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  • glucosylceramide
    ±Û·çÄڽǼ¼¶ó¸¶À̵å
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  • glucosyl group
    ±Û·çÄڽDZâ(Ðñ)
  • glucosylation
    ±Û·çÄÚ½ÇÈ­(ûù)
  • glucosylceramide lipidosis
    ±Û·çÄڽǼ¼¶ó¸¶À̵å Áö¹æÁõ(ò·Û¸ñø)
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GTF glucose tolerance factor; glucosyl-transferase
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CGTase Cyclodextrin Glucosyl Transferase
GGT galactosylhydroxylysyl glucosyl-transferase
GT glucosyl transferase
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 9 ÆäÀÌÁö: 1
glucosyl The radical of glucose that has lost its hemiacetal (C-1) OH.
(05 Mar 2000)
glucosylation <biochemistry> Transfer of glucose residues, usually from the nucleotide sugar derivative UDPG.
Enzymic glucosylation to generate the glucosyl galactosyl disaccharide on the hydroxylysine of collagen is a normal process. A recent theory suggests that glucosylation of certain long lived proteins by a nonenzymic reaction with free glucose may contribute to ageing.
(18 Nov 1997)
glucosylceramidase <enzyme> A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in gaucher's disease.
Chemical name: D-Glucosyl-N-acylsphingosine glucosylhydrolase
Registry number: EC 3.2.1.45
(12 Dec 1998)
glucosylceramide A neutral glycolipid containing equimolar amounts of fatty acid, glucose, and sphingosine (or a derivative thereof); accumulates in individuals with Gaucher disease.
Synonym: glucocerebroside.
(05 Mar 2000)
glucosylceramide beta-1-4-galactosyltransferase <enzyme> Catalyses the formation of lactosylceramide from glucosylceramide and udp galactose; also uses dihexosides as acceptor
Registry number: EC 2.4.1.-
Synonym: udpgalactose ceramide monohexoside galactosyltransferase, glccer galactosyltransferase, galt-2, udpgalactose-glucosylceramide beta-1-4-galactosyltransferase
(26 Jun 1999)
glucosylceramides Cerebrosides which contain as their polar head group a glucose moiety bound in glycosidic linkage to the hydroxyl group of ceramides. Their accumulation in tissue, due to a defect in beta-glucosidase, is the cause of gaucher's disease.
(12 Dec 1998)
glucosylglycerol-phosphate phosphatase <enzyme> Isolated from synechocystis; do not confuse with stpa protein from e. Coli
Registry number: EC 3.1.3.-
Synonym: stpa gene product, synechocystis
(26 Jun 1999)
glucosyltransferase <enzyme> An enzyme which transfers residues of glucose (a sugar) to acceptor molecules.
(09 Oct 1997)
glucosyltransferases <enzyme> Enzymes that catalyze the transfer of glucose from a nucleoside diphosphate glucose to an acceptor molecule which is frequently another carbohydrate.
Registry number: EC 2.4.1.-
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
beta-glucosyl-hydroxymethylcytosine-alpha-glucosyltransferase <enzyme> Generates gentobiosyl groups on the hydroxymethylcytosine of phage t2 and t6 DNA
Registry number: EC 2.4.1.-
Synonym: b-glc-hmc-a-glucosyltransferase
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 3 ÆäÀÌÁö: 1
  • Glucosylceramidase - »õâ A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in GAUCHER DISEASE. EC 3.2.1.45.
    Synonyms : Acid beta-Glucosidase, Glucocerebroside beta-Glucosidase, Glucosyl Ceramidase, Glucosylceramide beta-Glucosidase, Glucosylsphingosine Glucosyl Hydrolase, beta-Glucocerebrosidase, Acid beta Glucosidase, Ceramidase, Glucosyl, Glucocerebroside beta Glucosidase
  • Glucosylceramides - »õâ Cerebrosides which contain as their polar head group a glucose moiety bound in glycosidic linkage to the hydroxyl group of ceramides. Their accumulation in tissue, due to a defect in beta-glucosidase, is the cause of Gaucher's disease.
    Synonyms : Ceramides, Glucosyl
  • Glucosyltransferases - »õâ Enzymes that catalyze the transfer of glucose from a nucleoside diphosphate glucose to an acceptor molecule which is frequently another carbohydrate. EC 2.4.1.-.
    Synonyms :
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glucosyl a glucose radical.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
glucosylceramidase [EC 3.2.1.45] an enzyme of the hydrolase class that catalyzes the hydrolytic cleavage of glucose from glucocerebrosides to form ceramides, a reaction occurring in the lysosomal degradation of sphingolipids. Deficiency of enzyme activity, an autosomal recessive trait, results in Gaucher disease. Called also glucocerebrosidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
glucosylceramide glucocerebroside.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
glucosylceramide l. Gaucher's disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
glucosyltransferase a term used in the trivial and recommended names of some hexosyltransferases [EC 2.4.1] that catalyze the transfer of a glucosyl group from a donor to an acceptor compound. Called also transglucosylase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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