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ganglioside <biochemistry> A glycosphingolipid that contains one or more residues of N acetyl or other neuraminic acid derivatives.
Gangliosides are found in highest concentration in cells of the nervous system, where they can constitute as much as 5% of the lipid.
(18 Nov 1997)
ganglioside galactosyltransferase <enzyme> Consider also EC 2.4.1.45
Registry number: EC 2.4.1.62
Synonym: udpgalactose-n-acetylgalactosaminyl-(n-acetylneuraminyl)-galactosyl-glucosyl-ceramide galactosyltransferase, udpgalactose-gm2 galactosyltransferase, ganglioside gm1 synthase, udpgalactose-ceramide galactosyltransferase, udp-galactose-gm2 gangliosidebeta-1-3-galactosyltransferase, udpgal-gm2 beta1-3-galactosyltransferase
(26 Jun 1999)
ganglioside lipidosis Any disease characterised, in part, by the abnormal accumulation within the nervous system of specific gangliosides, e.g., GM2 gangliosidosis, Tay-Sachs disease, caused by hexosaminidase A enzyme deficiency with accumulation of GM2 ganglioside
Synonym: gangliosialidosis, ganglioside lipidosis.
(05 Mar 2000)
ganglioside O-acetyltransferase <enzyme> Gd2 ganglioside is an acceptor for the above enzyme in human melanoma cells
Registry number: EC 2.3.1.-
(26 Jun 1999)
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g(m1) ganglioside <chemical> Galactosyl-n-acetylgalactosaminyl-(n-acetylneuraminyl)- galactosyl-glucosylceramide. Ganglioside present in abnormally large amounts in neurons and in elevated levels in liver and kidney due to a deficiency of beta-galactosidase in the genetically determined disease gm1-gangliosidosis.
Chemical name: Ganglioside GM1
(12 Dec 1998)
g(m2) ganglioside <chemical> N-acetylgalactosaminyl-galactosyl-(n-acetylneuraminyl)-glucosyl-ceramide. This is the defective ganglioside manifested in tay-sachs disease and sandhoff disease.
Chemical name: Ganglioside GM2
(12 Dec 1998)
g(m3) ganglioside N-acetylneuraminyl-galactosyl-glucosylceramide. This ganglioside is present in abnormally large amounts in the brain and liver due to a deficient biosynthetic enzyme, g(m3):udp-n-acetylgalactosaminyltransferase. Deficiency of this enzyme prevents the formation of g(m2) ganglioside from g(m3) ganglioside and is the cause of an anabolic sphingolipidosis.
(12 Dec 1998)
GM3 ganglioside sialidase <enzyme> Enzyme deficient in mucolipidosis iv
Registry number: EC 3.2.1.-
Synonym: haematoside neuraminidase, ganglioside sialidase
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 2 ÆäÀÌÁö: 1
  • Ganglioside Galactosyltransferase - »õâ Catalyzes the final step in the galactocerebroside biosynthesis pathway.
    Synonyms : Ganglioside GM1 Synthase, UDP Galactose-Ceramide Galactosyltransferase, UDP Galactose-GM2 Galactosyltransferase, UDP-Galactose-GM2 Ganglioside Beta-1-3-Galactosyltransferase, UDPGal-GM2 Beta1-3-Galactosyltransferase, GM1 Synthase, Ganglioside
  • Gangliosides - »õâ A subclass of ACIDIC GLYCOSPHINGOLIPIDS. They contain one or more sialic acid (N-ACETYLNEURAMINIC ACID) residues. Using the Svennerholm system of abbrevations, gangliosides are designated G for ganglioside, plus subscript M, D, or T for mono-, di-, or trisialo, respectively, the subscript letter being followed by a subscript arabic numeral to indicated sequence of migration in thin-layer chromatograms. (From Oxford Dictionary of Biochemistry and Molecular Biology, 1997)
    Synonyms :
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ganglioside Complex, carbohydrate-rich lipids found in cell membranes, most concentrated at the surface of brain cells.
Ãâó: members.tripod.com/~cripkorner/glossary.html
ganglioside (noun) a particular class of glycosphingolipid present in nerve tissue and the spleen
Ãâó: www.orgsites.com/fl/adjuvantdisease/_pgg9.php3
ganglioside A complex molecule that contains both lipids (fats) and carbohydrates (sugars) and is found in the plasma (outer) membrane of many kinds of cells. Several different types of gangliosides have been identified.
Ãâó: goldbamboo.com/glossary-1g.html
ganglioside sialidase sialidase (def. 2).
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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