| 영문 | dwarfism | 한글 | 난쟁이, 왜소증 |
|---|---|---|---|
| 설명 | 신장발육이 부진하여 표준보다 훨씬 키가 작은 경우, 또는 그런 사람을 말한다. 병명도 주유증, 소치증, 유치증, 발육부전, 왜소증 등 여러 가지이다. 같은 인종, 같은 연령의 평균 키에 대한 표준편차의 3~4배가 작을 경우, 성인의 경우 1m미만인 경우로 정의하고 있으나 그 판단기준이 애매하다. 난쟁이 중에서 지능 및 생식기의 발육장애가 없고 연령과 뼈의 X-선 촬영으로 측정되는 골연령이 일치되어 있는 경우를 원발난쟁이(primordial dwarfism)라 한다. 이 경우에는 유전적 소인 외에는 원인이 될 만한 결함을 찾을 수 없다고 한다. 대뇌의 밑부분에 존재하면서 여러 가지 호르몬을 분비하는 뇌하수체의 이상으로 인해서 뼈의 성장에 관여하는 성장호르몬의 분비 저하에 의한 소인증을 하수체난쟁이(pituitary dwarfism)라고 한다. 즉 종양, 외상 등으로 인해서 뇌하수체 부위에 기질적인 변화가 생기거나 원인이 없이 성장 호르몬의 분비 저하가 되는 경우이다. 지능의 발육 정도는 비교적 양호하지만 대개 제2차 성징을 볼 수 없다. 성인이 될 때까지 갑상선 기능이 쇠퇴해서 호르몬 분비량이 적어서 일어나는 갑상샘성 난쟁이가 있다. 어릴 때 갑상샘제거수술을 해도 같은 결과가 된다. 손발의 성장이 정지될 뿐 아니라, 지능-정신의 발육부전을 동반한다. 얼굴은 어린애같지만 피부에 주름이 잡혀 노인같이 보인다. |
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| ABCDES | abnormal alignment, bones-periarticular osteoporosis, cartilage-joint space loss, deformities, margi... |
|---|---|
| SJS | Stevens-Johnson syndrome; stiff joint syndrome; Swyer-James syndrome |
| SMS | senior medical student; serial motor seizures; Shared Medical Systems; Smith-Magenis syndrome; somat... |
| CMD | campomelic dysplasia; camptomelic dwarfism; cartilage matrix deficiency; chief medical director; chi... |
| LTD | Laron-type dwarfism; leukotriene D; long-term disability |
| LTD | Laron type dwarfism |
|---|---|
| SMS | Stiff man syndrome |
| BFNC | Benign Familial Neonatal Convulsions |
| FAD | Familial Alzheimer's disease |
| FALS | Familial ALS |
| stiff | 1. Not easily bent; not flexible or pliant; not limber or flaccid; rigid; firm; as, stiff wood, paper, joints. "[They] rising on stiff pennons, tower The mid aerial sky." (Milton) 2. Not liquid or fluid; thick and tenacious; inspissated; neither soft nor hard; as, the paste is stiff. 3. Firm; strong; violent; difficult to oppose; as, a stiff gale or breeze. 4. Not easily subdued; unyielding; stubborn; obstinate; pertinacious; as, a stiff adversary. "It is a shame to stand stiff in a foolish argument." (Jer. Taylor) "A war ensues: the Cretans own their cause, Stiff to defend their hospitable laws." (Dryden) 5. Not natural and easy; formal; constrained; affected; starched; as, stiff behavior; a stiff style. "The French are open, familiar, and talkative; the Italians stiff, ceremonious, and reserved." (Addison) 6. Harsh; disagreeable; severe; hard to bear. "This is stiff news." 7. Bearing a press of canvas without careening much; as, a stiff vessel; opposed to crank. 8. Very large, strong, or costly; powerful; as, a stiff charge; a stiff price. Stiff neck, a condition of the neck such that the head can not be moved without difficulty and pain. Synonym: Rigid, inflexible, strong, hardly, stubborn, obstinate, pertinacious, harsh, formal, constrained, affected, starched, rigorous. Origin: OE. Stif, AS. Stif; akin to D. Stijf, G. Steif, Dan. Stiv, Sw. Styf, Icel. Stifr, Lith. Stipti to be stiff; cf. L. Stipes a post, trunk of a tree, stipare to press, compress. Cf. Costive, Stifle, Stipulate, Stive to stuff. Source: Websters Dictionary (01 Mar 1998) |
|---|---|
| stiff-hearted | Obstinate; stubborn; contumacious. Origin: Stiff + heart. Source: Websters Dictionary (01 Mar 1998) |
| stiff heart syndrome | <syndrome> Any condition, usually acute, that causes the heart to be restricted in diastole mainly affecting the ventricles and at one time a complication of cardiac surgery. (05 Mar 2000) |
| stiff lamb disease | A muscular dystrophy occurring in young lambs fed on ewe's milk or on feed that is deficient in vitamin E or selenium, or both. See: white muscle disease. (05 Mar 2000) |
| stiff-man syndrome | <syndrome> Rare central nervous system disorder of unknown aetiology characterised by progressive rigidity and painful spasms of the axial and limb musculature. Diagnosis is based on the appropriate clinical signs, continuous motor activity on electromyography, and significant favourable response to diazepam. It has been suggested that the syndrome may result from an imbalance between the gaba-ergic and catecholaminergic pathways that control motor unit activity; the imbalance may be caused by autoantibodies against glutamic acid decarboxylase. (12 Dec 1998) |
| stiff neck | Non-specific term for limited neck mobility, often due to muscle cramps and accompanied by pain. (05 Mar 2000) |
| stiff-tailed | <zoology> Having the quill feathers of the tail somewhat rigid. Source: Websters Dictionary (01 Mar 1998) |
| stiff toe | A condition in which there is stiffness in the first metatarsophalangeal joint; the joint may be the site of a osteoarthritis. Synonym: stiff toe. (05 Mar 2000) |
| achondroplastic dwarfism | See: achondroplasia. (05 Mar 2000) |
| acromelic dwarfism | A form of dwarfism in which shortening is striking in the most distal segment of the limbs; autosomal recessive inheritance. Synonym: acromelic dwarfism. Origin: acro-+ G. Melos, limb, + ia, condition (05 Mar 2000) |
| aortic dwarfism | Underdevelopment of physical stature associated with severe aortic stenosis. (05 Mar 2000) |
| asexual dwarfism | Dwarfism in which adult sexual development is deficient. (05 Mar 2000) |
| ateliotic dwarfism | A state in which the secretion of all anterior pituitary hormones is inadequate or absent; caused by a variety of disorders that result in destruction or loss of function of all or most of the anterior pituitary gland. Rare forms of PHP are inherited as autosomal recessive or as an X-linked recessive. Synonym: ateliotic dwarfism, hypophyseal cachexia, hypophysial cachexia. (05 Mar 2000) |
| camptomelic dwarfism | Dwarfism with shortening of the lower limbs due to anterior bending of the femur and tibia. (05 Mar 2000) |
| panhypopituitary dwarfism | Type I is an autosomal recessive disorder with deficient human growth hormone, ACTH, FSH, etc., having delayed sexual development, hypothyroidism, and adrenal insufficiency; type II is similar but is an X-linked disorder. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|