¼±Åà - È­»ìǥŰ/¿£ÅÍŰ ´Ý±â - ESC

 
"hereditary epithelial dystrophy"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
¿µ¹® muscular dystrophy ÇÑ±Û ±ÙÀ°ÅðÇàÀ§Ãà
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  ±Ù¼¶À¯ÀÇ ÆÄ±«·Î ÀÎÇÑ Á¡ÁøÀûÀΠ±ÙÀ§Ãà°ú Çã¾àÀ» Æ¯Â¡À¸·Î Çϴ ÀÏ·ÃÀÇ ¼±ÃµÀûÀΠÁúȯ±ºÀ» ÅëÅо»ÇÑ´Ù. ´ëÇ¥ÀûÀΠ°æ¿ì°¡ µÚ½¨(Duchenne)ÇüÀ¸·Î ¼º¿°»öü ¿­¼ºÀ¯ÀüÀ» Çϸç, ´ë°³ 4 ¼¼À̳»¿¡ ¹ßº´Çؠû³â±â¸¦ ³Ñ±â´Â °æ¿ì°¡ µå¹°´Ù. Æ¯Â¡Àû ¼Ò°ßÀ¸·Î ÀåµýÁö±Ù(gastronemius)ÀÇ °ÅÁþºñ´ë(pseudohypertrophy)(½ÇÁ¦ÀûÀ¸·Î´Â ±ÙÀ§ÃàÀÌ ÀϾÁö¸¸, ±Ù¼¶À¯ ´ë½Å¿¡ Áö¹æ¼¼Æ÷°¡ µé¾îÂ÷ µµ¸®¾î ¸¶Ä¡ ±ÙÀ°ÀÌ Áõ°¡ÇÑ °Íó·³ º¸À̴ Çö»ó) ¼Ò°ßÀ» º¼ ¼ö ÀÖ´Ù.
¿µ¹® epithelial tumor ÇÑ±Û »óÇǼºÁ¾¾ç
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  Á¤»ó »ç¶÷ÀÇ Á¶Á÷Àº Ã¼Ç¥¸éÀ» µ¤´Â ¿ªÇÒÀ» Çϴ Á¶Á÷°ú, ÁַΠ¹ß»ý±âÀÇ Á߹迱¿¡¼­ ºÐÈ­ÇÑ °£¿±Á¶Á÷¿¡¼­ À¯·¡Çϴ °áÇÕÁ¶Á÷, »À, ¿¬°ñ, Áö¹æ, ±ÙÀ°, Ç÷°ü µîÀÇ Á¶Á÷ÀÇ µÎ °èÅëÀ¸·Î ³ª´­ ¼ö ÀÖ´Ù. ÀüÀÚ¸¦ »óÇǼº Á¶Á÷, ÈÄÀÚ¸¦ ºñ»óÇǼº Á¶Á÷À̶ó Çϸ砱נ°¢°¢À» ±¸¼ºÇϴ ¼¼Æ÷¸¦ »óÇǼº ¼¼Æ÷, ºñ»óÇǼ¼Æ÷¶ó ÃÑĪÇÑ´Ù. »óÇǼº ¼¼Æ÷¿¡¼­ ±â¿øÇϴ Á¾¾çÀÌ »óÇǼº Á¾¾çÀ̸ç, ±ÙóÀÇ Á¶Á÷À¸·Î Ä§Åõ³ª Ç÷·ù, ¸²ÇÁÀÇ Á¶Á÷À» Å¸°í ¿ø°Å¸®ÀÇ Àå±â·Î À̵¿ÇÏÁö ¾Ê´Â ¾ç¼ºÁ¾¾ç¿¡´Â ¼±Á¾, À¯µÎÁ¾ µîÀÌ ÀÖ°í ¾ç¼º°ú ¹Ý´ë·Î ±ÙóÀÇ Á¶Á÷À¸·Î Ä§Åõ, ¿ø°ÝÀå±â·Î ÀüÀÌÇϴ ¾Ç¼ºÁ¾¾çÀ» ¸ðµÎ ÅëĪÇÏ¿© ¾ÏÁ¾(carcinoma)À̶ó°í ÇÑ´Ù.
¿µ¹® epithelial tissue ÇÑ±Û »óÇÇÁ¶Á÷
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  »óÇǴ ÇÑ Ãþ ¶Ç´Â ¿©·¯ ÃþÀÇ ¼¼Æ÷·Î ÀÌ·ç¾îÁø ÆÇ ¸ð¾çÀÇ ±¸Á¶·Î ½ÅüÀǠǥ¸é°ú °ü»ó±¸Á¶ÀÇ ³»°­À» µÑ·¯½Î°í ÀÖ´Ù. »óÇǼ¼Æ÷¿Í »óÇǼ¼Æ÷»çÀÌÀÇ ÀûÀº ¾çÀ¸·Î Á¸ÀçÇÏ¿© »óÇÇ»çÀÌÀÇ °ø°£À» Ã¤¿ì°í Àִ ¼¼Æ÷°£ÁúÀ» ÇÕÃÄ »óÇÇÁ¶Á÷À̶ó ÇÑ´Ù. »óÇÇÁ¶Á÷¿¡´Â ¿øÄ¢ÀûÀ¸·Î Ç÷°üÀÌ ºÐÆ÷µÇ¾î ÀÖÁö ¾Ê´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epithelial
    »óÇÇ-, »óÇǼº-
  • epithelial cell
    »óÇǼ¼Æ÷
  • epithelial gland
    »óÇÇ»ù, »óÇǼ±
  • epithelial ingrowth
    »óÇÇ´«¼ÓÁõ½Ä, »óÇǾȳ»Áõ½Ä
  • epithelial membrane antigen
    »óÇǸ·Ç׿ø
  • epithelial rest
    »óÇÇÀÜ·ù¹°
  • epithelial root sheath
    »óÇǻѸ®Áý
  • epithelial sac
    »óÇÇÁÖ¸Ó´Ï
  • epithelial tissue
    »óÇÇÁ¶Á÷
  • punctate epithelial erosion
    Á¡»ó»óÇǹ̶õ, Á¡»ó»óÇDZîÁü
  • sclerosing epithelial hamartoma
    °æÈ­Ç¥Çǰú¿ÀÁ¾
  • adiposogenital dystrophy
    Áö¹æÁõ»ý½Ä±âÅðÇàÀ§Ãà
  • Becker muscular dystrophy
    º£Ä¿±Ù(À°)µð½ºÆ®·ÎÇÇ
  • dystrophy
    ÀÌ»óÁõ, µð½ºÆ®·ÎÇÇ, ¿µ¾çÀå¾Ö
  • facioscapulohumeral muscular dystrophy
    ¾ó±¼¾î±úÀ§ÆÈ±ÙÀ°µð½ºÆ®·ÎÇÇ
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epithelial
    »óÇÇ-
  • dystrophy
    ÅðÇàÀ§Ãà, ¿µ¾çÀå¾Ö, ÀÌ»óÁõ, µð½ºÆ®·ÎÇÇ
  • muscular dystrophy
    ±ÙÀ°ÅðÇàÀ§Ãà
  • reflex sympathetic dystrophy
    ¹Ý»ç±³°¨½Å°æÀÌ»óÁõ
  • hereditary
    À¯Àü-
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´Áõ
  • hereditary spherocytosis
    À¯ÀüµÕ±ÙÀûÇ÷±¸Áõ, À¯Àü±¸ÇüÀûÇ÷±¸Áõ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • borderline malignant epithelial ovarian neoplasm
    °æ°è¾Ç¼º»óÇdz­¼ÒÁ¾¾ç
  • epithelial cell
    »óÇǼ¼Æ÷
  • epidermal-epithelial viral disease
    Ç¥ÇÇ»óÇǹÙÀÌ·¯½ºº´
  • epithelial
    »óÇÇ-
  • epithelial follicle
    »óÇÇÁÖ¸Ó´Ï
  • epithelial gland
    »óÇÇ»ù
  • epithelial ingrowth
    »óÇÇ´«¼ÓÁõ½Ä, »óÇǾȳ»Áõ½Ä
  • epithelial rest
    »óÇÇÀÜ·ù¹°
  • epithelial sac
    »óÇÇÁÖ¸Ó´Ï
  • epithelial sheath
    »óÇÇÁý
  • epithelial tissue
    »óÇÇÁ¶Á÷
  • epithelial root sheath
    »óÇǻѸ®Áý
  • punctate epithelial erosion
    Á¡»ó°¢¸·»óÇÇÁø¹«¸§
  • sclerosing epithelial hamartoma
    °æÈ­Ç¥Çǰú¿ÀÁ¾
  • adiposogenital dystrophy
    Áö¹æÁõ¼º±âÅðÇàÀ§Ãà
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary corneal dystrophy
    À¯Àü¼º°¢¸·ÀÌ¿µ¾çÁõ.
  • hereditary corneal dystrophy
    À¯Àü¼º °¢¸·ÀÌ ¿µ¾çÁõ.
  • hereditary macular dystrophy
    À¯Àü¼ºÈ²¹ÝÀÌ¿µ¾ç(Áõ)
  • Hertwlg s epithelial sheath
    Ç츣ƮºñÈ÷»óÇÇÃÊ.
  • inner epithelial root sheath
    ¼Ó»óÇǻѸ®Áý
  • pigment epithelial cell
    »ö¼Ò»óÇǼ¼Æ÷
  • pulmonary epithelial cell
    Æó»óÇǼ¼Æ÷(øËß¾ù«á¬øà).
  • Fuchs dystrophy
    Ç«½ºÀÌ¿µ¾çÁõ
  • Groenouws dystrophy
    ±×·Ú³ëÀÌ¿µ¾ç(Áõ)
  • Meesman dystrophy
    ¹Ì½º¸¸ÀÌ¿µ¾ç(Áõ)
  • Meesmans corneal dystrophy
    ¹Ì½º¸¸°¢¸·ÀÌ¿µ¾ç(Áõ)
  • Salzmanns nodular corneal dystrophy
    ÀßÂ길°áÀý°¢¸·ÀÌ¿µ¾ç(Áõ)
  • albipunctate retinal dystrophy
    ÈòÁ¡¸Á¸·ÀÌ¿µ¾ç(Áõ)
  • infantile neuroaxonal dystrophy
    ¿µ¾Æ½Å°æÃà»è¼º ÀÌ¿µ¾çÁõ, »çÀÌÅйö°Å¾¾º´.
  • peroneal muscular dystrophy
    ºñ°ñ±ÙÀ§ÃàÁõ(Þ¡ÍéÐÆê×õêñø)
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • juvenile epithelial corneal dystrophy
    ¿¬¼Ò±â°¢¸·»óÇǼ¼Æ÷ÀÌ¿µ¾ç(Áõ)
  • hereditary corneal dystrophy
    À¯Àü¼º °¢¸·ÀÌ ¿µ¾çÁõ.
  • hereditary corneal dystrophy
    À¯Àü¼º°¢¸·ÀÌ¿µ¾çÁõ.
  • hereditary macular dystrophy
    À¯Àü¼ºÈ²¹ÝÀÌ¿µ¾ç(Áõ)
  • basal epithelial cell
    ±âÀú»óÇǼ¼Æ÷
  • basal epithelial cell
    ¹Ù´Ú»óÇǼ¼Æ÷
  • borderline malignant epithelial ovarian neoplasms
    °æ°è¼º »óÇǼº ³­¼ÒÁ¾¾ç
  • bronchial epithelial cell
    ±â°üÁö»óÇǼ¼Æ÷
  • cell, thymic epithelial
    °¡½¿»ù»óÇǼ¼Æ÷, Èä¼±»óÇǼ¼Æ÷
  • ciliated epithelial cell
    ¼¶¸ð»óÇǼ¼Æ÷
  • columnar epithelial cell
    ¿øÁÖ»óÇǼ¼Æ÷
  • cornified epithelial cell
    °¢È­»óÇǼ¼Æ÷(ÊÇûùß¾ù«á¬øà).
  • cornified epithelial cell
    °¢È­»óÇǼ¼Æ÷(ÊÇûùß¾ù«á¬øà)
  • cuboidal epithelial cell
    ÁÖ»çÀ§ »óÇǼ¼Æ÷
  • cuboidal epithelial cell
    ÀÔ¹æ»óÇǼ¼Æ÷
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Sensory epithelial cell
    °¨°¢»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] °¨°¢»óÇǼ¼Æ÷
  • Microvillous epithelial cell
    ¹Ì¼¼À¶¸ð»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] ¹Ì¼¼À¶¸ð»óÇǼ¼Æ÷
  • Microplica epithelial cell
    ¹Ì¼¼ÁÖ¸§»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] ¹Ì¼¼ÁÖ¸§»óÇǼ¼Æ÷
  • Basal epithelial cell
    ¹Ù´Ú»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] ±âÀúÃþ»óÇǼ¼Æ÷
  • Secretory epithelial cell [Glandular cell]
    ºÐºñ»óÇǼ¼Æ÷ [»ù¼¼Æ÷]
    [¿¾ ¿ë¾î] ºÐºñ»óÇǼ¼Æ÷
  • Intercalated epithelial cell
    »çÀÌ»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] Áß°£Ãþ»óÇǼ¼Æ÷
  • Epithelial root sheath
    »óÇǻѸ®Áý
    [¿¾ ¿ë¾î] »óÇǼº±ÙÃÊ
  • Epithelial reticular cell
    »óÇǼ¼¸Á¼¼Æ÷
    [¿¾ ¿ë¾î] »óÇǼº¼¼¸Á¼¼Æ÷
  • Epithelial cells
    »óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] »óÇǼ¼Æ÷
  • Epithelial rest
    »óÇÇÀÜ¿©
    [¿¾ ¿ë¾î] »óÇÇÀÜ¿©
  • Epithelial follicle
    »óÇÇÁÖ¸Ó´Ï
    [¿¾ ¿ë¾î] »óÇÇ¼ÒÆ÷
  • Pigment epithelial cell
    »ö¼Ò»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] »ö¼Ò»óÇǼ¼Æ÷
  • Ciliated epithelial cell
    ¼¶¸ð»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] ¼¶¸ð»óÇǼ¼Æ÷
  • Inner epithelial root sheath
    ¼Ó»óÇǻѸ®Áý
    [¿¾ ¿ë¾î] ³»»óÇǼº±ÙÃÊ
  • Neurosensory epithelial cell
    ½Å°æ°¨°¢»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] ½Å°æ°¨°¢»óÇǼ¼Æ÷
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epithelial growth factor
    »óÇǼºÀåÀÎÀÚ (ß¾ù«à÷íþì×í­)
  • hereditary code
    À¯Àü ºÎÈ£(ë¶îîݬûÜ)
  • hereditary material
    À¯Àü ¹°Áú(ë¶îîÚªòõ)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 10 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • epithelial
    »óÇǼº
  • adrenogenital dystrophy
    ºÎ½Å¼º±â¹ßÀ°ÀÌ»ó
  • dystrophy
    ÀÌ¿µ¾çÁõ, ¿µ¾ç½ÇÁ¶, ±â´ÉÀå¾Ö, À§ÃàÁõ
  • muscular dystrophy
    ±ÙÀÌ¿µ¾çÁõ
  • progressive muscle dystrophy
    ÁøÇ༺±ÙÀÌ¿µ¾çÁõ
  • hereditary
    À¯Àü¼ºÀÇ
  • hereditary craniofacial dysostosis
    À¯Àü¼ºµÎ°³¾È¸éÀ̰ñÁõ
  • hereditary disease
    À¯Àüº´
  • hereditary ectodermal polydysplasia
    À¯Àü¼º¿Ü¹è¿±¼º´Ù¹ßÀÌÇü¼ºÁõ
  • hereditary hemorrhagic telangiectasia
    À¯Àü¼ºÃâÇ÷¼º¸ð¼¼Ç÷°üÈ®Àå
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
EECD endothelial-epithelial corneal dystrophy
PMD Progressive Muscular Dystrophy; ÁøÇ༺ ±ÙÀÌ¿µ¾çÁõ
  Types of PMD(Progressive Muscular Dystroph...
CMD campomelic dysplasia; camptomelic dwarfism; cartilage matrix deficiency; chief medical director; chi...
LCD coal tar solution [liquor carbonis detergens]; lattice corneal dystrophy; liquid crystal diode; loca...
MD Doctor of Medicine [Lat. Medicinae Doctor]; magnesium deficiency; main duct; maintenance dose; major...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
CHED Congenital Hereditary Endothelial Dystrophy
APECED Autoimmune polyendocrinopathy candidiasis ectodermal dystrophy
BMD Becker Muscular Dystrophy
CMD Congenital muscular dystrophy
CMD Congenital myotonic dystrophy
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • juvenile epithelial corneal dystrophy
    ¿¬¼Ò±â °¢¸· »óÇÇ ¼¼Æ÷ ÀÌ¿µ¾çÁõ
  • adiposogenital dystrophy
    Áö¹æ »ý½Ä±â ÀÌ¿µ¾çÁõ
    ºóÀÇ ½Å°æÇÐÀÚ Alfred Frohlich¿¡ ÀÇÇØ ÃÖÃÊ·Î ±âÀçµÈ °ÍÀ¸·Î ÇÁ·Ü¸®Èå ºñ¸¸Áõ ¶Ç´Â ½Ã»ó ÇϺμº ºñ¸¸ÁõÀ¸·Îµµ ºÒ¸°´Ù. ½Ã»ó ÇϺΠÁÖº¯ÀÇ Á¾¾ç Áõ»ó, °©Àڱ⠾ÇÈ­ÇÏ´Â ºñ¸¸, ¼º±â ¹ßÀ° ºÎÀüÀÌ 3ÁÖ Áõ»óÀ̰í Ç㸮, ÇϺ¹ºÎ, µÐºÎ µî¿¡ Áö¹æÀÌ Ä§ÂøÇÑ´Ù. »çÃá±â¿¡´Â 2Â÷ ¼ºÂ¡ÀÌ ¿ÀÁö ¾Ê°í ³²¼ºÀÇ °æ¿ì, ¿©¼º°ú °°Àº üÇüÀÌ µÈ´Ù. °ú·Î ½Ã¿¡´Â ½É½ÅÀÇ ÇǷΰ¡ µÎµå·¯Áø´Ù. JonsonÀº ƯÈ÷ ½Ã»ó ÇϺÎÀÇ Á¾¾ç, ±× ¹ÛÀÇ ¿øÀÎÀ¸·Î ÀÎÇÑ ±âÁú Àå¾Ö°¡ ÀÖ´Â »çÃá±â¹ßÁõÀÇ °ÍÀ» ÇÁ·Ü¸®Èå ÁõÈıºÀ̶ó Çϰí À̰ÍÀÌ ¾Æ´Ò ¶§¸¦ Áö¹æ¼º±â¼º ÀÌ¿µ¾çÁõÀ̶ó°í ¸»Çϰí ÀÖ´Ù.
  • adrenogenital dystrophy
    ºÎ½Å ¼º±â ¹ßÀ° ÀÌ»ó, ºÎ½Å ¼º±â ÀÌ¿µ¾çÁõ
  • central areolar choroidal dystrophy
    Á߽ɼº ¿øÇü ¸Æ¶ô¸· ÀÌ¿µ¾ç
  • central cloudy corneal dystrophy
    Á߽ɼº ȥŹ °¢¸· ÀÌ¿µ¾ç
  • distal muscular dystrophy
    ¿øÀ§ ±ÙÀÌ¿µ¾çÁõ
  • dominant cystoid macular dystrophy
    ¿ì¼º ³¶Æ÷ Ȳ¹Ý ÀÌ¿µ¾çÁõ
  • Duchenne pseudohypertrophic muscular dystrophy
    Duchenne À§ºñ´ë¼º ±ÙÀÌ¿µ¾çÁõ
  • dystrophy
    ¹ßÀ° ÀÌ»ó, ÀÌ¿µ¾çÁõ, ¿µ¾ç Àå¾Ö, ÀÌ¿µ¾ç, ¿µ¾ç½ÇÁ¶, ±â´ÉÀå¾Ö, À§ÃàÁõ
    ºÒ¿ÏÀüÇÑ ¿µ¾ç »óÅ·κÎÅÍ À¯¹ßµÇ´Â ±ÙÀ°ÀÇ ¹ßÀ°¼º º¯È­·Î¼­ ÁßÃ߽Űæ°è´Â Æ÷ÇÔÇÏÁö ¾ÊÀ¸¸ç, Áö¹æ º¯¼º, Å©±â´Â Áõ°¡ÇÏÁö¸¸ ÈûÀº °¨¼ÒÇÏ´Â »óŰ¡ Ư¡ÀÌ´Ù. ¿µ¾ç ºÎÁ· ¶Ç´Â ¿µ¾ç °áÇÌ¿¡ À¯·¡ÇÏ´Â ÀÏ¹Ý ÁúȯÀÇ. ƯÈ÷ ±Ù ÀÌ¿µ¾çÀ» ¶æÇÑ´Ù.
  • facioscapulohumeral muscular dystrophy
    ¾È¸é °ß°© »ó¿Ï±Ù ÀÌ¿µ¾çÁõ
  • fascioscapulohumeral dystrophy
    ¾È¸é °ß°© »ó¿Ï ±ÙÀÌ¿µ¾çÁõ
    »ó¿°»öü ¿ì¼ºÀ¸·Î À¯ÀüµÇ°í ±Ù ¼è¾àÀÌ ¾È¸é°ú °ß°©ºÎ ±ÙÀ°¿¡ ÁÖ·Î ³ªÅ¸³ª³ª Èı⿡´Â ´Ù¸® ±ÙÀ°¿¡µµ ³ªÅ¸³¯ ¼ö ÀÖ´Ù. °ß°©ºÎ ±ÙÀ°ÀÌ ÁַΠħ¹üµÇ±â ¶§¹®¿¡ »ó¿Ï À̵αÙÀ̳ª »ï°¢±Ù¿¡¼­ ±Ù »ý°ËÀ» ÇØ¾ßÇÑ´Ù. º´¸®ÇÐÀû ¼Ò°ßÀº ¹Ì¹ÌÇÏ¿© ¸¹Àº ¼öÀÇ È¯ÀÚ¿¡¼­ ±Ù »ý°Ë»ó ¼Ò¼öÀÇ ¿øÇü ±Ù¼¶À¯¸¸ ³ªÅ¸³ª¼­ °ÅÀÇ Á¤»ó ±ÙÀ°°ú °°ÀÌ º¸ÀÏ ¼ö ÀÖ´Ù. ÀϺΠ±Ù¼¶À¯°¡ Á»¸ÔÀº ±Ù¼¶À¯³ª À±»ýºÐÁö ¼¶À¯¸¦ º¸À̰í NADH °°Àº »êÈ­ È¿¼Ò ¿°»ö¿¡ ÁøÇÏ°Ô ¿°»öµÇ´Â ÀûÀº °¢Áø ±Ù¼¶À¯°¡ ³ªÅ¸³ªÁö¸¸ °¢Áø ±Ù¼¶À¯´Â ±ä°æ¿ø¼º ±Ù À§Ãà°ú °°ÀÌ ÁýÇÕÀ» ÀÌ·ç¾î ³ªÅ¸³ªÁö ¾Ê°í Á¤»ó ±Ù¼¶À¯ »çÀÌ¿¡ »êÀçÇÑ´Ù. ºñ´ë ±Ù¼¶À¯µéÀº ÈçÈ÷ ³ªÅ¸³ªÁö¸¸ Á᫐ ÇÙ, ±Ù¼¶À¯ ºÐÇÒ°ú ¼¶À¯È­´Â ÈçÇÏÁö ¾Ê´Ù.
  • myotonic dystrophy
    ±Ù ±äÀ强 ÀÌ¿µ¾çÁõ
    ±Ù ±äÀåÁõ°ú ±Ù µð½ºÆ®·ÎÇÇ¿ÍÀÇ ¼º°ÝÀ» Áß½ÉÀ¸·Î ÇÑ ´Ù°èÅ뼺 À¯Àü¼º ÁúȯÀÌ°í ±Ù ±äÀ强 ÁõÈıº¿¡ ¼ÓÇÏ´Â Áúȯ °¡¿îµ¥ °¡Àå ºóµµ°¡ ³ô´Ù. ±Ù ±äÀåÁõÀº ÀÏÁ¾ÀÇ ´ë»ç¼º ¹Ì¿ÀÆÄƼ·Î¼­ÀÇ º´ÅÂÀÌ°í ¼ÕÀ» Áå µÚ Æì±â ¾î·Æ°í ÇØ¸Ó µîÀ¸·Î µÎµé±ä µÚ ±Ù ¼öÃàÀÌ ºÎÇ®¾î¿À¸¥ ÇüÅ·ΠÁö¼ÓÇÏ´Â °Í µîÀÌ Æ¯Â¡ÀÌ´Ù. º¸Åë »ó¿°»öü¼º ¿ì¼º À¯ÀüÀ̰í ÇÑ ´ë°¡ ³»·Á°¥ ¶§¸¶´Ù ¹ß»ý ¿¬·É ÀúÇϳª ÁßÁõÈ­¸¦ ¼ö¹ÝÇÏ´Â ÁøÇ༺ À¯ÀüÀ» ³ªÅ¸³»´Â °æ¿ì°¡ ¸¹´Ù. Ä¡·á´Â ±Ù ±äÀå¿¡ ´ëÇØ¼­´Â ÇÑ·©À» ÇÇÇÏ°í ¿îµ¿ ½Ã¿¡ ¿ö¹Ö¾÷À» ÇÏ´Â ½À°üÀ» ÀÍÈ÷°Ô ÇÏ´Â °ÍÀε¥ ¾à¹° ¿ä¹ýÀ¸·Î¼­ ÇÁ·ÎÄ«ÀξƸ¶À̵å, µðÆä´ÒÈ÷´ÜÅäÀÎ µîÀÇ Ç×°æ·ÃÁ¦µµ ½ÃµµµÈ´Ù. ±Ù·Â ÀúÇÏ¿Í ±Ù À§Ãà¿¡ ´ëÇØ¼­´Â ÀçȰ ÇÁ·Î±×·¥ÀÇ ½Ç½Ã, ´ç´¢º´, ¹é³»Àå µî¿¡ ´ëÇØ¼­´Â °³°³ÀÇ ÀϹÝÀû Ä¡·á¸¦ ÇàÇÑ´Ù.
  • progressive muscular dystrophy
    ÁøÇ༺ ±Ù ÀÌ¿µ¾çÁõ
  • reflex sympathetic dystrophy
    ¹Ý»ç¼º ±³°¨¼º ¹ßÀ° ÀÌ»ó, ¹Ý»ç¼º ±³°¨½Å°æ ¹ßÀ° ÀÌ»ó, ¹Ý»ç¼º ±³°¨½Å°æ¼º ÀÌ¿µ¾çÁõ, ¹Ý»ç¼º ±³°¨½Å°æ ¿µ¾ç Àå¾Ö
    µ¿ÀǾî=causalgia, Sudeck's atro
  • reflex sympathetic dystrophy syndrome
    ¹Ý»ç ±³°¨½Å°æ¼º À§Ãà ÁõÈıº
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microcystic epithelial dystrophy Bilateral, symmetrical intraepithelial cysts in the central area of the cornea of healthy women, without hereditary predisposition.
(05 Mar 2000)
epithelial dystrophy Corneal dystrophy affecting primarily the epithelium and its basement membrane.
See: juvenile epithelial corneal dystrophy.
(05 Mar 2000)
juvenile epithelial corneal dystrophy Epithelial dystrophy characterised by progressive cysts and opacities of the corneal epithelium, with onset in infancy.
Inheritance: autosomal dominant with incomplete penetrance.
Synonym: Meesman dystrophy.
(22 Sep 2002)
Fuchs' epithelial dystrophy Epithelial oedema secondary to endothelial dystrophy of the cornea.
(05 Mar 2000)
calcifying epithelial odontogenic tumour A benign epithelial odontogenic neoplasm derived from the stratum intermedium of the enamel organ; a painless, slowly growing, mixed radiolucent-radiopaque lesion characterised histologically by cords of polyhedral epithelial cells, deposits of amyloid, and spherical calcifications.
Synonym: Pindborg tumour.
(05 Mar 2000)
Malassez' epithelial rests Epithelial remains of Hertwig's root sheath in the periodontal ligament.
(05 Mar 2000)
retinal pigmented epithelial cell See: pigmented retinal epithelium, retina.
(18 Nov 1997)
Golgi epithelial cell A glial cell found in the cerebellar cortex.
See: Bergmann's fibres.
(05 Mar 2000)
polymorphic epithelial mucin <protein> See episialin.
(18 Nov 1997)
neoplasms, glandular and epithelial Neoplasms composed of glandular tissue, an aggregation of epithelial cells that elaborate secretions, and of any type of epithelium itself. The concept does not refer to neoplasms located in the various glands or in epithelial tissue.
(12 Dec 1998)
odontogenic epithelial cell Epithelial layer that will give rise to teeth.
(18 Nov 1997)
oral epithelial nevus An autosomal dominant condition of the oral cavity characterised by soft, white or opalescent, thickened and corrugated folds of mucous membrane; other mucosal sites are occasionally involved simultaneously.
Synonym: familial white folded dysplasia, oral epithelial nevus.
(05 Mar 2000)
epithelial Pertaining to or composed of epithelium.
(16 Dec 1997)
epithelial attachment A collar of epthelial cells attached to the tooth surface and subepithelial connective tissue found at the base of the gingival crevice.
Synonym: epithelial attachment.
(05 Mar 2000)
epithelial body <anatomy, endocrinology> Four small endocrine glands lying close or embedded in the posterior surface of the thyroid gland. They secrete the hormone parathormone.
(27 Sep 1997)
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