| glutaryl-CoA | The mono thiol ester of coenzyme A and glutaric acid; an intermediate in l-lysine and l-tryptophan catabolism. Glutaryl-CoA dehydrogenase, an enzyme that catalyses the reaction of glutaryl-CoA with an acceptor to form crotonoyl-CoA, CO2, and the reduced acceptor; a deficiency of this enzyme will lead to either glutaric acidemia type I or hyperoxaluria type II. Glutaryl-CoA synthetase, an enzyme similar to acyl-CoA synthetase, but which splits ATP, GTP, or ITP to the nucleoside diphosphate and orthophosphate in acting on glutarate, thus forming glutaryl-Coa. (05 Mar 2000) |
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| glutaryl-CoA dehydrogenase | <enzyme> Glutaric aciduria may be due to deficiency of this enzyme Registry number: EC 1.3.99.7 Synonym: glutaryl CoA dehydrogenase, glutaryl-coenzyme a dehydrogenase (26 Jun 1999) |
Synonyms : Glutaryl CoA Dehydrogenase, Glutaryl-Coenzyme A Dehydrogenase, CoA Dehydrogenase, Glutaryl, Dehydrogenase, Glutaryl CoA, Dehydrogenase, Glutaryl-CoA, Dehydrogenase, Glutaryl-Coenzyme A, Glutaryl Coenzyme A Dehydrogenase
| glutaryl-CoA dehydrogenase |
[EC 1.3.99.7] an enzyme of the oxidoreductase class that catalyzes the oxidative decarboxylation of glutaryl CoA, with sequential reduction of FAD and then electron transfer flavoprotein; the reaction is a step in the degradation of lysine, hydroxylysine, and tryptophan. Deficiency of the enzyme, an autosomal recessive trait, causes glutaricaciduria, type I.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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보험코드 | 성분/함량 | 구분/보험급여 |
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보험코드 | 성분/함량 | 구분/보험급여 |
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