| XGPT | xylosylprotein-4-beta-galactosyltransferase |
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| GalTase | 1,4-Galactosyltransferase |
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| GT | 1----4)galactosyltransferase |
| GalT | 4-galactosyltransferase |
| alpha1,3GT | Alpha1,3-galactosyltransferase |
| beta 1,4-GT | Beta 1,4-galactosyltransferase |
| ganglioside galactosyltransferase | <enzyme> Consider also EC 2.4.1.45 Registry number: EC 2.4.1.62 Synonym: udpgalactose-n-acetylgalactosaminyl-(n-acetylneuraminyl)-galactosyl-glucosyl-ceramide galactosyltransferase, udpgalactose-gm2 galactosyltransferase, ganglioside gm1 synthase, udpgalactose-ceramide galactosyltransferase, udp-galactose-gm2 gangliosidebeta-1-3-galactosyltransferase, udpgal-gm2 beta1-3-galactosyltransferase (26 Jun 1999) |
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| ganglioside | <biochemistry> A glycosphingolipid that contains one or more residues of N acetyl or other neuraminic acid derivatives. Gangliosides are found in highest concentration in cells of the nervous system, where they can constitute as much as 5% of the lipid. (18 Nov 1997) |
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| ganglioside lipidosis | Any disease characterised, in part, by the abnormal accumulation within the nervous system of specific gangliosides, e.g., GM2 gangliosidosis, Tay-Sachs disease, caused by hexosaminidase A enzyme deficiency with accumulation of GM2 ganglioside Synonym: gangliosialidosis, ganglioside lipidosis. (05 Mar 2000) |
| ganglioside O-acetyltransferase | <enzyme> Gd2 ganglioside is an acceptor for the above enzyme in human melanoma cells Registry number: EC 2.3.1.- (26 Jun 1999) |
| g(m1) ganglioside | <chemical> Galactosyl-n-acetylgalactosaminyl-(n-acetylneuraminyl)- galactosyl-glucosylceramide. Ganglioside present in abnormally large amounts in neurons and in elevated levels in liver and kidney due to a deficiency of beta-galactosidase in the genetically determined disease gm1-gangliosidosis. Chemical name: Ganglioside GM1 (12 Dec 1998) |
| g(m2) ganglioside | <chemical> N-acetylgalactosaminyl-galactosyl-(n-acetylneuraminyl)-glucosyl-ceramide. This is the defective ganglioside manifested in tay-sachs disease and sandhoff disease. Chemical name: Ganglioside GM2 (12 Dec 1998) |
| g(m3) ganglioside | N-acetylneuraminyl-galactosyl-glucosylceramide. This ganglioside is present in abnormally large amounts in the brain and liver due to a deficient biosynthetic enzyme, g(m3):udp-n-acetylgalactosaminyltransferase. Deficiency of this enzyme prevents the formation of g(m2) ganglioside from g(m3) ganglioside and is the cause of an anabolic sphingolipidosis. (12 Dec 1998) |
| GM3 ganglioside sialidase | <enzyme> Enzyme deficient in mucolipidosis iv Registry number: EC 3.2.1.- Synonym: haematoside neuraminidase, ganglioside sialidase (26 Jun 1999) |
| beta-n-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase | <enzyme> An enzyme that catalyses the transfer of galactose from udp-galactose to a specific glycoprotein receptor, 2-acetamido-2-deoxy-d-glucosyl-glycopeptide, during glycopeptide synthesis. Chemical name: UDPgalactose:N-acetyl-beta-D-glucosaminylglycopeptide beta-1,4-galactosyltransferase Registry number: EC 2.4.1.38 (12 Dec 1998) |
| galactosylxylosylprotein 3-beta-galactosyltransferase | <enzyme> Catalyses the reaction of udpgalactose and 4-beta-d-(galactosyl-o-beta-d-xylosylprotein to yield udp and 3-beta-d-galactosyl-o-beta-d-xylosylprotein Registry number: EC 2.4.1.134 Synonym: galactosyltransferase II, (26 Jun 1999) |
| GalNAc beta1-4 GlcNAc-R beta1-3-galactosyltransferase | <enzyme> From connective tissue of the snail lymnaea stagnalis; transfers galactose from udp galactose to haemocyanin glycans with side chains galnac beta 1-4 glcnac beta1-2 man-r where r is a branched side chain ultimately linked to asparagine Registry number: EC 2.4.1.- Synonym: udp-gal-galnac(beta1-4)glcnac-r(beta1-3)-galactosyltransferase, galnac-glcnac-beta-3-gal-t (26 Jun 1999) |
| GD2 beta1,3-galactosyltransferase | <enzyme> Catalyses synthesis of gd1b from gd2, gm1 from gm2, and ga1 from ga2 gangliosides; genbank ab003478 Registry number: EC 2.4.1.- Synonym: gd2 beta1,3gal-t (26 Jun 1999) |
| mannosylglycoprotein alpha-1,2-galactosyltransferase | <enzyme> From schizosaccharomyes pompe golgi apparatus; transfers galactose from udpgal to form an alpha 1,2-galactosyl mannoside linkage Registry number: EC 2.4.1.- Synonym: man-1,2-galt (26 Jun 1999) |
| globoside galactosyltransferase | <enzyme> Mouse kidney microsome enzyme which participates in the formation of galactosylgloboside (stage-specific embryonic antigen-3 glycolipid) Registry number: EC 2.4.1.- Synonym: udpgalactose-globoside beta 1-3 galactosyltransferase, gb4-galactosyltransferase, gb4 synthetase, beta-1,3-galnac-tf (26 Jun 1999) |
| glucosaminylgalactosylglucosylceramide beta-galactosyltransferase | <enzyme> Attaches galactose in a beta 1-3 bond to form the tetrasaccharide-ceramide Registry number: EC 2.4.1.86 Synonym: lc3 galactosyltransferase, udp-galactose-lc3 galactosyltransferase, lactotriosylceramide galactosyltransferase, glcnac beta1-3 gal beta1-4 glc beta1-cer galactosyltransferase, lactatriaosylceramide beta 1-3-galactosyltransferase (26 Jun 1999) |
| glucosylceramide beta-1-4-galactosyltransferase | <enzyme> Catalyses the formation of lactosylceramide from glucosylceramide and udp galactose; also uses dihexosides as acceptor Registry number: EC 2.4.1.- Synonym: udpgalactose ceramide monohexoside galactosyltransferase, glccer galactosyltransferase, galt-2, udpgalactose-glucosylceramide beta-1-4-galactosyltransferase (26 Jun 1999) |
Synonyms : Ganglioside GM1 Synthase, UDP Galactose-Ceramide Galactosyltransferase, UDP Galactose-GM2 Galactosyltransferase, UDP-Galactose-GM2 Ganglioside Beta-1-3-Galactosyltransferase, UDPGal-GM2 Beta1-3-Galactosyltransferase, GM1 Synthase, Ganglioside
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