| GAL | galactose; galactosyl; glucuronic acid lactone |
|---|---|
| GGTB | glycoprotein 4-beta-galactosyl transferase |
| GT | gait training; galactosyl transferase; gastrostomy; generation time; genetic therapy; gingiva treatm... |
| GalCer | Galactosyl ceramide |
|---|---|
| NGA | Galactosyl-neoglycoalbumin |
| CGalt | UDP-galactose-ceramide galactosyl transferase |
| CGT | UDP-galactose:ceramide galactosyl transferase |
| Gal | galactosyl |
| galactosyl | A compound in which the -OH attached to carbon-1 of galactose is replaced by an organic radical. (05 Mar 2000) |
|---|---|
| galactosyl transferase | <enzyme> Enzyme catalysing the transfer of galactose units from the sugar nucleotide, uridine diphospho galactose UDP galactose) to an acceptor, commonly N acetyl glucosamine in a glycan chain, forming a glycosidic bond involving C1 of galactose. (18 Nov 1997) |
| galactosyl(alpha 1-4)galactosylceramide galactosyl hydrolase | <enzyme> Active in pH 3.0 component of human plasma (pn-a-2); greatly decreased in fabry's disease Registry number: EC 3.2.1.- Synonym: digalactosylceramidase (26 Jun 1999) |
| galactosyl-1-3-N-acetylgalactosaminyl-specific 2,6-sialyltransferase | <enzyme> Genbank x77775 Registry number: EC 2.4.99.- Synonym: galbeta1,3galnac 2,6-sialyltransferase, st6galnac II (26 Jun 1999) |
| galactosylceramidase | <enzyme> An enzyme that hydrolyzes galactose from ceramide monohexosides. Chemical name: D-Galactosyl-N-acylsphingosine galactohydrolase Registry number: EC 3.2.1.46 (12 Dec 1998) |
| galactosylceramide | A sphingolipid that accumulates in individuals with Krabbe's disease. (05 Mar 2000) |
| galactosylceramide lipoidosis | <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia Synonym: Krabbe leukodystrophy (12 Dec 1998) |
| galactosylceramide sulfotransferase | <enzyme> Models for the study of inborn errors of metabolism Registry number: EC 2.8.2.11 Synonym: cerebroside sulfotransferase, galactocerebroside sulfotransferase, glycosphingolipid sulfotransferase, galcst, glycolipid sulfotransferase, galcer-st, galactosylceramide sulphotransferase (26 Jun 1999) |
| galactosylceramides | Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy. (12 Dec 1998) |
| galactosyltransferases | <enzyme> Enzymes that catalyze the transfer of galactose from a nucleoside diphosphate galactose to an acceptor molecule which is frequently another carbohydrate. Registry number: EC 2.4.1.- (12 Dec 1998) |
| galactosylxylosylprotein 3-beta-galactosyltransferase | <enzyme> Catalyses the reaction of udpgalactose and 4-beta-d-(galactosyl-o-beta-d-xylosylprotein to yield udp and 3-beta-d-galactosyl-o-beta-d-xylosylprotein Registry number: EC 2.4.1.134 Synonym: galactosyltransferase II, (26 Jun 1999) |
| beta-1,3-galactosyl-0-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase | <enzyme> Capable of adding a glcnac residue to g1cnacman(3)g1cnac; from mung bean seedlings Registry number: EC 2.4.1.146 Synonym: n-acetylglucosaminyltransferase II, gal3-(glcnac6)galnac-mucin (glcnac--gal)3-glcnactransferase (26 Jun 1999) |
|---|---|
| beta-1,3-galactosyl-O-glycosyl-glycoprotein beta-1,6-acetylglucosaminyl transferase | <enzyme> With EC 2.4.1.148 this is called beta6-glcnac-transferase b Registry number: EC 2.4.1.102 Synonym: gal3-galnac-mucin-6-glcnac transferase, udp-glcnac-gal1-3galnac-r-(glcnac to galnac)-beta1-6glcnac transferase, core 2 glcnac transferase, core 2-n-acetylglucosaminyltransferase, core 2 beta6-gn-t (26 Jun 1999) |
| beta-galactosyl(1-3)N-acetylglucosaminide alpha(2-3)-sialyltransferase | <enzyme> Found in rat liver golgi apparatus Registry number: EC 2.4.99.- Synonym: gal-1-3-glcnac-sialyltransferase (26 Jun 1999) |
| UDP-galactose 4-O-beta-D-galactosyl-D-xylose galactosyltransferase | <enzyme> Involved in chondroitin sulfate synthesis Registry number: EC 2.4.1.- (26 Jun 1999) |
Synonyms : Galactosylceramide Galactosidase, Galactosylceramide beta-Galactosidase, Galactosylcerebroside beta-Galactosidase, Galactosidase, Galactosylceramide, beta-Galactosidase, Galactosylceramide, beta-Galactosidase, Galactosylcerebroside
Synonyms : Ceramides, Galactosyl
Synonyms :
| galactosyl |
a radical of galactose.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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|---|---|
| galactosylceramidase |
[EC 3.2.1.46] an enzyme of the hydrolase class that catalyzes the hydrolytic cleavage of galactose from galactocerebrosides to form ceramides, a reaction occurring in the lysosomal degradation of sphingolipids. Deficiency of the enzyme, an autosomal recessive trait, causes Krabbe's disease. Called also galactocerebroside β-galactosidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| galactosylceramide |
galactocerebroside.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| galactosylceramide β-galactosidase |
galactosylceramidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| galactosylceramide l. |
Krabbe's disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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