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Gb4 globoside
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globoside <biochemistry> An organic macromolecule, a type of oligomeric glycoside, containing a number of different sugar groups which is found in the red blood cells of certain mammals, including humans, pigs, and sheep.
(09 Oct 1997)
globoside galactosyltransferase <enzyme> Mouse kidney microsome enzyme which participates in the formation of galactosylgloboside (stage-specific embryonic antigen-3 glycolipid)
Registry number: EC 2.4.1.-
Synonym: udpgalactose-globoside beta 1-3 galactosyltransferase, gb4-galactosyltransferase, gb4 synthetase, beta-1,3-galnac-tf
(26 Jun 1999)
globosides Glycosphingolipids containing n-acetylglucosamine (paragloboside) or n-acetylgalactosamine (globoside). Globoside is the p antigen on erythrocytes and paragloboside is an intermediate in the biosynthesis of erythrocyte blood group abh and p 1 glycosphingolipid antigens. The accumulation of globoside in tissue, due to a defect in hexosaminidases a and b, is the cause of sandhoff disease.
(12 Dec 1998)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Globosides - »õâ Glycosphingolipids containing N-acetylglucosamine (paragloboside) or N-acetylgalactosamine (globoside). Globoside is the P antigen on erythrocytes and paragloboside is an intermediate in the biosynthesis of erythrocyte blood group ABH and P 1 glycosphingolipid antigens. The accumulation of globoside in tissue, due to a defect in hexosaminidases A and B, is the cause of Sandhoff disease.
    Synonyms : Lactoneotetraosylceramide, Lacto N neotetraosylceramide, Lacto N tetraosylceramide
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globoside a glycosphingolipid containing acetylated amino sugars and simple hexoses of the general composition N-acetylgalactosamine-galactose-galactose-glucose-ceramide; it accumulates in tissues in Sandhoff's disease, but not in Tay-Sachs disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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