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EH enlarged heart; external hyperalimentation; epidermolytic hyperkeratosis; epoxide hydratase; essenti...
FH facial hemihyperplasia; familial hypercholesterolemia; family history; fasting hyperbilirubinemia; f...
PPH past pertinent history; persistent pulmonary hypertension; phosphopyruvate hydratase; postpartum hem...
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FA Fumaric acid
NHase Nitrile Hydratase
EC 4.2.1.17 enoyl-CoA hydratase
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fumaric <chemistry> Pertaining to, or derived from, fumitory (Fumaria officinalis).
<chemistry> Fumaric acid, a widely occurring organic acid, exttracted from fumitory as a white crystallline substance, C2H2(CO2H)2, and produced artificially in many ways, as by the distillation of malic acid; boletic acid. It is found also in the lichen, Iceland moss, and hence was also called lichenic acid.
Source: Websters Dictionary
(01 Mar 1998)
fumaric acid Trans-Butanedioic acid;an unsaturated dicarboxylic acid occurring as an intermediate in the tricarboxylic acid cycle.
Synonym: allomaleic acid.
(05 Mar 2000)
fumaric acidemia Elevated levels of fumarate in blood plasma; due to a decrease in activity of fumarate hydratase.
(05 Mar 2000)
fumaric aminase <enzyme> An enzyme that catalyses the conversion of aspartic acid to ammonia and fumaric acid in plants and some microorganisms.
Chemical name: L-Aspartate ammonia-lyase
Registry number: EC 4.3.1.1
(12 Dec 1998)
fumaric hydrogenase <enzyme> Registry number: EC 1.3.99.1
(12 Dec 1998)
acetylene hydratase <enzyme> A tungsten iron-sulfur protein; catalyses the hydration of acetylene to acetaldehyde
Registry number: EC 4.2.1.-
(26 Jun 1999)
aconitate hydratase <enzyme> An enzyme that catalyses the reversible hydration of cis-aconitate to yield citrate or isocitrate. It is one of the citric acid cycle enzymes.
Chemical name: Citrate(isocitrate) hydro-lyase
Registry number: EC 4.2.1.3
(12 Dec 1998)
benzo(a)pyrene-4,5-oxide hydratase <enzyme> Aspect of epoxide hydrolase, EC 3.3.2.3
Registry number: EC 3.3.2.-
(26 Jun 1999)
gamma-oxalomesaconate hydratase <enzyme> From pseudomonas ochraceae; forms gamma-oxalocitramalate
Registry number: EC 4.2.1.-
Synonym: gom hydratase
(26 Jun 1999)
methylglutaconyl-CoA hydratase <enzyme> Catalyses conversion of 3-hydroxy-3-methylglutaryl-CoA to trans-3-methylglutaconyl-CoA and water
Registry number: EC 4.2.1.18
Synonym: 3-hydroxy-3-methylglutaryl-CoA hydro-lyase, 3-methylglutaconyl-coenzyme a hydratase, 3-methylglutaconyl-CoA hydratase
(26 Jun 1999)
phosphopyruvate hydratase <enzyme> An enzyme of the lyase class that catalyses the dehydration of 2-phosphoglycerate to form phosphoenolpyruvate.
Chemical name: 2-Phospho-D-glycerate hydro-lyase
Registry number: EC 4.2.1.11
(12 Dec 1998)
cyanide hydratase <enzyme> Converts hcn to formamide in the fungus gloeocercospora sorghi
Registry number: EC 4.2.1.66
Synonym: formamide hydro-lyase
(26 Jun 1999)
cyclohexylideneacetyl-CoA hydratase <enzyme> From arthrobacter; forms (1-hydroxycyclohexan-1-yl)acetyl-CoA
Registry number: EC 4.2.1.-
Synonym: ca-CoA-hydratase, cyclohexylideneacetyl-coenzyme a hydratase
(26 Jun 1999)
homoaconitate hydratase <enzyme> Catalyses conversion of 2-hydroxybutane-1,2,4-tricarboxylic acid to but-1-ene-1,2,4-tricarboxylic acid; isolated from aspergillus nidulans.
Registry number: EC 4.2.1.36
Synonym: 2-hydroxybutane-1,2,4-tricarboxylate hydro-lyase, lysf gene product, homoaconitase
(26 Jun 1999)
hydratase Trivial name applied, together with dehydratase, to certain hydro-lyases (EC class 4.2.1) catalyzing hydration-dehydration; e.g., fumarate-malate interconversion by fumarate hydratase.
(05 Mar 2000)
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