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"fibrous dysplasia polyostotic"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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¿µ¹® fibrous dysplasia ÇÑ±Û ¼¶À¯Çü¼ºÀÌ»ó
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  ±¹¼Ò ¹ßÀ°Àå¾Ö·Î »ÀÀÇ ¸ðµç ¼ººÐÀÌ ³ªÅ¸³ª³ª ¼º¼÷ÇÑ ±¸Á¶·Î ºÐÈ­ÇÏÁö´Â ¸øÇϴ º´ÀÌ´Ù. ÀÓ»óÀ¸·Î ÇϳªÀÇ »À È¤Àº ¿©·¯°³ÀÇ »À¸¦ µ¿½Ã¿¡ Ä§¹üÇÒ ¼ö ÀÖ´Ù. ¿©·¯»À À¯ÇüÀº °¥»ö»ö¼Ò Ä§Âø°ú ³»ºÐºñ Àå¾Ö¸¦ µ¿¹ÝÇϸç Á¶¼÷ÇÑ ¼ºÀû ¹ßÀ°À» µ¿¹ÝÇÑ´Ù. À°¾È¼Ò°ßÀ¸·Î °æ°è°¡ ¶Ñ·ÇÇÑ º´ÅͷΠÁ¶Á÷¼Ò°ßÀ¸·Î´Â ¼¶À¯¸ð¼¼Æ÷ÀÇ Áõ½Ä°ú °î¼±»óÀÇ »ÀÀܱâµÕÀ¸·Î ±¸¼ºµÇ¾î Àִµ¥ »ÀÀܱâµÕÀº »À¸ð¼¼Æ÷·Î µ¤¿©ÀÖÁö ¾ÊÀº ¹«Ãþ»À(woven bone)ÀÌ´Ù.
¿µ¹® cervical dysplasia ÇÑ±Û ÀڱøñÇü¼ºÀÌ»ó
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  ÀڱøñÀ̶õ ÀÚ±ÃÀÌ Áú°ú ¿¬°áµÈ ºÎÀ§·Î ÀÚ±ÃÀÇ ÀÔ±¸¿¡ ÇØ´çÇϴ ºÎÀ§ÀÌ´Ù. À̰÷Àº »óÇǷΠµÑ·¯½×¿© ÀÖ´Ù. »óÇǶõ ½ÅüÀÇ ³»ºÎ³ª ¿ÜºÎ¸¦ ½×°í Àִ Á¶Á÷À» À̸£´Â ¸»·Î, ÀÌ »óÇÇÀÇ ¾Æ·¡¿¡´Â ´ë°³ »óÇǸ¦ ÁöÁöÇϰí Àִ Á¶Á÷ÀÌ Á¸ÀçÇÑ´Ù. ±×¸®°í ÀÌ ÁöÁöÁ¶Á÷°ú »óÇÇÀÇ »çÀÌ¿¡´Â ±âÀú¸·À̶ó´Â ¸·ÀÌ À־ »óÇǿ͠ÁöÁöÁ¶Á÷À» ±¸ºÐÇÑ´Ù. ÀڱðæºÎÀÌÇü¼ºÀ̶õ ¿©·¯ °¡Áö Àڱؿ¡ ÀÇÇØ¼­ ¾Ï¼ºº¯È­¸¦ ÇÑ ÀڱûóÇÇÀÇ ¼¼Æ÷°¡ ÀڱûóÇÇÀÇ ÀϺΰ¡ Â÷ÁöÇϰí Àִ °æ¿ì¸¦ À̸£´Â ¸»ÀÌ´Ù. Áï »óÇÇÀÇ ÀϺΰ¡ ¾Ï¼ºº¯È­¸¦ ÇÑ ¼¼Æ÷°¡ ¸Þ¿ì°í Àִ °ÍÀ» À̸¥´Ù. À̰͠ÀÚü°¡ ¾ÏÀº ¾Æ´ÏÁö¸¸ Àü¾Ï¼º º´º¯À̸ç À̰ÍÀÌ °è¼Ó Áø ÇàÀÌ µÇ¾î ÀڱûóÇÇÀÇ ÀüÃþÀ» ¾Ï¼¼Æ÷°¡ Ã¤¿ì°Ô µÇ¸é À̰ÍÀ» »óÇdz»¾ÏÁ¾À̶ó°í ºÎ¸£°í ¸¸¾à ´õ ÁøÇàÀÌ µÇ¾î¼­ ¾Ï¼¼Æ÷°¡ ±âÀú¸·À» ¶Õ°í »óÇǹØÀÇ ÁöÁö Á¶Á÷À» Ä§¹üÇÑ´Ù¸é À̰ÍÀ» Ä§À±¾ÏÀ̶ó°í ºÎ¸¥´Ù.
  
  ÀڱøñÇü¼ºÀÌ»ó
  
  
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous dysplasia polyostotic
    ¿©·¯»À¼¶À¯Çü¼ºÀÌ»ó, ´Ù°ñ¼¶À¯ÀÌÇü¼º
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous dysplasia
    ¼¶À¯Çü¼ºÀÌ»ó
  • fibrous dysplasia of bone
    »À¼¶À¯Çü¼ºÀÌ»ó
  • polyostotic
    ¹µ»À-, ´Ù°ñ-
  • fibrous
    ¼¶À¯-
  • fibrous ankylosis
    ¼¶À¯°üÀý±»À½, ¼¶À¯°üÀý°­Á÷
  • fibrous astrocyte
    ¼¶À¯º°¾Æ±³¼¼Æ÷
  • fibrous attachment
    ¼¶À¯¼ººÎÂø
  • fibrous capsule
    ¼¶À¯ÇǸ·
  • fibrous cartilage
    ¼¶À¯¿¬°ñ
  • fibrous cavernitis
    ¼¶À¯Çظéü¿°
  • fibrous coat
    ¼¶À¯¸·, ¹Ù±ù¸·
  • fibrous contracture
    ¼¶À¯±¸Ãà
  • fibrous histiocytoma
    ¼¶À¯Á¶Á÷±¸Á¾
  • fibrous joint
    ¼¶À¯°üÀý
  • fibrous layer
    ¼¶À¯ÆÇ, ¼¶À¯Ãþ
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous
    ¼¶À¯-
  • fibrous joint
    ¼¶À¯°üÀý
  • dysplasia
    Çü¼ºÀÌ»ó
  • cerebral cortical dysplasia
    ´ë³ú°ÑÁúÇü¼ºÀÌ»ó
  • hip developmental dysplasia
    ¾ûµ¢»ÀÇü¼ºÀÌ»ó
  • moderate dysplasia
    ÁߵÇü¼ºÀÌ»ó
  • spondyloepiphyseal dysplasia
    ôÃßÆÈ´Ù¸®»À³¡Çü¼ºÀÌ»ó, ôÃß»çÁö°ñ´ÜÇü¼ºÀÌ»ó
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • polyostotic fibrous dysplasia
    ¿©·¯»À¼¶À¯Çü¼ºÀÌ»ó, ´Ù°ñ¼¶À¯ÀÌÇü¼º
  • fibrous dysplasia
    ¼¶À¯Çü¼ºÀÌ»ó
  • fibrous attachment
    ¼¶À¯ºÎÂø
  • fibrous capsule
    ¼¶À¯ÇǸ·
  • fibrous cartilage
    ¼¶À¯¿¬°ñ
  • fibrous cavernitis
    ¿Ã±â¼ºÇظéü¿°
  • fibrous coat
    ¹Ù±ù¸·, ¼¶À¯¸·
  • fibrous contracture
    ¼¶À¯±¸Ãà
  • fibrous epulis
    ¼¶À¯ÀÕ¸öÁ¾, ¼¶À¯Ä¡ÀºÁ¾
  • fibrous
    ¼¶À¯-
  • fibrous histiocytoma
    (¢¡dermatofibroma) ÇǺμ¶À¯Á¾
  • fibrous joint
    ¼¶À¯°üÀý
  • fibrous layer
    ¼¶À¯ÆÇ, ¼¶À¯Ãþ
  • fibrous membrane
    ¼¶À¯¸·
  • fibrous myocarditis
    ¼¶À¯½É±Ù¿°
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ).
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ)(ÒýÍéàõ àéë«àõ °ñÀÌÇü¼º(Áõ))
  • polyostotic
    ´Ù°ñ¼º(ÒýÍéàõ), ~ÀÇ.
  • polyostotic
    ´Ù°ñ¼ºÀÇ(ÒýÍéàõ¡­)
  • Left fibrous ring
    ¿Ü¼¶À¯°í¸®
  • annular part of digital fibrous sheath
    ¼¶À¯Áý°í¸®ºÎºÐ
  • generalized fibrous ost(e)itis<³ª> o. fibrosa genera lisata
    ¹ü¹ß¼º ¼¶À¯¼º °ñ¿°(ÛñÛ¡àõàéë«àõÍéæú).
  • histiocytoma,fibrous
    ¼¶À¯¼º
  • histiocytoma,malignant fibrous
    Á¶Á÷±¸Á¾, ¾Ç¼º ¼¶À¯¼º
  • Engelmanns diaphyseal dysplasia
    ¿¨°Ö¸¸ °ñ°£ ÀÌÇü¼ºÁõ.
  • Goldenhars syndrome->oculo-auriculo-vertebral dysplasia
    °ñµçÇÏÁõÈıº
  • Scheibe dysplasia
    »þÀ̺£ÀÌÇü¼º
  • X-linked hypohidrotic ectodermal dysplasia
    ¼º¿°»öü ¿¬°ü ¼ÒÇÑ ¿Ü¹è¿°Çü¼ºÀå¾Ö
  • acetabular dysplasia
    ºñ±¸ ÀÌÇü¼ºÁõ(ºñÏ¿ì¶û¡àõñø), °ü°ñ±¸ ÀÌÇü¼º(Áõ)(ΰÍéÏ¿ì¶û¡à÷ñø), ºñ±¸Çü¼ººÎÀüÁõ(ºñÏ¿ì¶û¡Üôàõñø).
  • anhidrotic ectodermal dysplasia
    ¹«ÇѼº ¿Ü¹è¿± ÀÌÇü¼º.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous dysplasia, polyostotic
    ´Ù°ñ(¼º)¼¶À¯ ÀÌÇü¼ºÁõ
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ).
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ)(ÒýÍéàõ àéë«àõ °ñÀÌÇü¼º(Áõ))
  • polyostotic fiberous dysplasia
  • fibrous dysplasia
    ¼¶À¯¼º ÀÌÇü¼ºÁõ(¡­ì¶û¡à÷ñø)
  • fibrous dysplasia, monostotic
    ´Ü°ñ(¼º)¼¶À¯ ÀÌÇü¼ºÁõ
  • fibrous dysplasia, orbital
    ¾È¿Í¼¶À¯ ÀÌÇü¼ºÁõ
  • monostotic fibrous dysplasia
    ¹æ»ç ´Ü°ñ¼¶À¯¼º ÀÌÇü¼ºÁõ.
  • monostotic fibrous dysplasia
    ´Ü°ñ¼¶À¯¼º ÀÌÇü¼ºÁõ(Û¯ÞÒ Ó¤Íéàéë«àõ ì¶û¡à÷ñø)
  • monostotic fibrous dysplasia
    ´ÜÀϰñ ¼¶À¯ ÀÌÇü¼ºÁõ(Ó¤ìéÍéàéë«ì¶û¡à÷ñø), ¹æ»ç ´Ü°ñ¼¶À¯¼º ÀÌÇü¼ºÁõ.
  • osteitis fibrosa disseminata => fibrous dysplasia
  • fibrous membrane fibrous layer
    ¼¶À¯¸·
  • polyostotic
    ´Ù°ñ¼º(ÒýÍéàõ), ~ÀÇ.
  • polyostotic
    ´Ù°ñ¼ºÀÇ(ÒýÍéàõ¡­)
  • acetabular dysplasia
    ºñ±¸ ÀÌÇü¼ºÁõ(ºñÏ¿ì¶û¡àõñø), °ü°ñ±¸ ÀÌÇü¼º(Áõ)(ΰÍéÏ¿ì¶û¡à÷ñø), ºñ±¸Çü¼ººÎÀüÁõ(ºñÏ¿ì¶û¡Üôàõñø).
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Fibrous membrane [Fibrous layer]
    ¼¶À¯¸·
    [¿¾ ¿ë¾î] ¼¶À¯¸·
  • (Fibrous appendix of liver)
    (°£¼¶À¯¶ì)
    [¿¾ ¿ë¾î] ¼¶À¯ºÎ¼Ó
  • Fibrous cartilage
    (¾Æ±³)¼¶À¯¿¬°ñ
    [¿¾ ¿ë¾î] ¼¶À¯¿¬°ñ
  • Fibrous coat
    ¹Ù±ù¸·
    [¿¾ ¿ë¾î] ¿Ü¸·
  • External layer [Fibrous layer]
    ¹Ù±ùÃþ [¼¶À¯Ãþ]
    [¿¾ ¿ë¾î] ¿ÜÃþ
  • Digital fibrous sheaths of foot
    ¹ß°¡¶ô¼¶À¯Áý
    [¿¾ ¿ë¾î] Á·Áö¼¶À¯ÃÊ
  • Rib of fibrous sheath
    ¼¶À¯°¥ºñ
    [¿¾ ¿ë¾î] ¼¶À¯¸¤
  • Fibrous bone marrow
    ¼¶À¯°ñ¼ö [¼¶À¯»À¼ÓÁú]
    [¿¾ ¿ë¾î] ¼¶À¯¼º°ñ¼ö
  • Fibrous coat
    ¼¶À¯¸·
    [¿¾ ¿ë¾î] ¼¶À¯¸·
  • Fibrous astrocyte
    ¼¶À¯º°¾Æ±³¼¼Æ÷
    [¿¾ ¿ë¾î] ¼¶À¯¼º¼º»ó±³¼¼Æ÷
  • Fibrous pericardium
    ¼¶À¯½ÉÀ帷
    [¿¾ ¿ë¾î] ¼¶À¯¼º½É¸·
  • Fibrous sheath
    ¼¶À¯Áý
    [¿¾ ¿ë¾î] ¼¶À¯ÃÊ
  • Annular part of digital fibrous sheath
    ¼¶À¯Áý°í¸®ºÎºÐ
    [¿¾ ¿ë¾î] ¼¶À¯ÃÊÀ±»óºÎ
  • Annular part of digital fibrous sheath
    ¼¶À¯Áý°í¸®ºÎºÐ
    [¿¾ ¿ë¾î] Á·Áö¼¶À¯ÃÊÀ±»óºÎ
  • Cruciate part of digital fibrous sheath
    ¼¶À¯Áý½ÊÀںκÐ
    [¿¾ ¿ë¾î] ¼¶À¯ÃʽÊÀÚºÎ
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous actin
    ¼¶À¯»ó(àéë«ßÒ) ¾×ƾ
  • fibrous lamina
    ¼¶À¯ÆÇ(àéë«÷ù)
  • fibrous protein
    ¼¶À¯»ó ´Ü¹éÁú (àéë«ßÒÓ±ÛÜòõ)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • fibrous dysplasia, polyostotic
    ´Ù°ñ¼º¼¶À¯¼ºÀÌÇü¼ºÁõ
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º¼¶À¯¼º°ñÀÌÇü¼º(Áõ)
  • fibrous dysplasia
    ¼¶À¯¼º ÀÌÇü¼ºÁõ
  • polyostotic
    ´Ù°ñ¼ºÀÇ
  • dysplasia
    ÀÌÇü¼ºÁõ, Çü¼ºÀå¾Ö
  • epiphyseal dysplasia
    °ñ´ÜÀÌÇü¼ºÁõ
  • multiple epiphyseal dysplasia
    ´Ù¹ß¼º°ñ´ÜÀÌÇü¼ºÁõ
  • progressive diaphyseal dysplasia
    ÁøÇ༺°ñ°£¼ºÀÌÇü¼º(Áõ)
  • septooptic dysplasia
    °Ý¸·¾ÈÀÌÇü¼ºÁõ
  • fibrous
    ¼¶À¯¼ºÀÇ
  • fibrous capsule
    ¼¶À¯ÇǸ·
  • fibrous cartilage
    ¼¶À¯¿¬°ñ, ¼¶À¯¼º¿¬°ñ
  • fibrous histiocytoma
    ¼¶À¯¼ºÁ¶Á÷±¸Á¾
  • fibrous layer
    ¼¶À¯ÆÇ, ¼¶À¯Ãþ
  • fibrous polyp
    ¼¶À¯¼ºÆú¸³
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
PFD polyostotic fibrous dysplasia; pseudoinflammatory fundus disease
HEPOD hereditary expansile polyostotic dysplasia
FD familial dysautonomia; family doctor; fan douche; fatal dose; fetal danger; fibrin derivative; fibro...
FDM fetus of diabetic mother; fibrous dysplasia of the mandible
MFH Malignant Fibrous Histocytoma
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
FD Fibrous dysplasia
MFH malignant fibrous histocytoma
SFT Solitary Fibrous Tumor
FS fibrous sheath
ARVD Arrhythmogenic Right Ventricular Dysplasia
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º ÀÌÇü¼ºÁõ
  • polyostotic fibrous
    ´Ù°ñ¼º ¼¶À¯¼º
  • familial fibrous dysplasia
    °¡Á·¼º ¼¶À¯ ÀÌÇü¼º
  • fibrous dysplasia
    ¼¶À¯¼º ÀÌÇü¼ºÁõ, ¼¶À¯ ÀÌÇü¼ºÁõ, ¼¶À¯¼º ÀÌÇü¼º, ¼¶À¯¼º Çü¼º Àå¾Ö
    °ñ¼ö°¡ ºñÁ¤»óÀûÀ¸·Î ¼¶À¯ Á¶Á÷À¸·Î ´ëÄ¡µÈ °ÍÀ¸·Î¼­ º¸Åë ¾î¸° ½ÃÀý¿¡ ¹ßº´ÇÑ´Ù.
  • monostotic fibrous dysplasia
    ´Ü°ñ ¼¶À¯¼º ÀÌÇü¼ºÁõ
  • anhidrotic ectodermal dysplasia
    ¹«ÇѼº ¿Ü¹è¿± ÀÌÇü¼º, ¹«ÇѼº ¿Ü¹è¿± ÀÌÇü¼ºÁõ
  • cemental dysplasia
    ¹é¾ÇÁú ÀÌÇü¼º
    ¹é¾ÇÁúÀÌ Çü»ó, Å©±â, ±¸¼º¿¡ À־ÀÇ º¯È­¸¦ ¸»ÇÑ´Ù.
  • congenital alveolar dysplasia
    ¼±Ãµ¼º ÆóÆ÷ ÀÌÇü¼º, ¼±Ãµ¼º ÆóÆ÷ ÀÌÇü¼ºÁõ
  • dentinal dysplasia
    »ó¾ÆÁú ÀÌÇü¼º, »ó¾ÆÁú ÀÌÇü¼ºÁõ
    À¯ÀüÀûÀÌ¸ç ¹ý¶ûÁúÀº Á¤»óÀ̰í, ºÒ±ÔÄ¢ÇÑ »ó¾ÆÁúÀ» °¡Áö¸ç Ä¡¼ö Æó¼â. Ä¡±Ù Çü¼ºÀÇ °áÇÔ°ú ¶Ñ·ÇÇÑ ¿øÀÎ ¾øÀÌ ¹ß»ýµÇ´Â Ä¡±Ù´ÜºÎÀÇ º´Àû »óŸ¦ º¸ÀδÙ.
  • dysplasia
    Çü¼º Àå¾Ö, ÀÌÇü¼º, ¹ßÀ°ÀÇ ÀÌ»ó, ÀÌÇü¼ºÁõ, ÀÌÇü¼º
    ¹ßÀ°ÀÇ ÀÌ»ó. º´¸®Çп¡¼­´Â ¼º¼÷ ¼¼Æ÷ÀÇ Å©±â, Çü»ó, ±¸¼º¿¡ À־ÀÇ º¯È­.
  • ectodermal dysplasia
    ¿Ü¹è¿± ÀÌÇü¼ºÁõ
    ¹ß»ýµµÁß ¿ÜºÎ Àڱؿ¡ ÀÇÇØ »ý¼ºµÇ¾î¾ß ÇÒ ¿Ü¹è¿±ÀÌ »ý¼ºµÇÁö ¾Ê°í ´Ù¸¥ Á¶Á÷ÀÌ ¹ß»ýÇÏ´Â °Í.
  • epiphyseal dysplasia
    °ñ´Ü ÀÌÇü¼ºÁõ
  • hereditary ectodermal dysplasia
    À¯Àü¼º ¿Ü¹è¿±¼º ÀÌÇü¼ºÁõ
  • mesoectodermal dysplasia
    Á߿ܹ迱¼º ÀÌÇü¼ºÁõ
    ¿¬°ñ ¿Ü¹è¿±¼º ÀÌÇü¼ºÁõ. ¿¤¸®½º ¹Ý Å©·¹º§Æ® ÁõÈıº.
  • multiple epiphyseal dysplasia
    ´Ù¹ß¼º °ñ´Ü ÀÌÇü¼ºÁõ
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
polyostotic fibrous dysplasia The occurrence of lesions of fibrous dysplasia in multiple bones, commonly on one side of the body; may occur with areas of pigmentation and endocrine dysfunction (McCune-Albright syndrome).
Synonym: multifocal osteitis fibrosa, osteitis fibrosa disseminata.
(05 Mar 2000)
fibrous dysplasia, polyostotic Fibrous dysplasia of bone affecting several or many bones. When associated with melanotic pigmentation of the skin and endocrine disorders, it is known as albright's syndrome.
(12 Dec 1998)
monostotic fibrous dysplasia Fibrous dysplasia of a single bone.
Synonym: localised osteitis fibrosa, osteitis fibrosa circumscripta.
(05 Mar 2000)
fibrous dysplasia A condition of cystic bone growth that results from abnormal bone development. May occur with bone lesions, skin pigmentation and endocrine abnormalities.
See: McCune-Albright syndrome.
Origin: Gr. Plassein = to form
(27 Sep 1997)
fibrous dysplasia, monostotic Fibrous dysplasia of bone involving only one bone.
(12 Dec 1998)
fibrous dysplasia of bone A disease of bone marked by thinning of the cortex and replacement of bone marrow by gritty fibrous tissue containing bony spicules, producing pain, disability, and gradually increasing deformity. Only one bone may be involved (fibrous dysplasia, monostotic) or several (fibrous dysplasia, polyostotic).
(12 Dec 1998)
fibrous dysplasia of jaws <radiology> Hereditary form of polyostotic fibrous dysplasia, involves mandible
(12 Dec 1998)
polyostotic <orthopaedics> Involving more than one bone.
Origin: poly-+ G. Osteon, bone
(05 Mar 2000)
anhidrotic ectodermal dysplasia A hereditary condition (most often x linked) that is characterised by the abnormal development of skin, absence of sweat glands, dry eyes and abnormal development of teeth.
Symptoms include absent teeth, peg teeth, inability to sweat, thin skin and heat intolerance. Mucous membrane involvement may result in a foul-smelling nasal discharge. The inability to sweat leads to the inability to maintain normal body temperature in a warm environment. Some may exhibit fevers and will require artificial cooling.
Inheritance: mostly sex-linked (X chromosome).
Origin: Gr. Plassein = to form
(12 Nov 1997)
anterofacial dysplasia Abnormal growth of the face or cranium in an anteroposterior direction as seen and measured with a cephalogram.
(05 Mar 2000)
arrhythmogenic right ventricular dysplasia A congenital cardiomyopathy in which transmural infiltration of adipose tissue results in weakness and aneurysmal bulging of the infundibulum, apex, and posterior basilar region of the right ventricle and leads to ventricular tachycardia arising in the right ventricle.
(12 Dec 1998)
asphyxiating thoracic dysplasia Hereditary hypoplasia of the thorax, associated with pelvic skeletal abnormality.
Synonym: asphyxiating thoracic chondrodystrophy, Jeune's syndrome, thoracic-pelvic-phalangeal dystrophy.
(05 Mar 2000)
bronchopulmonary dysplasia <embryology, paediatrics> A form of chronic lung disease of uncertain cause sometimes seen in children who have received mechanical respiratory support (with high oxygenation) in the neonatal period. Often associated with those infants who have been treated for hyaline membrane disease.
Origin: Gr. Plassein = to form
(27 Sep 1997)
mammary dysplasia An obsolete term for fibrocystic condition of the breast.
(05 Mar 2000)
mandibulofacial dysplasia A hereditary disorder occurring in two forms: the complete form (franceschetti's syndrome) is characterised by antimongoloid slant of the palpebral fissures, coloboma of the lower lid, micrognathia and hypoplasia of the zygomatic arches, and microtia. It is transmitted as an autosomal trait. The incomplete form (treacher collins syndrome) is characterised by the same anomalies in less pronounced degree. It occurs sporadically, but an autosomal dominant mode of transmission is suspected.
(12 Dec 1998)
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