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"hepatic phosphorylase kinase deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
¿µ¹® iron deficiency anemia ÇÑ±Û Ã¶°áÇ̺óÇ÷
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  ÀûÇ÷±¸ÀÇ ±â´ÉÀº »ê¼Ò¸¦ ¿î¹ÝÇϴµ¥ ÀÖ´Ù. ÀûÇ÷±¸ ¼Ó¿¡ »ê¼Ò¿Í °áÇÕÀ» ÇÏ¿© »ê¼Ò¸¦ ¿î¹ÝÇϴ Ç÷»ö¼Ò¶ó´Â ¹°ÁúÀÌ ÀÖ´Ù. Ã¶Àº ÀÌ Ç÷»ö¼ÒÀÇ Áß¿äÇÑ ºÎºÐÀ» ÀÌ·ç´Â °ÍÀ¸·Î Ã¶ÀÌ ¾øÀ¸¸é Ç÷»ö¼Ò°¡ ¸¸µé¾îÁú ¼ö°¡ ¾ø´Ù. Ç÷»ö¼Ò°¡ ¾øÀ¸¸é ¿ª½Ã ÀûÇ÷±¸µµ ¸¸µé¾îÁöÁö ¾ÊÀ¸¹Ç·Î Ã¼³»¿¡ Ã¶ÀÌ ºÎÁ·Çϸ頺óÇ÷ÀÌ »ý±ä´Ù. À̠ö°áÇ̼º ºóÇ÷Àº ºóÇ÷ÀÇ ¿øÀΠÁß¿¡¼­ °¡Àå ÈçÇÑ °ÍÀÌ´Ù(¾à 25%¸¦ Â÷ÁöÇÑ´Ù). Ã¶ÀúÀå·®ÀÇ ÀúÇÏ-°áÇÌ, Ç÷ûö³óµµÀÇ ÀúÇÏ, Æ®¶õ½ºÆä¸°·® »ó½Â, Æ®¶õ½ºÆä¸°Æ÷È­µµÀÇ ÀúÇÏ, Ç÷»ö¼Ò³óµµ ¶Ç´Â Ç츶ÅäÅ©¸®Æ®ÀÇ ÀúÇÏ, Àú»ö¼Ò¼º´ëÀûÇ÷±¸¸¦ Æ¯Â¡À¸·Î Çϴ ºóÇ÷·Î¼­, »ýü ³»¿¡¼­ Ã¶ÀÌ Àå±â¿¡ °ÉÃÄ °áÇ̵Ǹ砱נ¶§¹®¿¡ Ç÷»ö¼Ò »ý»ê °¨¼Ò¿¡ ÀÇÇØ ÀϾ´Ù. Ã¢ÀÚ¿¡¼­ÀǠöÈí¼ö·® ºÎÁ·, Ã¶ÀÇ ¼ö¿ä Áõ´ë(À¯¾Æ±â, »çÃá±â, ÀÓ½Å), Ã¶¼Ò½Ç°úÀ×(ÃâÇ÷)¿¡ ÀÇÇØ ÀϾ¸ç, Æ¯È÷ »çÃá±â¿¡¼­ Æó°æ±â±îÁöÀÇ ¿©¼º¿¡°Ô ¸¹´Ù. Áõ»óÀ¸·Î¼­´Â ¾ó±¼Ã¢¹é, ÇǷΰ¨, ÇǺÎâ¹é, ¼ÕÅé º¯È­(½ºÇ¬ ¸ð¾ç) µîÀ» ³ªÅ¸³½´Ù. ±¸°­ ¿µ¿ª¿¡¼­´Â ÇôÀÇ Á¢ÃËÅë, ¹ßÀû, °ÇÁ¶°¨, »ïÅ´°ï¶õÀ» ¼ö¹ÝÇϸé Ç÷¯¸Ó-ºó½¼(Plummer-Vinson)ÁõÈıºÀ̶ó°í ÇÑ´Ù. Ç÷¾× ¼Ò°ßÀº Ç÷ûöÀº ÀúÇÏÇϸç, Ã¶°áÇÕ´É·ÂÀÇ »ó½Â, Àú»ö¼Ò¼º ÀÛÀºÀûÇ÷±¸¼ºÀ» ³ªÅ¸³½´Ù.
¿µ¹® hepatic duct ÇÑ±Û °£°ü
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  °£¿¡¼­ »ý¼ºµÈ ´ãÁóÀÌ Áö³ª´Â Åë·Î·Î °£¿¡¼­ Á÷Á¢ ´ãÁóÀ» ¿î¹ÝÇϴ °üÀ» ¸»ÇÑ´Ù. °£¿¡¼­ ¸¸µé¾îÁø ´ãÁóÀº °£°ü, ¾µ°³ÁָӴϰü¸¦ °ÅÃļ­ ¾µ°³¿¡ º¸°üµÇ¾ú´Ù°¡ ¿Â¾µ°³°üÀ» ÅëÇØ¼­ »ùâÀڷΠº¸³»Áø´Ù. 
  
  °£°ü
¿µ¹® hepatic portal system ÇÑ±Û °£¹®¸Æ°è
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  À§, ÀÛÀºÃ¢ÀÚÀ̳ª Å«Ã¢ÀÚ¿¡¼­ ¿µ¾çºÐÀ» Èí¼öÇϱâ À§ÇÑ ¸ð¼¼Ç÷°üÁ¶Á÷Àº ¸ðµÎ °£À¸·Î ¿¬°áµÈ´Ù. Áï ¼ÒÈ­±â¿¡ Èí¼öÇÑ ¿µ¾çºÐÀÌ °¡µæÇÑ ÇǴ ¸ðµÎ °£À¸·Î ¿¬°áµÇ´Âµ¥ À̰ÍÀ» ¹®¸Æ°è¶ó°í ÇÑ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • phosphorylase kinase
    Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦Å°³ª¾ÆÁ¦
  • phosphorylase
    ÀλêÈ­È¿¼Ò
  • adenylate kinase
    ¾Æµ¥´Ò»êŰ³ª¾ÆÁ¦
  • beta-adrenergic receptor kinase
    º£Å¸¾Æµå·¹³¯¸°¼ö¿ëüÀλêÈ­È¿¼Ò
  • creatine kinase
    Å©·¹¾ÆÆ¾Å°³ª¾ÆÁ¦
  • creatine kinase isoenzymes
    Å©·¹¾ÆÆ¾Å°³ª¾ÆÁ¦µ¿Á¾È¿¼Ò
  • kinase
    1. Ű³ª¾ÆÁ¦ 2. Ȱ¼ºÈ¿¼Ò 3. ÀλêÈ­È¿¼Ò
  • mitogen-activated protein kinase
    ¹ÌÅä°ÕȰ¼ºÈ­´Ü¹éÁúŰ³ª¾ÆÁ¦
  • protein kinase
    ´Ü¹éÁúŰ³ª¾ÆÁ¦
  • protein kinase C
    ´Ü¹éÁúŰ³ª¾ÆÁ¦C
  • pyruvate kinase
    ÇÇ·çºê»ê¿°Å°³ª¾ÆÁ¦
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • biotin deficiency syndrome
    ºñ¿Àƾ°áÇÌÁõÈıº
  • deficiency
    1. °áÇÌ 2. °áÇÌÁõ
  • deficiency disease
    °áÇ̺´
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 11 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • kinase
    Ȱ¼ºÈ¿¼Ò, Ű³ª¾ÆÁ¦
  • phosphorylase
    ÀλêÈ­È¿¼Ò
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • deficiency
    °áÇÌ(Áõ)
  • hepatic artery embolization
    °£µ¿¸Æ»öÀü¼ú
  • fulminant hepatic failure
    Àü°Ý°£±â´É»ó½Ç, Àü°Ý°£ºÎÀü
  • hepatic
    °£-
  • massive hepatic necrosis
    ±¤¹üÀ§°£±«»ç
  • subacute hepatic necrosis
    ¾Æ±Þ¼º°£±«»ç
  • hepatic resection
    °£ÀýÁ¦¼ú
  • hepatic vein
    °£Á¤¸Æ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • phosphorylase
    ÀλêÈ­È¿¼Ò
  • beta-adrenergic receptor kinase
    º£Å¸¾Æµå·¹³¯¸°¼º¼ö¿ëüÀλêÈ­È¿¼Ò
  • creatine kinase
    Å©·¹¾ÆÆ¾Å°³ª¾ÆÁ¦
  • kinase
    Ȱ¼ºÈ¿¼Ò, Ű³ª¾ÆÁ¦
  • mitogen-activated protein kinase
    ºÐ¿­Á¦È°¼º´Ü¹éŰ³ª¾ÆÁ¦
  • protein kinase
    ´Ü¹éÁúŰ³ª¾ÆÁ¦
  • pyruvate kinase
    ÇÇ·çºó»ê¿°Å°³ª¾ÆÁ¦
  • acid lipase deficiency
    »ê¼ºÁöÁúºÐÇØÈ¿¼Ò°áÇÌ
  • acquired immune deficiency
    ÈÄõ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • adhesion deficiency disorder
    À¯Âø°áÇÌÀå¾Ö
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾°áÇ̺óÇ÷
  • folate deficiency anemia
    ¿±»ê°áÇÌ
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • phosphorylase kinase
    Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦Å°³ª¾ÆÁ¦
  • inosine phosphorylase deficiency
    À̳ë½ÅÆ÷½ºÆ÷¸±¶óÁ¦°áÇÌ(Áõ)
  • glycogen phosphorylase
    ±Û¸®ÄÚ°ÕÆ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • phosphorylase
    Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • phosphorylase =PR
    Æ÷½ºÆ÷¸±·¹À̽º.
  • purine nucleoside phosphorylase
    Ç»¸° ´©Å¬·¹¿À½Ãµå Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • Creatine kinase
    Å©·¹¾ÆÆ¾ Ű³ªÁ¦
  • Kinase
    Ä«À̳×ÀÌÁî
  • adenyl kinase
    ¾Æµ¥´ÒŰ³ªÁ¦
  • adenylate kinase
    ¾Æµ¥´Ò·¹ÀÌÆ®Ä«À̳×ÀÌÁî, ¾Æµ¥´Ò·¹ÀÌÆ®Å°³ªÁ¦
  • phosphoglycerate kinase
    Æ÷½ºÆ÷±Û¸®¼¼·¹ÀÌÆ®Å°³ªÁ¦
  • pyruvate kinase
    ÇÇ·çºê»ê¿° Ű³ªÁ¦
  • Acquiered immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª °áÇÌÁõÈıº
  • Fluorine deficiency
    ºÒ¼Ò°áÇÌÁõ(Ý×áÈÌÀù¹ñø)
  • Folate deficiency
    ¿±»ê°áÇÌÁõ(ç¨ß«ÌÀù¹ñø)
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • phosphorylase kinase
    Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦Å°³ª¾ÆÁ¦
  • inosine phosphorylase deficiency
    À̳ë½ÅÆ÷½ºÆ÷¸±¶óÁ¦°áÇÌ(Áõ)
  • glycogen phosphorylase
    ±Û¸®ÄÚ°ÕÆ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • muscle phosphorylase
    ±ÙÆ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • phosphorylase
    Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • phosphorylase =PR
    Æ÷½ºÆ÷¸±·¹À̽º.
  • purine nucleoside phosphorylase
    Ç»¸° ´©Å¬·¹¿À½Ãµå Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦
  • adenyl kinase
    ¾Æµ¥´ÒŰ³ªÁ¦
  • adenylate kinase
    ¾Æµ¥´Ò·¹ÀÌÆ®Ä«À̳×ÀÌÁî, ¾Æµ¥´Ò·¹ÀÌÆ®Å°³ªÁ¦
  • beta-ARK : beta-adrenergic receptor kinase
    º£Å¸-¾Æµå·¹³¯¸°(¼º)¼ö¿ëü ÀλêÈ­È¿¼Ò.
  • creatine kinase
    Å©·¹¾ÆÆ¾Å°³ªÁ¦
  • creatine kinase assay
    Å©·¹¾ÆÆ¾Å°³ªÁ¦ÃøÁ¤
  • creatine kinase isoenzyme
    Å©·¹¾ÆÆ¾Å°³ªÁ¦À̼ҿ£ÀÚÀÓ<µ¿È°È¿¼Ò
  • cyclic AMP-dependent kinase
    °í¸® AMP ÀÇÁ¸¼º Ű³ªÁ¦
  • kinase
    Ä«À̳×À̽º.
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Deficiency (Nanismus)
    °áÇÌ(³­ÀåÀÌÁõ)
    [¿¾ ¿ë¾î] °áÇÌ
  • Organogenetic deficiency
    ±â°ü¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ±â°ü¹ß»ý°áÇÌ
  • Functional deficiency
    ±â´É°áÇÌ
    [¿¾ ¿ë¾î] ±â´ÉÀû°áÇÌ
  • Pituitary hormone deficiency (Pituitary dwarfism)
    ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
    [¿¾ ¿ë¾î] ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
  • Reaction deficiency
    ¹ÝÀÀ°áÇÌ
    [¿¾ ¿ë¾î] ¹ÝÀÀ°áÇÌ
  • Vitamin deficiency (Fetal osteodystrophy)
    ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
    [¿¾ ¿ë¾î] ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
  • Cellular deficiency (Acallosal cerebrum)
    ¼¼Æ÷°áÇÌ (³úµéº¸°á¿©³ú)
    [¿¾ ¿ë¾î] ¼¼Æ÷°áÇÌ
  • Intracellular deficiency (Albinism)
    ¼¼Æ÷¼Ó°áÇÌ (¹é»öÁõ)
    [¿¾ ¿ë¾î] ¼¼Æ÷³»°áÇÌ
  • Chromosomal deficiency
    ¿°»öü°áÇÌ
    [¿¾ ¿ë¾î] ¿°»öü°á½Ç
  • Stimulation deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Sensory deficiency
    °¨°¢°áÇÌ
    [¿¾ ¿ë¾î] °¨°¢°áÇÌ
  • Thyroid hormone deficiency (Cretinism)
    °©»ó»ùÈ£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
    [¿¾ ¿ë¾î] °©»ó¼±È£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
  • Deficiency
    °áÇÌ
    [¿¾ ¿ë¾î] °áÇÌ
  • Deficiency (Monstrous tumor)
    °áÇÌ (±«¹°Á¾)
    [¿¾ ¿ë¾î] °áÇÌ
  • Secretion deficiency
    ºÐºñ°áÇÌ
    [¿¾ ¿ë¾î] ºÐºñ°áÇÌ
´ëÇѱâ»ýÃæÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hepatic amebiasis
    °£¾Æ¸Þ¹ÙÁõ
  • hepatic ascariasis
    °£È¸ÃæÁõ
  • hepatic echinococcosis
    °£Æ÷ÃæÁõ
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • phosphorylase kinase
    Æ÷½ºÆ÷¸±·¹À̽ºÄ«À̳×À̽º
  • synthase-phosphorylase kinase
    ½ÅÅ×À̽º-Æ÷½ºÆ÷¸±·¹À̽º Ä«À̳×À̽º
  • hepatic porphyria
    °£¼º(ÊÜàõ) Æ÷¸£ÇǸ°Áõ(ñø)
  • glycogen phosphorylase
    ±Û¶óÀÌÄÚÀü Æ÷½ºÆ÷¸±·¹À̽º
  • phosphorylase
    Æ÷½ºÆ÷¸±·¹À̽º
  • phosphorylase phosphatase
    Æ÷½ºÆ÷¸±·¹À̽ºÆ÷½ºÆÄÅ×À̽º
  • polynucleotide phosphorylase
    Æú¸®´©Å¬·¹¿ÀŸÀÌµå Æ÷½ºÆ÷¸±·¹À̽º
  • polyribonucleotide phosphorylase
    Æú¸®¶óÀ̺¸´©Å¬·¹¿ÀŸÀÌµå Æ÷½ºÆ÷¸±·¹À̽º
  • polysaccharide phosphorylase
    ´Ù´çÁú(ÒýÓØòõ) Æ÷½ºÆ÷¸±·¹À̽º
  • starch phosphorylase
    ³ì¸» Æ÷½ºÆ÷¸±·¹À̽º
  • conditioned vitamin deficiency
    Á¶°ÇºÎ(ðÉËìݾ) ºñŸ¹Î°áÇË(ÌÀù¹)
  • deficiency
    °áÇÌ(ÌÀù¹)
  • deficiency disease
    °áÇÌ Áúȯ(ÌÀù¹òðü´)
  • deficiency mutant
    "°áÇÌ º¯ÀÌü(ÌÀù¹Ü¨ì¶ô÷), (ÔÒ) auxotroph"
  • dietary deficiency
    ½ÄÀ̰áÇÌ(ç½å×ÌÀù¹)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • deficiency
    °áÇÌÁõ
  • deficiency anemia
    °áÇ̼ººóÇ÷
  • iron deficiency anemia
    ö°áÇ̼ººóÇ÷
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)
  • nutritional deficiency disease
    ¿µ¾ç°áÇÌÁõ
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
  • common hepatic artery
    ÃѰ£µ¿¸Æ
  • CT hepatic arteriography(CTHA)
    CTµ¿¸ÆÁ¶¿µ¼ú,CTHA
  • hepatic
    °£ÀÇ
  • hepatic artery
    °£µ¿¸Æ
  • hepatic coma
    °£¼ºÈ¥¼ö
  • hepatic duct
    °£°ü
  • hepatic failure
    °£ºÎÀü
  • hepatic flexure
    ¿ì°áÀå°î
  • hepatic vein
    °£Á¤¸Æ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
MD Doctor of Medicine [Lat. Medicinae Doctor]; magnesium deficiency; main duct; maintenance dose; major...
AK above knee; acetate kinase; adenosine kinase; adenylate kinase; artificial kidney
CK calf kidney; casein kinase; chicken kidney; cholecystokinin; choline kinase; contralateral knee; cre...
TK thymidine kinase; transketolase; triose-kinase; tyrosine kinase
PBK phosphorylase B kinase
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
PHK Phosphorylase kinase
GKD Glycerol kinase deficiency
MAP-KKK MAP kinase kinase kinase
MAPKKK mitogen activated protein kinase kinase kinase
MEKK1 mitogen-activated protein kinase kinase kinase 1
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • nucleoside phosphorylase
    ´ºÅ¬·¹¿À½Ãµå Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦
    ´ºÅ¬·¹¿À½Ãµå¸¦ °¡ÀλêºÐÇØÇÏ¿© Ç»¸°, ÇǸ®¹Ìµò ¿°±â¿Í ÆæÅä¿À½º ÀλêÀ» »ý¼ºÇÏ´Â ¹ÝÀÀ¿¡ °ü¿©ÇÏ´Â È¿¼Ò. ±âÁú ƯÀ̼ºÀÌ ´Ù¸¥ °ÍÀÌ ¸î °¡Áö ¾Ë·ÁÁ® ÀÖ´Ù. ¿¹¸¦ µé¸é, Ç»¸° ´ºÅ¬·¹¿À½Ãµå Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦´Â ±¸¾Æ³ë½Å, µð¿Á½Ã±¸¾Æ³ë½Å, À̳ë½Å, µð¿Á½ÃÀ̳ë½Å¿¡ ÀÛ¿ëÇϸç, Áö¶ó, Æó, °£, ½É±Ù, ÀûÇ÷±¸, È¿¸ð¿¡, ¼Ò·®Àº ¼ÒÀå, Ç÷¾×¿¡ ÀÖ´Ù. ±×¹Û¿¡ ÇǸ®¹Ìµò ´ºÅ¬·¹¿À½Ãµå Æ÷½ºÆ÷ ¸±¶ó¾ÆÁ¦·Î¼­ ¿ì¸®µò, Ƽ¹Ìµò¿¡ °¢°¢ ƯÀÌÀûÀÎ È¿¼Ò°¡ ¾Ë·ÁÁ® ÀÖ´Ù. ÁÖ·Î ´ºÅ¬·¹¿À½ÃµåÀÇ ºÐÇØ, ¶Ç´Â ´Ù¸¥ Á¾·ùÀÇ ´ºÅ¬·¹¿À½Ãµå »ý¼ºÀ» À§ÇÑ ¸®º¸¿À½ºÀλêÀ» °ø±ÞÇÏ´Â ¿ªÇÒÀ» ÇÑ´Ù.
  • adenosine kinase
    ¾Æµ¥³ë½Å Ä«À̳×À̽º
    ATP+adenosine=ADP+AMPÀÇ È­ÇйÝÀÀÀ» Ã˸ÅÇÏ´Â ÀüÀÌÈ¿¼ÒÀÇ ÇϳªÀÌ´Ù. ÀÌ ¹ÝÀÀÀº
  • adenyl kinase
    ¾Æµ¥´ÒŰ³ªÁ¦
  • adenylate kinase
    ¾Æµ¥´Ò·¹ÀÌÆ® Ä«À̳×À̽º
  • creatinaemia : excess of creatine in the blood.

    creatine kinase

    Å©·¹¾ÆÆ¾ Ű³ª¾ÆÁ¦
  • myotonin-protein kinase
    ¹Ì¿ÀÅä´Ñ-´Ü¹é Ű³ªÁ¦
  • nucleoside kinase
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  • hepatic encephalopathy
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CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
muscle phosphorylase deficiency Type V glycogen storage disease, affecting muscle, caused by deficiency of muscle phosphorylase.
(05 Mar 2000)
MAP kinase kinase kinase <enzyme> From pc12 cells; reactivates map kinase kinase inactivated by protein phosphatase 2a by phosphorylation of serine residues; tak1 (tgf-beta-activated kinase 1) is a member of the mapkkk family; genbank ab006787 (mouse)
Registry number: EC 2.7.10.-
Synonym: mapkkk, tak1 mapkkk, ask1 (kinase), apoptosis signal-regulating kinase 1
(26 Jun 1999)
phosphorylase kinase <enzyme> The enzyme that regulates the activity of phosphorylase and glycogen synthetase by addition of phosphate groups. A large and complex enzyme, itself regulated by phosphorylation. Integrates the hormonal and calcium signals in muscle.
(18 Nov 1997)
phosphorylase kinase phosphatase <enzyme> Aspect of phosphoprotein phosphatase EC 3.1.3.16
Registry number: EC 3.1.3.-
(26 Jun 1999)
pyruvate kinase deficiency A disorder in which there is a deficiency of pyruvate kinase in red blood cells; characterised by haemolytic anaemia varying in degree from one patient to another; autosomal recessive inheritance.
(05 Mar 2000)
AMP-activated protein kinase kinase <enzyme> An endogenous kinase kinase; reactivates the inactive form of AMP-activated protein kinase (AMP-pk); phosphorylates the 63-kD subunit of AMP-pk
Registry number: EC 2.7.1.-
Synonym: AMP-pk reactivator, hmg CoA reductase kinase kinase
(26 Jun 1999)
calmodulin-dependent protein kinase IV kinase <enzyme> Phosphorylates and activates cam-kinase iv; from brain
Registry number: EC 2.7.10.-
Synonym: cam-kinase iv kinase
(26 Jun 1999)
MAPKAP kinase-2 reactivating kinase <enzyme> A mapk-like enzyme; homologous to p42(mapk) and p44(mapk); activated by phosphorylation of serine/threonine and tyrosine residues
Registry number: EC 2.7.1.-
Synonym: mapkap kinase-2 rk
(26 Jun 1999)
ribosomal protein S6 kinase kinase <enzyme> Isolated from unfertilised xenopus eggs; a 41 kD enzyme that is associated, in vivo, with phosphorylation on threonine and tyrosine residues and, in vitro, with phosphorylation on serine as well
Registry number: EC 2.7.1.-
Synonym: rsk kinase
(26 Jun 1999)
protein kinase B kinase <enzyme> Phosphorylates and activates protein kinase b on threonine-308; requires phosphatidylinositol-3,4,5-trisphosphate
Registry number: EC 2.7.10.-
Synonym: upstream kinase, pkb kinase
(26 Jun 1999)
leukocyte tyrosine kinase receptor tyrosine kinase <enzyme> May be receptor for pre-b lymphocyte growth or differentiation factor; aa sequence given in first source
Registry number: EC 2.7.1.-
Synonym: ltk receptor tyrosine kinase, ltk receptor tk, ltk protein, leukocyte tyrosine kinase (ltk)
(26 Jun 1999)
alpha,alpha-trehalose phosphorylase <enzyme> Chemical name: alpha-d-glucopyranosyl-alpha-d-glucopyranose orthophosphate glucosyltransferase
Registry number: EC 2.4.1.64
Synonym: trehalose phosphorylase
(26 Jun 1999)
alpha-glucan phosphorylase <enzyme> Enzyme that catalyses the sequential removal of glycosyl residues from glycogen to yield one glucose-1-phosphate per reaction. Its activity is controlled by phosphorylation (by phosphorylase kinase).
(21 Jun 2000)
maltodextrin phosphorylase <enzyme> From E coli
Registry number: EC 2.4.1.-
Synonym: e350a
(26 Jun 1999)
GDPmannose phosphorylase <enzyme> A transferase that catalyses the transfer of GDP to the mannose of mannose-1-phosphate.
Consider also the bifunctional enzyme, phosphomannose isomerase-guanosine diphospho-d-mannose pyrophosphorylase; rfbm has similarity to long-chain, iron-containing alcohol dehydrogenases
Registry number: EC 2.7.7.13
Synonym: GDPmannose phosphorylase, GDP mannose pyrophosphorylase, GTP-alpha-d-mannose-1-phosphate guanylyltransferase, GDP-mannose pyrophosphorylase, rfbm gene product, rfbm protein
(26 Jun 1999)
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hepatic phosphorylase kinase deficiency phosphorylase b kinase deficiency.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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