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"familial benign chronic neutropenia"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
¿µ¹® neutropenia ÇÑ±Û È£Áß¼º¹éÇ÷±¸°¨¼ÒÁõ
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  ¿©·¯ °¡Áö ¿øÀÎÀ¸·Î È£Áß±¸ÀÇ °¨¼Ò¸¦ ÀÏÀ¸Å°´Â º´ÅÂÀÇ ÃÑĪÀ̸ç, Ç÷¾×ÁßÀǠȣÁß±¸°¡ 2,000/mm3 ÀÌÇÏÀÇ »óŸ¦ ¸»ÇÑ´Ù. ¿øÀÎÀ¸·Î ¼±ÃµÀû, Ã¼ÁúÀûÀΠ°Í°ú, ÀÌÂ÷ÀûÀΠ°ÍÀ¸·Î Å©°Ô ³ª´¶´Ù. ¼±ÃµÀû ¶Ç´Â Ã¼ÁúÀûÀΠ°Í¿¡´Â À¯Àü¼ºÈ£Áß±¸°¨¼ÒÁõ, ÀÌÀÚ±â´ÉºÎÁ·À» ¼ö¹ÝÇϴ ȣÁß±¸°¨¼ÒÁõ, ¸¸¼ºÀúÇü¼º¼ºÈ£Áß±¸°¨¼ÒÁõ, ¸¸¼º¹«°ú¸³±¸Áõ, Áֱ⼺ȣÁß±¸°¨¼ÒÁõ µîÀÌ ÀÖ´Ù. ÀÌÂ÷ÀûÀΠ°Í¿¡´Â ¾à¹°, È­Çй°Áú¿¡ ÀÇÇÑ °Í, ¹æ»ç¼±¿¡ ÀÇÇÑ °Í, °¨¿°Áõ, ¸é¿ª¼ºÈ£Áß±¸°¨¼ÒÁõ µîÀÌ ÀÖ´Ù. ±Þ¼º, ¸¸¼ºÀÌ ÀÖÀ¸¸ç, Æ¯È÷ ¸¸¼ºÀǠȣÁß±¸°¨¼ÒÁõ¿¡¼­´Â °¨¿°ÀÌ ¹Ýº¹µÇ¾î¼­ Ä¡·á¿¡ ´ëÇÑ ¹ÝÀÀÀÌ ³ª»Ú´Ù.
¿µ¹® chronic lymphocytic leukemia ÇÑ±Û ¸¸¼º¸²ÇÁ¼º ¹éÇ÷º´
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  ¹éÇ÷º´(leukemia)¶õ ºñÁ¤»óÀûÀΠ¹éÇ÷±¸ ¼¼Æ÷ÀÇ Áõ½Ä¿¡ ÀÇÇØ ÀϾ´Â º´ÀûÀΠ»óŸ¦ ¸»Çϴµ¥, ÈçÈ÷ ¸»ÃÊÇ÷¾×¿¡ ¹ÌºÐÈ­¼¼Æ÷°¡ ³ªÅ¸³ª¸ç, Á¤»óÀûÀΠÀûÇ÷±¸¼¼Æ÷¿Í ¹éÇ÷±¸¼¼Æ÷, Ç÷¼ÒÆÇÀÇ ±Þ°ÝÇÑ °¨¼Ò¸¦ °¡Á®¿Í Á¤»óÀûÀΠ¼¼Æ÷¿¡ ÀÇÇØ ÇàÇØÁö´Â ¿©·¯ ±â´ÉÀÇ °¨¼Ò¸¦ ÁÖÁõ»óÀ¸·Î ÇÏ¿© º´¿ø¿¡ Ã£¾Æ¿À°Ô µÈ´Ù. µû¶ó¼­ ÀûÇ÷±¸¼¼Æ÷ÀÇ °¨¼Ò·Î ÀÎÇÑ ºóÇ÷, ¹éÇ÷±¸¼¼Æ÷ÀÇ °¨¼Ò·Î ÀÎÇÑ ¸¹Àº °¨¿°Áõ¼¼(ÈçÈ÷ °É¸®Áö ¾Ê´Â ¼¼±Õ¿¡ ÀÇÇÑ °¨¿°, Áö³ªÄ¡°Ô ÀæÀº °¨±â, Æó·Å µî), Ç÷¼ÒÆÇ¼¼Æ÷ÀÇ °¨¼Ò·Î ÀÎÇÑ ÃâÇ÷Áõ»óÀÌ ³ªÅ¸³­´Ù. ¶ÇÇÑ ÇǸ¦ »ý»êÇϴ °ñ¼ö Á¶Á÷¿¡¼­´Â ÀÌ·± ºñÁ¤»óÀûÀΠ¼¼Æ÷ÀÇ Áõ½Ä¸¸À» º¼ ¼ö ÀÖÀ¸¸ç, Á¤»óÀûÀΠ¼¼Æ÷ÀÇ Áõ½ÄÀº º¸±â Èûµé´Ù.
  
  ¸¸¼º¸²ÇÁ¼º ¹éÇ÷º´Àº ¼­¾ç¿¡¼­´Â ºñ±³Àû ¹éÇ÷º´ Áß¿¡¼­ ÈçÇÑ ÇüÀÌÁö¸¸ µ¿¾ç±Ç¿¡¼­´Â ¾ÆÁÖ µå¹® ¹éÇ÷º´ÀÇ ÇüÅÂÀÌ´Ù. ´ë°³ 60¼¼ ÀÌ»óÀÇ °í·ÉÃþ¿¡¼­ ¸¹ÀÌ »ý±â°í 30¼¼ ÀÌÇÏ¿¡¼­´Â °ÅÀǠã¾Æº¼ ¼ö°¡ ¾ø´Ù. Ç÷¾×°Ë»ç»ó¿¡¼­ ¸²ÇÁ±¸ÀÇ ¸¹Àº Áõ°¡¸¦ º¼ ¼ö°¡ ÀÖ°í, ´ë½Å¿¡ ´Ù¸¥ Ç÷¾×¼¼Æ÷µéÀº °¨¼Ò¸¦ ³ªÅ¸³½´Ù. ¹éÇ÷º´ Áß ¿¹Èİ¡ ÁÁÀº ÆíÀ̸破밳 Ä¡·á´Â Ç×¾ÏÁ¦¸¦ ÀÌ¿ëÇÑ È­Çпä¹ýÀ» ¸¹ÀÌ »ç¿ëÇϸç, Æò±Õ »ýÁ¸±â°£Àº 4~5³âÀÌ´Ù.
¿µ¹® chronic obstructive pulmonary disease ÇÑ±Û ¸¸¼ºÆó¼âÆóº´
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  ¸¸¼ºÀûÀ¸·Î ±âµµÀÇ Æó¼â¸¦ °¡Á®¿À´Â º´À» À̸£´Â ¸». ´ë°³ ¸¸¼º±â°üÁö¿°, ±â°üÁö Ãµ½Ä, Æó±âÁ¾ÀÇ 3°¡Áö º´À» ¸»ÇÑ´Ù.
  
  ¸¸¼º±â°üÁö¿°À̶õ ±â°üÁöÀÇ ¸¸¼º¿°ÁõÀ» ¸»ÇÑ´Ù. ±â°üÁöÀÇ ¿°ÁõÀ¸·Î ÀÎÇØ¼­ ±â°üÁöÀÇ Á¡¸·¿¡ ºÎÁ¾ÀÌ »ý±â°í À̷ΠÀÎÇØ¼­ ±â°üÁöÀÇ ³»°æÀÌ Á¼¾ÆÁ®¼­ ±âµµÀÇ Æó¼â¸¦ °¡Á®¿Â´Ù. ´ë°³ Èí¿¬°ú ¹ÐÁ¢ÇÑ ¿¬°üÀ» °¡Áö¸ç, È£Èí°ï¶õ, ±âħ, ±×¸®°í °¡·¡(´ë°³ »öÀ̠Ǫ¸£°í Á¡µµ°¡ ³ôÀº °¡·¡)°¡ Áõ»óÀ¸·Î ³ªÅ¸³­´Ù.
  
  Æó±âÁ¾Àº ±â°üÁöÀÇ º®À» ÁöÁöÇϴ Á¶Á÷ÀÇ ÆÄ±«¿¡ ÀÇÇØ¼­ ±â°üÁö°¡ Á¦ ¸ð¾çÀ» °®ÃßÁö ¸øÇÏ°í ¹«³ÊÁö°Ô µÇ¾î ±âµµÀÇ Æó¼â°¡ ÀϾ´Â º´ÀÌ´Ù. Áï ±â°üÁö°¡ °ü ¸ð¾çÀ¸·Î ÆØÆØÇϰԠÆìÁö´Â °ÍÀ» ÁöÁöÇϴ Á¶Á÷ÀÇ ÆÄ±«¿¡ ÀÇÇØ¼­ °ü¸ð¾çÀ¸·Î ÆìÁöÁö ¸øÇØ °á±¹Àº ÆóÆ÷³»¿¡ °ø±â°¡ Â÷°í ÆóÆ÷º®ÀÌ ÆÄ¿­µÇ°í ±â°üÁö°¡ Á¼¾ÆÁö°Ô µÇ´Â º´À» ¸»ÇÑ´Ù.
  
  ±â°üÁöõ½ÄÀ̶õ ¿©·¯ °¡Áö Àڱؿ¡ ´ëÇØ¼­ ±â°üÁö°¡ °ú¹ÎÇÑ ¹ÝÀÀÀ» º¸¿©¼­ »ý±â´Â ±â°üÁöÀÇ °¡¿ªÀûÀΠÆó¼â¸¦ ÀǹÌÇÑ´Ù. Áï Á¤»óÀο¡°Ô¼­´Â ±â°üÁöÀÇ Æó¼â¸¦ º¸ÀÌÁö ¾Ê´Â Àڱؿ¡ ´ëÇØ¼­ ±â°üÁöÀÇ Æó¼â°¡ »ý±â°í ±× ÀÚ±ØÀÌ ¾øÀ» °æ¿ì¿¡´Â ±â°üÁöÀÇ Æó¼â°¡ ¾ø¾îÁö´Â º´À» ¸»ÇÑ´Ù. 
¿µ¹® chronic active hepatitis ÇÑ±Û ¸¸¼ºÈ°µ¿°£¿°
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  BÇü °£¿°À̳ª ºñAÇü£­ºñBÇü °£¿°ÀÇ ¼Ó¹ßÁõÀ¸·Î ³ªÅ¸³ª´Â °£ÀÇ ¸¸¼º¿°ÁõÀÌ´Ù. °°Àº ÇüÅÂÀÇ º´ÀÌ ¼±Ãµ¼º ¶Ç´Â ÈÄõ°¨¸¶±Û·ÎºÒ¸°°áÇÌÁõÀ̳ª ¾î¶² Á¾·ùÀÇ ¾à¹° Åõ¿©¿¡ ¼ö¹ÝÇØ¼­ ³ªÅ¸³¯ ¼öµµ ÀÖ´Ù. Æ¯Â¡ÀûÀ¸·Î ¹®¸ÆºÎ¿¡ ÇüÁú¼¼Æ÷¿Í Å«Æ÷½Ä¼¼Æ÷ÀǠħÀ±, Á¶°¢±«»ç(°£¼Ò¿± ÁÖº¯ºÎ °£¼¼Æ÷ÀÇ ÆÄ±«) ¹× ¼¶À¯Áõ µîÀÇ Á¶Á÷¼Ò°ßÀ» ³ªÅ¸³½´Ù. º´ÀÇ °æ°ú´Â ¸Å¿ì ´Ù¾çÇϸç Àå±â°£ÀÇ ¹«Áõ»ó±â¸¦ º¸ÀÏ ¼öµµ ÀÖ°í ±× »çÀÌ »çÀÌ¿¡ È²´Þ, Àü½Å¼è¾à, ½Ä¿åºÎÁø ¹× ¹ß¿­ µîÀÇ Áõ»óÀÌ ³ªÅ¸³ª´Â ¼ö°¡ ÀÖÀ¸¸ç, ¶Ç ¹«¿ù°æÁõ, °üÀý¿°, ÇǺιßÁø, Ç÷°ü¿°, °©»ó»ù¿°, ÄáÆÏ»ç±¸Ã¼¿°, ±Ë¾ç¼º´ëÀå¿°, ½¦±×·»ÁõÈıº µî °£ ÀÌ¿ÜÀÇ Áõ»óÀÌ ³ªÅ¸³ª´Â ¼öµµ ÀÖ°í, °£°æÈ­Áõ°ú °£±â´É»ó½Ç·Î ÁøÇàµÇ´Â ¼öµµ ÀÖ´Ù. ÀÚ°¡¸é¿ª¸ÞÄ¿´ÏÁòÀÌ °ü¿©µÇ´Â °ÍÀ¸·Î ÃßÃøµÇ°í ÀÖ´Ù.
¿µ¹® benign ÇÑ±Û ¾ç¼º
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  Ä¡À¯°¡ Àß µÇ´Â, Á¾¾çÀÇ °æ¿ì¿¡¼­´Â ´Ù¸¥ Á¶Á÷À¸·Î ÆÛÁöÁö ¾Ê°í ±×ºÎºÐ¿¡¼­ ¸Ó¹°·¯ Àִ Á¾¾çÀ» ¸»ÇÑ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • alloimmune neutropenia
    µ¿Á¾¸é¿ªÁß¼º±¸°¨¼Ò(Áõ)
  • cyclic neutropenia
    ÁÖ±âÁß¼º±¸°¨¼Ò(Áõ)
  • neutropenia
    Áß¼º±¸°¨¼Ò(Áõ)
  • benign
    ¾ç¼º-
  • benign cyst
    1. ¾ç¼º³¶, ¾ç¼º¹°È¤ 2. ¾ç¼º³¶Á¾
  • benign juvenile melanoma
    ¾ç¼º¼Ò¾ÆÈæ»öÁ¾
  • benign lichenoid keratosis
    ¾ç¼ºÅ¼±°¢È­Áõ
  • benign lymphoid hyperplasia
    ¾ç¼º¸²ÇÁ°ú´ÙÇü¼º
  • benign masseteric hypertrophy
    ¾ç¼º±ú¹°±Ùºñ´ë, ¾ç¼º±³±Ùºñ´ë
  • benign migratory glossitis
    ¾ç¼ºÀÌÁÖÇô¿°, ¾ç¼ºÀÌÁÖ¼³¿°
  • benign neoplasm
    ¾ç¼ºÁ¾¾ç
  • benign papular acantholytic dermatosis
    ¾ç¼º±¸Áø°¡½Ã¼¼Æ÷ÇØ¸®ÇǺκ´
  • benign prostatic hypertrophy
    ¾ç¼ºÀü¸³»ùºñ´ë, ¾ç¼ºÀü¸³¼±ºñ´ë
  • benign tumor
    ¾ç¼ºÁ¾¾ç
  • hereditary benign intraepithelial dyskeratosis
    À¯Àü¾ç¼º»óÇdz»ÀÌ»ó°¢È­Áõ
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 10 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • neutropenia
    È£Áß¼º±¸°¨¼Ò, È£Áß±¸°¨¼Ò
  • familial adenomatous polyposis
    °¡Á·¼ºÅ«Ã¢ÀÚÆú¸³Áõ, °¡Á·¼º´ëÀåÆú¸³Áõ
  • benign cyst
    1.¾ç¼º³¶, ¾ç¼º¹°È¤, 2.¾ç¼º³¶Á¾
  • benign tumor
    ¾ç¼ºÁ¾¾ç
  • benign cystic teratoma
    ¾ç¼º³¶±âÇüÁ¾
  • anemia of chronic disease
    ¸¸¼ºº´ºóÇ÷
  • chronic
    ¸¸¼º-
  • chronic renal failure
    ¸¸¼ºÄáÆÏ±â´É»ó½Ç, ¸¸¼º½ÅºÎÀü(Áõ)
  • chronic atrophic gastritis
    ¸¸¼ºÀ§ÃàÀ§¿°
  • chronic relapsing pancreatitis
    ¸¸¼ºÀç¹ßÀÌÀÚ¿°, ¸¸¼ºÀç¹ßÃéÀå¿°
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • alloimmune neutropenia
    µ¿Á¾¸é¿ªÈ£Áß¼º¹éÇ÷±¸°¨¼ÒÁõ
  • cyclic neutropenia
    ÁÖ±âÈ£Áß¼º¹éÇ÷±¸°¨¼ÒÁõ
  • neutropenia
    È£Áß¼º¹éÇ÷±¸°¨¼ÒÁõ
  • benign
    ¾ç¼º-
  • benign tumor
    ¾ç¼ºÁ¾¾ç
  • benign cystic teratoma
    ¾ç¼º³¶±âÇüÁ¾
  • benign juvenile melanoma
    ¾ç¼º¿¬¼ÒÈæ»öÁ¾
  • benign lichenoid keratosis
    ¾ç¼ºÅ¼±¾ç°¢È­Áõ
  • benign lymphoid hyperplasia
    ¾ç¼º¸²ÇÁ°ú´ÙÇü¼º
  • benign masseteric hypertrophy
    ¾ç¼º±ú¹°±Ùºñ´ë
  • benign migratory glossitis
    ¾ç¼ºÀÌÁÖÇô¿°
  • benign papular acantholytic dermatosis
    ¾ç¼º±¸Áø°¡½Ã¼¼Æ÷ÇØ¸®ÇǺκ´
  • benign prostatic hypertrophy
    ¾ç¼ºÀü¸³»ùºñ´ë
  • hereditary benign intraepithelial dyskeratosis
    À¯Àü¾ç¼º»óÇdz»ÀÌ»ó°¢È­Áõ
  • chronic
    ¸¸¼º-
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Hailey-Hailey disease = familial benign chronic pemphigus
    ÇìÀϸ®-ÇìÀϸ®º´
  • immune neutropenia
    ¸é¿ªÈ£Áß±¸°¨¼ÒÁõ.
  • hereditary benign intraepithelial dyskeratosis
    À¯Àü¼º ¾ç¼º »óÇdz» ÀÌ»ó°¢È­Áõ
  • hypertension,benign nephrosclerosis
    ¾ç¼º ½Å°æÈ­Áõ
  • COPD=> chronic obstructive pulmonary disease
    ¸¸¼ºÆó»ö(¼â)¼º ÆóÁúȯ(Ø·àõøÍßáàõøËòðü´)
  • Chronic fatigue syndrome
    ¸¸¼ºÇÇ·Î ÁõÈıº
  • hepatitis,chronic active
    ¸¸¼ºÈ°µ¿¼º(Ø·àõüÀÔÑàõ)
  • hepatitis,chronic persistent
    ¸¸¼ºÁö¼Ó¼º(Ø·àõò¥áÙàõ)
  • pharyngitis, chronic
    ¸¸¼ºÀεο°
  • pharyngitis, chronic hypertrophic
    ¸¸¼ººñÈÄ(¼º) Àεο°
  • pharyngitis, chronic lateral
    ¸¸¼º¿ÜÃø(¼º) Àεο°
  • Familial hypercholesterolemia
    °¡Á·¼º(Ê«ðéàõ) °í(ÍÔ)ÄÝ·¹½ºÅ×·ÑÇ÷Áõ(úìñø)
  • amaurotic familial idiocy =Tay-Sachs disease
    °¡Á·¼ºÈæ¾Ï½Ã¹éÄ¡(Ê«ðéàõýÙÒ®î¡ÛÜöÁ).
  • amaurotic familial idiocy =Tay-Sachs disease
    °¡Á·¼º Èæ³»Àå ¹éÄ¡(Ê«ðéàõýÙÒ®î¡ÛÜöÁ).
  • hearing loss, familial pregressive
    °¡Á· ÁøÇà(¼º) ³­Ã»
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • familial benign chronic pemphigus
    °¡Á·¼º ¾ç¼º¸¸¼º õÆ÷â(¡­åÐàõØ·àõô¸øÞóê)
  • familial neutropenia
    °¡Á·¼º È£Áß±¸°¨¼ÒÁõ.
  • benign familial pemphigus
    ¾ç¼º °¡Á·¼º(åÐàõ Ê«ðéàõ) õÆ÷â(ô¸øÞóê)
  • chronic familial jaundice
    ¸¸¼º°¡Á·¼º Ȳ´Þ(¡­Ê«ðéàõüÜÓ¸).
  • autoimmune neutropenia =AIN
    ÀÚ°¡¸é¿ª¼ºÈ£Áß±¸ °¨¼ÒÁõ
  • cyclic neutropenia
    Áֱ⼺ È£Áß±¸°¨¼ÒÁõ(¡­û¿ñéϹÊõá´ñø).
  • cyclic neutropenia
    Áֱ⼺ È£Áß±¸°¨¼ÒÁõ(?̴̡˴˧ËÛÌ¡).
  • cyslic neutropenia
  • immune neutropenia
    ¸é¿ªÈ£Áß±¸°¨¼ÒÁõ.
  • isoimmune neonatal neutropenia
    ½Å»ý¾Æµ¿Á¾¸é¿ª¼º È£Áß±¸°¨¼Ò(Áõ).
  • malignant neutropenia
    ¾Ç¼ºÈ£Áß±¸°¨¼ÒÁõ(¡­û¿ñéϹÊõá´ñø).
  • malignant neutropenia
    ¾Ç¼ºÈ£Áß±¸°¨¼ÒÁõ(?̴̡˴˧ËÛÌ¡).
  • neutropenia
    È£Áß±¸°¨¼Ò(Áõ)(̴̡˴˧ËÛÌ¡).
  • neutropenia
    È£Áß±¸°¨¼ÒÁõ
  • neutropenia
    È£Áß±¸ °¨¼ÒÁõ(û¿ñéϹ Êõá´ñø)
´ëÇѱâ»ýÃæÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • chronic malaria
    ¸¸¼º¸»¶ó¸®¾Æ
  • familial aggregation
    °¡Á·ÁýÀû¼º
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • chronic toxicity test
    ¸¸¼º µ¶¼º½ÃÇè(Ø·àõÔ¸àõãËúÐ)
  • familial high-density lipoprotein deficiency °¡Á·¼º °í¹Ðµµ ÁöÁú´Ü¹éÁú °áÇÌ (Ê«ðéàõÍÔÚËÓøò·òõ
    Ó±ÛÜòõÌÀù¹)
  • familial hypercholesterolemia
    °¡Á·¼º(Ê«ðéàõ) °ú(Φ)ÄÝ·¹½ºÅ×·ÑÇ÷Áõ(úìñø)
  • familial lysosomal lipase deficiency
    °¡Á·¼º(Ê«ðéàõ) ¶óÀÌ¼Ò¼Ø ¶óÀÌÆäÀ̽º °áÇÌ(ÌÀù¹)
  • familial methemoglobinemia
    °¡Á·¼º(Ê«ðéàõ) ¸ÞÅ׸ð±Û·ÎºóÇ÷Áõ(úìñø)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 6 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • chronic
    ¸¸¼ºÀÇ
  • familial
    °¡Á·¼ºÀÇ
  • familial polyposis
    °¡Á·¼ºÆú¸³Áõ
  • benign
    ¾ç¼º
  • benign prostatic hypertrophy
    ¾ç¼ºÀü¸³¼±ºñ´ë(Áõ)
  • benign tumor
    ¾ç¼ºÁ¾¾ç
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
FHH Familial Hypocalciuric Hypercalcemia
  = Familial Benign Hypercalcemia
FBCP familial benign chronic pemphigus
INP idiopathic neutropenia
ONMRS onychotrichodysplasia-neutropenia-mental retardation syndrome
CP candle power; capillary pressure; cardiac pacing; cardiac performance; cardiopulmonary; caudate puta...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
BFNC Benign Familial Neonatal Convulsions
FBH Familial benign hypercalcaemia
AIN Autoimmune neutropenia
CN Cyclic neutropenia
FN Febrile neutropenia
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  • familial benign chronic pemphigus
    °¡Á·¼º ¾ç¼º ¸¸¼º õÆ÷â
  • familial neutropenia
    °¡Á·¼º È£Áß±¸ °¨¼ÒÁõ
  • benign familial pemphigus
    ¾ç¼º °¡Á·¼º õÆ÷â
    µå¹°°Ô ¹ß»ýÇÏ´Â, À¯Àü¼ºÀ̸ç Áö¼ÓÀûÀ¸·Î Àç¹ßÀ» ¹Ýº¹ÇÏ´Â ¼ÒÆ÷¼º ¹× ÀÛÀº ¼öÆ÷¼º ÇǺο°À¸·Î, ¾×¿Í, ¼­ÇýºÎ ¹× ¸ñ ºÎÀ§¸¦ °¡Àå Àß Ä§¹üÇÏÁö¸¸, ¶§·Î´Â ±¤¹üÇÑ ºÎÀ§¸¦ ħ¹üÇÑ´Ù. º´º¯Àº ´Ù¹ß¼ºÀ̸ç, ¼öÁÖÀÏ ³»Áö ¼ö°³¿ù ÈÄ¿¡ ¼èÅðÇÑ´Ù. ÀÌ ÁúȯÀº »ó¿°»öü ¿ì¼º À¯ÀüÀ» ÇÑ´Ù.
  • cyclic neutropenia
    Áֱ⼺ È£Áß±¸ °¨¼ÒÁõ
    °ñ¼öÀÇ ¼º¼÷ Á¤Áö·Î ÀÎÇÑ Áúº´ÀÌ´Ù. Áõ»óÀÌ ¹«°ú¸³±¸Áõ
  • idiopathic cyclic neutropenia
    Ư¹ß¼º Áֱ⼺ È£Áß±¸ °¨¼ÒÁõ
    ¸¸¼ºÇüÀÇ È£Áß±¸ °¨¼ÒÁõÀ¸·Î¼­, ÁÖ±âÀûÀ¸·Î ÀϾ´Â Àç¹ßÀ» Ư¡À¸·Î Çϸç, º´°¨, ¹ß¿­, ±¸³»¿° ¹× °¢Á¾ÀÇ °¨¿°À» µ¿¹ÝÇÑ´Ù.
  • neutropenia
    È£Áß±¸ °¨¼ÒÁõ
    Ç÷Áß¿¡¼­ È£Áß±¸°¡ Ư¡ÀûÀ¸·Î °¨¼ÒÇÏ´Â ¹éÇ÷±¸ °¨¼ÒÁõ.
  • amaurotic familial idiocy
    °¡Á·¼º Èæ³»Àå ¹éÄ¡
    µ¿ÀǾî=Tay-Sach's disease.
  • asymptomatric familial hyperbilirubinemia
    ¹«ÁõÈÄ °¡Á·¼º °úºô¸®·çºóÇ÷Áõ
  • familial adenomatous polyposis
    °¡Á·¼º ¼±Á¾¼º ¿ëÁ¾Áõ
  • familial amyloid polyneuropathy
    °¡Á·¼º ¾Æ¹Ð·ÎÀÌµå ´Ù¹ß ½Å°æº´Áõ
  • familial cold urticaria
    °¡Á·¼º Çѳà µÎµå·¯±â
  • familial cutaneous collagenosis
    °¡Á·¼º ÇǺΠ±³¿øÁõ
  • familial dysbetalipoproteinemia
    °¡Á·¼º ÀÌ»ó º£Å¸ ¸®Æ÷ ÇÁ·ÎÅ×ÀÎ Ç÷Áõ
  • familial fibrous dysplasia
    °¡Á·¼º ¼¶À¯ ÀÌÇü¼º
  • familial genuine malfomation of root
    °¡Á·¼º ¼±Ãµ¼º Ä¡±Ù ±âÇü
    µ¿ÀǾî=dentinal dys
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
benign familial chronic pemphigus Recurrent eruption of vesicles and bullae that become scaling and crusted lesions with vesicular borders, predominantly of the neck, groin, and axillary regions; autosomal dominant inheritance, presenting in late adolescence or early adult life.
Synonym: Hailey-Hailey disease.
(05 Mar 2000)
benign familial chorea A rare, nonprogressive movement disorder characterised by chorea and athetosis appearing in early childhood, most commonly manifested as gait ataxia and upper limb coordination. Intellect is unaffected. Probably autosomal-dominance inheritance with incomplete penetrance.
(05 Mar 2000)
benign familial icterus Mild jaundice due to increased amounts of unconjugated bilirubin in the plasma without evidence of liver damage, biliary obstruction, or haemolysis; thought to be due to an inborn error of metabolism in which the excretion of bilirubin by the liver is defective, ascribed to decreased conjugation of bilirubin as a glucuronide or impaired uptake of hepatic bilirubin.
Synonym: benign familial icterus, constitutional hepatic dysfunction, Gilbert's disease, Gilbert's syndrome, Hebra's disease.
(05 Mar 2000)
pemphigus, benign familial Rare hereditary disease characterised by recurrent eruptions of vesicles and bullae mainly on the neck, axillae, and groin. It exhibits autosomal dominant inheritance and is unrelated to pemphigus vulgaris though it closely resembles that disease.
(12 Dec 1998)
periodic neutropenia Neutropenia recurring at regular intervals (14 to 45 days), in association with various types of infectious diseases, e.g., stomatitis, cutaneous ulcers, furuncles, arthritis, and others.
Synonym: cyclic neutropenia.
(05 Mar 2000)
cyclic neutropenia Neutropenia recurring at regular intervals (14 to 45 days), in association with various types of infectious diseases, e.g., stomatitis, cutaneous ulcers, furuncles, arthritis, and others.
Synonym: cyclic neutropenia.
(05 Mar 2000)
neutropenia <haematology> Leucopenia in which the decrease in white blood cells is chiefly in neutrophils.
(18 Nov 1997)
chronic familial icterus <haematology> A hereditary disorder that leads to a chronic haemolytic anaemia due to an abnormality in the red blood cell membrane.
This disorder is caused by a defective gene. Red cells are resistant to stress and rupture easily. Infants may appear jaundiced and pale. Fatigue, weakness and shortness of breath are other symptoms that may be seen in older patients. The spleen may also be enlarged.
Treatment includes splenectomy (removal of the spleen). After this is accomplished the life-span of the red blood cells returns to normal.
(27 Sep 1997)
chronic familial jaundice <haematology> A hereditary disorder that leads to a chronic haemolytic anaemia due to an abnormality in the red blood cell membrane.
This disorder is caused by a defective gene. Red cells are resistant to stress and rupture easily. Infants may appear jaundiced and pale. Fatigue, weakness and shortness of breath are other symptoms that may be seen in older patients. The spleen may also be enlarged.
Treatment includes splenectomy (removal of the spleen). After this is accomplished the life-span of the red blood cells returns to normal.
(27 Sep 1997)
chronic familial polyneuritis Inflammation of nerves related to infiltration by amyloid.
(05 Mar 2000)
benign <oncology> Something that does not metastasise and treatment or removal is curative.
Compare: malignant.
Origin: L. Benignus
(11 Jan 1998)
benign albuminuria A collective term for types that are not the result of pathologic changes in the kidneys.
Synonym: essential albuminuria.
(05 Mar 2000)
benign bone aneurysm <radiology> ABC, 10 - 30 yrs, 75% before skeletal maturity, sites: long bones; also, flat bones Findings: metaphyseal if unfused, metaepiphyseal after fusion, lytic, expansile, thin, continuous rim, thin internal bony strands
(12 Dec 1998)
benign cementoblastoma <tumour> A benign odontogenic tumour of functional cementoblasts; it appears as a mixed radiolucent-radiopaque lesion attached to a tooth root and may cause expansion of the bone cortex or be associated with pain.
Synonym: benign cementoblastoma, true cementoma.
(05 Mar 2000)
benign childhood epilepsy with centrotemporal spikes A specific epilepsy syndrome beginning in childhood and remitting in adolescence, characterised by nocturnal simple partial motor seizures or generalised tonic-clonic seizures. EEG shows centrotemporal spikes that are activated by sleep and an otherwise normal EEG background.
(05 Mar 2000)
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