÎ¸®¸é °í¸®ÆÇ »çÀ̰¡ ´õ ¹ú¾îÁ® Æ´ÀÌ Ä¿Áø´Ù. ¹Ù´ÃÀÌ ¶Õ°í Áö³ª°¡´Â ±¸Á¶´Â ¹Ù±ù¿¡¼­ ¼ÓÀ¸·Î ¨ç ÇǺÎ, ¨è ÇǺιØÁ¶Á÷, ¨é ±ÙÀ°¸·, ¨ê °¡½Ã³¡Àδë, ¨ë °¡½Ã»çÀÌÀδë, ¨ì È²»öÀδë, ¨í °æÁú¸·, ¨î °Å¹Ì¸·, ¨ï ³úô¼ö¾×ÀÌ µÈ´Ù. 
  
  Ç㸮õÀÚ, ¿äÃßõÀÚ, ¿äÃß¶Õ±â
¿µ¹® sclerosis ÇÑ±Û °æÈ­(Áõ), ±»À½(Áõ)
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  ¿°Áõ ¹× °£º´¿¡ ÀÇÇØ¼­ ÁøÇdz» ¼¶À¯¸ð¼¼Æ÷ÀÇ Áõ½Ä°ú ¾Æ±³Áú ¼¶À¯ÀÇ Áõ½ÄÀÌ Àִ °æ¿ì¸¦ ¸»ÇÑ´Ù.
  
  
¿µ¹® amyotrophic laternal sclerosis ÇÑ±Û ±ÙÀ§ÃàÃø»è°æÈ­Áß
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  »ç¶÷ÀÌ ±ÙÀ° Çϳª¸¦ ¿òÁ÷À϶§ »ç¿ëÇϴ ½Å°æ¿¬°áÀ» »ìÆìº¸¸é ´ÙÀ½°ú °°´Ù. ¿ì¼± ´ë³ú¿¡ Àִ ¿îµ¿À» °üÀåÇϴ °÷ÀΠ¿îµ¿°ÑÁú¿¡¼­ÀÇ ¸í·ÉÀÌ ¶³¾îÁö¸é À̰ÍÀº Ã´¼ö¸¦ Å¸°í °è¼ÓÇØ¼­ ³»·Á¿À°Ô µÈ´Ù. ±×¸®°í Ã´¼ö¿¡¼­ Çѹø ½Å°æ¼¼Æ÷¸¦ ¹Ù²Ù¾î¼­ ¸»ÃʽŰ栱ÙÀ°¿¡ °¡¼­ ±ÙÀ°À» ¿òÁ÷ÀδÙ. Áï ´ë³ú¿¡¼­ ¶³¾îÁø ¸í·ÉÀÌ ½Å°æ¼¼Æ÷ Çϳª¸¦ Å¸°í Ã´¼ö±îÁö °¡°í Ã´¼ö¿¡¼­ ÇÑ ¹ø ½Å°æÀ» ¹Ù²Ù¾î ±ÙÀ°À¸·Î °£´Ù.
  
  Ã´¼ö¿¡¼­ ½ÃÀÛÇÏ¿© ±ÙÀ°±îÁö °¡´Â ½Å°æ ¼¼Æ÷¸¦ ¾Õ»Ô¼¼Æ÷¶ó°í ÇÑ´Ù. ¿øÀΠ¹Ì»óÀΠÀÌ º´Àº ¾Õ»Ô¼¼Æ÷ÀÇ ¼Ò½Ç¿¡ ÀÇÇØ¼­ ±×°ÍÀÇ Áö¹è¸¦ ¹Þ´Â ±ÙÀ°ÀÇ À§ÃàÀÌ ³ªÅ¸³ª´Â °ÍÀ» ÁÖÁõ»óÀ¸·Î ÇÑ´Ù. ÀÌ º´¿¡ Æ¯È¿°¡ Àִ ġ·á¹ýÀº ¾ÆÁ÷ ¾ø´Ù.
¿µ¹® multiple sclerosis ÇÑ±Û ´Ù¹ß°æÈ­Áõ
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  ½Å°æÃà»èÀ» µÑ·¯½Î°í Àִ ¸»ÀÌÁý(myelin sheath)ÀÇ ÆÄ±«·Î ÀÎÇÑ º´Àû»óŸ¦ ¸»ÇÔ. ÆÄ±«µÈ ¸»ÀÌÁýÀº ÈäÅ͸¦ ³²±â°Ô µÇ¾î ½Å°æÃà»èÀ» ÅëÇÑ ½Å°æÀü´ÞÀÌ Á¦´ë·Î µÇÁö ¾Ê¾Æ ¿îµ¿, °¨°¢, ÀÚÀ²½Å°æ ¸ðµÎÀÇ ½Å°æÀü´ÞÀå¾Ö°¡ ³ªÅ¸³­´Ù. ÀÌ º´Åʹ ¾îµð¼­³ª ³ªÅ¸³¯ ¼ö À־ ±× Àå¾Ö°¡ ³ªÅ¸³ª´Â ºÎÀ§¿¡ µû¶ó ¼­·Î ´Ù¸¥ Áõ»óÀ» È£¼ÒÇÑ´Ù.
¿µ¹® spinal cord ÇÑ±Û Ã´¼ö
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  Ã´Ãß³»¿¡ À§Ä¡Çϴ ÁßÃ߽Űæ°èÀÇ ÀϺκÐ. À§¿¡¼­ºÎÅÍ ¸ñô¼ö, µîô¼ö, Ç㸮ô¼ö, ¾ûġô¼ö·Î ±¸ºÐµÊ. ³»ºÎ´Â ¹Ù±ùÂÊÀÇ ¹é»öÁú°ú ¾ÈÂÊÀǠȸ»öÁú·Î ±¸ºÐµÈ´Ù. Ã´¼öÀÇ ¾Æ·¡³¡Àº Ã´¼ö ¿ø»ÔÀ̶ó Çϸç Ã¹¹øÂ° Ç㸮»À ³ôÀ̱îÁö ³»·Á¿Â´Ù. ³ú¿Í ¸»ÃʽŰæ»çÀÌÀÇ ½Å°æ Åë·Î ¿ªÇÒÀ» Çϸç Ã´¼ö¹Ý»ç(¿¹: ¹«¸­¹Ý»ç)¿¡¼­´Â ³ú¸¦ ÅëÇÏÁö ¾Ê°í ¹Ý»çÀÇ ÁßÃß ÀÛ¿ëÀ» ÇÑ´Ù.
  
  Ã´¼ö
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • posterior spinal sclerosis
    µÚô¼ö°æÈ­Áõ, ô¼öÈÄ»è°æÈ­Áõ
  • congenital hereditary hearing loss
    ¼±ÃµÀ¯Àü³­Ã»
  • hereditary
    À¯Àü-
  • hereditary ataxia
    À¯Àü½ÇÁ¶
  • hereditary benign intraepithelial dyskeratosis
    À¯Àü¾ç¼º»óÇdz»ÀÌ»ó°¢È­Áõ
  • hereditary cerebellar ataxia
    À¯Àü¼Ò³ú½ÇÁ¶
  • hereditary chorea
    À¯Àü¹«µµº´
  • hereditary coagulation disorder
    À¯ÀüÀÀ°íÀå¾Ö
  • hereditary coproporphyria
    À¯ÀüÄÚÇÁ·ÎÆ÷¸£ÇǸ°Áõ
  • hereditary disease
    À¯Àüº´
  • hereditary disorder
    À¯ÀüÀå¾Ö, À¯ÀüÁúȯ
  • hereditary epilepsy
    À¯Àü°£Áú
  • hereditary hearing impairment
    À¯Àüû·ÂÀå¾Ö
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¸ð¼¼Ç÷°üÈ®ÀåÁõ
  • hereditary leptocytosis
    À¯ÀüÇ¥ÀûÀûÇ÷±¸Áõ
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary
    À¯Àü-
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´Áõ
  • hereditary spherocytosis
    À¯ÀüµÕ±ÙÀûÇ÷±¸Áõ, À¯Àü±¸ÇüÀûÇ÷±¸Áõ
  • sclerosis
    °æÈ­(Áõ), ±»À½(Áõ)
  • amyotrophic lateral sclerosis
    ±ÙÀ°À§Ãà°¡ÂʰæÈ­Áõ
  • multiple sclerosis
    ´Ù¹ß°æÈ­Áõ
  • systemic sclerosis
    Àü½Å°æÈ­Áõ
  • spinal muscular atrophy
    ô¼ö±ÙÀ°À§Ãà(Áõ)
  • spinal cord
    ô¼ö
  • spinal disease
    ô¼öº´
  • spinal ganglion
    ô¼ö½Å°æÀý
  • spinal headache
    ôÃ߸¶ÃëµÎÅë
  • spinal cord injury
    ô¼ö¼Õ»ó
  • spinal nerve
    ô¼ö½Å°æ
  • spinal reflex
    ô¼ö¹Ý»ç
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • posterior spinal sclerosis
    µÚô¼ö°æÈ­Áõ
  • hereditary ataxia
    À¯ÀüÁ¶È­¿îµ¿ºÒ´É
  • congenital hereditary hearing loss
    ¼±ÃµÀ¯Àü³­Ã»
  • hereditary chorea
    À¯Àü¹«µµº´
  • hereditary coproporphyria
    À¯ÀüÄÚÇÁ·ÎÆ÷¸£ÇǸ°Áõ
  • hereditary methemoglobinemic cyanosis
    À¯Àü¸ÞÆ®Çì¸ð±Û·ÎºóÇ÷û»öÁõ
  • hereditary disease
    À¯Àüº´
  • hereditary disorder
    À¯ÀüÀå¾Ö, À¯ÀüÁúȯ
  • hereditary benign intraepithelial dyskeratosis
    À¯Àü¾ç¼º»óÇdz»ÀÌ»ó°¢È­Áõ
  • hereditary coagulation disorder
    À¯ÀüÀÀ°íÀå¾Ö
  • hereditary opalescent dentine
    À¯ÀüÀ¯¹é»ö»ó¾ÆÁú
  • recessive hereditary disease
    ¿­¼ºÀ¯Àüº´
  • hereditary epilepsy
    À¯Àü°£Áú
  • hereditary bullous epidermolysis
    À¯Àü¹°ÁýÇ¥Çǹڸ®Áõ
  • hereditary multiple exostosis
    À¯Àü´Ù¹ß»Àµ¹ÃâÁõ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö °æÈ­Áõ(¡­Ìãûùñø).
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö°æÈ­Áõ(¡­Ìãûùñø).
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • anterior spinal sclerosis
    Àü»è°æÈ­Áõ(îñßãÌãûùñø).
  • posterior spinal sclerosis
    ÈÄô¼ö°æÈ­Áõ (¡­Ìãûùñø).
  • posterior spinal sclerosis
    ÈÄô¼ö°æÈ­Áõ(ý­ô±âÐÌãûùñø)
  • hereditary cerebellar sclerosis
    À¯Àü¼º ¼Ò³ú°æÈ­Áõ.
  • hereditary spinal ataxia
    À¯Àü¼º ô¼ö¿îµ¿½ÇÁ¶(¡­ô±âÐê¡ÔÑã÷ðà).
  • Bournevilles disease->tuberous sclerosis
    ºÎ¸£³×ºôº´
  • SSP= spasmodic spinal paralysis
    °­Á÷¼º ô¼ö¸¶ºñ.
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ(¡­ö°ßãÌãûùñø).
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ(ÐÉê×õêàõö°ÞþÌãûùñø)
  • annular sclerosis
    À±»ó°æÈ­Áõ(¡­Ìãûùñø).
  • anterior spinal artery
    ¾Õô¼öµ¿¸Æ
  • anterior spinal artery syndrome
    Àüô¼öµ¿¸ÆÁõÈıº(¡­ñøý¦ÏØ).
  • anterior spinal syndrome
    Àü»èÁõÈıº(¡­ñøý¦ÏØ).
  • anterior spinal veins
    ¾Õô¼öÁ¤¸Æ
  • aortic sclerosis
    ´ëµ¿¸Æ°æÈ­(Áõ)(¡­Ìãûùñø).
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö°æÈ­Áõ(¡­Ìãûùñø).
  • hereditary spinal sclerosis
    À¯Àü¼º ô¼ö °æÈ­Áõ(¡­Ìãûùñø).
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary cerebellar sclerosis
    À¯Àü¼º ¼Ò³ú°æÈ­Áõ.
  • anterior spinal sclerosis
    Àü»è°æÈ­Áõ(îñßãÌãûùñø).
  • posterior spinal sclerosis
    ÈÄô¼ö°æÈ­Áõ (¡­Ìãûùñø).
  • posterior spinal sclerosis
    ÈÄô¼ö°æÈ­Áõ(ý­ô±âÐÌãûùñø)
  • hereditary spinal ataxia
    À¯Àü¼º ô¼ö¿îµ¿½ÇÁ¶(¡­ô±âÐê¡ÔÑã÷ðà).
  • spinal roots [spinal part]
    ô¼ö»Ñ¸® [ô¼öºÎºÐ]
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ(¡­ö°ßãÌãûùñø).
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ(ÐÉê×õêàõö°ÞþÌãûùñø)
  • annular sclerosis
    À±»ó°æÈ­Áõ(¡­Ìãûùñø).
  • aortic sclerosis
    ´ëµ¿¸Æ°æÈ­(Áõ)(¡­Ìãûùñø).
  • areolar choroidal sclerosis
    ¿øÇü¸Æ¶ô¸·°æÈ­(Áõ)
  • arteriolar sclerosis
    ¼¼µ¿¸Æ¼º °æÈ­Áõ.
  • bulbar sclerosis
    ±¸<¿¬¼ö>°æÈ­Áõ(Ϲ<æÅâÐ>Ìãûùñø).
  • calcific sclerosis
    ¼®È¸¼º°æÈ­Áõ(à´üéàõÌãûùñø).
  • calcific sclerosis
    ¼®È¸È­°æÈ­Áõ(¡­Ìãûùñø)
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Spinal roots [Spinal part]
    ô¼ö»Ñ¸® [ô¼öºÎºÐ]
    [¿¾ ¿ë¾î] ô¼ö±Ù
  • Posterior spinal artery
    µÚô¼öµ¿¸Æ
    [¿¾ ¿ë¾î] ÈÄô¼öµ¿¸Æ
  • Posterior spinal veins
    µÚô¼öÁ¤¸Æ
    [¿¾ ¿ë¾î] ÈÄô¼öÁ¤¸Æ
  • Spinal tract of trigeminal nerve
    »ïÂ÷½Å°æÃ´¼ö·Î
    [¿¾ ¿ë¾î] »ïÂ÷½Å°æÃ´¼ö·Î
  • Spinal nucleus of trigeminal nerve
    »ïÂ÷½Å°æÃ´¼öÇÙ
    [¿¾ ¿ë¾î] »ïÂ÷½Å°æÃ´¼ö·ÎÇÙ
  • Anterior spinal artery
    ¾Õô¼öµ¿¸Æ
    [¿¾ ¿ë¾î] Àüô¼öµ¿¸Æ
  • Anterior spinal veins
    ¾Õô¼öÁ¤¸Æ
    [¿¾ ¿ë¾î] Àüô¼öÁ¤¸Æ
  • Spinal cord
    ô¼ö
    [¿¾ ¿ë¾î] ô¼ö
  • SPINAL CORD
    ô¼ö [µî°ñ]
    [¿¾ ¿ë¾î] ô¼ö
  • Spinal branch
    ô¼ö°¡Áö
    [¿¾ ¿ë¾î] ô¼öÁö
  • Spinal branches
    ô¼ö°¡Áö
    [¿¾ ¿ë¾î] ô¼öÁö
  • Arachnoid of spinal cord
    ô¼ö°Å¹Ì¸·
    [¿¾ ¿ë¾î] ô¼öÁöÁÖ¸·
  • SPINAL ARACHNOID MATER
    ô¼ö°Å¹Ì¸·
    [¿¾ ¿ë¾î] ô¼öÁöÁÖ¸·
  • Defect of spinal cord
    ô¼ö°áÇÔ
    [¿¾ ¿ë¾î] ô¼ö°áÇÔ
  • Dura mater of spinal cord
    ô¼ö°æÁú¸·
    [¿¾ ¿ë¾î] ô¼ö°æ¸·
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary code
    À¯Àü ºÎÈ£(ë¶îîݬûÜ)
  • hereditary material
    À¯Àü ¹°Áú(ë¶îîÚªòõ)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ãà¼ºÃø»è°æÈ­Áõ
  • multiple sclerosis
    ´Ù¹ß¼º°æÈ­Áõ
  • posterolateral sclerosis
    ÈÄ»èÃø»è°æÈ­Áõ
  • tuberous sclerosis
    °áÀý¼º°æÈ­Áõ
  • hereditary
    À¯Àü¼ºÀÇ
  • hereditary craniofacial dysostosis
    À¯Àü¼ºµÎ°³¾È¸éÀ̰ñÁõ
  • hereditary disease
    À¯Àüº´
  • hereditary ectodermal polydysplasia
    À¯Àü¼º¿Ü¹è¿±¼º´Ù¹ßÀÌÇü¼ºÁõ
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°üÈ®Àå
  • anterior spinal artery
    Àüô¼öµ¿¸Æ
  • progressive spinal amyotrophy
    ÁøÇ༺ô¼ö¼º±ÙÀ§ÃàÁõ
  • spinal
    ô¼öÀÇ, ôÃßÀÇ
  • spinal artery
    ô¼öµ¿¸Æ
  • spinal canal
    ôÃß°ü
  • spinal cord
    ô¼ö
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
ALS acute lateral sclerosis; advanced life support; afferent loop syndrome; amyotrophic lateral sclerosi...
TSC technetium sulfur colloid; thiosemicarbazide; transverse spinal sclerosis; tuberous sclerosis
NS natural science; Neosporin; nephrosclerosis; nephrotic syndrome; nervous system; neurological surger...
PSA parasternal short axis; pleomorphic salivary gland adenoma; polyethylene sulfonic acid; polysacchari...
SC conditioned stimulus; sacrococcygeal; Sanitary Corps; scalenus [muscle]; scapula; Schwann cell; scia...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
HCSMA Hereditary Canine Spinal Muscular Atrophy
AHS Ammon's horn sclerosis
ALS amylotrophic lateral sclerosis
DMS Diffuse mesangial sclerosis
FALS Familial Amyotrophic Lateral Sclerosis
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • amyotrophic lateral sclerosis
    ±ÙÀ§Ã༺ Ãø»è °æÈ­Áõ, ±ÙÀ§Ã༺ Ãø¹æ °æÈ­
    1. Ãßü·ÎÀÇ ´º·Ð ¹× ³ú°£°ú ô¼öÀÇ ¿îµ¿¼¼Æ÷ÀÇ ÁøÇ༺ÀÎ º¯¼ºÀ» Ư¡À¸·Î ÇÏ´Â ÁúȯÀ¸·Î¼­, »óÀ§ ¹× ÇÏÀ§ÀÇ ¿îµ¿½Å°æÀÇ °á¼ÕÀ» ÃÊ·¡ÇÑ´Ù. º¸Åë 2-3³â³»¿¡ »ç¸ÁÇÑ´Ù. 2. »óÀ§ 1Â÷ ¿îµ¿ ´º·Ð°ú ÇÏÀ§ 2Â÷ ¿îµ¿ ´º·ÐÀÌ ÇÔ²² ħ¹üµÇ´Â ¿øÀÎ ºÒ¸íÀÇ °èÅ뼺 ÁúȯÀ¸·Î 30-50¼¼ÀÇ ³²¼º¿¡°Ô ¸¹´Ù. Áö°¢Àå¾Ö´Â ¾ø´Ù. ´ë°³ ¼Õ ±ÙÀ°ÀÇ ±Ù·Â ÀúÇÏ¿Í À§ÃàÀÌ µÇ¸é¼­ Â÷Ãû ÁøÇàÇÏ¿© ÆÈ, ¾î±úÀÇ ±ÙÀ°¿¡ ¹ÌÄ£´Ù. ´õ ³ª¾Æ°¡ ÇÏÁöÀÇ ±ÙÀ°ÀÌ À§ÃàÇϰųª, ±¸À½, ¿¬Çϱٵµ ħ¹üµÇ¾î ±¸¸¶ºñ Áõ»óÀ» ³ªÅ¸³½´Ù. ½ÉºÎ¹Ý»ç´Â Åë»ó Ç×ÁøÇÏ°í ±ÙÀ°¿¡´Â ¼¶À¯¼º ¿¬ÃàÀ» º¸°Ô µÈ´Ù. ƯȿÀûÀÎ Ä¡·á¹ýÀº ¾ø°í ¿¹Èİ¡ ºÒ·®ÇÏ¸ç Æò±Õ 3³â, ´ëºÎºÐ 5³â À̳»¿¡ »ç¸ÁÇÑ´Ù.
  • annular sclerosis
    À±»ó °æÈ­Áõ
    ôÃß ÁÖÀ§¿¡ ´ë»óÀ¸·Î »ý±â´Â °æÈ­Áõ.
  • areolar choroidal sclerosis
    ¿øÇü ¸Æ¶ô¸· °æÈ­
  • condylar sclerosis
    °úµÎ °æÈ­Áõ
  • dentinal sclerosis
    »ó¾Æ ¼¼°ü °æ»ö, »ó¾ÆÁú °æÈ­Áõ
    Àڱؿ¡ ´ëÇÑ »ó¾ÆÁúÀÇ ¹ÝÀÀÀ¸·Î¼­ »ó¾Æ¼¼°üÀÇ Á¡Â÷ÀûÀÎ ¼®È¸È­¸¦ ¸»ÇÑ´Ù. ÀÌ´Â ¿ì½Ä, ±³¸ðÁõ, ¶Ç´Â Ä¡°æºÎ ¸¶¸ðÁõ¿¡ ÀÇÇØ »ó¾ÆÁúÀÌ ±¸°­ ȯ°æ¿¡ ¸¸¼ºÀûÀ¸·Î ³ëÃâµÇ´Â °æ¿ì ¹ß»ýµÇ¸ç ³ëÃâµÈ »ó¾ÆÁúÀº À¯¸®¿Í °°ÀÌ ¹Ý¦À̴ ǥ¸é Áú°¨À» °®°í ÀÖ´Ù. ÇÑÆí, »ó¾ÆÁú¿¡ ´ëÇÑ ¿­Àû, È­ÇÐÀû, Ã˰¢ÀûÀÎ Àڱؿ¡ ´ëÇØ Ä¡¼ö¸¦ È¿°úÀûÀ¸·Î º¸È£ÇÏ´Â ÀÛ¿ëÀ» Áö´Ï°í ÀÖ´Ù.
  • diffuse sclerosis
    ¹ü¹ß¼º °æÈ­Áõ
  • hereditary
    À¯Àü¼º
    ºÎ¸ð·ÎºÎÅÍ ´ÙÀ½ ¼¼´ë·Î À¯ÀüÀÚ¿¡ ÀÇÇØ Àü´ÞµÇ´Â.
  • hereditary amyloidosis
    À¯Àü¼º À¯ÀüºÐÁõ
    1. À¯Àü¿¡ ÀÇÇØ ¿ø¼¶À¯¼º ´ç ´Ü¹éÀÌ ÇǺÎ, Á¡¸·, ³»ºÎ Àå±â¿¡ ħÀüµÇ´Â º´. 2. À¯ÀüÀûÀ¸·Î ½ÅüÀÇ °¢Á¾ ºÎÀ§¿¡ ¾Æ¹Ð·ÎÀ̵å
  • hereditary angioedema
    À¯Àü¼º ¸Æ°ü ºÎÁ¾, À¯Àü¼º Ç÷°ü ºÎÁ¾
    ½ÉºÎÀÇ ÁøÇÇ, ÇÇÇÏ Á¶Á÷, Á¡¸·ÇÏÁ¶Á÷À» ħ½ÀÇÏ´Â Ç÷°ü ¹ÝÀÀÀ¸·Î¼­, ¸ð¼¼Ç÷°üÀÇ È®Àå°ú Åõ°ú¼º Ç×Áø¿¡ ÀÇÇØ ÀϾ´Â ±¹ÇѼº ºÎÁ¾À» ³ªÅ¸³»¸ç °Å´ëÇÑ ÆØÁøÀÇ ¹ß»ýÀ» Ư¡À¸·Î ÇÑ´Ù. »ó¿°»öü¼º ¿ì¼º ÇüÁú·Î À¯ÀüÇÑ´Ù. »ê¹ß¼ºº¸´Ù ³»Àå º´º¯À» ´õ Àß ÀÏÀ¸Å°´Â °æÇâÀÌ ÀÖ´Ù.
  • hereditary aphasia
    À¯Àü ½Ç¾î, À¯Àü¼º ½Ç¾î, À¯Àü ½Ç¾îÁõ, À¯Àü¼º ½Ç¾îÁõ
  • hereditary brown tooth
    À¯Àü¼º °¥»ö Ä¡¾Æ
  • hereditary cerebrospinal paralysis
    ¿ìÀü¼º ³úô¼ö ¸¶ºñ
    º¸Åë Áß³â Ãʱ⿡ ÁøÇàÇÏ´Â À¯Àü¼º ÁúȯÀ¸·Î »óÁö ¶Ç´Â ÇÏÁöÀÇ ¾çÁö ¶Ç´Â ÀÏÃøÀ̳ª »çÁö¿¡ ³ªÅ¸³ª¸ç, ¼­¼­È÷ ÁøÇàµÇ´Â ¸¶ºñ°¡ Ư¡ÀÌ´Ù.
  • hereditary craniofacial dysostosis
    À¯Àü¼º µÎ°³ ¾È¸é À̰ñÁõ
    ž»ó µÎ°³, ¾È±¸ µ¹Ãâ, ¾ç¾È °Ý¸®, »ç½Ã, ¾Þ¹«»õ ºÎ¸® ¸ð¾ç1114-377786/377786Àüµ¹À» ¼ö¹ÝÇÏ´Â »ó¾Ç Çü¼º ºÎÀüÀ» Ư¡À¸·Î ÇÏ´Â À¯ÀüÀû Áúȯ.
  • hereditary disease
    À¯Àüº´
    À¯ÀüÀÚ¿¡ ÀÇÇÏ¿© ÀϾ´Â ½ÅüÀû, Á¤½ÅÀûÀÎ ÀÌ»óÀÇ ÃÑĪ. À¯Àü¼º ÁúȯÀ̶ó°íµµ ÇÑ´Ù. º´, ÀÌ»ó ÇüÁúÀÌ À¯ÀüÀû ¿äÀΰú °ü·ÃÀÌ ÀÖÀ½¿¡ µû¶ó¼­ ¹Ýµå½Ã À¯ÀüÀÚ¿¡ ÀÇÇÏÁö ¾Ê´Â À¯ÀüÀûÀÎ º´µµ À¯Àüº´À̶ó°í ÇÏ°Ô µÇ¾ú´Ù. 1°³ÀÇ ¿ì¼º À¯ÀüÀÚ¿¡ ÀÇÇÏ¿© ÀϾ´Â ÇåÆÃÅÏ ¹«µµº´, ¹ß·»ºÎ¸£Å© ÁõÈıº, ¿­¼º À¯ÀüÀÚÀÇ µ¿Çü Á¢ÇÕ¿¡ ÀÇÇÏ¿© ³ªÅ¸³ª´Â ¹éÀÚ, Æä´ÒÄÉÅæ´¢Áõ, X ¿°»öü À§ÀÇ ¹Ý¼º À¯ÀüÀÚ¿¡ ÀÇÇÑ Àû·Ï »ö¸Í, Ç÷¿ìº´, ÁøÇ༺ ±Ù µð½ºÆ®·ÎÇÇÁõ µîÀº ¸í¹éÈ÷ ÀÌÀ¯ ÀüÀÚ¿¡ ÀÇÇÑ °ÍÀ¸·Î¼­, À¯Àüº´ÀÇ ´ëÇ¥ÀûÀÎ °ÍÀ̶ó°í ÇÒ ¼ö ÀÖ´Ù. ¹Ý¼º À¯ÀüÀÚ´Â X ¿°»öü À§¿¡ À§Ä¡ÇÏ´Â °Í¸¸ ¾Ë·ÁÁ® ÀÖ°í, ³²¼ºÀ» °áÁ¤ÇÏ´Â Y ¿°»öü À§¿¡´Â ÇöÀç±îÁö ƯÈ÷ È®½ÇÇÑ ÇüÁúÀ» °áÁ¤ÇÏ´Â À¯ÀüÀÚ´Â Á¸ÀçÇÏÁö ¾Ê´Â´Ù°í º¸°í ÀÖ´Ù. À¯ÀüÀÚ¿¡ ÀÇÇÑ ÀÌ»óÀ̳ª º´Àº Ãâ»ýÇÏ´Â ¾Æ±âÀÇ 1 %°¡ ÀÌ¹Ì °¡Áö°í Àְųª ¹ßº´ÇÒ °¡´É¼ºÀ» Áö´Ï°í ÀÖ´Ù. ¿°»öüÀÇ ±¸Á¶ ¶Ç´Â ±¸¼ºÀÇ ÀÌ»ó¿¡ ÀÇÇÏ¿© ÀϾ´Â ¿©·¯ °¡Áö ÀÌ»ó ´Ù¿î ÁõÈıº, ÅÍ³Ê ÁõÈıº, Ŭ¶óÀÎÆçÅÍ ÁõÈıº µîµµ ¿°»öü À§¿¡ À¯ÀüÀÚ°¡ ÀÖ´Ù°í ÇÏ´Â Àǹ̿¡¼­´Â À¯ÀüÇÐÀûÀÎ °ÍÀ̶ó°í ÇÒ ¼ö ÀÖ´Ù. ±×·¯³ª ´ë°³´Â ÀÌ»ó °³Ã¼¸¦ ¸¸µç ¹è¿ìÀÚ
  • hereditary disturbance
    À¯Àü¼º Àå¾Ö
    ¼±ÃµÀûÀ¸·Î ¾î¹öÀ̷κÎÅÍ ÀÚ¼Õ¿¡°Ô ¹°·ÁÁ® ³»¸®´Â Áúº´.
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posterior spinal sclerosis See Tabes dorsalis.
(12 Dec 1998)
lateral spinal sclerosis Considered by many to be a subgroup of motor neuron disease; a slowly progressive degenerative disorder of the motor neurons of the cerebral cortex, resulting in widespread weakness on an upper motor neuron basis; spasticity, hyperreflexia, and Babinski signs are present, but not fasciculation potentials, nor any electrodiagnostic evidence of a lower motor neuron lesion.
Synonym: lateral spinal sclerosis.
(05 Mar 2000)
hereditary spinal ataxia Sclerosis of the posterior and lateral columns of the spinal cord, occurring in children and marked by ataxia in the lower extremities, extending to the upper, followed by paralysis and contractures; autosomal recessive inheritance.
See: spinocerebellar ataxia.
Synonym: Friedreich's ataxia, heredotaxia.
(05 Mar 2000)
Alzheimer's sclerosis Hyaline degeneration of the medium and smaller blood vessels of the brain.
(05 Mar 2000)
amyotrophic lateral sclerosis A serious neurologic disease that results from the progressive degeneration of the motor neurons.
(27 Sep 1997)
amyotropic lateral sclerosis A chronic progressive disease of motor neurons (the nerves that come from the spinal cord to supply electrical energy to the muscles).
(12 Dec 1998)
arterial sclerosis <cardiology, disease> Imprecise term for various disorders of arteries, particularly hardening due to fibrosis or calcium deposition, often used as a synonym for atherosclerosis.
(17 Oct 1997)
arteriocapillary sclerosis Arteriosclerosis, especially of the finer vessels.
(05 Mar 2000)
arteriolar sclerosis <cardiology, disease> Sclerosis and thickening of the walls of the smaller arteries (arterioles). Hyaline arteriolosclerosis, in which there is homogeneous pink hyaline thickening of the arteriolar walls, is associated with benign nephrosclerosis.
Hyperplastic arteriolosclerosis, in which there is a concentric thickening with progressive narrowing of the lumina may be associated with malignant hypertension, nephrosclerosis and scleroderma.
(17 Oct 1997)
bone sclerosis <medicine> A condition of bone cartilage occurring in certain diseases of these tissues, in which they acquire an unnatural density, and come to resemble ivory.
Origin: L. Eburnus of ivory, fr. Ebur ivory: cf. F. Eburnation. See Ivory.
Source: Websters Dictionary
(01 Mar 1998)
Canavan's sclerosis Autosomal recessive degenerative disease of infancy; mostly in Jewish infants; onset typically within first 3-4 months of birth, consisting of blindness, psychomotor regression, enlarged head, optic atrophy, hypotonia, spasticity, increased N-acetylaspartic acid urinary excretion. MRI shows enlarged brain, decreased attenuation of cerebral and cerebellar white matter, and normal ventricles. Pathologically, there is increased brain volume and weight, and spongy degeneration in the subcortical white matter.
See: leukodystrophy.
Synonym: Canavan's sclerosis, Canavan-van Bogaert-Bertrand disease, spongy degeneration of infancy.
(05 Mar 2000)
valvular sclerosis Fibrosis, often with calcification of valves, considered to be an aging change and not due to primary valvular disease.
(05 Mar 2000)
vascular sclerosis <cardiology, disease> Imprecise term for various disorders of arteries, particularly hardening due to fibrosis or calcium deposition, often used as a synonym for atherosclerosis.
(17 Oct 1997)
mantle sclerosis A common cerebral lesion in the palsied states of early life characterised by nodular cortical atrophy.
(05 Mar 2000)
glomerular sclerosis Hyaline deposits or scarring within the renal glomeruli, a degenerative process occurring in association with renal arteriosclerosis or diabetes.
Synonym: glomerular sclerosis.
Origin: Glomerulus + G. Sklerosis, hardness
(05 Mar 2000)
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